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Estella M. Alonso

ann and robert h. lurie children's hospital

63H指数
325论文数
1.2W被引数
收录论文 110
发表时间
Lack of clinical change in longitudinal vibration controlled transient elastography among children with cystic fibrosis and poor association with non-invasive biomarkers of liver disease囊性纤维化儿童中纵向振动控制瞬时弹性成像的临床变化缺乏及与非侵入性肝病生物标志物的关联性差
err2026-04-15
err0
PREAI
errWen Ye; Suiyuan Huang; Molly Bozic; Boaz Karmazyn; Roger Harned; Daniel H. Leung; Prakash Masand; Adina Alazraki; Simon C. Ling; Oscar M. Navarro; Nicole Green; Randolph K Otto; Joseph J Palermo; Alexander J Towbin; Estella M Alonso; Jennifer L. Nicholas; John C. Magee; Michael R Narkewicz; A. Jay Freeman
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CD8 TRM-like T cells expressing perforin and IFN-γ define a pediatric activated T-cell acute liver failure endotype表达穿孔素和IFN-γ的CD8 TRM样T细胞定义了一种儿科活化T细胞急性肝功能衰竭表型
err2026-03-31
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errOAAI
errDiamond, Tamir; Chapin, Catherine A.; Diorio, Caroline J.; McCuaig, Sarah; Lau, Michelle; Chu, Niansheng; Gibson, Nora M.; Kreiger, Portia A.; Horslen, Simon; Loomes, Kathleen M.; Banc-Husu, Anna M.; Chu, Jaime; Jensen, M. Kyle; Leung, Daniel H.; Narang, Amrita; Carter, Beth A.; Elisofon, Scott; Fischer, Ryan; Lobritto, Steven J.; Leonis, Mike; Peters, Anna L.; Rodriguez-Baez, Norberto; Romero, Rene; Rosenthal, Philip; Rudnick, David; Squires, James; Sundaram, Shikha; Tolliver, Kyla M.; Valentino, Pamela; Durkalski, Valerie; Alonso, Estella M.; Behrens, Edward M.
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Defining a Histologic Scoring System for Gestational Alloimmune Liver Disease定义妊娠同种免疫性肝病组织学评分系统
err2025-12-01
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PREAI
errConover, Katie R.; Saul, Samantha; Chapin, Catherine A.; Alonso, Estella M.; Gupta, Anita; Bodmer, Jenna L.; Lovell, Mark; Melin-Aldana, Hector; Taylor, Sarah A.
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Impact of elexacaftor/tezacaftor/ivacaftor on biomarkers of cystic fibrosis hepatobiliary involvement in the PUSH study在PUSH研究中,elexacaftor/tezacaftor/ivacaftor对囊性纤维化肝胆受累生物标志物的影响
err2025-11-01
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PREAI
errYe, Wen; Magee, John C.; Huang, Suiyuan; Leung, Daniel H.; Bozic, Molly; Stoll, Janis; C Ling, Simon; Paranjape, Shruti M.; Karnsakul, Wikrom; Jay Freeman, A.; Schwarzenberg, Sarah Jane; Palermo, Joseph; Alonso, Estella; Green, Nicole; Masand, Prakash; Karmazyn, Boaz; Harned, Roger; Navarro, Oscar M.; Siegel, Marilyn J.; Towbin, Alex; Alazraki, Adina; Otto, Randolph K.; Nicholas, Jennifer L.; Narkewicz, Michael R.
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Increased serum GM-CSF at diagnosis of biliary atresia is associated with improved biliary drainage
err2025-01-29
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PREAI
errTaylor, Sarah A.; Harpavat, Sanjiv; Gromer, Kyle D.; Andreev, Victor; Loomes, Kathleen M.; Bezerra, Jorge A.; Jarasvaraparn, Chaowapong; Wang, Kasper; Horslen, Simon; Rosenthal, Philip; Teckman, Jeffrey; Valentino, Pamela L.; Ng, Vicky L.; Karpen, Saul J.; Sokol, Ronald J.; Alonso, Estella M.; Mack, Cara L.
