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Proximal and Distal Bronchioles Contribute to the Pathogenesis of Non-Cystic Fibrosis Bronchiectasis Asakura, Takanori; Okuda, Kenichi; Chen, Gang; Dang, Hong; Kato, Takafumi; Mikami, Yu; Schworer, Stephen A.; Gilmore, Rodney C.; Radicioni, Giorgia; Hawkins, Padraig; Cardenas, Selene Margarita Barbosa; Saito, Minako; Cawley, Anne Marie; De la Cruz, Gabriela; Chua, Michael; Alexis, Neil E.; Masugi, Yohei; Noone, Peadar G.; Ribeiro, Carla M. P.; Kesimer, Mehmet; Olivier, Kenneth N.; Hasegawa, Naoki; Randell, Scott H.; O'Neal, Wanda K.; Boucher, Richard C. 分享 收藏
A Novel Co-Culture Model Reveals Enhanced CFTR Rescue in Primary Cystic Fibrosis Airway Epithelial Cultures with Persistent Pseudomonas aeruginosa Infection Cholon, Deborah M.; Greenwald, Matthew A.; Higgs, Matthew G.; Quinney, Nancy L.; Boyles, Susan E.; Meinig, Suzanne L.; Minges, John T.; Chaubal, Ashlesha; Tarran, Robert; Ribeiro, Carla M. P.; Wolfgang, Matthew C.; Gentzsch, Martina 分享 收藏
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Chronic E-Cigarette Exposure Alters Human Alveolar Macrophage Morphology and Gene Expression Davis, Eric S.; Ghosh, Arunava; Coakley, Raymond D.; Wrennall, Joe A.; Lubamba, Bob A.; Rowell, Temperance R.; Dang, Hong; Pawlak, Erica A.; Li, Quefeng; Alexis, Neil E.; Ribeiro, Carla M. P.; Tarran, Robert 分享 收藏
Pharmacological modulation of mitochondrial calcium uniporter controls lung inflammation in cystic fibrosis 线粒体钙单向转运蛋白的药理调节可控制囊性纤维化的肺部炎症 Rimessi, Alessandro; Pozzato, Chiara; Carparelli, Lorenzo; Rossi, Alice; Ranucci, Serena; De Fino, Ida; Cigana, Cristina; Talarico, Anna; Wieckowski, Mariusz R.; Ribeiro, Carla M. P.; Trapella, Claudio; Rossi, Giacomo; Cabrini, Giulio; Bragonzi, Alessandra; Pinton, Paolo 分享 收藏
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IL-1β dominates the promucin secretory cytokine profile in cystic fibrosis IL-1β 在囊性纤维化的前粘蛋白分泌细胞因子谱中占主导地位 Chen, Gang; Sun, Ling; Kato, Takafumi; Okuda, Kenichi; Martino, Mary B.; Abzhanova, Aiman; Lin, Jennifer M.; Gilmore, Rodney C.; Batson, Bethany D.; O'Neal, Yvonne K.; Volmer, Allison S.; Dang, Hong; Deng, Yangmei; Randell, Scott H.; Button, Brian; Livraghi-Butrico, Alessandra; Kesimer, Mehmet; Ribeiro, Carla M. P.; O'Neal, Wanda K.; Boucher, Richard C. 分享 收藏
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XBP1S Regulates MUC5B in a Promoter Variant-Dependent Pathway in Idiopathic Pulmonary Fibrosis Airway Epithelia Chen, Gang; Ribeiro, Carla M. P.; Sun, Ling; Okuda, Kenichi; Kato, Takafumi; Gilmore, Rodney C.; Martino, Mary B.; Dang, Hong; Abzhanova, Aiman; Lin, Jennifer M.; Hull-Ryde, Emily A.; Volmer, Allison S.; Randell, Scott H.; Livraghi-Butrico, Alessandra; Deng, Yingfeng; Scherer, Philipp E.; Stripp, Barry R.; O'Neal, Wanda K.; Boucher, Richard C. 分享 收藏
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PLCB3 Loss of Function Reduces Pseudomonas aeruginosa-Dependent IL-8 Release in Cystic Fibrosis Rimessi, Alessandro; Bezzerri, Valentino; Salvatori, Francesca; Tamanini, Anna; Nigro, Federica; Dechecchi, Maria Cristina; Santangelo, Alessandra; Prandini, Paola; Munari, Silvia; Provezza, Lisa; de Loubresse, Nicolas Garreau; Muller, Jean; Ribeiro, Carla M. P.; Lippi, Giuseppe; Gambari, Roberto; Pinton, Paolo; Cabrini, Giulio 分享 收藏
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Mucin Production and Hydration Responses to Mucopurulent Materials in Normal versus Cystic Fibrosis Airway Epithelia Abdullah, Lubna H.; Coakley, Raymond; Webster, Megan J.; Zhu, Yunxiang; Tarran, Robert; Radicioni, Giorgia; Kesimer, Mehmet; Boucher, Richard C.; Davis, C. William; Ribeiro, Carla M. P. 分享 收藏
Transient Receptor Potential Ankyrin 1 Channels Modulate Inflammatory Response in Respiratory Cells from Patients with Cystic Fibrosis Prandini, Paola; De Logu, Francesco; Fusi, Camilla; Provezza, Lisa; Nassini, Romina; Montagner, Giulia; Materazzi, Serena; Munari, Silvia; Gilioli, Eliana; Bezzerri, Valentino; Finotti, Alessia; Lampronti, Ilaria; Tamanini, Anna; Dechecchi, Maria Cristina; Lippi, Giuseppe; Ribeiro, Carla M.; Rimessi, Alessandro; Pinton, Paolo; Gambari, Roberto; Geppetti, Pierangelo; Cabrini, Giulio 分享 收藏