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Didier Dulon

centre national de la recherche scientifique (cnrs)

39H指数
110论文数
4.0K被引数
收录论文 16
发表时间
Compensatory Interplay Between Clarin-1 and Clarin-2 Deafness-Associated Proteins Governs Phenotypic Variability in Hearing (Adv. Sci. 20/2026)Clarin-1和Clarin-2耳聋相关蛋白间的补偿性相互作用调控听力的表型可变性
err2026-04-10
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errMaureen Wentling; Aïda Yakhlef Sanchez; Nicolas Thelen; Müge Senarisoy; Maria Hogg; Steven Condamine; Andrea Lelli; Emilia Wysocka; Pranav Patni; Sandrine Vitry; Kerem Yasin Yildizhan; Sébastien Le Gal; Sylvie Nouaille; Michael R. Bowl; Marc Thiry; Didier Dulon; Sedigheh Delmaghani; Aziz El-Amraoui
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Compensatory Interplay Between Clarin-1 and Clarin-2 Deafness-Associated Proteins Governs Phenotypic Variability in Hearing
err2026-01-22
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errMaureen Wentling; Aïda Yakhlef Sanchez; Nicolas Thelen; Müge Senarisoy; Maria Hogg; Steven Condamine; Andrea Lelli; Emilia Wysocka; Pranav Patni; Sandrine Vitry; Kerem Yasin Yildizhan; Sébastien Le Gal; Sylvie Nouaille; Michael R. Bowl; Marc Thiry; Didier Dulon; Sedigheh Delmaghani; Aziz El-Amraoui
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A free intravesicular C-terminal of otoferlin is essential for synaptic vesicle docking and fusion at auditory inner hair cell ribbon synapses
err2024-09-01
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errDulon, Didier; de Monvel, Jacques Boutet; Plion, Baptiste; Mallet, Adeline; Petit, Christine; Condamine, Steven; Bouleau, Yohan; Safieddine, Saaid
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Clarin-2 gene supplementation durably preserves hearing in a model of progressive hearing loss
err2024-03-01
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errMendia, Clara; Peineau, Thibault; Zamani, Mina; Felgerolle, Chloe; Yahiaoui, Nawal; Christophersen, Nele; Papal, Samantha; Maudoux, Audrey; Maroo, Reza; Patni, Pranav; Nouaille, Sylvie; Bowl, Michael R.; Delmaghani, Sedigheh; Galehdari, Hamid; Vona, Barbara; Dulon, Didier; Vitry, Sandrine; El-Amraoui, Aziz
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Synaptic Release Potentiation at Aging Auditory Ribbon Synapses
err2021-10-18
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errPeineau, Thibault; Belleudy, Severin; Pietropaolo, Susanna; Bouleau, Yohan; Dulon, Didier
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Clarin-2 is essential for hearing by maintaining stereocilia integrity and function
err2019-08-26
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errDunbar, Lucy A.; Patni, Pranav; Aguilar, Carlos; Mburu, Philomena; Corns, Laura; Wells, Helena R. R.; Delmaghani, Sedigheh; Parker, Andrew; Johnson, Stuart; Williams, Debbie; Esapa, Christopher T.; Simon, Michelle M.; Chessum, Lauren; Newton, Sherylanne; Dorning, Joanne; Jeyarajan, Prashanthini; Morse, Susan; Lelli, Andrea; Codner, Gemma F.; Peineau, Thibault; Gopal, Suhasini R.; Alagramam, Kumar N.; Hertzano, Ronna; Dulon, Didier; Wells, Sara; Williams, Frances M.; Petit, Christine; Dawson, Sally J.; Brown, Steve D. M.; Marcotti, Walter; El-Amraoui, Aziz; Bowl, Michael R.
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Clustered Ca2+ Channels Are Blocked by Synaptic Vesicle Proton Release at Mammalian Auditory Ribbon Synapses
err2018-12-01
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errVincent, Philippe F. Y.; Cho, Soyoun; Tertrais, Margot; Bouleau, Yohan; von Gersdorff, Henrique; Dulon, Didier
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Clarin-1 gene transfer rescues auditory synaptopathy in model of Usher syndrome
err2018-07-09
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errDulon, Didier; Papal, Samantha; Patni, Pranav; Cortese, Matteo; Vincent, Philippe F. Y.; Tertrais, Margot; Emptoz, Alice; Tlili, Abdelaziz; Bouleau, Yohan; Michel, Vincent; Delmaghani, Sedigheh; Aghaie, Alain; Pepermans, Elise; Alegria-Prevot, Olinda; Akil, Omar; Lustig, Lawrence; Avan, Paul; Safieddine, Saaid; Petit, Christine; El-Amraoui, Aziz
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Otoferlin acts as a Ca2+ sensor for vesicle fusion and vesicle pool replenishment at auditory hair cell ribbon synapses
err2017-11-07
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errMichalski, Nicolas; Goutman, Juan D.; Auclair, Sarah Marie; de Monvel, Jacques Boutet; Tertrais, Margot; Emptoz, Alice; Parrin, Alexandre; Nouaille, Sylvie; Guillon, Marc; Sachse, Martin; Ciric, Danica; Bahloul, Amel; Hardelin, Jean-Pierre; Sutton, Roger Bryan; Avan, Paul; Krishnakumar, Shyam S.; Rothman, James E.; Dulon, Didier; Safieddine, Saaid; Petit, Christine
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Local gene therapy durably restores vestibular function in a mouse model of Usher syndrome type 1G在1g型Usher综合征小鼠模型中,局部基因治疗可持久恢复前庭功能
err2017-08-23
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errEmptoz, Alice; Michel, Vincent; Lelli, Andrea; Akil, Omar; de Monvel, Jacques Boutet; Lahlou, Ghizlene; Meyer, Anais; Dupont, Typhaine; Nouaille, Sylvie; Ey, Elody; de Barros, Filipa Franca; Beraneck, Mathieu; Dulon, Didier; Hardelin, Jean-Pierre; Lustig, Lawrence; Avan, Paul; Petit, Christine; Safieddine, Saaid
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A synaptic F-actin network controls otoferlin-dependent exocytosis in auditory inner hair cells
err2015-11-14
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errVincent, Philippe F. Y.; Bouleau, Yohan; Petit, Christine; Dulon, Didier
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