arrow
返回
B

Bruno Crestani

université parís cité

83H指数
928论文数
2.8W被引数
收录论文 340
发表时间
Antifibrotic therapy in patients with pleuroparenchymal fibroelastosis: a multicentric observational study胸膜实质纤维弹力增生患者的抗纤维化治疗:一项多中心观察性研究
err2026-09-07
err0
errOAAI
errInès Ali-Pacha; Pei Zhi Li; Raphaël Borie; Alice Camboulive; Hilario Nunes; Bruno Crestani; Yurdagül Uzunhan; Jacques Cadranel; Sébastien Quétant; Julie Traclet; Bernard Aguilaniu; Vincent Cottin
err分享
err收藏
Aspergillosis complicating idiopathic lung fibrosis: a multicentric series曲霉菌病并发特发性肺纤维化:一项多中心病例系列
err2026-07-01
err0
errOAAI
errBermudez, Julien; Debray, Marie-Pierre; Uzunhan, Yurdagul; Marchand-Adam, Sylvain; Nunes, Hilario; Godet, Cendrine; Maitre, Thomas; Claustre, Johanna; Milesi, Jules; Nasser, Mouhamad; Cottin, Vincent; Reynaud-Gaubert, Martine; Crestani, Bruno
err分享
err收藏
Epithelial PCSK6 Promotes Proliferation and Decreases Collagen Deposition by Fibroblasts Potentially via MMP Activation上皮PCSK6通过MMP激活促进成纤维细胞增殖并减少胶原沉积
err2026-06-04
err0
errOAAI
errQian Tian; Annemiek Dijkhuis; Ester B. M. Remmerswaal; Hella Aberson; Bruno Crestani; Tom van der Poll; C. Arnold Spek; Jan Willem Duitman
err分享
err收藏
The pleuroparenchymal fibroelastosis atlas reveals aberrant cell states and their zonation as an alternate roadmap to lung fibrosis胸膜实质纤维弹力组织增生图谱揭示了异常细胞状态及其分区,作为肺纤维化的替代路线图
err2026-05-08
err0
errOAAI
errJannik Ruwisch; Aurélie Cazes; Lena M. Leiber; Raphaël Borie; Lavinia Neubert; Leonard Christian; Vincent Thomas de Montpréville; Adam Szmul; Farah Moussa; Stijn E. Verleden; Svenja Gaedcke; Jan Hegermann; Jan Fuge; Matthias Ballmaier; Jan C. Kamp; Mark Greer; Peter Braubach; Christopher Werlein; Fabius Ius; Theresa Graalmann; Kalil Aburahma; Laurens J. De Sadeleer; Ryoko Egashira; Maximilian Ackermann; Daisuke Yamada; Marius M. Hoeper; Christine Falk; Jens Gottlieb; Herbert B. Schiller; Bart Vanaudenaerde; Benjamin Seeliger; Marie-Pierre Debray; Jean Francois Bernaudin; Lars Knudsen; Emmanuel Bergot; Joseph Jacob; Hervé Mal; Danny Jonigk; Sabine Dettmer; Pierre Mordant; Antje Prasse; Elie Fadel; Wim A. Wuyts; Bruno Crestani; Naftali Kaminski; Aurélien Justet; Jonas C. Schupp
err分享
err收藏
Adult male patients with DKC1 mutations present early-onset pulmonary fibrosis and severe prognosis成年男性DKC1基因突变患者表现为早发性肺纤维化和严重预后
err2026-01-19
err0
PREAI
errEvrard, Ophelie; Philippot, Quentin; Kannengiesser, Caroline; Debray, Marie Pierre; Guyard, Alice; Fattori, Antonin; Schuller, Armelle; Nunes, Hilario; Montani, David; Bours, Vincent; Cottin, Vincent; Traclet, Julie; Benattia, Amira; Berthoux, Emilie; Daniel, Adrien; Yan-Min, Xu; Lainey, Elodie; Saussereau, Julien; Viallon, Malika Chelbi; Oudin, Claire; Morel, Helene; Crestani, Bruno; Borie, Raphael; Ba, Ibrahima
err分享
err收藏
