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Barry H. Paw

peking university

61H指数
158论文数
1.5W被引数
收录论文 46
发表时间
Identification of ZBP-89 as a novel GATA-1-Associated transcription factor involved in megakaryocytic and erythroid development鉴定ZBP-89作为参与巨核细胞和红系细胞发育的新型GATA-1-Associated转录因子
err2023-03-27
err66
errOAAI
errWoo, Andrew J.; Moran, Tyler B.; Schindler, Yocheved L.; Choe, Seong-Kyu; Langer, Nathaniel B.; Sullivan, Matthew R.; Fujiwara, Yuko; Paw, Barry H.; Cantor, Alan B.
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Identification of Distal cis-Regulatory Elements at Mouse Mitoferrin Loci Using Zebrafish Transgenesis
err2023-03-20
err37
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errAmigo, Julio D.; Yu, Ming; Troadec, Marie-Berengere; Gwynn, Babette; Cooney, Jeffrey D.; Lambert, Amy J.; Chi, Neil C.; Weiss, Mitchell J.; Peters, Luanne L.; Kaplan, Jerry; Cantor, Alan B.; Paw, Barry H.
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Mutations in the iron-sulfur cluster biogenesis protein HSCB cause congenital sideroblastic anemia
err2020-08-31
err19
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errCrispin, Andrew; Guo, Chaoshe; Chen, Caiyong; Campagna, Dean R.; Schmidt, Paul J.; Lichtenstein, Daniel; Cao, Chang; Sendamarai, Anoop K.; Hildick-Smith, Gordon J.; Huston, Nicholas C.; Boudreaux, Jeanne; Bottomley, Sylvia S.; Heeney, Matthew M.; Paw, Barry H.; Fleming, Mark D.; Ducamp, Sarah
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The mitochondrial metal transporters mitoferrin1 and mitoferrin2 are required for liver regeneration and cell proliferation in mice
err2020-08-01
err42
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errSeguin, Alexandra; Jia, Xuan; Earl, Aubree M.; Li, Liangtao; Wallace, Jared; Qiu, Andong; Bradley, Thomas; Shrestha, Rishna; Troadec, Marie-Berengere; Hockin, Matt; Titen, Simon; Warner, Dave E.; Dowdle, P. Tom; Wohlfahrt, Martin E.; Hillas, Elaine; Firpo, Matthew A.; Phillips, John D.; Kaplan, Jerry; Paw, Barry H.; Barasch, Jonathan; Ward, Diane M.
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Strong correlation of ferrochelatase enzymatic activity with Mitoferrin-1 mRNA in lymphoblasts of patients with protoporphyria
err2019-11-01
err6
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errPhillips, John; Farrell, Collin; Wang, Yongming; Singal, Ashwani K.; Anderson, Karl; Balwani, Manisha; Bissell, Montgomery; Bonkovsky, Herbert; Seay, Toni; Paw, Barry; Desnick, Robert; Bloomer, Joseph
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FAM210B is an erythropoietin target and regulates erythroid heme synthesis by controlling mitochondrial iron import and ferrochelatase activity
err2018-12-01
err33
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errYien, Yvette Y.; Shi, Jiahai; Chen, Caiyong; Cheung, Jesmine T. M.; Grillo, Anthony S.; Shrestha, Rishna; Li, Liangtao; Zhang, Xuedi; Kafina, Martin D.; Kingsley, Paul D.; King, Matthew J.; Ablain, Julien; Li, Hojun; Zon, Leonard I.; Palis, James; Burke, Martin D.; Bauer, Daniel E.; Orkin, Stuart H.; Koehler, Carla M.; Phillips, John D.; Kaplan, Jerry; Ward, Diane M.; Lodish, Harvey F.; Paw, Barry H.
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Mutation in human CLPX elevates levels of δ-aminolevulinate synthase and protoporphyrin IX to promote erythropoietic protoporphyria
err2017-09-05
err65
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errYien, Yvette Y.; Ducamp, Sarah; van der Vorm, Lisa N.; Kardon, Julia R.; Manceau, Hana; Kannengiesser, Caroline; Bergonia, Hector A.; Kafina, Martin D.; Karim, Zoubida; Gouya, Laurent; Baker, Tania A.; Puy, Herve; Phillips, John D.; Nicolas, Gael; Paw, Barry H.
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Reductions in the mitochondrial ABC transporter Abcb10 affect the transcriptional profile of heme biosynthesis genes
err2017-09-01
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errSeguin, Alexandra; Takahashi-Makise, Naoko; Yien, Yvette Y.; Huston, Nicholas C.; Whitman, Jared C.; Musso, Gabriel; Wallace, Jared A.; Bradley, Thomas; Bergonia, Hector A.; Kafina, Martin D.; Matsumoto, Mitsuyo; Igarashi, Kazuhiko; Phillips, John D.; Paw, Barry H.; Kaplan, Jerry; Ward, Diane M.
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Erythropoietin signaling regulates heme biosynthesis
err2017-05-29
err40
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errChung, Jacky; Wittig, Johannes G.; Ghamari, Alireza; Maeda, Manami; Dailey, Tamara A.; Bergonia, Hector; Kafina, Martin D.; Coughlin, Emma E.; Minogue, Catherine E.; Hebert, Alexander S.; Li, Liangtao; Kaplan, Jerry; Lodish, Harvey F.; Bauer, Daniel E.; Orkin, Stuart H.; Cantor, Alan B.; Maeda, Takahiro; Phillips, John D.; Coon, Joshua J.; Pagliarini, David J.; Dailey, Harry A.; Paw, Barry H.
