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Amyloid

IF
论文数67
被引数
期刊论文 67
发表时间
Exploring light chain cardiotoxicity in AL amyloidosis: impact on hiPSC-derived cardiomyocyte activity探索AL淀粉样变性中的轻链心肌毒性:对hiPSC衍生心肌细胞活性的影响
delete2026-06-19
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deleteOAAI
deleteSerena Calamaio; Anthony Frosio; Dario Melgari; Luca Broggini; Federica Sonzini; Rachele Prevostini; Davide Pignatelli; Luigi Anastasia; Carlo Pappone; Alice Nevone; Giovanni Palladini; Mario Nuvolone; Stefano Ricagno; Ilaria Rivolta
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Long-term efficacy and safety of vutrisiran in hereditary transthyretin amyloidosis with polyneuropathy: final analysis of the HELIOS-A randomized treatment extension在伴有周围神经病的遗传性甲状腺素转运蛋白淀粉样变性中vutrisiran的长期疗效与安全性:HELIOS-A随机治疗扩展的最终分析
delete2026-06-15
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deleteOAAI
deleteCécile Cauquil; David Adams; Julian Gillmore; Alejandra Gonzalez-Duarte; Michelle Mezei; Laura Obici; Yoshiki Sekijima; Weizhi Zhao; Katherine Boyle; Prajakta Badri; Marianne Sweetser; Colleen Moffitt; Márcia Waddington-Cruz
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RNA-based full length immunoglobulin light chain sequencing reveals lambda constant domain mutations with potential implications for thermodynamic stability in light chain amyloidosis基于RNA的全长免疫球蛋白轻链测序揭示在轻链淀粉样变性中λ恒定区突变对热力学稳定性的潜在影响
delete2026-06-04
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deleteOAAI
deleteEyad Naser; Sara Oubari; Josefine Jakob; Björn Häupl; Bettina Budeus; Bernd Walkenfort; Melanie Nowakowski; Gabriele Hessler; Claudine Kühn; Mike Hasenberg; Thomas Oellerich; Hans Christian Reinhardt; Alexander Carpinteiro
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Efficacy of diflunisal for hereditary transthyretin amyloidosis: the Swedish real-world experience二氟尼柳治疗遗传性甲状腺素转运蛋白淀粉样变性:瑞典真实世界经验
delete2026-06-03
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deleteOAAI
deleteJohn L. Berk; Kevin J. Carroll; Jorge Mejia Baranda; Björn Pilebro; Kristin Samuelsson; Per Eldhagen; Jonas Wixner
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Proline-rich, polybasic peptides are a structurally distinct class of amyloid-reactive peptides富含脯氨酸、多碱性肽是一类结构独特的淀粉样蛋白反应性肽
delete2026-05-25
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PREAI
deleteTrevor J. Hancock; Manasi Balachandran; Angela Williams; James Foster; Anna Sparks; Joseph Jackson; Nic Angell; Ashlyn Wilson; Sallie Macy; Craig Wooliver; Jonathan Wall
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Artificial intelligence-enhanced electrocardiogram findings before and after heart transplantation in cardiac amyloidosis人工智能增强的心脏移植前后心房粘液瘤的心电图表现
delete2026-05-18
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PREAI
deleteKamal Awad; Juan M. Farina; Jose N. Nativi Nicolau; Melissa A. Lyle; Andrew N. Rosenbaum; Barry A. Boilson; Omar F. Abou Ezzeddine; Francisco Lopez-Jimenez; Angela Dispenzieri; Martha Grogan; D. Eric Steidley; Reza Arsanjani; Julie L. Rosenthal
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The prognostic value of red blood cell distribution width in AL amyloidosisAL淀粉样变性中红细胞分布宽度的预后价值
delete2026-05-16
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PREAI
deleteDespina Fotiou; Erasmia Boutakoglou; Konstantinos Giannakas; Foteini Theodorakakou; Eirini Solia; Magdalini Migkou; Panagiotis Malandrakis; Ioannis Ntanasis-Stathopoulos; Vasiliki Spiliopoulou; Nikolaos Kanellias; Evangelos Eleutherakis-Papaiakovou; Maria Gavriatopoulou; Evangelos Terpos; Efstathios Kastritis; Meletios A. Dimopoulos
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Evaluation of the yield index of genetic counselling for first-degree relatives of patients with hereditary transthyretin cardiac amyloidosis对遗传性甲状腺素转运蛋白心脏淀粉样变性患者一级亲属遗传咨询收益指数的评估
delete2026-05-15
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PREAI
deleteBérénice Hébrard; Francois Sauer; Julie Pompougnac; Ariane Lunati-Rozie; Silvia Oghina; Arnault Galat; Amira Zaroui; Mounira Kharoubi; Marina Konyukh; Pascale Fanen; Sophie Mallet; Benoit Funalot; Thibaud Damy
