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Saul J. Karpen

universidade federal da bahia

74H指数
322论文数
1.6W被引数
收录论文 162
发表时间
A multisociety consensus statement on a new common definition and diagnostic criteria for PSVD or NCPF
err2026-05-28
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PREAI
errVirginia Hernandez-Gea; Valerie Paradis; Maha Guindi; Venancio A. F. Alves; Amal Aqul; Eira Cerda; Sarwa Darwish Murad; Prasenjit Das; Angelo Di Giorgio; Luiz A. R. de Freitas; Tassos Grammatikopoulos; Kenichi Harada; Nelia Hernandez; Samar H. Ibrahim; Sanjay Kakar; Saul Karpen; David E. Kleiner; Necati Ormeci; Xiaolong Qi; Puja Sakhuja; Maria Isabel Schinoni; Romil Saxena; Alexandre Sayadi; Akash Shukla; Dina G. Tiniakos; Elizabeth Verna; Kerry Wong; Laure Elkrief; Christine Sempoux; Theo Heller; Pierre-Emmanuel Rautou
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A multisociety consensus statement on a new common definition and diagnostic criteria for PSVD or NCPF多学会共识声明:关于PSVD或NCPF的新共同定义和诊断标准
err2026-05-27
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errOAAI
errVirginia Hernandez-Gea; Valerie Paradis; Maha Guindi; Venancio A.F. Alves; Amal Aqul; Eira Cerda; Sarwa Darwish Murad; Prasenjit Das; Angelo Di Giorgio; Luiz A.R. de Freitas; Tassos Grammatikopoulos; Kenichi Harada; Nelia Hernandez; Samar H. Ibrahim; Sanjay Kakar; Saul Karpen; David E. Kleiner; Necati Ormeci; Xiaolong Qi; Puja Sakhuja
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A multisociety consensus statement on a new common definition and diagnostic criteria for PSVD or NCPF关于PSVD或NCPF的新的通用定义和诊断标准的多社会共识声明
err2026-05-27
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errOAAI
errVirginia Hernández-Gea; Valerie Paradis; Maha Guindi; Venancio A.F. Alves; Amal Aqul; Eira Cerda; Sarwa Darwish Murad; Prasenjit Das; Angelo Di Giorgio; Luiz A.R. de Freitas; Tassos Grammatikopoulos; Kenichi Harada; Nelia Hernandez; Samar H. Ibrahim; Sanjay Kakar; Saul Karpen; David E. Kleiner; Necati Ormeci; Xiaolong Qi; Puja Sakhuja
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A multisociety consensus statement on a new common definition and diagnostic criteria for PSVD or NCPF多学会共识声明:关于PSVD或NCPF的新共同定义和诊断标准
err2026-05-01
err0
PREAI
errHernandez-Gea, Virginia; Paradis, Valerie; Guindi, Maha; Alves, Venancio A. F.; Aqul, Amal; Cerda, Eira; Darwish Murad, Sarwa; Das, Prasenjit; Di Giorgio, Angelo; de Freitas, Luiz A. R.; Grammatikopoulos, Tassos; Harada, Kenichi; Hernandez, Nelia; Ibrahim, Samar H.; Kakar, Sanjay; Karpen, Saul; Kleiner, David E.; Ormeci, Necati; Qi, Xiaolong; Sakhuja, Puja; Schinoni, Maria Isabel; Saxena, Romil; Sayadi, Alexandre; Shukla, Akash; Tiniakos, Dina G.; Verna, Elizabeth; Wong, Kerry; Elkrief, Laure; Sempoux, Christine; Heller, Theo; Rautou, Pierre-Emmanuel
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Multi-Society Expert Panel Consensus Guidance Regarding Clinical Assessment and Clinical Trial Endpoints in Adults with Alpha-1 Antitrypsin Deficiency-Associated Liver Disease (AATD-LD)关于成人α1-抗胰蛋白酶缺乏相关肝病(AATD-LD)临床评估和临床试验终点的多学会专家小组共识指南
err2025-12-11
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PREAI