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Diagnostic accuracy of serum matrix metalloproteinase-7 as a biomarker of biliary atresia in a large North American cohort在北美大型队列中,血清基质metalloproteinase-7作为胆道闭锁的生物标志物的诊断准确性
err2024-03-06
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errOAAI
errPandurangi, Sindhu; Mourya, Reena; Nalluri, Shreya; Fei, Lin; Dong, Shun; Harpavat, Sanjiv; Guthery, Stephen L.; Molleston, Jean P.; Rosenthal, Philip; Sokol, Ronald J.; Wang, Kasper S.; Ng, Vicky; Alonso, Estella M.; Hsu, Evelyn K.; Karpen, Saul J.; Loomes, Kathleen M.; Magee, John C.; Shneider, Benjamin L.; Horslen, Simon P.; Teckman, Jeffrey H.; Bezerra, Jorge A.
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Protein biomarkers GDF15 and FGF21 to differentiate mitochondrial hepatopathies from other pediatric liver diseases
err2024-01-01
err7
PREAI
errVan Hove, Johan L. K.; Friederich, Marisa W.; Strode, Dana K.; Van Hove, Roxanne A.; Miller, Kristen R.; Sharma, Rohit; Shah, Hardik; Estrella, Jane; Gabel, Linda; Horslen, Simon; Kohli, Rohit; Lovell, Mark A.; Miethke, Alexander G.; Molleston, Jean P.; Romero, Rene; Squires, James E.; Alonso, Estella M.; Guthery, Stephen L.; Kamath, Binita M.; Loomes, Kathleen M.; Rosenthal, Philip; Mysore, Krupa R.; Cavallo, Laurel A.; Valentino, Pamela L.; Magee, John C.; Sundaram, Shikha S.; Sokol, Ronald J.
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Immunosuppression-Free Life after Pediatric Liver Transplant: A Case-Control Study from the Society of Pediatric Liver Transplant (SPLIT) Registry
err2024-01-01
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PREAI
errKortbeek, Simone; Anderson, Sarah G.; Alonso, Estella M.; Rand, Elizabeth B.; Bucuvalas, John; Mazariegos, George V.; Campbell, Kathleen M.; Lobritto, Steven J.; Feldman, Amy G.; Mysore, Krupa R.; Anand, Ravinder; Selzner, Nazia; Ng, Vicky L.
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Immunosuppression minimization is safe and associated with good long-term success in pediatric recipients of liver transplant
err2023-11-08
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PREAI
errChapin, Catherine A.; Whitehead, Bridget; Shakhin, Victoria; Taylor, Sarah A.; Kriegermeier, Alyssa; Mohammad, Saeed; Alonso, Estella M.
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Sarcopenia is associated with osteopenia and impaired quality of life in children with genetic intrahepatic cholestatic liver disease
err2023-11-01
err4
errOAAI
errBoster, Julia M.; Goodrich, Nathan P.; Spino, Cathie; Loomes, Kathleen M.; Alonso, Estella M.; Kamath, Binita M.; Sokol, Ronald J.; Karpen, Saul; Miethke, Alexander; Shneider, Benjamin L.; Molleston, Jean P.; Kohli, Rohit; Horslen, Simon P.; Rosenthal, Philip; Valentino, Pamela L.; Teckman, Jeffrey H.; Hangartner, Thomas N.; Sundaram, Shikha S.
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Heterogeneous liver on research ultrasound identifies children with cystic fibrosis at high risk of advanced liver disease
err2023-07-01
err5
errOAAI
errSiegel, Marilyn J.; Leung, Daniel H.; Molleston, Jean P.; Ye, Wen; Paranjape, Shruti M.; Freeman, A. Jay; Palermo, Joseph J.; Stoll, Janis; Masand, Prakash; Karmazyn, Boaz; Harned, Roger; Ling, Simon C.; Navarro, Oscar M.; Karnsakul, Wikrom; Alazraki, Adina; Schwarzenberg, Sarah Jane; Towbin, Alex J.; Alonso, Estella M.; Nicholas, Jennifer L.; Green, Nicole; Otto, Randolph K.; Magee, John C.; Narkewicz, Michael R.