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Characterization of genomic deletion efficiency mediated by clustered regularly interspaced short palindromic repeats (CRISPR)/Cas9 nuclease system in mammalian cells (vol 289, pg 21312, 2014)
err2017-02-01
err37
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errCanver, Matthew C.; Bauer, Daniel E.; Dass, Abhishek; Yien, Yvette Y.; Chung, Jacky; Masuda, Takeshi; Maeda, Takahiro; Paw, Barry H.; Orkin, Stuart H.
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Homozygous knockout of the piezo1 gene in the zebrafish is not associated with anemia
err2015-08-20
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errShmukler, Boris E.; Huston, Nicholas C.; Thon, Jonathan N.; Ni, Chih-Wen; Kourkoulis, George; Lawson, Nathan D.; Paw, Barry H.; Alper, Seth L.
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The mTORC1/4E-BP pathway coordinates hemoglobin production with L-leucine availability
err2015-04-14
err54
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errChung, Jacky; Bauer, Daniel E.; Ghamari, Alireza; Nizzi, Christopher P.; Deck, Kathryn M.; Kingsley, Paul D.; Yien, Yvette Y.; Huston, Nicholas C.; Chen, Caiyong; Schultz, Iman J.; Dalton, Arthur J.; Wittig, Johannes G.; Palis, James; Orkin, Stuart H.; Lodish, Harvey F.; Eisenstein, Richard S.; Cantor, Alan B.; Paw, Barry H.
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TMEM14C is required for erythroid mitochondrial heme metabolism
err2014-08-26
err62
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errYien, Yvette Y.; Robledo, Raymond F.; Schultz, Iman J.; Takahashi-Makise, Naoko; Gwynn, Babette; Bauer, Daniel E.; Dass, Abhishek; Yi, Gloria; Li, Liangtao; Hildick-Smith, Gordon J.; Cooney, Jeffrey D.; Pierce, Eric L.; Mohler, Kyla; Dailey, Tamara A.; Miyata, Non; Kingsley, Paul D.; Garone, Caterina; Hattangadi, Shilpa M.; Huang, Hui; Chen, Wen; Keenan, Ellen M.; Shah, Dhvanit I.; Schlaeger, Thorsten M.; DiMauro, Salvatore; Orkin, Stuart H.; Cantor, Alan B.; Palis, James; Koehler, Carla M.; Lodish, Harvey F.; Kaplan, Jerry; Ward, Diane M.; Dailey, Harry A.; Phillips, John D.; Peters, Luanne L.; Paw, Barry H.
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Characterization of Genomic Deletion Efficiency Mediated by Clustered Regularly Interspaced Palindromic Repeats (CRISPR)/Cas9 Nuclease System in Mammalian Cells
err2014-08-01
err310
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errCanver, Matthew C.; Bauer, Daniel E.; Dass, Abhishek; Yien, Yvette Y.; Chung, Jacky; Masuda, Takeshi; Maeda, Takahiro; Paw, Barry H.; Orkin, Stuart H.
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Iron regulatory protein-1 protects against mitoferrin-1-deficient porphyria.
err2014-05-01
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errChung, Jacky; Anderson, Sheila A.; Gwynn, Babette; Deck, Kathryn M.; Chen, Michael J.; Langer, Nathaniel B.; Shaw, George C.; Huston, Nicholas C.; Boyer, Leah F.; Datta, Sumon; Paradkar, Prasad N.; Li, Liangtao; Wei, Zong; Lambert, Amy J.; Sahr, Kenneth; Wittig, Johannes G.; Chen, Wen; Lu, Wange; Galy, Bruno; Schlaeger, Thorsten M.; Hentze, Matthias W.; Ward, Diane M.; Kaplan, Jerry; Eisenstein, Richard S.; Peters, Luanne L.; Paw, Barry H.
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Iron Regulatory Protein-1 Protects against Mitoferrin-1-deficient Porphyria
err2014-03-01
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errChung, Jacky; Anderson, Sheila A.; Gwynn, Babette; Deck, Kathryn M.; Chen, Michael J.; Langer, Nathaniel B.; Shaw, George C.; Huston, Nicholas C.; Boyer, Leah F.; Datta, Sumon; Paradkar, Prasad N.; Li, Liangtao; Wei, Zong; Lambert, Amy J.; Sahr, Kenneth; Wittig, Johannes G.; Chen, Wen; Lu, Wange; Galy, Bruno; Schlaeger, Thorsten M.; Hentze, Matthias W.; Ward, Diane M.; Kaplan, Jerry; Eisenstein, Richard S.; Peters, Luanne L.; Paw, Barry H.
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Macrocytic Anemia and Mitochondriopathy Resulting from a Defect in Sideroflexin 4
err2013-11-01
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errHildick-Smith, Gordon J.; Cooney, Jeffrey D.; Garone, Caterina; Kremer, Laura S.; Haack, Tobias B.; Thon, Jonathan N.; Miyata, Non; Lieber, Daniel S.; Calvo, Sarah E.; Akman, H. Orhan; Yien, Yvette Y.; Huston, Nicholas C.; Branco, Diana S.; Shah, Dhvanit I.; Freedman, Matthew L.; Koehler, Carla M.; Italiano, Joseph E., Jr.; Merkenschlager, Andreas; Beblo, Skadi; Strom, Tim M.; Meitinger, Thomas; Freisinger, Peter; Donati, M. Alice; Prokisch, Holger; Mootha, Vamsi K.; DiMauro, Salvatore; Paw, Barry H.
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