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Ernesto R. Bongarzone

University of Illinois System

40H指数
138论文数
4.5K被引数
收录论文 50
发表时间
Secondary accumulation of lyso-platelet activating factors in lysosomal storage diseases溶酶体贮积症中溶血性血小板活化因子的二次累积
err2025-06-17
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PREAI
errPamela Kell; Sonali Mishra; Heather L. Gray-Edwards; Douglas R. Martin; Angel Gaudioso; María Dolores Ledesma; Ernesto R. Bongarzone; Mark S. Sands; Ellen Sidransky; Daniel S. Ory; Xuntian Jiang
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Secondary accumulation of lyso-platelet activating factors in lysosomal diseases
err2025-02-01
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PREAI
errJiang, Xuntian; Kell, Pamela; Mishra, Sonali; Gray-Edwards, Heather; Bongarzone, Ernesto R.; Sands, Mark; Martin, Douglas R.
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Deficiency of galactosyl-ceramidase in adult oligodendrocytes worsens disease severity during chronic experimental allergic encephalomyelitis
err2024-09-01
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errOAAI
errSaldivia, Natalia; Heller, Gregory; Zelada, Diego; Whitehair, Jason; Venkat, Nikhil; Konjeti, Ashna; Savitzky, Reina; Samano, Shayla; Simchuk, Daniel; van Breemen, Richard; Givogri, Maria I.; Bongarzone, Ernesto R.
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CD8+ T cell depletion prevents neuropathology in a mouse model of globoid cell leukodystrophy
err2023-06-13
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errOAAI
errSutter, Pearl A.; Menoret, Antoine; Jellison, Evan R.; Nicaise, Alexandra M.; Bradbury, Allison M.; Vella, Anthony T.; Bongarzone, Ernesto R.; Crocker, Stephen J.
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Tumor-targeting cell-penetrating peptide, p28, for glioblastoma imaging and therapy
err2022-07-22
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errOAAI
errMander, Sunam; Naffouje, Samer A.; Gao, Jin; Li, Weiguo; Christov, Konstantin; Green, Albert; Bongarzone, Ernesto R.; Das Gupta, Tapas K.; Yamada, Tohru
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CRISPR-Cas9 Knock-In of T513M and G41S Mutations in the Murine β-Galactosyl-Ceramidase Gene Re-capitulates Early-Onset and Adult-Onset Forms of Krabbe Disease
err2022-05-10
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errOAAI
errRebiai, Rima; Rue, Emily; Zaldua, Steve; Nguyen, Duc; Scesa, Giuseppe; Jastrzebski, Martin; Foster, Robert; Wang, Bin; Jiang, Xuntian; Tai, Leon; Brady, Scott T.; van Breemen, Richard; Givogri, Maria I.; Sands, Mark S.; Bongarzone, Ernesto R.
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The Pathogenic Sphingolipid Psychosine is Secreted in Extracellular Vesicles in the Brain of a Mouse Model of Krabbe Disease
err2022-03-18
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errOAAI
errReiter, Cory R.; Rebiai, Rima; Kwak, Angelika; Marshall, Jeff; Wozniak, Dylan; Scesa, Giusepe; Nguyen, Duc; Rue, Emily; Pathmasiri, Chandimal; Pijewski, Robert; van Breemen, Richard; Cologna, Stephanie; Crocker, Stephen J.; Givogri, M. Irene; Bongarzone, Ernesto R.
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Waning efficacy in a long-term AAV-mediated gene therapy study in the murine model of Krabbe disease
err2021-05-01
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errOAAI
errHeller, Gregory J.; Marshall, Michael S.; Issa, Yazan; Marshall, Jeffrey N.; Nguyen, Duc; Rue, Emily; Pathmasiri, Koralege C.; Domowicz, Miriam S.; van Breemen, Richard B.; Tai, Leon M.; Cologna, Stephanie M.; Crocker, Stephen J.; Givogri, Maria, I; Sands, Mark S.; Bongarzone, Ernesto R.
