arrow
返回
L

Luis J. V. Galietta

fondazione telethon

56H指数
269论文数
1.3W被引数
收录论文 141
发表时间
A critical analysis on ENaC inhibitors, unravelling molecular medicinal insights and promising research roadmap in the treatment of cystic fibrosis对ENaC抑制剂的批判性分析,揭示分子药物学见解和治疗囊性纤维化研究的可行路线图
err2026-09-30
err0
PREAI
errLo Mascolo, Fabiana; Lipani, Alessandra; Giuffrida, Stefano; Barreca, Marilia; Bivacqua, Roberta; Spano, Virginia; Raimondi, Maria Valeria; Montalbano, Alessandra; Borrelli, Anna; Venturini, Arianna; Guidone, Daniela; Genovese, Michele; Galietta, Luis J. V.; Barraja, Paola
err分享
err收藏
Functional correction of the untreatable CFTR 1717-1G>A mutation through mRNA- and sgRNA-optimized base editing通过优化mRNA和sgRNA的碱基编辑纠正无法治疗的CFTR 1717-1G>A突变
err2026-04-22
err0
PREAI
errAlessandro Umbach; Annalisa Santini; Mattijs Bulcaen; Daniela Guidone; Giulia Maule; Daniele Arosio; Irene Carrozzo; Matteo Ciciani; Enrica Brugnara; Anabela Ramalho; François Vermeulen; Luis J. V. Galietta; Marianne S. Carlon; Anna Cereseto
err分享
err收藏
Evaluation of ATP12A and NFKBIZ as potential markers of inflammatory status in cystic fibrosis airway epithelial cells评估ATP12A和NFKBIZ作为囊性纤维化气道上皮细胞炎症状态潜在标志物的价值
err2026-03-17
err0
errOAAI
errCaterina Allegretta; Daniela Guidone; Silvia Boscia; Laura Pisano; Silvia Ricci; Chiara Azzari; Cristina Fevola; Martina De Santis; Fabiana Ciciriello; Enza Montemitro; Daniela Dolce; Giulio Cabrini; Luis J. V. Galietta; Vito Terlizzi; Onofrio Laselva
err分享
err收藏
Modulators of anion channels and transporters as alternative therapeutic agents to normalize airway surface liquid in cystic fibrosis阴离子通道和转运蛋白调节剂作为纠正囊性纤维化气道表面液体的替代治疗剂
err2025-10-31
err0
errOAAI
errAlessandra Lipani; Fabiana Lo Mascolo; Stefano Giuffrida; Marilia Barreca; Roberta Bivacqua; Virginia Spanò; Maria Valeria Raimondi; Anna Borrelli; Arianna Venturini; Daniela Guidone; Michele Genovese; Alessandra Montalbano; Luis J.V. Galietta; Paola Barraja
err分享
err收藏
Beyond Trikafta: new models to assess tissue dependent rescue of N1303K-CFTR超越Trikafta:评估组织依赖性N1303K-CFTR挽救的新模型
err2025-10-29
err0
errOAAI
errIwona Pranke†; Valeria Capurro†; Benoit Chevalier†; Emanuela Pesce†; Valeria Tomati; Cristina Pastorino; Mairead Kelly-Aubert; Aurelie Hatton; Elise Dreano; Mariateresa Lena; Renata Bocciardi; Federico Zara; Stefano Pantano; Vito Terlizzi; Cristina Lucanto; Stefano Costa; Laura Claut; Valeria Daccò; Piercarlo Poli; Massimo Maschio; Benedetta Fabrizzi; Nicole Caporelli; Marco Cipolli; Sonia Volpi; Frederique Chedevergne; Laure Cosson; Julie Macey; Sophie Ramel; Laurence Weiss; Dominique Grenet; Laurence Le Clainche-Viala; Benoit Douvry; Bruno Ravoninjatovo; Camille Audousset; Aurélie Tatopoulos; Bénédicte Richaud-Thiriez; Melissa Baravalle; Guillaume Thouvenin; Guillaume Labbé; Marie Mittaine; Philippe Reix; Isabelle Durieu; Julie Mankikian; Stéphanie Bui; Thao Nguyen-Khoa; Karim Khoukh; Clémence Martin; Jennifer Da Silva; Paola De Carli; Carlo Castellani; Federico Cresta; Luis Galietta; Anne Guillemaut; Emmanuelle Girodon; Natacha Remus; Mathis Bulcaen; Marjolein Ensinck; Miroslaw Zajac; Marianne Carlon; Jean LeBihan; Pierre-Régis Burgel; Isabelle Sermet-Gaudelus‡; Alexandre Hinzpeter‡; Nicoletta Pedemonte‡