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Clinical spectrum and genetic causes of mitochondrial hepatopathy phenotype in children
err2023-06-01
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errOAAI
errSquires, James E.; Miethke, Alexander G.; Valencia, C. Alexander; Hawthorne, Kieran; Henn, Lisa; Van Hove, Johan L. K. H.; Squires, Robert; Bove, Kevin; Horslen, Simon; Kohli, Rohit; Molleston, Jean P.; Romero, Rene; Alonso, Estella M.; Bezerra, Jorge A.; Guthery, Stephen L.; Hsu, Evelyn; Karpen, Saul J.; Loomes, Kathleen M.; Ng, Vicky L.; Rosenthal, Philip; Mysore, Krupa; Wang, Kasper S.; Friederich, Marisa W.; Magee, John C.; Sokol, Ronald J.
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Long-term follow-up and liver outcomes in children with cystic fibrosis and nodular liver on ultrasound in a multi-center study * , **
err2023-03-01
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errOAAI
errLeung, Daniel H.; Ye, Wen; Schwarzenberg, Sarah J.; Freeman, A. Jay; Palermo, Joseph J.; Weymann, Alexander; Alonso, Estella M.; Karnsakul, Wikrom W.; Murray, Karen F.; Stoll, Janis M.; Huang, Suiyuan; Karmazyn, Boaz; Masand, Prakash; Magee, John C.; Alazraki, Adina L.; Towbin, Alexander J.; Nicholas, Jennifer L.; Green, Nicole; Otto, Randolph K.; Siegel, Marilyn J.; Ling, Simon C.; Navarro, Oscar M.; Harned, Roger K.; Narkewicz, Michael R.; Molleston, Jean P.
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Serum bile acids as a prognostic biomarker in biliary atresia following Kasai portoenterostomy
err2023-02-17
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errOAAI
errHarpavat, Sanjiv; Hawthorne, Kieran; Setchell, Kenneth D. R.; Rivas, Monica Narvaez; Henn, Lisa; Beil, Charlotte A.; Karpen, Saul J.; Ng, Vicky L.; Alonso, Estella M.; Bezerra, Jorge A.; Guthery, Stephen L.; Horslen, Simon; Loomes, Kathy M.; McKiernan, Patrick; Magee, John C.; Merion, Robert M.; Molleston, Jean P.; Rosenthal, Philip; Thompson, Richard J.; Wang, Kasper S.; Sokol, Ronald J.; Shneider, Benjamin L.
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Acute-on-chronic liver failure before liver transplantation does not impact post-transplant survival in children with biliary atresia
err2023-02-03
err2
PREAI
errBanc-Husu, Anna M.; Hall, Matt; Thurm, Cary; Whitehead, Bridget A.; Godown, Justin A.; Alonso, Estella M.
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RNA-Sequencing Analysis Identifies Etiology Specific Transcriptional Signatures in Neonatal Acute Liver Failure
err2023-02-01
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errOAAI
errSaul, Samantha A.; Chapin, Catherine A.; Malladi, Padmini; Melin-Aldana, Hector; Wechsler, Joshua B.; Alonso, Estella M.; Taylor, Sarah A.
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Genotype-phenotype relationships of truncating mutations, p.E297G and p.D482G in bile salt export pump deficiency截断突变p.E297G和p.D482G在胆汁盐输出泵缺乏症中的基因型-表型关系
err2023-02-01
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errOAAI
errFelzen, Antonia; van Wessel, Daan B. E.; Gonzales, Emmanuel; Thompson, Richard J.; Jankowska, Irena; Shneider, Benjamin L.; Sokal, Etienne; Grammatikopoulos, Tassos; Kadaristiana, Agustina; Jacquemin, Emmanuel; Spraul, Anne; Lipinski, Patryk; Czubkowski, Piotr; Rock, Nathalie; Shagrani, Mohammad; Broering, Dieter; Nicastro, Emanuele; Kelly, Deirdre; Nebbia, Gabriella; Arnell, Henrik; Fischler, Bjoern; Hulscher, Jan B. F.; Serranti, Daniele; Arikan, Cigdem; Polat, Esra; Debray, Dominique; Lacaille, Florence; Goncalves, Cristina; Hierro, Loreto; Bartolo, Gema Munoz; Mozer-Glassberg, Yael; Azaz, Amer; Brecelj, Jernej; Dezsofi, Antal; Calvo, Pier Luigi; Grabhorn, Enke; Hartleif, Steffen; van der Woerd, Wendy J.; Kamath, Binita M.; Wang, Jian-She; Li, Liting; Durmaz, Ozlem; Kerkar, Nanda; Jorgensen, Marianne Horby; Fischer, Ryan; Jimenez-Rivera, Carolina; Alam, Seema; Cananzi, Mara; Laverdure, Noemie; Ferreira, Cristina Targa; Guerrero, Felipe Ordonez; Wang, Heng; Sency, Valerie; Kim, Kyung Mo; Chen, Huey-Ling; de Carvalho, Elisa; Fabre, Alexandre; Bernabeu, Jesus Quintero; Zellos, Aglaia; Alonso, Estella M.; Sokol, Ronald J.; Suchy, Frederick J.; Loomes, Kathleen M.; McKiernan, Patrick J.; Rosenthal, Philip; Turmelle, Yumirle; Horslen, Simon; Schwarz, Kathleen; Bezerra, Jorge A.; Wang, Kasper; Hansen, Bettina E.; Verkade, Henkjan J.
