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Juan María Torres

consejo superior de investigaciones cientificas (csic)

40H指数
211论文数
5.4K被引数
收录论文 85
发表时间
Substitution of histidine 95 by tyrosine in the prion protein causes spontaneous neurodegeneration in transgenic mice朊病毒蛋白中组氨酸95被酪氨酸取代会导致转基因小鼠发生自发性神经退行。
err2025-10-01
err0
PREAI
errTorres, Juan-Maria; Marin-Moreno, Alba; Espinosa, Juan-Carlos; Canoyra, Sara; Burato, Anna; Ciullini, Arianna; De Luca, Chiara Maria Giulia; Bistaffa, Edoardo; Moda, Fabio; Legname, Giuseppe
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Optimization and evaluation of new decontamination procedures inactivating human prions新型去污程序对人类朊病毒的失活优化与评估
err2025-02-01
err0
errOAAI
errHerzog, L.; Reine, F.; Castille, J.; Passet, B.; Moudjou, M.; Bonnet, R.; Torres, J. M.; Rezaei, H.; Vilotte, J. -L.; Beringue, V.; Igel, A.
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Classical BSE dismissed as the cause of CWD in Norwegian red deer despite strain similarities between both prion agents
err2024-05-15
err1
errOAAI
errMarin-Moreno, Alba; Benestad, Sylvie L.; Barrio, Tomas; Pirisinu, Laura; Espinosa, Juan Carlos; Tran, Linh; Huor, Alvina; Di Bari, Michele Angelo; Erana, Hasier; Maddison, Ben C.; D'Agostino, Claudia; Fernandez-Borges, Natalia; Canoyra, Sara; Jerez-Garrido, Nuria; Castilla, Joaquin; Spiropoulos, John; Bishop, Keith; Gough, Kevin C.; Nonno, Romolo; Vage, Jorn; Andreoletti, Olivier; Torres, Juan Maria
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Change in the molecular properties of CH1641 prions after transmission to wild-type mice: Evidence for a single strain
err2024-02-14
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errOAAI
errvan Keulen, Lucien J. M.; Dolstra, Corry H.; Vries, Ruth Bossers-de; Bossers, Alex; Jacobs, Jorg G.; Baron, Thierry; Torres, Juan Maria; Langeveld, Jan P. M.
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Experimental transmission of ovine atypical scrapie to cattle绵羊非典型瘙痒病对牛的实验传播
err2023-10-20
err3
errOAAI
errKonold, Timm; Spiropoulos, John; Hills, Janet; Abdul, Hasina; Cawthraw, Saira; Phelan, Laura; Mckenna, Amy; Read, Lauren; Canoyra, Sara; Marin-Moreno, Alba; Torres, Juan Maria
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An optimized Western blot assay provides a comprehensive assessment of the physiological endoproteolytic processing of the prion protein
err2023-02-01
err7
errOAAI
errVanni, Ilaria; Iacobone, Floriana; D'Agostino, Claudia; Giovannelli, Matteo; Pirisinu, Laura; Altmeppen, Hermann Clemens; Castilla, Joaquin; Torres, Juan Maria; Agrimi, Umberto; Nonno, Romolo
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Transgenic Mouse Models for the Study of Neurodegenerative Diseases
err2023-01-19
err8
errOAAI
errMarin-Moreno, Alba; Canoyra, Sara; Fernandez-Borges, Natalia; Carlos Espinosa, Juan; Maria Torres, Juan
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Bona fide atypical scrapie faithfully reproduced for the first time in a rodent model
err2022-12-13
err4
errOAAI
errVidal, Enric; Sanchez-Martin, Manuel A.; Erana, Hasier; Perez Lazaro, Sonia; Perez-Castro, Miguel A.; Otero, Alicia; Charco, Jorge M.; Marin, Belen; Lopez-Moreno, Rafael; Diaz-Dominguez, Carlos M.; Geijo, Marivi; Ordonez, Montserrat; Cantero, Guillermo; di Bari, Michele; Lorenzo, Nuria L.; Pirisinu, Laura; d'Agostino, Claudia; Maria Torres, Juan; Beringue, Vincent; Telling, Glenn; Badiola, Juan J.; Pumarola, Marti; Bolea, Rosa; Nonno, Romolo; Requena, Jesus R.; Castilla, Joaquin
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Glycans are not necessary to maintain the pathobiological features of bovine spongiform encephalopathy
err2022-10-07
err2
errOAAI
errOtero, Alicia; Barrio, Tomas; Erana, Hasier; Charco, Jorge M.; Betancor, Marina; Diaz-Dominguez, Carlos M.; Marin, Belen; Andreoletti, Olivier; Torres, Juan M.; Kong, Qingzhong; Badiola, Juan J.; Bolea, Rosa; Castilla, Joaquin
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Homozygous R136S mutation in PRNP gene causes inherited early onset prion diseasePRNP基因纯合R136S突变导致遗传性早发型朊病毒病
err2021-10-18
err8
errOAAI
errXimelis, Teresa; Marin-Moreno, Alba; Carlos Espinosa, Juan; Erana, Hasier; Charco, Jorge M.; Hernandez, Isabel; Riveira, Carmen; Alcolea, Daniel; Gonzalez-Roca, Eva; Aldecoa, Iban; Molina-Porcel, Laura; Parchi, Piero; Rossi, Marcello; Castilla, Joaquin; Ruiz-Garcia, Raquel; Gelpi, Ellen; Maria Torres, Juan; Sanchez-Valle, Raquel