errRohit Loomba; Virginia C. Clark; Mattias Mandorfer; Marc Miravitlles; Mark Brantly; Saul J. Karpen; Aleksander Krag; Paul Y. Kwo; Don C. Rockey; Mark W. Russo; Antonio J. Sanchez; Scott Santarella; Suzanne R. Sharpton; Charlie Strange; Jeffrey H. Teckman; Alice M. Turner; Hugo E. Vargas; Pavel Strnad
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Elevated Serum Bile Acids Predict Poor Liver Outcomes in Children With Alagille Syndrome: Results From the GALA Study Group血清胆汁酸升高可预测Alagille综合征患儿的肝脏不良结局:GALA研究小组的结果
err2025-11-18
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errOAAI
errPerez, Carla Fiorella Murillo; Vandriel, Shannon M.; Gonzales, Emmanuel M.; Wang, Jian- She; Li, Li- Ting; She, Huiyu; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-miedzinska, Dorota; Jacquemin, Emmanuel; Bouligand, Jerome; D'antiga, Lorenzo; Nicastro, Emanuele; Fischler, Bjorn; Arnell, Henrik; Siew, Susan M.; Stormon, Michael; Loomes, Kathleen M.; Piccoli, David A.; Rand, Elizabeth B.; Squires, James E.; Karpen, Saul J.; Romero, Rene; Kasahara, Mureo; Onal, Zerrin; Sokal, Etienne; Demaret, Tanguy; Wiecek, Sabina; Lacaille, Florence; Debray, Dominique; Hardikar, Winita; Shankar, Sahana; Valentino, Pamela L.; Sundaram, Shikha S.; Ebel, Noelle H.; Feinstein, Jeffrey A.; Waisbourd-zinman, Orith; Lin, Henry C.; Rock, Nathalie; Verkade, Henkjan J.; Jensen, M. Kyle; Jaramillo, Catalina; Kim, Kyung Mo; Oh, Seak Hee; Brecemiclj, Jernej; Alam, Seema; Indolfi, Giuseppe; Blondet, Niviann; Fawaz, Rima; Nastasio, Silvia; Calvo, Pier Luigi; Nebbia, Gabriella; Arikan, Cigdem; Larson-nath, Catherine; Zizzo, Andreanne N.; Sandahl, Thomas Damgaard; Tzivinikos, Christos; El-koofy, Nehal M.; Elmonem, Mohamed A.; Aqul, Amal A.; Karnsakul, Wikrom; Bulut, Pinar; Kerkar, Nanda; Wolters, Victorien M.; Roberts, Amin J.; Evans, Helen M.; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Kelly, Deirdre A.; Hartley, Jane; Lee, Way Seah; Hajinicolaou, Christina; Lertudomphonwanit, Chatmanee; Fischer, Ryan T.; Bernabeu, Jesus Quintero; Quiros-Tejeira, Ruben E.; Ferreira, Cristina Targa; Carvalho, Elisa; Eshun, John; Zellos, Aglaia; Dezsofi, Antal; Pinto, Raquel Borges; Schwarz, Kathleen; Rogalidou, Maria; Garcia, Jennifer; Tamara, Maria Legarda; Beretta, Marisa; Mujawar, Quais; Santos-Silva, Ermelinda; Busoms, Cristina Molera; Lurz, Eberhard; Goncalves, Cristina; Jimenez-Rivera, Carolina; Banales, Jesus M.; Thompson, Richard J.; Hansen, Bettina E.; Kamath, Binita M.
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Prospective Multicenter Longitudinal Measurement of Liver Stiffness in School-Age Children With Cholestatic Liver Disease前瞻性多中心纵向测量学龄儿童胆汁淤积性肝病的肝脏硬度
err2025-10-01
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errOAAI
errShneider, Benjamin L.; Goodrich, Nathan P.; Ye, Wen; Molleston, Jean P.; Leung, Daniel H.; Sokol, Ronald J.; Cavallo, Laurel; Wang, Kasper; Valentino, Pamela L.; Teckman, Jeffery H.; Squires, James E.; Sundaram, Shikha S.; Rosenthal, Philip; Romero, Rene; Miethke, Alexander G.; Loomes, Kathleen M.; Kohli, Rohit; Karpen, Saul J.; Kamath, Binita M.; Jensen, M. Kyle; Bezerra, Jorge A.; Bass, Lee M.; Magee, John C.
