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Luisa Sturiale

IPCB

35H指数
132论文数
3.7K被引数
收录论文 39
发表时间
IgG Glycosylation Analysis in Patients with Ring14 Syndrome Unveils Novel Pathomechanisms and New Therapy Perspectives环14综合征患者IgG糖基化分析揭示了新的致病机制和治疗前景
err2026-05-22
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errAngela Messina; Angelo Palmigiano; Donata Agata Romeo; Luisa Sturiale; Enrico Parano; Marco Crimi; Annunziata Carrese Cirillo; Alessandro Vaisfeld; Rita Barone; Domenico Garozzo
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A splice-altering intronic variant in two multiplex families refines COG4-related congenital disorder of glycosylation在两个多基因家族中发现的一个可改变剪接的内含子变异,可明确COG4相关的先天性糖基化障碍
err2026-05-22
err0
PREAI
errLucia Micale; Luisa Sturiale; Federica Russo; Ester Di Muro; Grazia Nardella; Riccardo Pracella; Sonia Lomuscio; Silvia Morlino; Mario Benvenuto; Angela Messina; Angelo Palmigiano; Massimo Carella; Giuseppe d'Orsi; Pietro Palumbo; Orazio Palumbo; Rita Barone; Marco Castori
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Severe kidney dysfunction in sialidosis mice reveals an essential role for neuraminidase 1 in reabsorption
err2023-10-23
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errKho, Ikhui; Demina, Ekaterina P.; Pan, Xuefang; Londono, Irene; Cairo, Christopher W.; Sturiale, Luisa; Palmigiano, Angelo; Messina, Angela; Garozzo, Domenico; Ung, Roth-Visal; Mac-Way, Fabrice; Bonneil, Eric; Thibault, Pierre; Lemaire, Mathieu; Morales, Carlos R.; Pshezhetsky, Alexey V.
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N-acetylneuraminate pyruvate lyase controls sialylation of muscle glycoproteins essential for muscle regeneration and function
err2023-06-30
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errDa Silva, Afitz; Dort, Junio; Orfi, Zakaria; Pan, Xuefang; Huang, Sjanie; Kho, Ikhui; Heckel, Emilie; Muscarnera, Giacomo; van Vliet, Patrick Piet; Sturiale, Luisa; Messina, Angela; Romeo, Donata Agata; van Karnebeek, Clara D. M.; Wen, Xiao-Yan; Hinek, Aleksander; Molina, Thomas; Andelfinger, Gregor; Ellezam, Benjamin; Yamanaka, Yojiro; Olivos, Hernando J.; Morales, Carlos R.; Joyal, Jean-Sebastien; Lefeber, Dirk J.; Garozzo, Domenico; Dumont, Nicolas A.; Pshezhetsky, Alexey V.
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CAMLG-CDG: a novel congenital disorder of glycosylation linked to defective membrane trafficking
err2022-03-09
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errWilson, Matthew P.; Durin, Zoe; Unal, Ozlem; Ng, Bobby G.; Marrecau, Thomas; Keldermans, Liesbeth; Souche, Erika; Rymen, Daisy; Gunduz, Mehmet; Kose, Guluen; Sturiale, Luisa; Garozzo, Domenico; Freeze, Hudson H.; Jaeken, Jaak; Foulquier, Francois; Matthijs, Gert
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Clinical, molecular and glycophenotype insights in SLC39A8-CDGSLC39A8-CDG的临床,分子和糖型见解
err2021-07-10
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errBonaventura, Eleonora; Barone, Rita; Sturiale, Luisa; Pasquariello, Rosa; Alessandri, Maria Grazia; Pinto, Anna Maria; Renieri, Alessandra; Panteghini, Celeste; Garavaglia, Barbara; Cioni, Giovanni; Battini, Roberta
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Lipopolysaccharide from Gut-Associated Lymphoid-Tissue-Resident Alcaligenes faecalis: Complete Structure Determination and Chemical Synthesis of Its Lipid A
err2021-03-22
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errShimoyama, Atsushi; Di Lorenzo, Flaviana; Yamaura, Haruki; Mizote, Keisuke; Palmigiano, Angelo; Pither, Molly D.; Speciale, Immacolata; Uto, Tomoya; Masui, Seiji; Sturiale, Luisa; Garozzo, Domenico; Hosomi, Koji; Shibata, Naoko; Kabayama, Kazuya; Fujimoto, Yukari; Silipo, Alba; Kunisawa, Jun; Kiyono, Hiroshi; Molinaro, Antonio; Fukase, Koichi
