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收藏Estrogen-related receptor gamma is a regulator of mitochondrial, autophagy, and immediate-early gene programs in spiny projection neurons: Relevance for transcriptional changes in Huntington disease
Fox, Stephanie N.; Savage, Cody H.; Amireddy, Narcy R.; Mcmeekin, Laura J.; Crossman, David K.; Detloff, Peter J.; Gray, Michelle; Cowell, Rita M.
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收藏Uninterrupted CAG repeat drives striatum-selective transcriptionopathy and nuclear pathogenesis in human Huntingtin BAC mice
Gu, Xiaofeng; Richman, Jeffrey; Langfelder, Peter; Wang, Nan; Zhang, Shasha; Banez-Coronel, Monica; Wang, Huei-Bin; Yang, Lucia; Ramanathan, Lalini; Deng, Linna; Park, Chang Sin; Choi, Christopher R.; Cantle, Jeffrey P.; Gao, Fuying; Gray, Michelle; Coppola, Giovanni; Bates, Gillian P.; Ranum, Laura P. W.; Horvath, Steve; Colwell, Christopher S.; Yang, X. William
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收藏Progressive cardiac arrhythmias and ECG abnormalities in the Huntington's disease BACHD mouse model
Zhu, Yujie; Shamblin, Isaac; Rodriguez, Efrain; Salzer, Grace E.; Araysi, Lita; Margolies, Katherine A.; Halade, Ganesh, V; Litovsky, Silvio H.; Pogwizd, Steven; Gray, Michelle; Huke, Sabine
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收藏Neuronal targets for reducing mutant huntingtin expression to ameliorate disease in a mouse model of Huntington's disease
Wang, Nan; Gray, Michelle; Lu, Xiao-Hong; Cantle, Jeffrey P.; Holley, Sandra M.; Greiner, Erin; Gu, Xiaofeng; Shirasaki, Dyna; Cepeda, Carlos; Li, Yuqing; Dong, Hongwei; Levine, Michael S.; Yang, X. William
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收藏Identifying polyglutamine protein species in situ that best predict neurodegeneration (vol 7, pg 925, 2011)
Miller, Jason; Arrasate, Montserrat; Brooks, Elizabeth; Libeu, Clare Peters; Legleiter, Justin; Hatters, Danny; Curtis, Jessica; Cheung, Kenneth; Krishnan, Preethi; Mitra, Siddhartha; Widjaja, Kartika; Shaby, Benjamin A.; Lotz, Gregor P.; Newhouse, Yvonne; Mitchell, Emily J.; Osmand, Alex; Gray, Michelle; Thulasiramin, Vanitha; Saudou, Frederic; Segal, Mark; Yang, X. William; Masliah, Eliezer; Thompson, Leslie M.; Muchowski, Paul J.; Weisgraber, Karl H.; Finkbeiner, Steven
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收藏Identifying polyglutamine protein species in situ that best predict neurodegeneration
Miller, Jason; Arrasate, Montserrat; Brooks, Elizabeth; Libeu, Clare Peters; Legleiter, Justin; Hatters, Danny; Curtis, Jessica; Cheung, Kenneth; Krishnan, Preethi; Mitra, Siddhartha; Widjaja, Kartika; Shaby, Benjamin A.; Lotz, Gregor P.; Newhouse, Yvonne; Mitchell, Emily J.; Osmand, Alex; Gray, Michelle; Thulasiramin, Vanitha; Saudou, Frederic; Segal, Mark; Yang, X. William; Masliah, Eliezer; Thompson, Leslie M.; Muchowski, Paul J.; Weisgraber, Karl H.; Finkbeiner, Steven
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收藏Puromycin-sensitive aminopeptidase (PSA/NPEPPS) impedes development of neuropathology in hPSA/TAUP301L double-transgenic mice
Kudo, Lili C.; Parfenova, Liubov; Ren, Guijie; Vi, Nancy; Hui, Maria; Ma, Zhongcai; Lau, Kimbley; Gray, Michelle; Bardag-Gorce, Fawzia; Wiedau-Pazos, Martina; Hui, Koon-Sea; Karsten, Stanislav L.
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收藏ACCUMULATION AND AGGREGATION OF HUMAN MUTANT HUNTINGTIN AND NEURON ATROPHY IN BAC-HD TRANSGENIC RAT
Yu, L.; Metzger, S.; Clemens, L. E.; Ehrismann, J.; Ott, T.; Gu, X.; Gray, M.; Yang, W.; Osmand, A. P.; Riess, O.; Nguyen, H. P.
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