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Juan Carlos Espinosa

consejo superior de investigaciones cientificas (csic)

31H指数
113论文数
3.8K被引数
收录论文 62
发表时间
Substitution of histidine 95 by tyrosine in the prion protein causes spontaneous neurodegeneration in transgenic mice朊病毒蛋白中组氨酸95被酪氨酸取代会导致转基因小鼠发生自发性神经退行。
err2025-10-01
err0
PREAI
errTorres, Juan-Maria; Marin-Moreno, Alba; Espinosa, Juan-Carlos; Canoyra, Sara; Burato, Anna; Ciullini, Arianna; De Luca, Chiara Maria Giulia; Bistaffa, Edoardo; Moda, Fabio; Legname, Giuseppe
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Classical BSE dismissed as the cause of CWD in Norwegian red deer despite strain similarities between both prion agents
err2024-05-15
err1
errOAAI
errMarin-Moreno, Alba; Benestad, Sylvie L.; Barrio, Tomas; Pirisinu, Laura; Espinosa, Juan Carlos; Tran, Linh; Huor, Alvina; Di Bari, Michele Angelo; Erana, Hasier; Maddison, Ben C.; D'Agostino, Claudia; Fernandez-Borges, Natalia; Canoyra, Sara; Jerez-Garrido, Nuria; Castilla, Joaquin; Spiropoulos, John; Bishop, Keith; Gough, Kevin C.; Nonno, Romolo; Vage, Jorn; Andreoletti, Olivier; Torres, Juan Maria
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Transgenic Mouse Models for the Study of Neurodegenerative Diseases
err2023-01-19
err8
errOAAI
errMarin-Moreno, Alba; Canoyra, Sara; Fernandez-Borges, Natalia; Carlos Espinosa, Juan; Maria Torres, Juan
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Homozygous R136S mutation in PRNP gene causes inherited early onset prion diseasePRNP基因纯合R136S突变导致遗传性早发型朊病毒病
err2021-10-18
err8
errOAAI
errXimelis, Teresa; Marin-Moreno, Alba; Carlos Espinosa, Juan; Erana, Hasier; Charco, Jorge M.; Hernandez, Isabel; Riveira, Carmen; Alcolea, Daniel; Gonzalez-Roca, Eva; Aldecoa, Iban; Molina-Porcel, Laura; Parchi, Piero; Rossi, Marcello; Castilla, Joaquin; Ruiz-Garcia, Raquel; Gelpi, Ellen; Maria Torres, Juan; Sanchez-Valle, Raquel
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Classical BSE prions emerge from asymptomatic pigs challenged with atypical/Nor98 scrapie
err2021-08-31
err11
errOAAI
errMarin, Belen; Otero, Alicia; Lugan, Severine; Carlos Espinosa, Juan; Marin-Moreno, Alba; Vidal, Enric; Hedman, Carlos; Romero, Antonio; Pumarola, Marti; Badiola, Juan J.; Maria Torres, Juan; Andreoletti, Olivier; Bolea, Rosa
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Canine D163-PrP polymorphic variant does not provide complete protection against prion infection in small ruminant PrP context
err2021-07-12
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errOAAI
errMarin-Moreno, Alba; Espinosa, Juan Carlos; Aguilar-Calvo, Patricia; Fernandez-Borges, Natalia; Pitarch, Jose Luis; Gonzalez, Lorenzo; Torres, Juan Maria
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Allelic Interference in Prion Replication Is Modulated by the Convertibility of the Interfering PrPC and Other Host-Specific Factors
errMBIO
IF4.7
err2021-04-27
err0
errOAAI
errCarlos Espinosa, Juan; Andreoletti, Olivier; Marin-Moreno, Alba; Lugan, Severine; Aguilar-Calvo, Patricia; Cassard, Herve; Lorenzo, Patricia; Douet, Jean-Yves; Villa-Diaz, Ana; Aron, Naima; Prieto, Irene; Huor, Alvina; Maria Torres, Juan
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TREM2 expression in the brain and biological fluids in prion diseases
err2021-04-21
err20
errOAAI
errDiaz-Lucena, Daniela; Kruse, Niels; Thuene, Katrin; Schmitz, Matthias; Villar-Pique, Anna; Gomes da Cunha, Jose Eriton; Hermann, Peter; Lopez-Perez, Oscar; Andres-Benito, Pol; Ladogana, Anna; Calero, Miguel; Vidal, Enric; Riggert, Joachim; Pineau, Hailey; Sim, Valerie; Zetterberg, Henrik; Blennow, Kaj; Antonio del Rio, Jose; Marin-Moreno, Alba; Carlos Espinosa, Juan; Maria Torres, Juan; Sanchez-Valle, Raquel; Mollenhauer, Brit; Ferrer, Isidre; Zerr, Inga; Llorens, Franc
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Classical scrapie in small ruminants is caused by at least four different prion strains
err2021-04-15
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errOAAI
