未登录A systematic bi-genomic split-GFP assay illuminates the mitochondrial matrix proteome and protein targeting routes系统性的双基因组split-GFP分析法阐明了线粒体基质蛋白质组及蛋白质靶向途径
Bykov, Yury S.; Zuttion, Solene; Edilbi, Dunya; Polozova, Marina; Arnold, Johanna; Malitsky, Sergey; Itkin, Maxim; Senger, Bruno; Klein, Ofir; Asraf, Yeynit; Meyer, Hadar; Becker, Hubert D.; Kucharczyk, Roza; Schuldiner, Maya
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收藏Bi-Genomic Mitochondrial-Split-GFP - the yeast system for screening the mitochondrial matrix echoforms of dually localized proteins双基因组线粒体-Split-GFP-用于筛选双重定位蛋白的线粒体基质回声的酵母系统
Bader, Gaetan; Enkler, Ludovic; Araiso, Yuhei; Hemmerle, Marine; Binko, Krystyna; Baranowska, Emilia; Wiesyk, Aneta; De Craene, Johan-Owen; Ruer-Laventie, Julie; Pieters, Jean; Tribouillard-Tanvier, Deborah; Senger, Bruno; di Rago, Jean-Paul; Friant, Sylvie; Becker, Hubert Dominique; Kucharczyk, Roza
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收藏A new mechanism of ATP synthase subunit 6 and 9 translation regulation by their assembly in yeast mitochondria
Kabala, Anna; Binko, Krystyna; Godard, Francois; Dautant, Alain; Baranowska, Emilia; Skoczen, Natalia; Gombeau, Kevin; Bouhier, Marine; Becker, Hubert; Ackerman, Sharon; Steinmetz, Lars; Tribouillard-Tanvier, Deborah; Kucharczyk, Roza; di Rago, Jean-Paul
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收藏Loss of seryl-tRNA synthetase (SARS1) causes complex spastic paraplegia and cellular senescence
Verdura, Edgard; Senger, Bruno; Raspall-Chaure, Miquel; Schluter, Agatha; Launay, Nathalie; Ruiz, Montserrat; Casasnovas, Carlos; Rodriguez-Palmero, Agusti; Macaya, Alfons; Dominique Becker, Hubert; Pujol, Aurora
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收藏RNA-dependent synthesis of ergosteryl-3β-O-glycine in Ascomycota expands the diversity of steryl-amino acids
Yakobov, Nathaniel; Mahmoudi, Nassira; Grob, Guillaume; Yokokawa, Daisuke; Saga, Yusuke; Kushiro, Tetsuo; Worrell, Danielle; Roy, Herve; Schaller, Hubert; Senger, Bruno; Huck, Laurence; Gascon, Gisela Riera; Becker, Hubert D.; Fischer, Frederic
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收藏Assembly-dependent translation of subunits 6 (Atp6) and 9 (Atp9) of ATP synthase in yeast mitochondria
Kabala, Anna M.; Binko, Krystyna; Godard, Francois; Charles, Camille; Dautant, Alain; Baranowska, Emilia; Skoczen, Natalia; Gombeau, Kewin; Bouhier, Marine; Becker, Hubert D.; Ackerman, Sharon H.; Steinmetz, Lars M.; Tribouillard-Tanvier, Deborah; Kucharczyk, Roza; Di Rago, Jean-Paul
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收藏De Novo and Bi-allelic Pathogenic Variants in NARS1 Cause Neurodevelopmental Delay Due to Toxic Gain-of-Function and Partial Loss-of-Function Effects
Manole, Andreea; Efthymiou, Stephanie; O'Connor, Emer; Mendes, Marisa, I; Jennings, Matthew; Maroofian, Reza; Davagnanam, Indran; Mankad, Kshitij; Lopez, Maria Rodriguez; Salpietro, Vincenzo; Harripaul, Ricardo; Badalato, Lauren; Walia, Jagdeep; Francklyn, Christopher S.; Athanasiou-Fragkouli, Alkyoni; Sullivan, Roisin; Desai, Sonal; Baranano, Kristin; Zafar, Faisal; Rana, Nuzhat; Ilyas, Muhammed; Horga, Alejandro; Kara, Majdi; Mattioli, Francesca; Goldenberg, Alice; Griffin, Helen; Piton, Amelie; Henderson, Lindsay B.; Kara, Benyekhlef; Aslanger, Ayca