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Merrill D. Benson

Icahn School of Medicine at Mount Sinai

63H指数
345论文数
1.7W被引数
收录论文 43
发表时间
Detection of Circulating Transthyretin Amyloid Aggregates in Plasma: A Novel Biomarker for Transthyretin Amyloidosis
err2024-05-21
err2
PREAI
errPedretti, Rose; Wang, Lanie; Hanna, Mazen; Benson, Merrill D.; Grodin, Justin L.; Tang, W. H. Wilson; Masri, Ahmad; Saelices, Lorena
err分享
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Structure-specific peptide probes detect aggregated transthyretin in plasma of transthyretin amyloidosis patients
err2024-03-01
err0
errOAAI
errPedretti, Rose; Wang, Lanie; Yakubovska, Ania; Benson, Merrill; Grodin, Justin; Masri, Ahmad; Saelices, Lorena
err分享
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Structural polymorphism of amyloid fibrils in ATTR amyloidosis revealed by cryo-electron microscopy
err2024-01-17
err11
errOAAI
errNguyen, Binh An; Singh, Virender; Afrin, Shumaila; Yakubovska, Anna; Wang, Lanie; Ahmed, Yasmin; Pedretti, Rose; Fernandez-Ramirez, Maria del Carmen; Singh, Preeti; Pekala, Maja; Hernandez, Luis O. Cabrera; Kumar, Siddharth; Lemoff, Andrew; Gonzalez-Prieto, Roman; Sawaya, Michael R.; Eisenberg, David S.; Benson, Merrill Douglas; Saelices, Lorena
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Guidelines and new directions in the therapy and monitoring of ATTRv amyloidosis
err2022-06-02
err90
errOAAI
errAndo, Yukio; Adams, David; Benson, Merrill D.; Berk, John L.; Plante-Bordeneuve, Violaine; Coelho, Teresa; Conceicao, Isabel; Ericzon, Bo-Goran; Obici, Laura; Rapezz, Claudio; Sekijima, Yoshiki; Ueda, Mitsuharu; Palladini, Giovanni; Merlini, Giampaolo
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Tissue biopsy for the diagnosis of amyloidosis: experience from some centres
err2021-11-12
err40
errOAAI
errBenson, Merrill D.; Berk, John L.; Dispenzieri, Angela; Damy, Thibaud; Gillmore, Julian D.; Hazenberg, Bouke P.; Lavatelli, Francesca; Picken, Maria M.; Roecken, Christoph; Schoenland, Stefan; Ueda, Mitsuharu; Westermark, Per
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Efficacy and safety with >3 years of inotersen treatment for the polyneuropathy of hereditary transthyretin amyloidosis
err2021-10-01
err0
PREAI
errCoelho, Teresa; Whelan, Carol; Conceicao, Isabel; Brannagan, Thomas; Wang, Annabel; Polydefkis, Michael; Dyck, Peter; Plante-Bordeneuve, Violaine; Berk, John; Merlini, Giampaolo; Obici, Laura; Drachman, Brian; Gorevic, Peter; Schmidt, Hartmut; Plana, Josep Maria Campistol; Gamez, Josep; Kristen, Arnt; Mazzeo, Anna; Narayana, Arvind; Olugemo, Kemi; Aquino, Peter; Benson, Merrill; Gertz, Morie
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Design and Rationale of the Global Phase 3 NEURO-TTRansform Study of Antisense Oligonucleotide AKCEA-TTR-LRx (ION-682884-CS3) in Hereditary Transthyretin-Mediated Amyloid Polyneuropathy
err2021-02-26
err42
errOAAI
errCoelho, Teresa; Ando, Yukio; Benson, Merrill D.; Berk, John L.; Waddington-Cruz, Marcia; Dyck, Peter J.; Gillmore, Julian D.; Khella, Sami L.; Litchy, William J.; Obici, Laura; Monteiro, Cecilia; Tai, Li-Jung; Viney, Nicholas J.; Buchele, Gustavo; Brambatti, Michela; Jung, Shiangtung W.; O'Dea, Louis St L.; Tsimikas, Sotirios; Schneider, Eugene; Geary, Richard S.; Monia, Brett P.; Gertz, Morie
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Ligand conjugated antisense oligonucleotide for the treatment of transthyretin amyloidosis: preclinical and phase 1 data
err2020-12-07
err65
errOAAI
errViney, Nicholas J.; Guo, Shuling; Tai, Li-Jung; Baker, Brenda F.; Aghajan, Mariam; Jung, Shiangtung W.; Yu, Rosie Z.; Booten, Sheri; Murray, Heather; Machemer, Todd; Burel, Sebastien; Murray, Sue; Buchele, Gustavo; Tsimikas, Sotirios; Schneider, Eugene; Geary, Richard S.; Benson, Merrill D.; Monia, Brett P.