err分享
err收藏
In silico, in vitro and ex vivo characterization of cystic fibrosis transmembrane conductance regulator pathogenic variants localized in the fourth intracellular loop and their rescue by modulators在体内外及细胞外对位于第四细胞内环的囊性纤维化跨膜电导调节因子致病性变异进行表征及其通过调节剂的修复
err2025-08-20
err0
errOAAI
errEmanuela Pesce; Valeria Tomati; Valeria Capurro; Mariateresa Lena; Cristina Pastorino; Miro Astore; Serdar Kuyucak; Benoit Chevalier; Elvira Sondo; Federico Cresta; Alice Dighero; Vito Terlizzi; Cristina Fevola; Stefano Costa; Maria Cristina Lucanto; Valeria Daccò; Laura Claut; Francesca Ficili; Benedetta Fabrizzi; Renata Bocciardi; Federico Zara; Carlo Castellani; Luis J. V. Galietta; Shafagh A. Waters; Alexandre Hinzpeter; Nicoletta Pedemonte
err分享
err收藏
Esc peptides and derivatives potentiate the activity of CFTR with gating defects and display antipseudomonal activity in cystic fibrosis-like lung diseaseEsc肽及其衍生物能够增强具有门控缺陷的CFTR的活性,并在类囊性纤维化肺病中显示出抗铜绿假单胞菌活性。
err2025-03-18
err0
errOAAI
errFerrera, Loretta; Cappiello, Floriana; Venturini, Arianna; Lu, Hexin; Casciaro, Bruno; Cappella, Giacomo; Bontempi, Giulio; Corrente, Alessandra; Strippoli, Raffaele; Zara, Federico; Di, Y. Peter; Galietta, Luis J. V.; Mori, Mattia; Mangoni, Maria Luisa
err分享
err收藏
Functional rescue of F508del-CFTR through revertant mutations introduced by CRISPR base editing通过CRISPR碱基编辑引入的返突变对F508del-CFTR的功能拯救
err2025-01-01
err0
errOAAI
errCarrozzo, Irene; Maule, Giulia; Gentile, Carmelo; Umbach, Alessandro; Ciciani, Matteo; Guidone, Daniela; De Santis, Martina; Petris, Gianluca; Galietta, Luis Juan Vicente; Arosio, Daniele; Cereseto, Anna
err分享
err收藏
Identification of 6,9-dihydro-5H-pyrrolo[3,2-h]quinazolines as a new class of F508del-CFTR correctors for the treatment of cystic fibrosis
err2024-10-01
err2
errOAAI
errBarreca, Marilia; Renda, Mario; Spano, Virginia; Montalbano, Alessandra; Raimondi, Maria Valeria; Giuffrida, Stefano; Bivacqua, Roberta; Bandiera, Tiziano; Galietta, Luis J. V.; Barraja, Paola
err分享
err收藏
Anoctamin pharmacology
err2024-07-01
err1
PREAI
errGenovese, Michele; Galietta, Luis J. V.
err分享
err收藏
A functional 3D full-thickness model for comprehending the interaction between airway epithelium and connective tissue in cystic fibrosis
err2024-07-01
err2
errOAAI
errMazio, Claudia; Scognamiglio, Laura Sara; Casale, Costantino; Panzetta, Valeria; Urciuolo, Francesco; Galietta, Luis J. V.; Imparato, Giorgia; Netti, Paolo A.
