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Longitudinal GGT trajectories identify prognostic phenotypes in paediatric primary sclerosing cholangitis 纵向GGT轨迹可识别儿童原发性硬化性胆管炎的预后表型 Denier, Daniela; Peng, Yiming (Emmett); Amin, Mansi; Aumar, Madeleine; Auth, Marcus; Fagundes, Eleonora Druve Tavares; El-Matary, Wael; Ferreira, Alexandre R.; Furuya, Katryn N.; Gupta, Nitika; Guthery, Stephen; Horslen, Simon; Jensen, M. Kyle; Kamath, Binita M.; Koot, Bart G. P.; Loomes, Kathleen M.; Mack, Cara; Martinez, Mercedes; Ovchinsky, Nadia; Papadopoulou, Alexandra; Perito, Emily R.; Sathya, Pushpa; Stevens, James P.; Tessier, M. Elizabeth; Valentino, Pamela; Deneau, Mark; Liu, Kuan; Ricciuto, Amanda 分享 收藏
The Frequency and Potential Implications of HFE Genetic Variants in Children With Cystic Fibrosis HFE基因变异在囊性纤维化儿童中的频率及潜在影响 Huang, Leslie; Lai, HuiChuan J.; Furuya, Katryn N.; Antos, Nicholas J.; Asfour, Fadi; Boyne, Kathleen L.; Howenstine, Michelle; Rock, Michael J.; Sawicki, Gregory S.; Gaffin, Jonathan M.; Worthey, Elizabeth A.; Farrell, Philip M. 分享 收藏
Oral vancomycin is associated with improved inflammatory bowel disease clinical outcomes in primary sclerosing cholangitis-associated inflammatory bowel disease (PSC-IBD): A matched analysis from the Paediatric PSC Consortium Ricciuto, Amanda; Liu, Kuan; El-Matary, Wael; Amin, Mansi; Amir, Achiya Z.; Aumar, Madeleine; Auth, Marcus; Di Guglielmo, Matthew D.; Druve Tavares Fagundes, Eleonora; Rodrigues Ferreira, Alexandre; Furuya, Katryn N.; Gupta, Nitika; Guthery, Stephen; Horslen, Simon P.; Jensen, Kyle; Kamath, Binita M.; Kerkar, Nanda; Koot, B. G. P.; Laborda, Trevor J.; Lee, Christine K.; Loomes, Kathleen M.; Mack, Cara; Martinez, Mercedes; Montano-Loza, Aldo; Ovchinsky, Nadia; Papadopoulou, Alexandra; Perito, Emily R.; Sathya, Pushpa; Schwarz, Kathleen B.; Shah, Uzma; Shteyer, Eyal; Soufi, Nisreen; Stevens, James Patrick; Taylor, Amy; Tessier, M. Elizabeth; Valentino, Pamela; Woynarowski, Marek; Deneau, Mark 分享 收藏
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Liver transplantation recovers hepatic N-glycosylation with persistent IgG glycosylation abnormalities: Three-year follow-up in a patient with phosphomannomutase-2-congenital disorder of glycosylation Tahata, Shawn; Weckwerth, Jody; Ligezka, Anna; He, Miao; Lee, Hee Eun; Heimbach, Julie; Ibrahim, Samar H.; Kozicz, Tamas; Furuya, Katryn; Morava, Eva 分享 收藏
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Recurrence of Primary Sclerosing Cholangitis After Liver Transplant in Children: An International Observational Study Martinez, Mercedes; Perito, Emily R.; Valentino, Pamela; Mack, Cara L.; Aumar, Madeleine; Broderick, Annemarie; Draijer, Laura G.; Fagundes, Eleonora D. T.; Furuya, Katryn N.; Gupta, Nitika; Horslen, Simon; Jonas, Maureen M.; Kamath, Binita M.; Kerkar, Nanda; Kim, Kyung Mo; Kolho, Kaija-Leena; Koot, Bart G. P.; Laborda, Trevor J.; Lee, Christine K.; Loomes, Kathleen M.; Miloh, Tamir; Mogul, Douglas; Mohammed, Saeed; Ovchinsky, Nadia; Rao, Girish; Ricciuto, Amanda; Ferreira, Alexandre Rodrigues; Schwarz, Kathleen B.; Smolka, Vratislav; Tanaka, Atsushi; Tessier, Mary E. M.; Venkat, Venna L.; Vitola, Bernadette E.; Woynarowski, Marek; Zerofsky, Melissa; Deneau, Mark R. 分享 收藏
