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Pharmacological Modulation of Autophagy Corrects Cellular Defects in Pediatric Crohn's Disease 自噬的药理学调控纠正了儿童克罗恩病中的细胞缺陷 Creoli, Mara; Buono, Pietro; Cenni, Sabrina; Casertano, Marianna; Vitale, Alessandra; Maglio, Mariantonia; Polishchuk, Roman; Polishchuk, Elena; Cinque, Laura; Miele, Erasmo; Martinelli, Massimo; Settembre, Carmine; Staiano, Annamaria; Dolce, Pasquale; Strisciuglio, Caterina 分享 收藏
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Evaluation of Promising Areas for Biogas Production by Indirect Assessment of Raw Materials Using Satellite Monitoring Opryshko, Oleksiy; Kiktev, Nikolay; Shvorov, Sergey; Hluhan, Fedir; Polishchuk, Roman; Murakhovskiy, Maksym; Hutsol, Taras; Glowacki, Szymon; Nurek, Tomasz; Sojak, Mariusz 分享 收藏
Copper impairs the intestinal barrier integrity in Wilson disease Fontes, Adriana; Pierson, Hannah; Bierla, Joanna B.; Eberhagen, Carola; Kinschel, Jennifer; Akdogan, Banu; Rieder, Tamara; Sailer, Judith; Reinold, Quirin; Cielecka-Kuszyk, Joanna; Szymanska, Sylwia; Neff, Frauke; Steiger, Katja; Seelbach, Olga; Zibert, Andree; Schmidt, Hartmut H.; Hauck, Stefanie M.; von Toerne, Christine; Michalke, Bernhard; Semrau, Jeremy D.; DiSpirito, Ana M.; Ramalho-Santo, Joao; Kroemer, Guido; Polishchuk, Roman; Azul, Anabela Marisa; Dispirito, Alan; Socha, Piotr; Lutsenko, Svetlana; Zischka, Hans 分享 收藏
A new Caenorhabditis elegans model to study copper toxicity in Wilson disease Catalano, Federico; O'Brien, Thomas J.; Mekhova, Aleksandra A.; Sepe, Lucia Vittoria; Elia, Mariantonietta; De Cegli, Rossella; Gallotta, Ivan; Santonicola, Pamela; Zampi, Giuseppina; Ilyechova, Ekaterina Y.; Romanov, Aleksei A.; Samuseva, Polina D.; Salzano, Josephine; Petruzzelli, Raffaella; Polishchuk, Elena V.; Indrieri, Alessia; Kim, Byung-Eun; Brown, Andre E. X.; Puchkova, Ludmila V.; Di Schiavi, Elia; Polishchuk, Roman S. 分享 收藏
The HSPB1-p62/SQSTM1 functional complex regulates the unconventional secretion and transcellular spreading of the HD-associated mutant huntingtin protein Bonavita, R.; Scerra, G.; Di Martino, R.; Nuzzo, S.; Polishchuk, E.; Di Gennaro, M.; Williams, S., V; Caporaso, M. G.; Caiazza, C.; Polishchuk, R.; D'Agostino, M.; Fleming, A.; Renna, M. 分享 收藏
RETRACTION: Lysosomal fusion and SNARE function are impaired by cholesterol accumulation in lysosomal storage disorders (Retraction of Vol 29, Pg 3607, 2010) Fraldi, Alessandro; Annunziata, Fabio; Lombardi, Alessia; Kaiser, Hermann-Josef; Luis Medina, Diego; Spampanato, Carmine; Olind Fedele, Anthony; Polishchuk, Roman; Sorrentino, Nicolina Cristina; Simons, Kai; Ballabio, Andrea 分享 收藏
Genistein improves renal disease in a mouse model of nephropathic cystinosis: a comparison study with cysteamine De Leo, Ester; Taranta, Anna; Raso, Roberto; Polishchuk, Elena; D'Oria, Valentina; Pezzullo, Marco; Goffredo, Bianca Maria; Cairoli, Sara; Bellomo, Francesco; Battafarano, Giulia; Camassei, Francesca Diomedi; Del Fattore, Andrea; Polishchuk, Roman; Emma, Francesco; Rega, Laura Rita 分享 收藏