Dilruba; Raaphorst, Joost; Pfundt, Rolph; Portier, Ruben; Shinawi, Marwan; Kirby, Amelia; Christensen, Katherine M.; Wang, Lu; Rosti, Rasim O.; Paracha, Sohail A.; Sarwar, Muhammad T.; Jenkins, Dagan; Ahmed, Jawad; Santoni, Federico A.; Ranza, Emmanuelle; Iwaszkiewicz, Justyna; Cytrynbaum, Cheryl; Weksberg, Rosanna; Wentzensen, Ingrid M.; Sacoto, Maria J. Guillen; Si, Yue; Telegrafi, Aida; Andrews, Marisa, V; Baldridge, Dustin; Gabriel, Heinz; Mohr, Julia; Oehl-Jaschkowitz, Barbara; Debard, Sylvain; Senger, Bruno; Fischer, Frederic; van Ravenwaaij, Conny; Fock, Annemarie J. M.; Stevens, Servi J. C.; Bahler, Jurg; Nasar, Amina; Mantovani, John F.; Manzur, Adnan; Sarkozy, Anna; Smith, Desiree E. C.; Salomons, Gajja S.; Ahmed, Zubair M.; Riazuddin, Shaikh; Riazuddin, Saima; Usmani, Muhammad A.; Seibt, Annette; Ansar, Muhammad; Antonarakis, Stylianos E.; Vincent, John B.; Ayub, Muhammad; Grimmel, Mona; Jelsig, Anne Marie; Hjortshoj, Tina Duelund; Karstensen, Helena Gasdal; Hummel, Marybeth; Haack, Tobias B.; Jamshidi, Yalda; Distelmaier, Felix; Horvath, Rita; Gleeson, Joseph G.; Becker, Hubert; Mandel, Jean-Louis; Koolen, David A.; Houlden, Henry
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收藏Assigning mitochondrial localization of dual localized proteins using a yeast Bi-Genomic Mitochondrial-Split-GFP使用酵母双基因组线粒体-Split-GFP分配双定位蛋白的线粒体定位
Bader, Gaetan; Enkler, Ludovic; Araiso, Yuhei; Hemmerle, Marine; Binko, Krystyna; Baranowska, Emilia; De Craene, Johan-Owen; Ruer-Laventie, Julie; Pieters, Jean; Tribouillard-Tanvier, Deborah; Senger, Bruno; di Rago, Jean-Paul; Friant, Sylvie; Kucharczyk, Roza; Becker, Hubert Dominique
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收藏RNA-dependent sterol aspartylation in fungi
Yakobov, Nathaniel; Fischer, Frederic; Mahmoudi, Nassira; Saga, Yusuke; Grube, Christopher D.; Roy, Herve; Senger, Bruno; Grob, Guillaume; Tatematsu, Shunsuke; Yokokawa, Daisuke; Mouyna, Isabelle; Latge, Jean-Paul; Nakajima, Harushi; Kushiro, Tetsuo; Becker, Hubert D.
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收藏Mutations in KARS cause a severe neurological and neurosensory disease with optic neuropathyKARS突变导致严重的神经和神经感觉疾病伴视神经病变
Scheidecker, Sophie; Bar, Severine; Stoetzel, Corinne; Geoffroy, Veronique; Lannes, Beatrice; Rinaldi, Bruno; Fischer, Frederic; Becker, Hubert D.; Pelletier, Valerie; Pagan, Cecile; Acquaviva-Bourdain, Cecile; Kremer, Stephane; Mirande, Marc; Tranchant, Christine; Muller, Jean; Friant, Sylvie; Dollfus, Helene
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收藏Nonconventional localizations of cytosolic aminoacyl-tRNA synthetases in yeast and human cells酵母和人类细胞中胞质氨酰tRNA合成酶的非常规定位
Debard, Sylvain; Bader, Gaetan; De Craene, Johan-Owen; Enkler, Ludovic; Bar, Severine; Laporte, Daphne; Hammann, Philippe; Myslinski, Evelyne; Senger, Bruno; Friant, Sylvie; Becker, Hubert Dominique
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收藏Expression of Nuclear and Mitochondrial Genes Encoding ATP Synthase Is Synchronized by Disassembly of a Multisynthetase Complex
Frechin, Mathieu; Enkler, Ludovic; Tetaud, Emmanuel; Laporte, Daphne; Senger, Bruno; Blancard, Corinne; Hammann, Philippe; Bader, Gaetan; Clauder-Muenster, Sandra; Steinmetz, Lars M.; Martin, Robert Pierre; di Rago, Jean-Paul; Becker, Hubert Dominique
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