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Synaptic Function and Dysfunction in Lysosomal Storage Diseases
err2021-03-04
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errOAAI
errRebiai, Rima; Givogri, Maria I.; Gowrishankar, Swetha; Cologna, Stephania M.; Alford, Simon T.; Bongarzone, Ernesto R.
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Brainstem development requires galactosylceramidase and is critical for pathogenesis in a model of Krabbe disease
err2020-10-23
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errOAAI
errWeinstock, Nadav, I; Kreher, Conlan; Favret, Jacob; Nguyen, Duc; Bongarzone, Ernesto R.; Wrabetz, Lawrence; Feltri, M. Laura; Shin, Daesung
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Krabbe disease successfully treated via monotherapy of intrathecal gene therapy
err2020-08-10
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errOAAI
errBradbury, Allison M.; Bagel, Jessica H.; Duc Nguyen; Lykken, Erik A.; Salvador, Jill Pesayco; Jiang, Xuntian; Swain, Gary P.; Assenmacher, Charles A.; Hendricks, Ian J.; Miyadera, Keiko; Hess, Rebecka S.; Ostrager, Arielle; ODonnell, Patricia; Sands, Mark S.; Ory, Daniel S.; Shelton, G. Diane; Bongarzone, Ernesto R.; Gray, Steven J.; Vite, Charles H.
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Mass spectrometry imaging and LC/MS reveal decreased cerebellar phosphoinositides in Niemann-Pick type C1-null mice[S]
err2020-07-01
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errOAAI
errPathmasiri, Koralege C.; Pergande, Melissa R.; Tobias, Fernando; Rebiai, Rima; Rosenhouse-Dantsker, Avia; Bongarzone, Ernesto R.; Cologna, Stephanie M.
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Macrophages Expressing GALC Improve Peripheral Krabbe Disease by a Mechanism Independent of Cross-Correction
errNEURON
IF15
err2020-07-01
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errOAAI
errWeinstock, Nadav I.; Shin, Daesung; Dhimal, Narayan; Hong, Xinying; Irons, Eric E.; Silvestri, Nicholas J.; Reed, Chelsey B.; Duc Nguyen; Sampson, Oliver; Cheng, Yung-Chih; Lau, Joseph T. Y.; Bongarzone, Ernesto R.; Kofler, Julia; Escolar, Maria L.; Gelb, Michael H.; Wrabetz, Lawrence; Feltri, M. Laura
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Lead Optimization of Benzoxazolone Carboxamides as Orally Bioavailable and CNS Penetrant Acid Ceramidase Inhibitors
err2020-03-16
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errDi Martino, Simona; Tardia, Piero; Cilibrasi, Vincenzo; Caputo, Samantha; Mazzonna, Marco; Russo, Debora; Penna, Ilaria; Realini, Natalia; Margaroli, Natasha; Migliore, Marco; Pizzirani, Daniela; Ottonello, Giuliana; Bertozzi, Sine Mandrup; Armirotti, Andrea; Duc Nguyen; Sun, Ying; Bongarzone, Ernesto R.; Lansbury, Peter; Liu, Min; Skerlj, Renato; Scarpelli, Rita
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Astrocyte Support for Oligodendrocyte Differentiation can be Conveyed via Extracellular Vesicles but Diminishes with Age
err2020-01-21
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errOAAI
errWillis, Cory M.; Nicaise, Alexandra M.; Bongarzone, Ernesto R.; Givogri, Maria; Reiter, Cory R.; Heintz, Olivia; Jellison, Evan R.; Sutter, Pearl A.; TeHennepe, Gregg; Ananda, Guruprasad; Vella, Anthony T.; Crocker, Stephen J.
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Extracellular vesicle fibrinogen induces encephalitogenic CD8+T cells in a mouse model of multiple sclerosis
err2019-05-08
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errOAAI
errWillis, Cory M.; Nicaise, Alexandra M.; Menoret, Antoine; Ryu, Jae Kyu; Mendiola, Andrew S.; Jellison, Evan R.; Givogri, Maria I.; Han, David K.; Bongarzone, Ernesto R.; Akassoglou, Katerina; Vella, Anthony T.; Crocker, Stephen J.
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