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Plasma proteome correlations with liver stiffness in pediatric cholestasis implicate epithelial to mesenchymal transition血浆蛋白质组与儿科胆汁淤积性肝刚度的相关性涉及上皮-间质转化
err2025-09-29
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errOAAI
errShneider, Benjamin L.; Kanchi, Rupa S.; Grimm, Sandra L.; Devaraj, Sridevi; Emamaullee, Juliet; Schraw, Jeremy; Lupo, Philip J.; Bezerra, Jorge A.; Loomes, Kathleen M.; Magee, John C.; Sokol, Ronald J.; Wang, Kasper S.; Kriegmeier, Alyssa; Hsu, Evelyn; Molleston, Jean P.; Rosenthal, Philip; Kohli, Rohit; Karpen, Saul J.; Horslen, Simon P.; Jensen, M. Kyle; Barbetta, Arianna; Coarfa, Cristian; on behalf of the Childhood Liver Disease Research Network
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Stage-dependent Effects of Systemic ASBT Inhibition in a Cholestasis-induced Cholemic Nephropathy Mouse Model系统ASBT抑制在胆汁淤积诱导的胆汁性肾病小鼠模型中的阶段依赖性效应
err2025-09-23
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errOAAI
errAhmed Ghallab; Maiju Myllys; Daniela González; Adrian Friebel; Zaynab Hobloss; Reham Hassan; Hannah Schmidt; Qasim Siddiqui; Deng Zhipeng; Rama Hendawi; Brigitte Begher-Tibbe; Joerg Reinders; Katharina Derksen; Ute Hofmann; Julia C. Duda; Lucia Ameis; Kathrin Möllenhoff; Abdellatief Seddek; Noha Abdelmageed; Ellen Strängberg; Peter Åkerblad; Mihael Vucur; Tom Luedde; Guido Stirnimann; Matthias Schwab; Tahany Abbas; Benedikt Hild; Hartmut Schmidt; Saul J. Karpen; Benedikt Simbrunner; Mattias Mandorfer; Jörg Rahnenführer; Karolina Edlund; Stefan Hoehme; Michael Trauner; Paul A. Dawson; Erik Lindström; Jan G. Hengstler
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Phenotypic Divergence of JAG1- and NOTCH2-Associated Alagille Syndrome & Disease-Specific NOTCH2 Variant Classification GuidelinesJAG1和NOTCH2相关Alagille综合征的表型分歧与疾病特异性NOTCH2变异分类指南
err2025-07-31
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errOAAI
errShannon M. Vandriel; Li-Ting Li; Huiyu She; Jian-She Wang; Kathleen M. Loomes; David A. Piccoli; Irena Jankowska; Piotr Czubkowski; Dorota Gliwicz-Miedzińska; Lorenzo D'Antiga; Emanuele Nicastro; Florence Lacaille; Dominique Debray; Étienne M. Sokal; Tanguy Demaret; Rima L. Fawaz; Silvia Nastasio; Kyung Mo Kim; Seak Hee Oh; Björn Fischler; Henrik Arnell; Catherine Larson-Nath; Winita Hardikar; Sahana Shankar; Shikha S. Sundaram; Alexander Chaidez; Pinar Bulut; Pier Luigi Calvo; Mureo Kasahara; Niviann Blondet; Eberhard Lurz; Anna-Maria Kavallar; Emmanuel M. Gonzales; Emmanuel Jacquemin; Jérôme Bouligand; Noelle H. Ebel; Jeffrey A. Feinstein; Susan M. Siew; Michael O. Stormon; Saul J. Karpen; Rene Romero; M. Kyle Jensen; Catalina Jaramillo; James E. Squires; Sarah M. Bedoyan; Deirdre A. Kelly; Jane Hartley; Henkjan J. Verkade; Way Seah Lee; Chatmanee Lertudomphonwanit; Ryan T. Fischer; Henry C. Lin; Nathalie Rock; Yael Mozer-Glassberg; Amin J. Roberts; Helen M. Evans; Wikrom Karnsakul; Gabriella Nebbia; Victorien M. Wolters; Pamela L. Valentino; Jesus Quintero Bernabeu; Amal A. Aqul; Cigdem Arikan; María Legarda Tamara; Cristina Molera Busoms; Thomas Damgaard Sandahl; Giuseppe Indolfi; Andréanne N. Zizzo; Aglaia Zellos; Ruben E. Quiros-Tejeira; Ermelinda Santos-Silva; Kathleen B. Schwarz; Jernej Brecelj; Maria Camila Sanchez; Maria Lorena Cavalieri; Christos Tzivinikos; Sabina Wiecek; John Eshun; Nanda Kerkar; Quais Mujawar; Zerrin Önal; Cristina Gonçalves; Jennifer Garcia; Seema Alam; Carolina Jimenez-Rivera; Luis Bujanda; Richard J. Thompson; Bettina E. Hansen; Nancy B. Spinner; Melissa A. Gilbert; Binita M. Kamath; The Global ALagille Alliance (GALA) Study Group
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Increased serum GM-CSF at diagnosis of biliary atresia is associated with improved biliary drainage
err2025-01-29
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PREAI
errTaylor, Sarah A.; Harpavat, Sanjiv; Gromer, Kyle D.; Andreev, Victor; Loomes, Kathleen M.; Bezerra, Jorge A.; Jarasvaraparn, Chaowapong; Wang, Kasper; Horslen, Simon; Rosenthal, Philip; Teckman, Jeffrey; Valentino, Pamela L.; Ng, Vicky L.; Karpen, Saul J.; Sokol, Ronald J.; Alonso, Estella M.; Mack, Cara L.
