Konrad Sandhoff - Publications, H-index & Citations

Konrad Sandhoff

university of bonn

103H指数

2.3K论文数

3.6W被引数

收录论文 141

发表时间

Ganglioside GM2 catabolism is inhibited by storage compounds of mucopolysaccharidoses and by cationic amphiphilic drugs

MOLECULAR GENETICS AND METABOLISM

IF3.5

2019-09-01

PREAI

Anheuser, Susi; Breiden, Bernadette; Sandhoff, Konrad

Lysosomal Glycosphingolipid Storage Diseases

ANNUAL REVIEW OF BIOCHEMISTRY

IF0

2019-06-20

PREAI

Breiden, Bernadette; Sandhoff, Konrad

Membrane lipids and their degradation compounds control GM2 catabolism at intralysosomal luminal vesicles

JOURNAL OF LIPID RESEARCH

IF4.1

2019-06-01

OAAI

Anheuser, Susi; Breiden, Bernadette; Sandhoff, Konrad

Inactivation of ceramide synthase 2 catalytic activity in mice affects transcription of genes involved in lipid metabolism and cell division

BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS

IF3.3

2018-07-01

PREAI

Bickert, Andreas; Kern, Paul; van Uelft, Martina; Herresthal, Stefanie; Ulas, Thomas; Gutbrod, Katharina; Breiden, Bernadette; Degen, Joachim; Sandhoff, Konrad; Schultze, Joachim L.; Doermann, Peter; Hartmann, Dieter; Bauer, Reinhard; Willecke, Klaus

Emerging concepts of ganglioside metabolism

FEBS LETTERS

IF3

2018-06-16

OAAI

Sandhoff, Roger; Sandhoff, Konrad

Unbalanced lipolysis results in lipotoxicity and mitochondrial damage in peroxisome-deficient Pex19 mutants

MOLECULAR BIOLOGY OF THE CELL

IF2.7

2018-02-15

OAAI

Buelow, Margret H.; Wingen, Christian; Senyilmaz, Deniz; Gosejacob, Dominic; Sociale, Mariangela; Bauer, Reinhard; Schulze, Heike; Sandhoff, Konrad; Teleman, Aurelio A.; Hoch, Michael; Sellin, Julia

Ceramide Synthase Schlank Is a Transcriptional Regulator Adapting Gene Expression to Energy Requirements

CELL REPORTS

IF6.9

2018-01-01

OAAI

Sociale, Mariangela; Wulf, Anna-Lena; Breiden, Bernadette; Klee, Kathrin; Thielisch, Melanie; Eckardt, Franka; Sellin, Julia; Buelow, Margret H.; Loebbert, Sinah; Weinstock, Nadine; Voelzmann, Andre; Schultze, Joachim; Sandhoff, Konrad; Bauer, Reinhard

Synthetic Glycoforms Reveal Carbohydrate-Dependent Bioactivity of Human Saposin D

ANGEWANDTE CHEMIE-INTERNATIONAL EDITION

IF16.9

2017-04-05

PREAI

Graf, Christopher G. F.; Schulz, Christian; Schmaelzlein, Marina; Heinlein, Christian; Moennich, Manuel; Perkams, Lukas; Puettner, Markus; Boos, Irene; Hessefort, Markus; Sanchez, Jose Nelson Lombana; Weyand, Michael; Steegborn, Clemens; Breiden, Bernadette; Ross, Kerstin; Schwarzmann, Guenter; Sandhoff, Konrad; Unverzagt, Carlo

Identification of a feedback loop involving β-glucosidase 2 and its product sphingosine sheds light on the molecular mechanisms in Gaucher disease

JOURNAL OF BIOLOGICAL CHEMISTRY

IF3.9

2017-04-01

OAAI

Schonauer, Sophie; Koerschen, Heinz G.; Penno, Anke; Rennhack, Andreas; Breiden, Bernadette; Sandhoff, Konrad; Gutbrod, Katharina; Dormann, Peter; Raju, Diana N.; Haberkant, Per; Gerl, Mathias J.; Bruegger, Britta; Zigdon, Hila; Vardi, Ayelet; Futerman, Anthony H.; Thiele, Christoph; Wachten, Dagmar

Lipids regulate the hydrolysis of membrane bound glucosylceramide by lysosomal β-glucocerebrosidase

JOURNAL OF LIPID RESEARCH

IF4.1

2017-03-01

OAAI

Abdul-Hammed, Misbaudeen; Breiden, Bernadette; Schwarzmann, Gunter; Sandhoff, Konrad

Characterization of Drosophila Saposin-related mutants as a model for lysosomal sphingolipid storage diseases

DISEASE MODELS & MECHANISMS

IF3.3

2017-01-01

OAAI

Sellin, Julia; Schulze, Heike; Paradis, Marie; Gosejacob, Dominic; Papan, Cyrus; Shevchenko, Andrej; Psathaki, Olympia Ekaterina; Paululat, Achim; Thielisch, Melanie; Sandhoff, Konrad; Hoch, Michael

Sphingolipidoses membrane lipids regulate and modify sphingolipid catabolism, its enzymes, lipid binding and transfer proteins

MOLECULAR GENETICS AND METABOLISM

IF3.5

2017-01-01

PREAI

Sandhoff, Konrad

Neuronal sphingolipidoses: Membrane lipids and sphingolipid activator proteins regulate lysosomal sphingolipid catabolism

BIOCHIMIE

IF3

2016-11-01

PREAI

Sandhoff, Konrad

Membrane-spanning lipids for an uncompromised monitoring of membrane fusion and intermembrane lipid transfer

JOURNAL OF LIPID RESEARCH

IF4.1

2015-10-01

OAAI

Schwarzmann, Guenter; Breiden, Bernadette; Sandhoff, Konrad

Membrane lipids regulate ganglioside GM2 catabolism and GM2 activator protein activity

JOURNAL OF LIPID RESEARCH

IF4.1

2015-09-01

OAAI

Anheuser, Susi; Breiden, Bernadette; Schwarzmann, Gunter; Sandhoff, Konrad

Accumulation of Glucosylceramide in the Absence of the Beta-Glucosidase GBA2 Alters Cytoskeletal Dynamics

PLOS GENETICS

IF3.7

2015-03-24

OAAI

Raju, Diana; Schonauer, Sophie; Hamzeh, Hussein; Flynn, Kevin C.; Bradke, Frank; Dorp, Katharina Vom; Doermann, Peter; Yildiz, Yildiz; Troetschel, Christian; Poetsch, Ansgar; Breiden, Bernadette; Sandhoff, Konrad; Koerschen, Heinz G.; Wachten, Dagmar

Partial synthesis of ganglioside and lysoganglioside lipoforms as internal standards for MS quantification

JOURNAL OF LIPID RESEARCH

IF4.1

2014-12-01

OAAI

Gantner, Martin; Schwarzmann, Guenter; Sandhoff, Konrad; Kolter, Thomas

Acid sphingomyelinase activity is regulated by membrane lipids and facilitates cholesterol transfer by NPC2

JOURNAL OF LIPID RESEARCH

IF4.1

2014-12-01

OAAI

Oninla, Vincent O.; Breiden, Bernadette; Babalola, Jonathan O.; Sandhoff, Konrad