未登录 Human brain tissue with MOGHE carrying somatic SLC35A2 variants reveal aberrant protein expression and protein loss in the white matter 携带MOGHE的人类脑组织显示体细胞SLC35A2变异导致白质中蛋白表达异常和蛋白缺失。 Cecchini, E; Geffers, S; Coras, R; Schultheis, D; Holtzhausen, C; Karandasheva, K; Herrmann, H; Paulsen, F; Stadelmann, C; Kobow, K; Hartlieb, T; Bien, CG; Lal, D; Blumcke, I; Hoffmann, L 分享 收藏
Clinical Implementation and Evaluation of Auto-Segmentation Tools for Multi-Site Contouring in Radiotherapy 放射治疗中多部位轮廓自动分割工具的临床实现与评价 Heilemann, Gerd; Buschmann, Martin; Lechner, Wolfgang; Dick, Vincent; Eckert, Franziska; Heilmann, Martin; Herrmann, Harald; Moll, Matthias; Knoth, Johannes; Konrad, Stefan; Simek, Inga-Malin; Thiele, Christopher; Zaharie, Alexandru; Georg, Dietmar; Widder, Joachim; Trnkova, Petra 分享 收藏
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An Absence of Nuclear Lamins in Keratinocytes Leads to Ichthyosis, Defective Epidermal Barrier Function, and Intrusion of Nuclear Membranes and Endoplasmic Reticulum into the Nuclear Chromatin 角质形成细胞中缺乏核Lamins会导致鱼鳞病,表皮屏障功能缺陷以及核膜和内质网侵入核染色质 Jung, Hea-Jin; Tatar, Angelica; Tu, Yiping; Nobumori, Chika; Yang, Shao H.; Goulbourne, Chris N.; Herrmann, Harald; Fong, Loren G.; Young, Stephen G. 分享 收藏
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Viscoelastic properties of suspended cells measured with shear flow deformation cytometry Gerum, Richard; Mirzahossein, Elham; Eroles, Mar; Elsterer, Jennifer; Mainka, Astrid; Bauer, Andreas; Sonntag, Selina; Winterl, Alexander; Bartl, Johannes; Fischer, Lena; Abuhattum, Shada; Goswami, Ruchi; Girardo, Salvatore; Guck, Jochen; Schruefer, Stefan; Stroehlein, Nadine; Nosratlo, Mojtaba; Herrmann, Harald; Schultheis, Dorothea; Rico, Felix; Mueller, Sebastian Johannes; Gekle, Stephan; Fabry, Ben 分享 收藏
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The desmin mutation R349P increases contractility and fragility of stem cell-generated muscle micro-tissues Spoerrer, Marina; Kah, Delf; Gerum, Richard C.; Reischl, Barbara; Huraskin, Danyil; Dessalles, Claire A.; Schneider, Werner; Goldmann, Wolfgang H.; Herrmann, Harald; Thievessen, Ingo; Clemen, Christoph S.; Friedrich, Oliver; Hashemolhosseini, Said; Schroeder, Rolf; Fabry, Ben 分享 收藏
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Dual Functional States of R406W-Desmin Assembly Complexes Cause Cardiomyopathy With Severe Intercalated Disc Derangement in Humans and in Knock-In Mice Herrmann, Harald; Cabet, Eva; Chevalier, Nicolas R.; Moosmann, Julia; Schultheis, Dorothea; Haas, Jan; Schowalter, Mirjam; Berwanger, Carolin; Weyerer, Veronika; Agaimy, Abbas; Meder, Benjamin; Muller, Oliver J.; Katus, Hugo A.; Schlotzer-Schrehardt, Ursula; Vicart, Patrick; Ferreiro, Ana; Dittrich, Sven; Clemen, Christoph S.; Lilienbaum, Alain; Schroeder, Rolf 分享 收藏
Plectin-related scapuloperoneal myopathy with treatment-responsive myasthenic syndrome Argente-Escrig, H.; Schultheis, D.; Kamm, L.; Schowalter, M.; Thiel, C.; Tuerk, M.; Clemen, C. S.; Muelas, N.; Castanon, M. J.; Wiche, G.; Herrmann, H.; Vilchez, J. J.; Schroeder, R. 分享 收藏
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The MyoRobot technology discloses a premature biomechanical decay of skeletal muscle fiber bundles derived from R349P desminopathy mice Haug, Michael; Meyer, Charlotte; Reischl, Barbara; Proelss, Gerhard; Vetter, Kristina; Iberl, Julian; Nuebler, Stefanie; Schuermann, Sebastian; Rupitsch, Stefan J.; Heckel, Michael; Poeschel, Thorsten; Winter, Lilli; Herrmann, Harald; Clemen, Christoph S.; Schroeder, Rolf; Friedrich, Oliver 分享 收藏
Oxygen and Conformation Dependent Protein Oxidation and Aggregation by Porphyrins in Hepatocytes and Light-Exposed Cells Maitra, Dhiman; Carter, Eric L.; Richardson, Rani; Rittie, Laure; Basrur, Venkatesha; Zhang, Haoming; Nesvizhskii, Alexey, I; Osawa, Yoichi; Wolf, Matthew W.; Ragsdale, Stephen W.; Lehnert, Nicolai; Herrmann, Harald; Omary, M. Bishr 分享 收藏
Altered nuclear envelope structure and proteasome function of micronuclei Maass, Kendra K.; Rosing, Fabian; Ronchi, Paolo; Willmund, Karolin, V; Devens, Frauke; Hergt, Michaela; Herrmann, Harald; Lichter, Peter; Ernst, Aurelie 分享 收藏
Assembly Kinetics of Vimentin Tetramers to Unit-Length Filaments: A Stopped-Flow Study Muecke, Norbert; Kaemmerer, Lara; Winheim, Stefan; Kirmse, Robert; Krieger, Jan; Mildenberger, Maria; Bassler, Jochen; Hurt, Ed; Goldmann, Wolfgang H.; Aebi, Ueli; Toth, Katalin; Langowski, Joerg; Herrmann, Harald 分享 收藏
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