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BiliQML: a supervised machine-learning model to quantify biliary forms from digitized whole slide liver histopathological images
err2024-07-01
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PREAI
errHellen, Dominick J.; Fay, Meredith E.; Lee, David H.; Klindt-Morgan, Caroline; Bennett, Ashley; Pachura, Kimberly J.; Grakoui, Arash; Huppert, Stacey S.; Dawson, Paul A.; Lam, Wilbur A.; Karpen, Saul J.
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Diagnostic accuracy of serum matrix metalloproteinase-7 as a biomarker of biliary atresia in a large North American cohort在北美大型队列中,血清基质metalloproteinase-7作为胆道闭锁的生物标志物的诊断准确性
err2024-03-06
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errOAAI
errPandurangi, Sindhu; Mourya, Reena; Nalluri, Shreya; Fei, Lin; Dong, Shun; Harpavat, Sanjiv; Guthery, Stephen L.; Molleston, Jean P.; Rosenthal, Philip; Sokol, Ronald J.; Wang, Kasper S.; Ng, Vicky; Alonso, Estella M.; Hsu, Evelyn K.; Karpen, Saul J.; Loomes, Kathleen M.; Magee, John C.; Shneider, Benjamin L.; Horslen, Simon P.; Teckman, Jeffrey H.; Bezerra, Jorge A.
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A novel model to study mechanisms of cholestasis in human cholangiocytes reveals a role for the SIPR2 pathway
err2024-03-01
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errOAAI
errIslam, Diana; Israr, Izza; Taleb, Mohamed A. B.; Rao, Aditya; Yosief, Robel; Sultana, Rukhsar; Sampaziotis, Fotios; Tysoe, Olivia C.; Trauner, Michael; Karpen, Saul J.; Ghanekar, Anand; Kamath, Binita M.
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Inhibition of the renal apical sodium dependent bile acid transporter prevents cholemic nephropathy in mice with obstructive cholestasis
err2024-02-01
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errOAAI
errGhallab, Ahmed; Gonzalez, Daniela; Straengberg, Ellen; Hofmann, Ute; Myllys, Maiju; Hassan, Reham; Hobloss, Zaynab; Brackhagen, Lisa; Begher-Tibbe, Brigitte; Duda, Julia C.; Drenda, Carolin; Kappenberg, Franziska; Reinders, Joerg; Friebel, Adrian; Vucur, Mihael; Turajski, Monika; Seddek, Abdel-latief; Abbas, Tahany; Abdelmageed, Noha; Morad, Samy A. F.; Morad, Walaa; Hamdy, Amira; Albrecht, Wiebke; Kittana, Naim; Assali, Mohyeddin; Vartak, Nachiket; Thriel, Christoph van; Sous, Ansam; Nell, Patrick; Villar-Fernandez, Maria; Cadenas, Cristina; Genc, Erhan; Marchan, Rosemarie; Luedde, Tom; Akerblad, Peter; Mattsson, Jan; Marschall, Hanns-Ulrich; Hoehme, Stefan; Stirnimann, Guido; Schwab, Matthias; Boor, Peter; Amann, Kerstin; Schmitz, Jessica; Braesen, Jan H.; Rahnenfuehrer, Joerg; Edlund, Karolina; Karpen, Saul J.; Simbrunner, Benedikt; Reiberger, Thomas; Mandorfer, Mattias; Trauner, Michael; Dawson, Paul A.; Lindstroem, Erik; Hengstler, Jan G.
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