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Tear N-glycomics in vernal and atopic keratoconjunctivitis
err2021-03-15
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PREAI
errMessina, Angela; Palmigiano, Angelo; Tosto, Claudia; Romeo, Donata Agata; Sturiale, Luisa; Garozzo, Domenico; Leonardi, Andrea
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SLC35A2-CDG: Functional characterization, expanded molecular, clinical, and biochemical phenotypes of 30 unreported Individuals
err2019-04-24
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errNg, Bobby G.; Sosicka, Paulina; Agadi, Satish; Almannai, Mohammed; Bacino, Carlos A.; Barone, Rita; Botto, Lorenzo D.; Burton, Jennifer E.; Carlston, Colleen; Chung, Brian Hon-Yin; Cohen, Julie S.; Coman, David; Dipple, Katrina M.; Dorrani, Naghmeh; Dobyns, William B.; Elias, Abdallah F.; Epstein, Leon; Gahl, William A.; Garozzo, Domenico; Hammer, Trine Bjorg; Haven, Jaclyn; Heron, Delphine; Herzog, Matthew; Hoganson, George E.; Hunter, Jesse M.; Jain, Mahim; Juusola, Jane; Lakhani, Shenela; Lee, Hane; Lee, Joy; Lewis, Katherine; Longo, Nicola; Lourenco, Charles Marques; Mak, Christopher C. Y.; McKnight, Dianalee; Mendelsohn, Bryce A.; Mignot, Cyril; Mirzaa, Ghayda; Mitchell, Wendy; Muhle, Hiltrud; Nelson, Stanley F.; Olczak, Mariusz; Palmer, Christina G. S.; Partikian, Arthur; Patterson, Marc C.; Pierson, Tyler M.; Quinonez, Shane C.; Regan, Brigid M.; Ross, M. Elizabeth; Guillen Sacoto, Maria J.; Scaglia, Fernando; Scheffer, Ingrid E.; Segal, Devorah; Singhal, Nilika Shah; Striano, Pasquale; Sturiale, Luisa; Symonds, Joseph D.; Tang, Sha; Vilain, Eric; Willis, Mary; Wolfe, Lynne A.; Yang, Hui; Yano, Shoji; Powis, Zoee; Suchy, Sharon F.; Rosenfeld, Jill A.; Edmondson, Andrew C.; Grunewald, Stephanie; Freeze, Hudson H.
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The lipopolysaccharide core oligosaccharide of Burkholderia plays a critical role in maintaining a proper gut symbiosis with the bean bug Riptortus pedestris
err2017-11-01
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errKim, Jiyeun Kate; Jang, Ho Am; Kim, Min Seon; Cho, Jae Hyun; Lee, Junbeom; Di Lorenzo, Flaviana; Sturiale, Luisa; Silipo, Alba; Molinaro, Antonio; Lee, Bok Luel
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The Very Long Chain Fatty Acid (C26:25OH) Linked to the Lipid A Is Important for the Fitness of the Photosynthetic Bradyrhizobium Strain ORS278 and the Establishment of a Successful Symbiosis with Aeschynomene Legumes
err2017-09-21
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errBusset, Nicolas; Di Lorenzo, Flaviana; Palmigiano, Angelo; Sturiale, Luisa; Gressent, Frederic; Fardoux, Joel; Gully, Djamel; Chaintreuil, Clemence; Molinaro, Antonio; Silipo, Alba; Giraud, Eric
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The LipidA from Rhodopseudomonas palustris Strain BisA53 LPS Possesses a Unique Structure and Low Immunostimulant Properties
err2016-12-22
err25
PREAI
errDi Lorenzo, Flaviana; Palmigiano, Angelo; Al Bitar-Nehme, Sami; Sturiale, Luisa; Duda, Katarzyna A.; Gully, Djamel; Lanzetta, Rosa; Giraud, Eric; Garozzo, Domenico; Bernardini, Maria Lina; Molinaro, Antonio; Silipo, Alba
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Structural Relationship of the Lipid A Acyl Groups to Activation of Murine Toll-Like Receptor 4 by Lipopolysaccharides from Pathogenic Strains of Burkholderia mallei, Acinetobacter baumannii, and Pseudomonas aeruginosa
err2015-11-23
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errKorneev, Kirill V.; Arbatsky, Nikolay P.; Molinaro, Antonio; Palmigiano, Angelo; Shaikhutdinova, Rima Z.; Shneider, Mikhail M.; Pier, Gerald B.; Kondakova, Anna N.; Sviriaeva, Ekaterina N.; Sturiale, Luisa; Garozzo, Domenico; Kruglov, Andrey A.; Nedospasov, Sergei A.; Drutskaya, Marina S.; Knirel, Yuriy A.; Kuprash, Dmitry V.