Colorectal Dysplasia and Cancer in Pediatric-Onset Ulcerative Colitis Associated With Primary Sclerosing Cholangitis El-Matary, Wael; Guthery, Stephen L.; Amir, Achiya Z.; DiGuglielmo, Matthew; Draijer, Laura G.; Furuya, Katryn N.; Gupta, Nitika; Hochberg, Jessica T.; Horslen, Simon; Kerkar, Nanda; Koot, Bart G. P.; Laborda, Trevor J.; Loomes, Kathleen M.; Mack, Cara; Martinez, Mercedes; Miethke, Alexander; Miloh, Tamir; Mogul, Douglas; Mohammed, Saeed; Moroz, Stacy; Ovchinsky, Nadia; Perito, Emily R.; Rao, Girish; Ricciuto, Amanda; Sathya, Pushpa; Schwarz, Kathleen B.; Shah, Uzma; Singh, Ruchi; Soufi, Nisreen; Valentino, Pamela L.; Zizzo, Andreanne; Deneau, Mark R. 分享 收藏
Oral Vancomycin, Ursodeoxycholic Acid, or No Therapy for Pediatric Primary Sclerosing Cholangitis: A Matched Analysis Deneau, Mark R.; Mack, Cara; Mogul, Douglas; Perito, Emily R.; Valentino, Pamela L.; Amir, Achiya Z.; DiGuglielmo, Matthew; Draijer, Laura G.; El-Matary, Wael; Furuya, Katryn N.; Gupta, Nitika; Hochberg, Jessica T.; Horslen, Simon; Jensen, M. Kyle; Jonas, Maureen M.; Kerkar, Nanda; Koot, Bart G. P.; Laborda, Trevor J.; Lee, Christine K.; Loomes, Kathleen M.; Martinez, Mercedes; Miethke, Alexander; Miloh, Tamir; Mohammad, Saeed; Ovchinsky, Nadia; Rao, Girish; Ricciuto, Amanda; Sathya, Pushpa; Schwarz, Kathleen B.; Shah, Uzma; Singh, Ruchi; Vitola, Bernadette; Zizzo, Andreanne; Guthery, Stephen L. 分享 收藏
The Sclerosing Cholangitis Outcomes in Pediatrics (SCOPE) Index: A Prognostic Tool for Children Deneau, Mark R.; Mack, Cara; Perito, Emily R.; Ricciuto, Amanda; Valentino, Pamela L.; Amin, Mansi; Amir, Achiya Z.; Aumar, Madeleine; Auth, Marcus; Broderick, Annemarie; DiGuglielmo, Matthew; Draijer, Laura G.; Fagundes, Eleonora Druve Tavares; El-Matary, Wael; Ferrari, Federica; Furuya, Katryn N.; Gupta, Nitika; Hochberg, Jessica T.; Homan, Matjaz; Horslen, Simon; Iorio, Raffaele; Jensen, M. Kyle; Jonas, Maureen M.; Kamath, Binita M.; Kerkar, Nanda; Kim, Kyung Mo; Kolho, Kaija-Leena; Koot, Bart G. P.; Laborda, Trevor J.; Lee, Christine K.; Loomes, Kathleen M.; Martinez, Mercedes; Miethke, Alexander; Miloh, Tamir; Mogul, Douglas; Mohammad, Saeed; Mohan, Parvathi; Moroz, Stacy; Ovchinsky, Nadia; Palle, Sirish; Papadopoulou, Alexandra; Rao, Girish; Ferreira, Alexandre Rodrigues; Sathya, Pushpa; Schwarz, Kathleen B.; Shah, Uzma; Shteyer, Eyal; Singh, Ruchi; Smolka, Vratislav; Soufi, Nisreen; Tanaka, Atsushi; Varier, Raghu; Vitola, Bernadette; Woynarowski, Marek; Zerofsky, Melissa; Zizzo, Andreanne; Guthery, Stephen L. 分享 收藏
