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Collagen IV of basement membranes: II. Emergence of collagen IVα345 enabled the assembly of a compact GBM as an ultrafilter in mammalian kidneys Pokidysheva, Elena N.; Redhair, Neve; Ailsworth, Octavia; Page-McCaw, Patrick; Rollins-Smith, Louise; Jamwal, Vijayishwer Singh; Ohta, Yuko; Bachinger, Hans Peter; Murawala, Prayag; Flajnik, Martin; Fogo, Agnes B.; Abrahamson, Dale; Hudson, Julie K.; Boudko, Sergei P.; Hudson, Billy G. 分享 收藏
FK506-Binding Protein 11 Is a Novel Plasma Cell-Specific Antibody Folding Catalyst with Increased Expression in Idiopathic Pulmonary Fibrosis FK506-Binding蛋白11是一种新型浆细胞特异性抗体折叠催化剂,在特发性肺纤维化中表达增加 Preisendoerfer, Stefan; Ishikawa, Yoshihiro; Hennen, Elisabeth; Winklmeier, Stephan; Schupp, Jonas C.; Knueppel, Larissa; Fernandez, Isis E.; Binzenhofer, Leonhard; Flatley, Andrew; Juan-Guardela, Brenda M.; Ruppert, Clemens; Guenther, Andreas; Frankenberger, Marion; Hatz, Rudolf A.; Kneidinger, Nikolaus; Behr, Jurgen; Feederle, Regina; Schepers, Aloys; Hilgendorff, Anne; Kaminski, Naftali; Meinl, Edgar; Baechinger, Hans Peter; Eickelberg, Oliver; Staab-Weijnitz, Claudia A. 分享 收藏
Defining the Extracellular Matrix of Rhabdomyosarcoma Lian, Xiaolei; Bond, J. Steffan; Bharathy, Narendra; Boudko, Sergei P.; Pokidysheva, Elena; Shern, Jack F.; Lathara, Melvin; Sasaki, Takako; Settelmeyer, Teagan; Cleary, Megan M.; Bajwa, Ayeza; Srinivasa, Ganapati; Hartley, Christopher P.; Bachinger, Hans Peter; Mansoor, Atiya; Gultekin, Sakir H.; Berlow, Noah E.; Keller, Charles 分享 收藏
Aberrant binding of mutant HSP47 affects posttranslational modification of type I collagen and leads to osteogenesis imperfecta Syx, Delfien; Ishikawa, Yoshihiro; Gebauer, Jan; Boudko, Sergei P.; Guillemyn, Brecht; Van Damme, Tim; D'hondt, Sanne; Symoens, Sofie; Nampoothiri, Sheela; Gould, Douglas B.; Baumann, Ulrich; Bachinger, Hans Peter; Malfait, Fransiska 分享 收藏
Type I and type V procollagen triple helix uses different subsets of the molecular ensemble for lysine posttranslational modifications in the rER Ishikawa, Yoshihiro; Taga, Yuki; Zientek, Keith; Mizuno, Nobuyo; Salo, Antti M.; Semenova, Olesya; Tufa, Sara F.; Keene, Douglas R.; Holden, Paul; Mizuno, Kazunori; Gould, Douglas B.; Myllyharju, Johanna; Bachinger, Hans Peter 分享 收藏
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The HDAC3-SMARCA4-miR-27a axis promotes expression of the PAX3:FOXO1 fusion oncogene in rhabdomyosarcoma Bharathy, Narendra; Berlow, Noah E.; Wang, Eric; Abraham, Jinu; Settelmeyer, Teagan P.; Hooper, Jody E.; Svalina, Matthew N.; Ishikawa, Yoshihiro; Zientek, Keith; Bajwa, Zia; Goros, Martin W.; Hernandez, Brian S.; Wolff, Johannes E.; Rudek, Michelle A.; Xu, Linping; Anders, Nicole M.; Pal, Ranadip; Harrold, Alexandria P.; Davies, Angela M.; Ashok, Arya; Bushby, Darnell; Mancini, Maria; Noakes, Christopher; Goodwin, Neal C.; Ordentlich, Peter; Keck, James; Hawkins, Douglas S.; Rudzinski, Erin R.; Chatterjee, Bishwanath; Bachinger, Hans Peter; Barr, Frederic G.; Liddle, Jennifer; Garcia, Benjamin A.; Mansoor, Atiya; Perkins, Theodore J.; Vakoc, Christopher R.; Michalek, Joel E.; Keller, Charles 分享 收藏
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Osteogenesis imperfecta Marini, Joan C.; Forlino, Antonella; Bachinger, Hans Peter; Bishop, Nick J.; Byers, Peter H.; De Paepe, Anne; Fassier, Francois; Fratzl-Zelman, Nadja; Kozloff, Kenneth M.; Krakow, Deborah; Montpetit, Kathleen; Semler, Oliver 分享 收藏
A Novel Antifibrotic Mechanism of Nintedanib and Pirfenidone Knueppel, Larissa; Ishikawa, Yoshihiro; Aichler, Michaela; Heinzelmann, Katharina; Hatz, Rudolf; Behr, Juergen; Walch, Axel; Baechinger, Hans Peter; Eickelberg, Oliver; Staab-Weijnitz, Claudia A. 分享 收藏
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Nintedanib and pirfenidone inhibit collagen synthesis and maturation at several regulatory levels Knuppel, Larissa; Ishikawa, Yoshihiro; Aichler, Michaela; Heinzelmann, Katharina; Hatz, Rudolf; Behr, Jurgen; Walch, Axel; Bachinger, Hans Peter; Eickelberg, Oliver; Staab-Weijnitz, Claudia A. 分享 收藏
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