Ernesto R. Bongarzone - Publications, H-index & Citations

Ernesto R. Bongarzone

University of Illinois System

40H指数

138论文数

4.5K被引数

收录论文 50

发表时间

Secondary accumulation of lyso-platelet activating factors in lysosomal storage diseases 溶酶体贮积症中溶血性血小板活化因子的二次累积

Molecular Genetics and Metabolism

IF3.5

2025-06-17

PREAI

Pamela Kell; Sonali Mishra; Heather L. Gray-Edwards; Douglas R. Martin; Angel Gaudioso; María Dolores Ledesma; Ernesto R. Bongarzone; Mark S. Sands; Ellen Sidransky; Daniel S. Ory; Xuntian Jiang

Secondary accumulation of lyso-platelet activating factors in lysosomal diseases

MOLECULAR GENETICS AND METABOLISM

IF3.5

2025-02-01

PREAI

Jiang, Xuntian; Kell, Pamela; Mishra, Sonali; Gray-Edwards, Heather; Bongarzone, Ernesto R.; Sands, Mark; Martin, Douglas R.

Deficiency of galactosyl-ceramidase in adult oligodendrocytes worsens disease severity during chronic experimental allergic encephalomyelitis

MOLECULAR THERAPY

IF12

2024-09-01

OAAI

Saldivia, Natalia; Heller, Gregory; Zelada, Diego; Whitehair, Jason; Venkat, Nikhil; Konjeti, Ashna; Savitzky, Reina; Samano, Shayla; Simchuk, Daniel; van Breemen, Richard; Givogri, Maria I.; Bongarzone, Ernesto R.

CD8+ T cell depletion prevents neuropathology in a mouse model of globoid cell leukodystrophy

JOURNAL OF EXPERIMENTAL MEDICINE

IF10.6

2023-06-13

OAAI

Sutter, Pearl A.; Menoret, Antoine; Jellison, Evan R.; Nicaise, Alexandra M.; Bradbury, Allison M.; Vella, Anthony T.; Bongarzone, Ernesto R.; Crocker, Stephen J.

Preclinical studies in Krabbe disease: A model for the investigation of novel combination therapies for lysosomal storage diseases

MOLECULAR THERAPY

IF12

2023-01-01

OAAI

Heller, Gregory; Bradbury, Allison M.; Sands, Mark S.; Bongarzone, Ernesto R.

Tumor-targeting cell-penetrating peptide, p28, for glioblastoma imaging and therapy

FRONTIERS IN ONCOLOGY

IF3.3

2022-07-22

OAAI

Mander, Sunam; Naffouje, Samer A.; Gao, Jin; Li, Weiguo; Christov, Konstantin; Green, Albert; Bongarzone, Ernesto R.; Das Gupta, Tapas K.; Yamada, Tohru

CRISPR-Cas9 Knock-In of T513M and G41S Mutations in the Murine β-Galactosyl-Ceramidase Gene Re-capitulates Early-Onset and Adult-Onset Forms of Krabbe Disease

FRONTIERS IN MOLECULAR NEUROSCIENCE

IF3.8

2022-05-10

OAAI

Rebiai, Rima; Rue, Emily; Zaldua, Steve; Nguyen, Duc; Scesa, Giuseppe; Jastrzebski, Martin; Foster, Robert; Wang, Bin; Jiang, Xuntian; Tai, Leon; Brady, Scott T.; van Breemen, Richard; Givogri, Maria I.; Sands, Mark S.; Bongarzone, Ernesto R.

The Pathogenic Sphingolipid Psychosine is Secreted in Extracellular Vesicles in the Brain of a Mouse Model of Krabbe Disease

ASN NEURO

IF3.7

2022-03-18

OAAI

Reiter, Cory R.; Rebiai, Rima; Kwak, Angelika; Marshall, Jeff; Wozniak, Dylan; Scesa, Giusepe; Nguyen, Duc; Rue, Emily; Pathmasiri, Chandimal; Pijewski, Robert; van Breemen, Richard; Cologna, Stephanie; Crocker, Stephen J.; Givogri, M. Irene; Bongarzone, Ernesto R.

Waning efficacy in a long-term AAV-mediated gene therapy study in the murine model of Krabbe disease

MOLECULAR THERAPY

IF12

2021-05-01

OAAI

Heller, Gregory J.; Marshall, Michael S.; Issa, Yazan; Marshall, Jeffrey N.; Nguyen, Duc; Rue, Emily; Pathmasiri, Koralege C.; Domowicz, Miriam S.; van Breemen, Richard B.; Tai, Leon M.; Cologna, Stephanie M.; Crocker, Stephen J.; Givogri, Maria, I; Sands, Mark S.; Bongarzone, Ernesto R.

Synaptic Function and Dysfunction in Lysosomal Storage Diseases

FRONTIERS IN CELLULAR NEUROSCIENCE

IF4

2021-03-04

OAAI

Rebiai, Rima; Givogri, Maria I.; Gowrishankar, Swetha; Cologna, Stephania M.; Alford, Simon T.; Bongarzone, Ernesto R.

