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收藏PPAR Gamma Agonist Leriglitazone Recovers Alterations Due to Pank2-Deficiency in hiPS-Derived Astrocytes
Santambrogio, Paolo; Cozzi, Anna; Di Meo, Ivano; Cavestro, Chiara; Vergara, Cristina; Rodriguez-Pascau, Laura; Martinell, Marc; Pizcueta, Pilar; Tiranti, Valeria; Levi, Sonia
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收藏Massive iron accumulation in PKAN-derived neurons and astrocytes: light on the human pathological phenotype
Santambrogio, Paolo; Ripamonti, Maddalena; Cozzi, Anna; Raimondi, Marzia; Cavestro, Chiara; Di Meo, Ivano; Rubio, Alicia; Taverna, Stefano; Tiranti, Valeria; Levi, Sonia
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收藏The relevance of mitochondrial DNA variants fluctuation during reprogramming and neuronal differentiation of human iPSCs
Palombo, Flavia; Peron, Camille; Caporali, Leonardo; Iannielli, Angelo; Maresca, Alessandra; Di Meo, Ivano; Fiorini, Claudio; Segnali, Alice; Sciacca, Francesca L.; Rizzo, Ambra; Levi, Sonia; Suomalainen, Anu; Prigione, Alessandro; Broccoli, Vania; Carelli, Valerio; Tiranti, Valeria
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收藏Stem Cell Modeling of Neuroferritinopathy Reveals Iron as a Determinant of Senescence and Ferroptosis during Neuronal Aging
Cozzi, Anna; Orellana, Daniel I.; Santambrogio, Paolo; Rubio, Alicia; Cancellieri, Cinzia; Giannelli, Serena; Ripamonti, Maddalena; Taverna, Stefano; Di Lullo, Giulia; Rovida, Ermanna; Ferrari, Maurizio; Forni, Gian Luca; Fiorillo, Chiara; Broccoli, Vania; Levi, Sonia
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收藏Mitochondrial Ferritin Is a Hypoxia-Inducible Factor 1α-Inducible Gene That Protects from Hypoxia-Induced Cell Death in Brain线粒体铁蛋白是一种缺氧诱导因子1α 诱导的基因,可保护大脑免受缺氧诱导的细胞死亡
Wu, Qiong; Wu, Wen-Shuang; Su, Lin; Zheng, Xin; Wu, Wen-Yue; Santambrogio, Paolo; Gou, Yu-Jing; Hao, Qian; Wang, Pei-Na; Li, Ya-Ru; Zhao, Bao-Lu; Nie, Guangjun; Levi, Sonia; Chang, Yan-Zhong
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收藏Peroxiredoxin-2: A Novel Regulator of Iron Homeostasis in Ineffective Erythropoiesis
Matte, Alessandro; De Falco, Luigia; Federti, Enrica; Cozzi, Anna; Iolascon, Achille; Levi, Sonia; Mohandas, Narla; Zamo, Alberto; Bruno, Mariasole; Lebouef, Christophe; Janin, Anne; Siciliano, Angela; Ganz, Tom; Federico, Giorgia; Carlomagno, Francesca; Mueller, Sebastian; Silva, Ines; Carbone, Carmine; Melisi, Davide; Kim, Dae Won; Choi, Soo Young; De Franceschi, Lucia
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收藏Peroxiredoxin-2 plays a pivotal role as multimodal cytoprotector in the early phase of pulmonary hypertension
Federti, Enrica; Matte, Alessandro; Ghigo, Alessandra; Andolfo, Immacolata; James, Cimino; Siciliano, Angela; Leboeuf, Christophe; Janin, Anne; Manna, Francesco; Choi, Soo Young; Iolascon, Achille; Beneduce, Elisabetta; Melisi, Davide; Kim, Dae Won; Levi, Sonia; De Franceschi, Lucia
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收藏Unexplained isolated hyperferritinemia without iron overload
Ravasi, Giulia; Pelucchi, Sara; Mariani, Raffaella; Casati, Marco; Greni, Federico; Arosio, Cristina; Pelloni, Irene; Majore, Silvia; Santambrogio, Paolo; Levi, Sonia; Piperno, Alberto
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收藏Coenzyme A corrects pathological defects in human neurons of PANK2-associated neurodegeneration
Orellana, Daniel I.; Santambrogio, Paolo; Rubio, Alicia; Yekhlef, Latefa; Cancellieri, Cinzia; Dusi, Sabrina; Giannelli, Serena G.; Venco, Paola; Mazzara, Pietro G.; Cozzi, Anna; Ferrari, Maurizio; Garavaglia, Barbara; Taverna, Stefano; Tiranti, Valeria; Broccoli, Vania; Levi, Sonia
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