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Modulation of mitochondrial and inflammatory homeostasis through RIP140 is neuroprotective in an adrenoleukodystrophy mouse model Ranea-Robles, Pablo; Galino, Jorge; Espinosa, Lluis; Schluter, Agatha; Ruiz, Montserrat; Calingasan, Noel Ylagan; Villarroya, Francesc; Naudi, Alba; Pamplona, Reinald; Ferrer, Isidre; Beal, M. Flint; Portero-Otin, Manuel; Fourcade, Stephane; Pujol, Aurora 分享 收藏
High-dose biotin restores redox balance, energy and lipid homeostasis, and axonal health in a model of adrenoleukodystrophy Fourcade, Stephane; Goicoechea, Leire; Parameswaran, Janani; Schluter, Agatha; Launay, Nathalie; Ruiz, Montserrat; Seyer, Alexandre; Colsch, Benoit; Calingasan, Noel Ylagan; Ferrer, Isidre; Beal, M. Flint; Sedel, Frederic; Pujol, Aurora 分享 收藏
Aberrant regulation of the GSK-3β/NRF2 axis unveils a novel therapy for adrenoleukodystrophy Ranea-Robles, Pablo; Launay, Nathalie; Ruiz, Montserrat; Calingasan, Noel Ylagan; Dumont, Magali; Naudi, Alba; Portero-Otin, Manuel; Pamplona, Reinald; Ferrer, Isidre; Beal, M. Flint; Fourcade, Stephane; Pujol, Aurora 分享 收藏
Rewiring of Glutamine Metabolism Is a Bioenergetic Adaptation of Human Cells with Mitochondrial DNA Mutations Chen, Qiuying; Kirk, Kathryne; Shurubor, Yevgeniya I.; Zhao, Dazhi; Arreguin, Andrea J.; Shahi, Ifrah; Valsecchi, Federica; Primiano, Guido; Calder, Elizabeth L.; Carelli, Valerio; Denton, Travis T.; Beal, M. Flint; Gross, Steven S.; Manfredi, Giovanni; D'Aurelio, Marilena 分享 收藏
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Activation of sirtuin 1 as therapy for the peroxisomal disease adrenoleukodystrophy Morato, L.; Ruiz, M.; Boada, J.; Calingasan, N. Y.; Galino, J.; Guilera, C.; Jove, M.; Naudi, A.; Ferrer, I.; Pamplona, R.; Serrano, M.; Portero-Otin, M.; Beal, M. F.; Fourcade, S.; Pujol, A. 分享 收藏
Methylene blue upregulates Nrf2/ARE genes and prevents tau-related neurotoxicity Stack, Cliona; Jainuddin, Shari; Elipenahli, Ceyhan; Gerges, Meri; Starkova, Natalia; Starkov, Anatoly A.; Jove, Mariona; Portero-Otin, Manuel; Launay, Nathalie; Pujol, Aurora; Kaidery, Navneet Ammal; Thomas, Bobby; Tampellini, Davide; Beal, M. Flint; Dumont, Magali 分享 收藏
PGC-1α overexpression exacerbates β-amyloid and tau deposition in a transgenic mouse model of Alzheimer's disease Dumont, Magali; Stack, Cliona; Elipenahli, Ceyhan; Jainuddin, Shari; Launay, Nathalie; Gerges, Meri; Starkova, Natalia; Starkov, Anatoly A.; Calingasan, Noel Y.; Tampellini, Davide; Pujol, Aurora; Beal, M. Flint 分享 收藏
Pioglitazone halts axonal degeneration in a mouse model of X-linked adrenoleukodystrophy Morato, Laia; Galino, Jorge; Ruiz, Montserrat; Calingasan, Noel Ylagan; Starkov, Anatoly A.; Dumont, Magali; Naudi, Alba; Jose Martinez, Juan; Aubourg, Patrick; Portero-Otin, Manuel; Pamplona, Reinald; Galea, Elena; Beal, M. Flint; Ferrer, Isidre; Fourcade, Stephane; Pujol, Aurora 分享 收藏
The negative impact of α-ketoglutarate dehydrogenase complex deficiency on matrix substrate-level phosphorylation Kiss, Gergely; Konrad, Csaba; Doczi, Judit; Starkov, Anatoly A.; Kawamata, Hibiki; Manfredi, Giovanni; Zhang, Steven F.; Gibson, Gary E.; Beal, M. Flint; Adam-Vizi, Vera; Chinopoulos, Christos 分享 收藏
Targeting Nrf2-Mediated Gene Transcription by Extremely Potent Synthetic Triterpenoids Attenuate Dopaminergic Neurotoxicity in the MPTP Mouse Model of Parkinson's Disease Kaidery, Navneet Ammal; Banerjee, Rebecca; Yang, Lichuan; Smirnova, Natalya A.; Hushpulian, Dmitry M.; Liby, Karen T.; Williams, Charlotte R.; Yamamoto, Masayuki; Kensler, Thomas W.; Ratan, Rajiv R.; Sporn, Michael B.; Beal, M. Flint; Gazaryan, Irina G.; Thomas, Bobby 分享 收藏
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Somatic mitochondrial DNA mutations in early parkinson and incidental lewy body disease Lin, Michael T.; Cantuti-Castelvetri, Ippolita; Zheng, Kangni; Jackson, Katie E.; Tan, Yong B.; Arzberger, Thomas; Lees, Andrew J.; Betensky, Rebecca A.; Beal, M. Flint; Simon, David K. 分享 收藏
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