Normal liver stiffness and influencing factors in healthy children: An individual participant data meta-analysis Li, Darrick K.; Khan, Muhammad Rehan; Wang, Zhen; Chongsrisawat, Voranush; Swangsak, Panida; Teufel-Schaefer, Ulrike; Engelmann, Guido; Goldschmidt, Imeke; Baumann, Ulrich; Tokuhara, Daisuke; Cho, Yuki; Rowland, Marion; Mjelle, Anders B.; Ramm, Grant A.; Lewindon, Peter J.; Witters, Peter; Cassiman, David; Ciuca, Ioana M.; Prokop, Larry D.; Haffar, Samir; Corey, Kathleen E.; Murad, M. H.; Furuya, Katryn N.; Bazerbachi, Fateh 分享 收藏
Homozygosity for a mutation affecting the catalytic domain of tyrosyl-tRNA synthetase (YARS) causes multisystem disease 影响酪氨酰-tRNA合成酶 (YARS) 催化结构域的突变的纯合性导致多系统疾病 Williams, Katie B.; Brigatti, Karlla W.; Puffenberger, Erik G.; Gonzaga-Jauregui, Claudia; Griffin, Laurie B.; Martinez, Erick D.; Wenger, Olivia K.; Yoder, Mark A.; Kandula, Vinay V. R.; Fox, Michael D.; Demczko, Matthew M.; Poskitt, Laura; Furuya, Katryn N.; Reid, Jeffrey G.; Overton, John D.; Baras, Aris; Miles, Lili; Radhakrishnan, Kadakkal; Carson, Vincent J.; Antonellis, Anthony; Jinks, Robert N.; Strauss, Kevin A. 分享 收藏
Gamma Glutamyltransferase Reduction Is Associated With Favorable Outcomes in Pediatric Primary Sclerosing Cholangitis Deneau, Mark R.; Mack, Cara; Abdou, Reham; Amin, Mansi; Amir, Achiya; Auth, Marcus; Bazerbachi, Fateh; Broderick, Anne Marie; Chan, Albert; DiGuglielmo, Matthew; El-Matary, Wale; El-Youssef, Mounif; Ferrari, Federica; Furuya, Katryn N.; Gottrand, Frederic; Gupta, Nitika; Homan, Matjaz; Jensen, M. K.; Kamath, Binita M.; Kim, Kyung Mo; Kolho, Kaija-Leena; Konidari, Anastasia; Koot, Bart; Iorio, Raffaele; Martinez, Mercedes; Mohan, Parvathi; Palle, Sirish; Papadopoulou, Alexandra; Ricciuto, Amanda; Saubermann, Lawrence; Sathya, Pushpa; Shteyer, Eyal; Smolka, Vratislav; Tanaka, Atsushi; Valentino, Pamela L.; Varier, Raghu; Venkat, Veena; Vitola, Bernadette; Vos, Miriam B.; Woynarowski, Marek; Yap, Jason; Miloh, Tamir 分享 收藏
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Frailty in Children with Liver Disease: A Prospective Multicenter Study Lurz, Eberhard; Quammie, Claudia; Englesbe, Michael; Alonso, Estella M.; Lin, Henry C.; Hsu, Evelyn K.; Furuya, Katryn N.; Gupta, Nitika A.; Venkat, Veena L.; Daniel, James F.; Leonis, Mike A.; Miloh, Tamir; Telega, Grzegorz W.; Yap, Jason; Menendez, Jerome; Book, Linda S.; Himes, Ryan W.; Sundaram, Shikha S.; Parekh, Rulan; Sonnenday, Chris; Bucuvalas, John; Ng, Vicky L.; Kamath, Binita M. 分享 收藏
The Natural History of Primary Sclerosing Cholangitis in 781 Children: AMulticenter, International Collaboration Deneau, Mark R.; El-Matary, Wael; Valentino, Pamela L.; Abdou, Reham; Alqoaer, Khaled; Amin, Mansi; Amir, Achiya Z.; Auth, Marcus; Bazerbachi, Fateh; Broderick, Annemarie; Chan, Albert; Cotter, Jillian; Doan, Sylvia; El-Youssef, Mounif; Ferrari, Federica; Furuya, Katryn N.; Gottrand, Madeleine; Gottrand, Frederic; Gupta, Nitika; Homan, Matjaz; Kamath, Binita M.; Kim, Kyung Mo; Kolho, Kaija-Leena; Konidari, Anastasia; Koot, Bart; Iorio, Raffaele; Ledder, Oren; Mack, Cara; Martinez, Mercedes; Miloh, Tamir; Mohan, Parvathi; O'Cathain, Niamh; Papadopoulou, Alexandra; Ricciuto, Amanda; Saubermann, Lawrence; Sathya, Pushpa; Shteyer, Eyal; Smolka, Vratislav; Tanaka, Atushi; Varier, Raghu; Venkat, Veena; Vitola, Bernadette; Vos, Miriam B.; Woynarowski, Marek; Yap, Jason; Jensen, M. Kyle 分享 收藏