AAV-Mediated GALC Gene Therapy Rescues Alpha-Synucleinopathy in the Spinal Cord of a Leukodystrophic Lysosomal Storage Disease Mouse Model

FRONTIERS IN CELLULAR NEUROSCIENCE

IF4

2020-12-23

OAAI

Marshall, Michael S.; Issa, Yazan; Heller, Gregory; Nguyen, Duc; Bongarzone, Ernesto R.

Deregulation of signalling in genetic conditions affecting the lysosomal metabolism of cholesterol and galactosyl-sphingolipids

NEUROBIOLOGY OF DISEASE

IF5.6

2020-12-01

OAAI

Gowrishankar, S.; Cologna, S. M.; Givogri, M. I.; Bongarzone, E. R.

Brainstem development requires galactosylceramidase and is critical for pathogenesis in a model of Krabbe disease

NATURE COMMUNICATIONS

IF15.7

2020-10-23

OAAI

Weinstock, Nadav, I; Kreher, Conlan; Favret, Jacob; Nguyen, Duc; Bongarzone, Ernesto R.; Wrabetz, Lawrence; Feltri, M. Laura; Shin, Daesung

Krabbe disease successfully treated via monotherapy of intrathecal gene therapy

JOURNAL OF CLINICAL INVESTIGATION

IF13.6

2020-08-10

OAAI

Bradbury, Allison M.; Bagel, Jessica H.; Duc Nguyen; Lykken, Erik A.; Salvador, Jill Pesayco; Jiang, Xuntian; Swain, Gary P.; Assenmacher, Charles A.; Hendricks, Ian J.; Miyadera, Keiko; Hess, Rebecka S.; Ostrager, Arielle; ODonnell, Patricia; Sands, Mark S.; Ory, Daniel S.; Shelton, G. Diane; Bongarzone, Ernesto R.; Gray, Steven J.; Vite, Charles H.

Mass spectrometry imaging and LC/MS reveal decreased cerebellar phosphoinositides in Niemann-Pick type C1-null mice[S]

JOURNAL OF LIPID RESEARCH

IF4.1

2020-07-01

OAAI

Pathmasiri, Koralege C.; Pergande, Melissa R.; Tobias, Fernando; Rebiai, Rima; Rosenhouse-Dantsker, Avia; Bongarzone, Ernesto R.; Cologna, Stephanie M.

Macrophages Expressing GALC Improve Peripheral Krabbe Disease by a Mechanism Independent of Cross-Correction

NEURON

IF15

2020-07-01

OAAI

Weinstock, Nadav I.; Shin, Daesung; Dhimal, Narayan; Hong, Xinying; Irons, Eric E.; Silvestri, Nicholas J.; Reed, Chelsey B.; Duc Nguyen; Sampson, Oliver; Cheng, Yung-Chih; Lau, Joseph T. Y.; Bongarzone, Ernesto R.; Kofler, Julia; Escolar, Maria L.; Gelb, Michael H.; Wrabetz, Lawrence; Feltri, M. Laura

Lead Optimization of Benzoxazolone Carboxamides as Orally Bioavailable and CNS Penetrant Acid Ceramidase Inhibitors

JOURNAL OF MEDICINAL CHEMISTRY

IF6.8

2020-03-16

OAAI

Di Martino, Simona; Tardia, Piero; Cilibrasi, Vincenzo; Caputo, Samantha; Mazzonna, Marco; Russo, Debora; Penna, Ilaria; Realini, Natalia; Margaroli, Natasha; Migliore, Marco; Pizzirani, Daniela; Ottonello, Giuliana; Bertozzi, Sine Mandrup; Armirotti, Andrea; Duc Nguyen; Sun, Ying; Bongarzone, Ernesto R.; Lansbury, Peter; Liu, Min; Skerlj, Renato; Scarpelli, Rita

Astrocyte Support for Oligodendrocyte Differentiation can be Conveyed via Extracellular Vesicles but Diminishes with Age

SCIENTIFIC REPORTS

IF3.9

2020-01-21

OAAI

Willis, Cory M.; Nicaise, Alexandra M.; Bongarzone, Ernesto R.; Givogri, Maria; Reiter, Cory R.; Heintz, Olivia; Jellison, Evan R.; Sutter, Pearl A.; TeHennepe, Gregg; Ananda, Guruprasad; Vella, Anthony T.; Crocker, Stephen J.

The Role of Vesicle Trafficking and Release in Oligodendrocyte Biology

NEUROCHEMICAL RESEARCH

IF3.8

2019-11-28

OAAI

Reiter, Cory R.; Bongarzone, Ernesto R.

Extracellular vesicle fibrinogen induces encephalitogenic CD8+T cells in a mouse model of multiple sclerosis

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

IF9.1

2019-05-08

OAAI

Willis, Cory M.; Nicaise, Alexandra M.; Menoret, Antoine; Ryu, Jae Kyu; Mendiola, Andrew S.; Jellison, Evan R.; Givogri, Maria I.; Han, David K.; Bongarzone, Ernesto R.; Akassoglou, Katerina; Vella, Anthony T.; Crocker, Stephen J.

研究方向