未登录 Substitution of histidine 95 by tyrosine in the prion protein causes spontaneous neurodegeneration in transgenic mice 朊病毒蛋白中组氨酸95被酪氨酸取代会导致转基因小鼠发生自发性神经退行。 Torres, Juan-Maria; Marin-Moreno, Alba; Espinosa, Juan-Carlos; Canoyra, Sara; Burato, Anna; Ciullini, Arianna; De Luca, Chiara Maria Giulia; Bistaffa, Edoardo; Moda, Fabio; Legname, Giuseppe 分享 收藏
Optimization and evaluation of new decontamination procedures inactivating human prions 新型去污程序对人类朊病毒的失活优化与评估 Herzog, L.; Reine, F.; Castille, J.; Passet, B.; Moudjou, M.; Bonnet, R.; Torres, J. M.; Rezaei, H.; Vilotte, J. -L.; Beringue, V.; Igel, A. 分享 收藏
Classical BSE dismissed as the cause of CWD in Norwegian red deer despite strain similarities between both prion agents Marin-Moreno, Alba; Benestad, Sylvie L.; Barrio, Tomas; Pirisinu, Laura; Espinosa, Juan Carlos; Tran, Linh; Huor, Alvina; Di Bari, Michele Angelo; Erana, Hasier; Maddison, Ben C.; D'Agostino, Claudia; Fernandez-Borges, Natalia; Canoyra, Sara; Jerez-Garrido, Nuria; Castilla, Joaquin; Spiropoulos, John; Bishop, Keith; Gough, Kevin C.; Nonno, Romolo; Vage, Jorn; Andreoletti, Olivier; Torres, Juan Maria 分享 收藏
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Experimental transmission of ovine atypical scrapie to cattle 绵羊非典型瘙痒病对牛的实验传播 Konold, Timm; Spiropoulos, John; Hills, Janet; Abdul, Hasina; Cawthraw, Saira; Phelan, Laura; Mckenna, Amy; Read, Lauren; Canoyra, Sara; Marin-Moreno, Alba; Torres, Juan Maria 分享 收藏
An optimized Western blot assay provides a comprehensive assessment of the physiological endoproteolytic processing of the prion protein Vanni, Ilaria; Iacobone, Floriana; D'Agostino, Claudia; Giovannelli, Matteo; Pirisinu, Laura; Altmeppen, Hermann Clemens; Castilla, Joaquin; Torres, Juan Maria; Agrimi, Umberto; Nonno, Romolo 分享 收藏
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Bona fide atypical scrapie faithfully reproduced for the first time in a rodent model Vidal, Enric; Sanchez-Martin, Manuel A.; Erana, Hasier; Perez Lazaro, Sonia; Perez-Castro, Miguel A.; Otero, Alicia; Charco, Jorge M.; Marin, Belen; Lopez-Moreno, Rafael; Diaz-Dominguez, Carlos M.; Geijo, Marivi; Ordonez, Montserrat; Cantero, Guillermo; di Bari, Michele; Lorenzo, Nuria L.; Pirisinu, Laura; d'Agostino, Claudia; Maria Torres, Juan; Beringue, Vincent; Telling, Glenn; Badiola, Juan J.; Pumarola, Marti; Bolea, Rosa; Nonno, Romolo; Requena, Jesus R.; Castilla, Joaquin 分享 收藏
Glycans are not necessary to maintain the pathobiological features of bovine spongiform encephalopathy Otero, Alicia; Barrio, Tomas; Erana, Hasier; Charco, Jorge M.; Betancor, Marina; Diaz-Dominguez, Carlos M.; Marin, Belen; Andreoletti, Olivier; Torres, Juan M.; Kong, Qingzhong; Badiola, Juan J.; Bolea, Rosa; Castilla, Joaquin 分享 收藏
Homozygous R136S mutation in PRNP gene causes inherited early onset prion disease PRNP基因纯合R136S突变导致遗传性早发型朊病毒病 Ximelis, Teresa; Marin-Moreno, Alba; Carlos Espinosa, Juan; Erana, Hasier; Charco, Jorge M.; Hernandez, Isabel; Riveira, Carmen; Alcolea, Daniel; Gonzalez-Roca, Eva; Aldecoa, Iban; Molina-Porcel, Laura; Parchi, Piero; Rossi, Marcello; Castilla, Joaquin; Ruiz-Garcia, Raquel; Gelpi, Ellen; Maria Torres, Juan; Sanchez-Valle, Raquel 分享 收藏
