未登录A CLN6-CLN8 complex recruits lysosomal enzymes at the ER for Golgi transfer (vol 130, pg 4118, 2020)CLN6-CLN8复合物在ER处招募溶酶体酶以进行高尔基体转运(vol 130, pg 4118, 2020)
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收藏Atypical free sialic acid storage disorder associated with tissue specific mosaicism of SLC17A5
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收藏Surveillance of ventilator associated pneumonia in a network of indian hospitals using modified definitions: a pilot study
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收藏D-mannose as a new therapy for fucokinase deficiency-related congenital disorder of glycosylation (FCSK-CDG)D-甘露糖作为岩藻激酶缺乏症相关的先天性糖基化障碍 (fcsk-cdg) 的新疗法
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收藏D-Mannose as a new therapy for fucokinase deficiency-related congenital disorder of glycosylation (FCSK-CDG)
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收藏Calpain activity is negatively regulated by a KCTD7-Cullin-3 complex via non-degradative ubiquitination
Sharma, Jaiprakash; Mulherkar, Shalaka; Chen, Uan-, I; Xiong, Yan; Bajaj, Lakshya; Cho, Byoung-Kyu; Goo, Young Ah; Leung, Hon-Chiu Eastwood; Tolias, Kimberley F.; Sardiello, Marco
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收藏CLN8 is an endoplasmic reticulum cargo receptor that regulates lysosome biogenesis
di Ronza, Alberto; Bajaj, Lakshya; Sharma, Jaiprakash; Sanagasetti, Deepthi; Lotfi, Parisa; Adamski, Carolyn Joy; Collette, John; Palmieri, Michela; Amawi, Abdallah; Popp, Lauren; Chang, Kevin Tommy; Meschini, Maria Chiara; Leung, Hon-Chiu Eastwood; Segatori, Laura; Simonati, Alessandro; Sifers, Richard Norman; Santorelli, Filippo Maria; Sardiello, Marco
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收藏NADPH oxidase promotes Parkinsonian phenotypes by impairing autophagic flux in an mTORC1-independent fashion in a cellular model of Parkinson's disease
Pal, Rituraj; Bajaj, Lakshya; Sharma, Jaiprakash; Palmieri, Michela; Di Ronza, Alberto; Lotfi, Parisa; Chaudhury, Arindam; Neilson, Joel; Sardiello, Marco; Rodney, George G.
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