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Connecting copper and cancer: from transition metal signalling to metalloplasia 连接铜和癌症: 从过渡金属信号到金属增生 Ge, Eva J.; Bush, Ashley I.; Casini, Angela; Cobine, Paul A.; Cross, Justin R.; DeNicola, Gina M.; Dou, Q. Ping; Franz, Katherine J.; Gohil, Vishal M.; Gupta, Sanjeev; Kaler, Stephen G.; Lutsenko, Svetlana; Mittal, Vivek; Petris, Michael J.; Polishchuk, Roman; Ralle, Martina; Schilsky, Michael L.; Tonks, Nicholas K.; Vahdat, Linda T.; Van Aelst, Linda; Xi, Dan; Yuan, Peng; Brady, Donita C.; Chang, Christopher J. 分享 收藏
Correction of oxidative stress enhances enzyme replacement therapy in Pompe disease Tarallo, Antonietta; Damiano, Carla; Strollo, Sandra; Minopoli, Nadia; Indrieri, Alessia; Polishchuk, Elena; Zappa, Francesca; Nusco, Edoardo; Fecarotta, Simona; Porto, Caterina; Coletta, Marcella; Iacono, Roberta; Moracci, Marco; Polishchuk, Roman; Medina, Diego Luis; Imbimbo, Paola; Monti, Daria Maria; De Matteis, Maria Antonietta; Parenti, Giancarlo 分享 收藏
Pharmacoproteomics pinpoints HSP70 interaction for correction of the most frequent Wilson disease-causing mutant of ATP7B Concilli, Mafalda; Petruzzelli, Raffaella; Parisi, Silvia; Catalano, Federico; Sirci, Francesco; Napolitano, Francesco; Renda, Mario; Galietta, Luis J., V; Di Bernardo, Diego; Polishchuk, Roman S. 分享 收藏
Characterization of the most frequent ATP7B mutation causing Wilson disease in hepatocytes from patient induced pluripotent stem cells (vol 53, pg 8312, 2018) Parisi, Silvia; Polishchuk, Elena V.; Allocca, Simona; Ciano, Michela; Musto, Anna; Gallo, Maria; Perone, Lucia; Ranucci, Giusy; Iorio, Raffaele; Polishchuk, Roman S.; Bonatti, Stefano 分享 收藏
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PERK-Mediated Unfolded Protein Response Activation and Oxidative Stress in PARK20 Fibroblasts Amodio, Giuseppina; Moltedo, Ornella; Fasano, Dominga; Zerillo, Lucrezia; Oliveti, Marco; Di Pietro, Paola; Faraonio, Raffaella; Barone, Paolo; Pellecchia, Maria Teresa; De Rose, Anna; De Michele, Giuseppe; Polishchuk, Elena; Polishchuk, Roman; Bonifati, Vincenzo; Nitsch, Lucio; Pierantoni, Giovanna Maria; Renna, Maurizio; Criscuolo, Chiara; Paladino, Simona; Remondelli, Paolo 分享 收藏
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Intein-mediated protein trans-splicing expands adeno-associated virus transfer capacity in the retina Tornabene, Patrizia; Trapani, Ivana; Minopoli, Renato; Centrulo, Miriam; Lupo, Mariangela; de Simone, Sonia; Tiberi, Paola; Dell'Aquila, Fabio; Marrocco, Elena; Iodice, Carolina; Iuliano, Antonella; Gesualdo, Carlo; Rossi, Settimio; Giaquinto, Laura; Albert, Silvia; Hoyng, Carel B.; Polishchuk, Elena; Cremers, Frans P. M.; Surace, Enrico M.; Simonelli, Francesca; De Matteis, Maria A.; Polishchuk, Roman; Auricchio, Alberto 分享 收藏
Activation of Autophagy, Observed in Liver Tissues From Patients With Wilson Disease and From ATP7B-Deficient Animals, Protects Hepatocytes From Copper-Induced Apoptosis Polishchuk, Elena, V; Merolla, Assunta; Lichtmannegger, Josef; Romano, Alessia; Indrieri, Alessia; Ilyechova, Ekaterina Y.; Concilli, Mafalda; De Cegli, Rossella; Crispino, Roberta; Mariniello, Marta; Petruzzelli, Raffaella; Ranucci, Giusy; Iorio, Raffaele; Pietrocola, Federico; Einer, Claudia; Borchard, Sabine; Zibert, Andree; Schmidt, Hartmut H.; Di Schiavi, Elia; Puchkova, Ludmila, V; Franco, Brunella; Kroemer, Guido; Zischka, Hans; Polishchuk, Roman S. 分享 收藏