errMarin-Moreno, Alba; Aguilar-Calvo, Patricia; Espinosa, Juan Carlos; Zamora-Ceballos, Maria; Pitarch, Jose Luis; Gonzalez, Lorenzo; Fernandez-Borges, Natalia; Orge, Leonor; Andreoletti, Olivier; Nonno, Romolo; Torres, Juan Maria
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PMCA-generated prions from the olfactory mucosa of patients with Fatal Familial Insomnia cause prion disease in mice
err2021-04-14
err2
errOAAI
errBistaffa, Edoardo; Marin-Moreno, Alba; Carlos Espinosa, Juan; De Luca, Chiara Maria Giulia; Cazzaniga, Federico Angelo; Portaleone, Sara Maria; Celauro, Luigi; Legname, Giuseppe; Giaccone, Giorgio; Maria Torres, Juan; Moda, Fabio
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Two distinct conformers of PrPD type 1 of sporadic Creutzfeldt-Jakob disease with codon 129VV genotype faithfully propagate in vivo
err2021-03-25
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errCali, Ignazio; Espinosa, Juan Carlos; Nemani, Satish K.; Marin-Moreno, Alba; Camacho, Manuel V.; Aslam, Rabail; Kitamoto, Tetsuyuki; Appleby, Brian S.; Torres, Juan Maria; Gambetti, Pierluigi
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GHG Balance of Agricultural Intensification & Bioenergy Production in the Orinoquia Region, Colombia
errLAND
IF3.2
err2021-03-11
err13
errOAAI
errElizabeth Ramirez-Contreras, Nidia; Munar-Florez, David; van der Hilst, Floor; Carlos Espinosa, Juan; Ocampo-Duran, Alvaro; Ruiz-Delgado, Jonathan; Molina-Lopez, Diego L.; Wicke, Birka; Alberto Garcia-Nunez, Jesus; Faaij, Andre P. C.
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Met166-Glu168 residues in human PrP β2-α2 loop account for evolutionary resistance to prion infection
err2020-12-22
err4
errOAAI
errCarlos Espinosa, Juan; Marin-Moreno, Alba; Aguilar-Calvo, Patricia; Maria Torres, Juan
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Prions from Sporadic Creutzfeldt-Jakob Disease Patients Propagate as Strain Mixtures来自散发性creutzfeldt-jakob病患者的病毒以菌株混合物的形式传播
errMBIO
IF4.7
err2020-06-30
err21
errOAAI
errCassard, Herve; Huor, Alvina; Espinosa, Juan-Carlos; Douet, Jean-Yves; Lugan, Severine; Aron, Naima; Vilette, Didier; Delisle, Marie-Bernadette; Marin-Moreno, Alba; Peran, Patrice; Beringue, Vincent; Maria Torres, Juan; Ironside, James W.; Andreoletti, Olivier
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Radical Change in Zoonotic Abilities of Atypical BSE Prion Strains as Evidenced by Crossing of Sheep Species Barrier in Transgenic Mice
err2020-06-01
err15
errOAAI
errMarin-Moreno, Alba; Huor, Alvina; Carlos Espinosa, Juan; Douet, Jean Yves; Aguilar-Calvo, Patricia; Aron, Naima; Piquer, Juan; Lugan, Severine; Lorenzo, Patricia; Tillier, Cecile; Cassard, Herve; Andreoletti, Olivier; Maria Torres, Juan
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Porcine Prion Protein as a Paradigm of Limited Susceptibility to Prion Strain Propagation (vol 52, jiz646, 2020)
err2020-03-02
err0
errOAAI
errCarlos Espinosa, Juan; Marin-Moreno, Alba; Aguilar-Calvo, Patricia; Benestad, Sylvie L.; Andreoletti, Olivier; Maria Torres, Juan
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Porcine Prion Protein as a Paradigm of Limited Susceptibility to Prion Strain Propagation
err2020-01-09
err15
errOAAI
errEspinosa, Juan Carlos; Marin-Moreno, Alba; Aguilar-Calvo, Patricia; Benestad, Sylvie L.; Andreoletti, Olivier; Torres, Juan Maria
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Characterization of goat prions demonstrates geographical variation of scrapie strains in Europe and reveals the composite nature of prion strains
err2020-01-08
err19
errOAAI
errNonno, Romolo; Marin-Moreno, Alba; Espinosa, Juan Carlos; Fast, Christine; Van Keulen, Lucien; Spiropoulos, John; Lantier, Isabelle; Andreoletti, Olivier; Pirisinu, Laura; Di Bari, Michele A.; Aguilar-Calvo, Patricia; Sklaviadis, Theodoros; Papasavva-Stylianou, Penelope; Acutis, Pier Luigi; Acin, Cristina; Bossers, Alex; Jacobs, Jorge G.; Vaccari, Gabriele; D'Agostino, Claudia; Chiappini, Barbara; Lantier, Frederic; Groschup, Martin H.; Agrimi, Umberto; Torres, Juan Maria; Langeveld, Jan P. M.
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