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Inotersen therapy of transthyretin amyloid cardiomyopathy转甲状腺素蛋白淀粉样心肌病的Inotersen治疗
err2019-11-12
err72
errOAAI
errDasgupta, Noel R.; Rissing, Stacy M.; Smith, Jessica; Jung, Jeesun; Benson, Merrill D.
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ALECT2 and NASH
err2019-07-25
err0
PREAI
errCummings, Oscar W.; Dasgupta, Noel R.; Benson, Merrill D.
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A cell-based high-throughput screening method to directly examine transthyretin amyloid fibril formation at neutral pH
err2019-07-01
err18
errOAAI
errUeda, Mitsuharu; Okada, Masamitsu; Mizuguchi, Mineyuki; Kluve-Beckerman, Barbara; Kanenawa, Kyosuke; Isoguchi, Aito; Misumi, Yohei; Tasaki, Masayoshi; Ueda, Akihiko; Kanai, Akinori; Sasaki, Ryoko; Masuda, Teruaki; Inoue, Yasuteru; Nomura, Toshiya; Shinriki, Satoru; Shuto, Tsuyoshi; Kai, Hirofumi; Yamashita, Taro; Matsui, Hirotaka; Benson, Merrill D.; Ando, Yukio
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A pair of peptides inhibits seeding of the hormone transporter transthyretin into amyloid fibrils
err2019-04-01
err36
errOAAI
errSaelices, Lorena; Nguyen, Binh A.; Chung, Kevin; Wang, Yifei; Ortega, Alfredo; Lee, Ji H.; Coelho, Teresa; Bijzet, Johan; Benson, Merrill D.; Eisenberg, David S.
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Amyloid nomenclature 2018: recommendations by the International Society of Amyloidosis (ISA) nomenclature committee淀粉样蛋白命名2018: 国际淀粉样变性学会 (ISA) 命名委员会的建议
err2019-01-07
err432
errOAAI
errBenson, Merrill D.; Buxbaum, Joel N.; Eisenberg, David S.; Merlini, Giampaolo; Saraiva, Maria J. M.; Sekijima, Yoshiki; Sipe, Jean D.; Westermark, Per
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Hereditary transthyretin amyloidosis: baseline characteristics of patients in the NEURO-TTR trial
err2018-08-31
err25
errOAAI
errWaddington-Cruz, Marcia; Ackermann, Elizabeth J.; Polydefkis, Michael; Heitner, Stephen B.; Dyck, Peter J.; Barroso, Fabio A.; Wang, Annabel K.; Berk, John L.; Dyck, P. James B.; Monia, Brett P.; Hughes, Steven G.; Tai, Li; Kwoh, T. Jesse; Jung, Shiangtung W.; Coelho, Teresa; Benson, Merrill D.; Gertz, Morie A.
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Inotersen Treatment for Patients with Hereditary Transthyretin Amyloidosis
err2018-07-05
err1.0K
errOAAI
errBenson, M. D.; Waddington-Cruz, M.; Berk, J. L.; Polydefkis, M.; Dyck, P. J.; Wang, A. K.; Plante-Bordeneuve, V.; Barroso, F. A.; Merlini, G.; Obici, L.; Scheinberg, M.; Brannagan, T. H., III; Litchy, W. J.; Whelan, C.; Drachman, B. M.; Adams, D.; Heitner, S. B.; Conceicao, I.; Schmidt, H. H.; Vita, G.; Campistol, J. M.; Gamez, J.; Gorevic, P. D.; Gane, E.; Shah, A. M.; Solomon, S. D.; Monia, B. P.; Hughes, S. G.; Kwoh, T. J.; McEvoy, B. W.; Jung, S. W.; Baker, B. F.; Ackermann, E. J.; Gertz, M. A.; Coelho, T.
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Safety and efficacy of a TTR specific antisense oligonucleotide in patients with transthyretin amyloid cardiomyopathy
err2017-09-14
err73
PREAI
errBenson, Merrill D.; Dasgupta, Noel R.; Rissing, Stacy M.; Smith, Jessica; Feigenbaum, Harvey
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Familial wild-type transthyretin cardiomyopathy
err2017-04-22
err0
PREAI
errBenson, Merrill D.; Berk, John L.; Connors, Lawreen H.; Dasgupta, Noel R.
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AA cardiomyopathy
err2017-04-22
err1
PREAI
errDasgupta, Noel R.; Cummings, Oscar W.; Phillips, Carrie L.; Benson, Merrill D.
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