RECURRENCE OF PRIMARY SCLEROSING CHOLANGITIS AFTER LIVER TRANSPLANTATION IN CHILDREN: DATA FROM THE PEDIATRIC PSC CONSORTIUM Bazerbachi, Fateh; Furuya, Katryn; Abdou, Reham; Alqoaer, Khaled; Amin, Mansi; Amir, Achiya Z.; Auth, Marcus; Broderick, Annemarie; Chan, Albert; Cotter, Jillian; Doan, Sylvia; El-Matary, Wael; El-Youssef, Mounif; Ferrari, Federica; Gottrand, Madeleine; Gottrand, Frederic; Gupta, Nitika; Homan, Matjaz; Jensen, M. K.; Kamath, Binita M.; Kim, Kyung M.; Kolho, Kaija-Leena Kola Kaija-Leena; Konidari, Anastasia; Koot, Bart; Iorio, Raffaele; Ledder, Oren; Mack, Cara L.; Martinez, Mercedes; Miloh, Tamir; Mohan, Parvathi; O'Cathain, Niamh; Papadopoulou, Alexandra; Ricciuto, Amanda; Saubermann, Lawrence; Sathya, Pushpa; Shteyer, Eyal; Tanaka, Atsushi; Varier, Raghu; Valentino, Pamela L.; Venkat, Veena; Vitola, Bernadette E.; Vos, Miriam B.; Vratislav, Smolka; Woynarowski, Marek; Yap, Jason Y.; Deneau, Mark R. 分享 收藏
A COMPARISON OF PRIMARY SCLEROSING CHOLANGITIS WITH AND WITHOUT ASSOCIATED INFLAMMATORY BOWEL DISEASE: DATA FROM THE PEDIATRIC PSC CONSORTIUM Ricciuto, Amanda; Kamath, Binita M.; Abdou, Reham; Alqoaer, Khaled; Amin, Mansi; Amir, Achiya Z.; Auth, Marcus; Bazerbachi, Fateh; Broderick, Annemarie; Chan, Albert; Cotter, Jillian; Doan, Sylvia; El-Matary, Wael; El-Youssef, Mounif; Ferrari, Federica; Furuya, Katryn; Gottrand, Madeleine; Gottrand, Frederic; Gupta, Nitika; Homan, Matjaz; Jensen, M. K.; Kim, Kyung M.; Kolho, Kaija-Leena Kola Kaija-Leena; Konidari, Anastasia; Koot, Bart; Iorio, Raffaele; Ledder, Oren; Mack, Cara L.; Martinez, Mercedes; Miloh, Tamir; Mohan, Parvathi; O'Cathain, Niamh; Papadopoulou, Alexandra; Sathya, Pushpa; Saubermann, Lawrence; Shteyer, Eyal; Tanaka, Atsushi; Varier, Raghu; Valentino, Pamela L.; Venkat, Veena; Vitola, Bernadette E.; Vos, Miriam B.; Vratislav, Smolka; Woynarowski, Marek; Yap, Jason Y.; Deneau, Mark R. 分享 收藏
Recurrence of primary sclerosing cholangitis after liver transplantation in children: data from the Pediatric PSC Consortium Bazerbachi, F.; Furuya, K. N.; Abdou, R.; Alqoaer, K.; Amin, M.; Amir, A.; Auth, M.; Broderick, A.; Chan, A.; Cotter, J.; Doan, S.; El-Matary, W.; El-Youssef, M.; Ferrari, F.; Gottrand, M.; Gottrand, F.; Gupta, N.; Homan, M.; Jensen, M. K.; Kamath, B. M.; Kim, K. M.; Kolho, K. -L.; Konidari, A.; Koot, B.; Iorio, R.; Ledder, O.; Mack, C.; Martinez, M.; Miloh, T.; Mohan, P.; O'Cathain, N.; Papadopoulou, A.; Ricciuto, A.; Sathya, P.; Shteyer, E.; Tanaka, A.; Varier, R.; Valentino, P. L.; Venkat, V.; Vitola, B.; Vos, M.; Vratislav, S.; Woynarowski, M.; Yap, J.; Deneau, M. R. 分享 收藏