err分享
err收藏
Functional restoration of a CFTR splicing mutation through RNA delivery of CRISPR adenine base editor
err2023-06-01
err9
errOAAI
errAmistadi, Simone; Maule, Giulia; Ciciani, Matteo; Ensinck, Marjolein M.; De Keersmaecker, Liesbeth; Ramalho, Anabela S.; Guidone, Daniela; Buccirossi, Martina; Galietta, Luis J. V.; Carlon, Marianne S.; Cereseto, Anna
err分享
err收藏
Novel tricyclic pyrrolo-quinolines as pharmacological correctors of the mutant CFTR chloride channel
err2023-05-10
err7
errOAAI
errRenda, Mario; Barreca, Marilia; Borrelli, Anna; Spano, Virginia; Montalbano, Alessandra; Raimondi, Maria Valeria; Bivacqua, Roberta; Musante, Ilaria; Scudieri, Paolo; Guidone, Daniela; Buccirossi, Martina; Genovese, Michele; Venturini, Arianna; Bandiera, Tiziano; Barraja, Paola; Galietta, Luis J. V.
err分享
err收藏
Rescue by elexacaf tor-tezacaf tor-ivacaf tor of the G1244E cystic fibrosis mutation's stability and gating defects are dependent on cell backgroundG1244E囊性纤维化突变的稳定性和门控缺陷依赖于细胞背景
err2023-05-01
err16
PREAI
errTomati, Valeria; Costa, Stefano; Capurro, Valeria; Pesce, Emanuela; Pastorino, Cristina; Lena, Mariateresa; Sondo, Elvira; Di Duca, Marco; Cresta, Federico; Cristadoro, Simona; Zara, Federico; Galietta, Luis J. V.; Bocciardi, Renata; Castellani, Carlo; Lucanto, Maria Cristina; Pedemonte, Nicoletta
err分享
err收藏
Easy-to-Build and Reusable Microfluidic Device for the Dynamic Culture of Human Bronchial Cystic Fibrosis Epithelia
err2023-04-05
err4
errOAAI
errMazio, Claudia; Scognamiglio, Laura S.; Passariello, Roberta; Panzetta, Valeria; Casale, Costantino; Urciuolo, Francesco; Galietta, Luis J. V.; Imparato, Giorgia; Netti, Paolo A.
err分享
err收藏
Analysis of inhibitors of the anoctamin-1 chloride channel (transmembrane member 16A, TMEM16A) reveals indirect mechanisms involving alterations in calcium signalling
err2022-12-18
err17
errOAAI
errGenovese, Michele; Buccirossi, Martina; Guidone, Daniela; De Cegli, Rossella; Sarnataro, Sergio; di Bernardo, Diego; Galietta, Luis J. V.
err分享
err收藏
Pharmacological potentiators of the calcium signaling cascade identified by high-throughput screening
err2022-12-09
err3
errOAAI
errGenovese, Michele; Guidone, Daniela; Buccirossi, Martina; Borrelli, Anna; Rodriguez-Gimeno, Alejandra; Bertozzi, Fabio; Bandiera, Tiziano; Galietta, Luis J. V.
err分享
err收藏
Airway surface hyperviscosity and defective mucociliary transport by IL-17/TNF-? are corrected by ?-adrenergic stimulus br
err2022-11-22
err6
errOAAI
errGuidone, Daniela; Buccirossi, Martina; Scudieri, Paolo; Genovese, Michele; Sarnataro, Sergio; De Cegli, Rossella; Cresta, Federico; Terlizzi, Vito; Planelles, Gabrielle; Crambert, Gilles; Sermet, Isabelle; Galietta, Luis J. V.
err分享
err收藏
Esc peptides as novel potentiators of defective cystic fibrosis transmembrane conductance regulator: an unprecedented property of antimicrobial peptides
err2021-12-31
err10
errOAAI
errFerrera, Loretta; Cappiello, Floriana; Loffredo, Maria Rosa; Puglisi, Elena; Casciaro, Bruno; Botta, Bruno; Galietta, Luis J., V; Mori, Mattia; Mangoni, Maria Luisa
err分享
err收藏