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Classical BSE prions emerge from asymptomatic pigs challenged with atypical/Nor98 scrapie
err2021-08-31
err11
errOAAI
errMarin, Belen; Otero, Alicia; Lugan, Severine; Carlos Espinosa, Juan; Marin-Moreno, Alba; Vidal, Enric; Hedman, Carlos; Romero, Antonio; Pumarola, Marti; Badiola, Juan J.; Maria Torres, Juan; Andreoletti, Olivier; Bolea, Rosa
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Canine D163-PrP polymorphic variant does not provide complete protection against prion infection in small ruminant PrP context
err2021-07-12
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errOAAI
errMarin-Moreno, Alba; Espinosa, Juan Carlos; Aguilar-Calvo, Patricia; Fernandez-Borges, Natalia; Pitarch, Jose Luis; Gonzalez, Lorenzo; Torres, Juan Maria
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Allelic Interference in Prion Replication Is Modulated by the Convertibility of the Interfering PrPC and Other Host-Specific Factors
errMBIO
IF4.7
err2021-04-27
err0
errOAAI
errCarlos Espinosa, Juan; Andreoletti, Olivier; Marin-Moreno, Alba; Lugan, Severine; Aguilar-Calvo, Patricia; Cassard, Herve; Lorenzo, Patricia; Douet, Jean-Yves; Villa-Diaz, Ana; Aron, Naima; Prieto, Irene; Huor, Alvina; Maria Torres, Juan
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TREM2 expression in the brain and biological fluids in prion diseases
err2021-04-21
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errDiaz-Lucena, Daniela; Kruse, Niels; Thuene, Katrin; Schmitz, Matthias; Villar-Pique, Anna; Gomes da Cunha, Jose Eriton; Hermann, Peter; Lopez-Perez, Oscar; Andres-Benito, Pol; Ladogana, Anna; Calero, Miguel; Vidal, Enric; Riggert, Joachim; Pineau, Hailey; Sim, Valerie; Zetterberg, Henrik; Blennow, Kaj; Antonio del Rio, Jose; Marin-Moreno, Alba; Carlos Espinosa, Juan; Maria Torres, Juan; Sanchez-Valle, Raquel; Mollenhauer, Brit; Ferrer, Isidre; Zerr, Inga; Llorens, Franc
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Classical scrapie in small ruminants is caused by at least four different prion strains
err2021-04-15
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errOAAI
errMarin-Moreno, Alba; Aguilar-Calvo, Patricia; Espinosa, Juan Carlos; Zamora-Ceballos, Maria; Pitarch, Jose Luis; Gonzalez, Lorenzo; Fernandez-Borges, Natalia; Orge, Leonor; Andreoletti, Olivier; Nonno, Romolo; Torres, Juan Maria
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PMCA-generated prions from the olfactory mucosa of patients with Fatal Familial Insomnia cause prion disease in mice
err2021-04-14
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errOAAI
errBistaffa, Edoardo; Marin-Moreno, Alba; Carlos Espinosa, Juan; De Luca, Chiara Maria Giulia; Cazzaniga, Federico Angelo; Portaleone, Sara Maria; Celauro, Luigi; Legname, Giuseppe; Giaccone, Giorgio; Maria Torres, Juan; Moda, Fabio
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Two distinct conformers of PrPD type 1 of sporadic Creutzfeldt-Jakob disease with codon 129VV genotype faithfully propagate in vivo
err2021-03-25
err4
errOAAI
errCali, Ignazio; Espinosa, Juan Carlos; Nemani, Satish K.; Marin-Moreno, Alba; Camacho, Manuel V.; Aslam, Rabail; Kitamoto, Tetsuyuki; Appleby, Brian S.; Torres, Juan Maria; Gambetti, Pierluigi
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Wide distribution of prion infectivity in the peripheral tissues of vCJD and sCJD patientsvCJD和sCJD患者外周组织中病毒感染性的广泛分布
err2021-02-02
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errDouet, Jean-Yves; Huor, Alvina; Cassard, Herve; Lugan, Severine; Aron, Naima; Arnold, Mark; Vilette, Didier; Torres, Juan-Maria; Ironside, James W.; Andreoletti, Olivier
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Met166-Glu168 residues in human PrP β2-α2 loop account for evolutionary resistance to prion infection
err2020-12-22
err4
errOAAI
errCarlos Espinosa, Juan; Marin-Moreno, Alba; Aguilar-Calvo, Patricia; Maria Torres, Juan
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Prions from Sporadic Creutzfeldt-Jakob Disease Patients Propagate as Strain Mixtures来自散发性creutzfeldt-jakob病患者的病毒以菌株混合物的形式传播
errMBIO
IF4.7
err2020-06-30
err21
errOAAI
errCassard, Herve; Huor, Alvina; Espinosa, Juan-Carlos; Douet, Jean-Yves; Lugan, Severine; Aron, Naima; Vilette, Didier; Delisle, Marie-Bernadette; Marin-Moreno, Alba; Peran, Patrice; Beringue, Vincent; Maria Torres, Juan; Ironside, James W.; Andreoletti, Olivier
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