Classical BSE prions emerge from asymptomatic pigs challenged with atypical/Nor98 scrapie Marin, Belen; Otero, Alicia; Lugan, Severine; Carlos Espinosa, Juan; Marin-Moreno, Alba; Vidal, Enric; Hedman, Carlos; Romero, Antonio; Pumarola, Marti; Badiola, Juan J.; Maria Torres, Juan; Andreoletti, Olivier; Bolea, Rosa 分享 收藏
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Allelic Interference in Prion Replication Is Modulated by the Convertibility of the Interfering PrPC and Other Host-Specific Factors Carlos Espinosa, Juan; Andreoletti, Olivier; Marin-Moreno, Alba; Lugan, Severine; Aguilar-Calvo, Patricia; Cassard, Herve; Lorenzo, Patricia; Douet, Jean-Yves; Villa-Diaz, Ana; Aron, Naima; Prieto, Irene; Huor, Alvina; Maria Torres, Juan 分享 收藏
TREM2 expression in the brain and biological fluids in prion diseases Diaz-Lucena, Daniela; Kruse, Niels; Thuene, Katrin; Schmitz, Matthias; Villar-Pique, Anna; Gomes da Cunha, Jose Eriton; Hermann, Peter; Lopez-Perez, Oscar; Andres-Benito, Pol; Ladogana, Anna; Calero, Miguel; Vidal, Enric; Riggert, Joachim; Pineau, Hailey; Sim, Valerie; Zetterberg, Henrik; Blennow, Kaj; Antonio del Rio, Jose; Marin-Moreno, Alba; Carlos Espinosa, Juan; Maria Torres, Juan; Sanchez-Valle, Raquel; Mollenhauer, Brit; Ferrer, Isidre; Zerr, Inga; Llorens, Franc 分享 收藏
Classical scrapie in small ruminants is caused by at least four different prion strains Marin-Moreno, Alba; Aguilar-Calvo, Patricia; Espinosa, Juan Carlos; Zamora-Ceballos, Maria; Pitarch, Jose Luis; Gonzalez, Lorenzo; Fernandez-Borges, Natalia; Orge, Leonor; Andreoletti, Olivier; Nonno, Romolo; Torres, Juan Maria 分享 收藏
PMCA-generated prions from the olfactory mucosa of patients with Fatal Familial Insomnia cause prion disease in mice Bistaffa, Edoardo; Marin-Moreno, Alba; Carlos Espinosa, Juan; De Luca, Chiara Maria Giulia; Cazzaniga, Federico Angelo; Portaleone, Sara Maria; Celauro, Luigi; Legname, Giuseppe; Giaccone, Giorgio; Maria Torres, Juan; Moda, Fabio 分享 收藏
Two distinct conformers of PrPD type 1 of sporadic Creutzfeldt-Jakob disease with codon 129VV genotype faithfully propagate in vivo Cali, Ignazio; Espinosa, Juan Carlos; Nemani, Satish K.; Marin-Moreno, Alba; Camacho, Manuel V.; Aslam, Rabail; Kitamoto, Tetsuyuki; Appleby, Brian S.; Torres, Juan Maria; Gambetti, Pierluigi 分享 收藏
Wide distribution of prion infectivity in the peripheral tissues of vCJD and sCJD patients vCJD和sCJD患者外周组织中病毒感染性的广泛分布 Douet, Jean-Yves; Huor, Alvina; Cassard, Herve; Lugan, Severine; Aron, Naima; Arnold, Mark; Vilette, Didier; Torres, Juan-Maria; Ironside, James W.; Andreoletti, Olivier 分享 收藏
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Prions from Sporadic Creutzfeldt-Jakob Disease Patients Propagate as Strain Mixtures 来自散发性creutzfeldt-jakob病患者的病毒以菌株混合物的形式传播 Cassard, Herve; Huor, Alvina; Espinosa, Juan-Carlos; Douet, Jean-Yves; Lugan, Severine; Aron, Naima; Vilette, Didier; Delisle, Marie-Bernadette; Marin-Moreno, Alba; Peran, Patrice; Beringue, Vincent; Maria Torres, Juan; Ironside, James W.; Andreoletti, Olivier 分享 收藏