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Neonates with acute liver failure have higher overall mortality but similar posttransplant outcomes as older infants
err2022-07-17
err8
errOAAI
errAntala, Swati; Whitehead, Bridget; Godown, Justin; Hall, Matt; Banc-Husu, Anna; Alonso, Estella M.; Taylor, Sarah A.
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Use of funded multicenter prospective longitudinal databases to inform clinical trials in rare diseases-Examination of cholestatic liver disease in Alagille syndrome
err2022-05-04
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errOAAI
errShneider, Benjamin L.; Kamath, Binita M.; Magee, John C.; Goodrich, Nathan P.; Loomes, Kathleen M.; Ye, Wen; Spino, Cathie; Alonso, Estella M.; Molleston, Jean P.; Bezerra, Jorge A.; Wang, Kasper S.; Karpen, Saul J.; Horslen, Simon P.; Guthery, Stephen L.; Rosenthal, Philip; Squires, Robert H.; Sokol, Ronald J.
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Impact of Genotype, Serum Bile Acids, and Surgical Biliary Diversion on Native Liver Survival in FIC1 Deficiency
err2021-07-13
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errOAAI
errvan Wessel, Daan B. E.; Thompson, Richard J.; Gonzales, Emmanuel; Jankowska, Irena; Shneider, Benjamin L.; Sokal, Etienne; Grammatikopoulos, Tassos; Kadaristiana, Agustina; Jacquemin, Emmanuel; Spraul, Anne; Lipinski, Patryk; Czubkowski, Piotr; Rock, Nathalie; Shagrani, Mohammad; Broering, Dieter; Algoufi, Talal; Mazhar, Nejat; Nicastro, Emanuele; Kelly, Deirdre; Nebbia, Gabriella; Arnell, Henrik; Fischler, Bjorn; Hulscher, Jan B. F.; Serranti, Daniele; Arikan, Cigdem; Debray, Dominique; Lacaille, Florence; Goncalves, Cristina; Hierro, Loreto; Bartolo, Gema Munoz; Mozer-Glassberg, Yael; Azaz, Amer; Brecelj, Jernej; Dezsofi, Antal; Calvo, Pier Luigi; Krebs-Schmitt, Dorothee; Hartleif, Steffen; van der Woerd, Wendy L.; Wang, Jian-She; Li, Li-Ting; Durmaz, Ozlem; Kerkar, Nanda; Jorgensen, Marianne Horby; Fischer, Ryan; Jimenez-Rivera, Carolina; Alam, Seema; Cananzi, Mara; Laverdure, Noemie; Ferreira, Cristina Targa; Ordonez, Felipe; Wang, Heng; Sency, Valerie; Kim, Kyung Mo; Chen, Huey-Ling; Carvalho, Elisa; Fabre, Alexandre; Bernabeu, Jesus Quintero; Alonso, Estella M.; Sokol, Ronald J.; Suchy, Frederick J.; Loomes, Kathleen M.; McKiernan, Patrick J.; Rosenthal, Philip; Turmelle, Yumirle; Rao, Girish S.; Horslen, Simon; Kamath, Binita M.; Rogalidou, Maria; Karnsakul, Wikrom W.; Hansen, Bettina; Verkade, Henkjan J.
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