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Left atrial strain identifies early cardiac involvement in variant transthyretin amyloidosis左心房应变可识别变异型转甲状腺素蛋白淀粉样变性早期的心脏受累
delete2026-05-07
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PREAI
deleteMatteo Serenelli; Elisa Gardini; Stefania Marazia; Alessandro Barbarossa; Alberto Cipriani; Anna Cantone; Beatrice Dal Passo; Federico Sanguettoli; Rita Pavasini; Matteo Arzenton; Gianluca Campo; Andrea Zaccaro; Emiliano Rossi; Gioele Fabbri; Enrico Monti; Carmine Pizzi; Erika Pedio; Federico Guerra; Giulio Sinigiani; Alberto Aimo; Michele Emdin; Francesco Cappelli; Federica Colio; Simone Longhi
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Accelerated apolipoprotein A-II senile amyloidosis in a plasminogen activator inhibitor-1 knock-out modelplasminogen activator inhibitor-1基因敲除模型中加速的载脂蛋白A-II老年性淀粉样变性
delete2026-04-27
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PREAI
deleteGilles R. Codo; Pauline Duchatelet; Gemma Martinez-Rivas; Alessio Lampis; Karolina Weronika Świderska; Emilie Pinault; Camille Cohen; Magali Colombat; Sebastien Bender; Christophe Sirac
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Transthyretin stabilizer therapy increases naturally-occurring antibodies in ATTR cardiomyopathy转甲状腺素蛋白稳定剂治疗可增加ATTR心肌病中自然发生的抗体
delete2026-04-06
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PREAI
deleteStephan Settelmeier; Daniel Agranovski; Maximilian Steinhardt; Sarah Waydhas; Ian Gering; Vladimir Cejka; Caroline Morbach; Stefan Störk; Dieter Willbold; Ralf Küppers; Julia Vogel; Lars Michel; Alexander Carpinteiro; H. Christian Reinhardt; Richard Dodel; Tienush Rassaf; Alexander J. Ross; Ulrike B. Hendgen-Cotta
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Incidence of second primary malignancies in patients with AL amyloidosis and the impact of disease stage and therapiesAL型淀粉样变性患者中第二原发恶性肿瘤的发生率及疾病分期和疗法的影响
delete2026-04-01
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PREAI
deleteEfstathios Kastritis; Vassiliki Spiliopoulou; Foteini Theodorakakou; Magdalini Migkou; Panagiotis Malandrakis; Evangelos Terpos; Maria Gavriatopoulou; Meletios Athanasios Dimopoulos
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Development and validation of the modified-comprehensive Kumamoto Score: a multi-organ assessment tool for hereditary transthyretin amyloidosis改良综合熊本评分的开发与验证:一种用于遗传性甲状腺素转运蛋白淀粉样变性的多器官评估工具
delete2026-03-31
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PREAI
deleteShiori Yamakawa; Toshiya Nomura; Yohei Misumi; Tomoaki Taguchi; Keiichi Nakahara; Masayoshi Tasaki; Naoto Kuyama; Hiroki Usuku; Yasuhiro Izumiya; Yuji Takihara; Emre Aldinc; Konen Obayashi; Toshihiro Inoue; Kenichi Tsujita; Yukio Ando; Mitsuharu Ueda
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Serum peripherin as a disease biomarker in hereditary transthyretin amyloidosis: a multicenter cohort study血清周蛋白作为遗传性甲状腺素转运蛋白淀粉样变性疾病的生物标志物:一项多中心队列研究
delete2026-03-16
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PREAI
deleteDomenico Plantone; Delia Righi; Angela Romano; Luca Leonardi; Valeria Guglielmino; Francesca Forcina; Marco Ceccanti; Maurizio Inghilleri; Fiore Manganelli; Stefano Tozza; Maria Ausilia Sciarrone; Francesca Vitali; Andrea Sabino; Carlo Manco; Angela Stufano; Maria Laura Stromillo; Nicola De Stefano; Paolo Calabresi; Guido Primiano; Marco Luigetti
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Clinical impact of lilac-colored aggregates on may-Grünwald-Giemsa-stained bone marrow smears in patients with amyloid light-chain amyloidosis在AL型淀粉样变性患者中,丁香色聚集物对May-Grünwald-Giemsa染色骨髓涂片的临床影响
delete2026-03-09
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PREAI
deleteAyaka Kodama; Ritsuko Nakagoshi; Ryuto Oshita; Suzuho Onagi; Satoshi Fujimura; Yuka Takezawa; Nagaaki Katoh; Yoshiki Sekijima; Masahide Yazaki; Yumiko Higuchi
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Systemic fibrinogen Aα-chain amyloidosis in Manchester Terrier dogs曼彻斯特梗犬系统性纤维蛋白原Aα链淀粉样变性
delete2026-03-04
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PREAI
deleteNatsumi Kobayashi; Keiichi Kuroki; Yoshiyuki Itoh; Tomoaki Murakami
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