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N-Linked Glycans of Chloroviruses Sharing a Core Architecture without Precedent
err2015-11-19
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errDe Castro, Cristina; Speciale, Immacolata; Duncan, Garry; Dunigan, David D.; Agarkova, Irina; Lanzetta, Rosa; Sturiale, Luisa; Palmigiano, Angelo; Garozzo, Domenico; Molinaro, Antonio; Tonetti, Michela; Van Etten, James L.
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Insect Gut Symbiont Susceptibility to Host Antimicrobial Peptides Caused by Alteration of the Bacterial Cell Envelope
err2015-08-01
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errKim, Jiyeun Kate; Son, Dae Woo; Kim, Chan-Hee; Cho, Jae Hyun; Marchetti, Roberta; Silipo, Alba; Sturiale, Luisa; Park, Ha Young; Huh, Ye Rang; Nakayama, Hiroshi; Fukatsu, Takema; Molinaro, Antonio; Lee, Bok Luel
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Persistent cystic fibrosis isolate Pseudomonas aeruginosa strain RP73 exhibits an under-acylated LPS structure responsible of its low inflammatory activity持续性囊性纤维化分离株铜绿假单胞菌菌株RP73表现出低酰化的LPS结构,导致其低炎症活性
err2015-02-01
err28
PREAI
errDi Lorenzo, Flaviana; Silipo, Alba; Bianconi, Irene; Lore', Nicola Ivan; Scamporrino, Andrea; Sturiale, Luisa; Garozzo, Domenico; Lanzetta, Rosa; Parrilli, Michelangelo; Bragonzi, Alessandra; Molinaro, Antonio
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Covalently linked hopanoid-lipid A improves outer-membrane resistance of a Bradyrhizobium symbiont of legumes
err2014-10-30
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errSilipo, Alba; Vitiello, Giuseppe; Gully, Djamel; Sturiale, Luisa; Chaintreuil, Clemence; Fardoux, Joel; Gargani, Daniel; Lee, Hae-In; Kulkarni, Gargi; Busset, Nicolas; Marchetti, Roberta; Palmigiano, Angelo; Moll, Herman; Engel, Regina; Lanzetta, Rosa; Paduano, Luigi; Parrilli, Michelangelo; Chang, Woo-Suk; Holst, Otto; Newman, Dianne K.; Garozzo, Domenico; D'Errico, Gerardino; Giraud, Eric; Molinaro, Antonio
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MAN1B1 Deficiency: An Unexpected CDG-II
err2013-12-12
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errRymen, Daisy; Peanne, Romain; Millon, Maria B.; Race, Valerie; Sturiale, Luisa; Garozzo, Domenico; Mills, Philippa; Clayton, Peter; Asteggiano, Carla G.; Quelhas, Dulce; Cansu, Ali; Martins, Esmeralda; Nassogne, Marie-Cecile; Goncalves-Rocha, Miguel; Topaloglu, Haluk; Jaeken, Jaak; Foulquier, Francois; Matthijs, Gert
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Intracellular Shigella remodels its LPS to dampen the innate immune recognition and evade inflammasome activation细胞内志贺氏菌重塑其LPS以抑制先天免疫识别并逃避炎症小体激活
err2013-10-28
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errPaciello, Ida; Silipo, Alba; Lembo-Fazio, Luigi; Curcuru, Laura; Zumsteg, Anna; Noel, Gaelle; Ciancarella, Valeria; Sturiale, Luisa; Molinaro, Antonio; Bernardini, Maria Lina
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