ERS/EULAR clinical practice guidelines for connective tissue disease-associated interstitial lung disease欧洲呼吸学会(ERS)/欧洲风湿病学会联盟(EULAR)结缔组织病相关间质性肺疾病临床实践指南由欧洲呼吸学会(ERS)和欧洲风湿病学会联盟(EULAR)结缔组织病相关间质性肺疾病工作组制定欧洲罕见呼吸疾病参考网络(ERN-LUNG)认可
err2026-01-01
err20
errOAAI
errAntoniou, Katerina M.; Distler, Oliver; Gheorghiu, Ana-Maria; Moor, Catharina C.; Vikse, Jens; Bizymi, Nikoleta; Galetti, Ilaria; Brown, Graham; Bargagli, Elena; Allanore, Yannick; Corte, Tamera J.; Dieude, Philippe; Cottin, Vincent; Fisher, Benjamin A.; Fabre, Aurelie; Giles, Jon T.; Kreuter, Michael; Lundberg, Ingrid E.; Poletti, Venerino; Maurer, Britta; Renzoni, Elisabetta A.; Muller-Ladner, Ulf; Strek, Mary E.; Sverzellati, Nicola; Studenic, Paul; Mohammed, Jibril; Nagavci, Blin; Stamm, Tanja; Tonia, Thomy; Crestani, Bruno; Hoffmann-Vold, Anna-Maria
err分享
err收藏
Short telomere length is associated with accelerated lung disease progression in rheumatoid arthritis-associated interstitial lung disease
err2025-12-01
err1
PREAI
errEl Husseini, Kinan; Lee, Joyce S.; Juge, Pierre-Antoine; Ebstein, Esther; Ottaviani, Sebastien; Borie, Raphael; Bancal, Catherine; Debray, Marie-Pierre; Kannengiesser, Caroline; Ba, Ibrahima; Marchand-Adam, Sylvain; Richez, Christophe; Nunes, Hilario; Avouac, Jerome; Flipo, Rene-Marc; Wemeau, Lidwine; Boissier, Marie-Christophe; Schaeverbeke, Thierry; Kermanac'h, Nathalie Saidenberg; Kawano-Dourado, Leticia; Cottin, Vincent; Wolters, Paul J.; Granger, Benjamin; Dieude, Philippe; Crestani, Bruno
err分享
err收藏
CT features of interstitial lung disease in systemic lupus erythematosus and overlap lupus-other connective tissue disease系统性红斑狼疮及重叠其他结缔组织病的间质性肺疾病CT特征
err2025-11-19
err0
PREAI
errAurore Sajust de Bergues de Escalup; Arthur Mageau; Lou Deneuville; Karim Sacre; Antoine Khalil; Nathalie Costedoat-Chalumeau; Eric Hachulla; Yurdagul Uzunhan; Erwan Le Tallec; Jacques Cadranel; Sylvain Marchand-Adam; David Montani; Martine Reynaud-Gaubert; Grégoire Prévot; Guillaume Beltramo; Bruno Crestani; Vincent Cottin; Raphaël Borie; Marie-Pierre Debray
err分享
err收藏
A novel RTEL1 nonsense variant in a case of familial pulmonary fibrosis: clinical description and genetic implications一种新型RTEL1无义变异在家族性肺纤维化病例中的发现:临床描述与遗传学意义
err2025-11-09
err0
errOAAI
errGiovanni Franco; Francesca Bertola; Filippo Aloisi; Samuele Promi; Umberto Zanini; Paola Faverio; Angela Bentivegna; Raphaël Borie; Bruno Crestani; Giovanni Cazzaniga; Fabrizio Luppi
err分享
err收藏
Nintedanib combined with pirfenidone in patients with idiopathic pulmonary fibrosis or progressive pulmonary fibrosis: a long-term retrospective multicentre study (Combi-PF)尼达尼布联合吡非尼酮在特发性肺纤维化或进行性肺纤维化患者中的应用:一项长期回顾性多中心研究(Combi-PF)
err2025-10-10
err0
errOAAI
errCorentin Meersseman; Elisa Martínez Besteiro; Nicolas Romain-Scelle; Bruno Crestani; Sylvain Marchand-Adam; Hilario Nunes; Lidwine Wémeau-Stervinou; Raphael Borie; Rémi Diesler; Claudia Valenzuela; Vincent Cottin
err分享
err收藏
Characterization of human lung immune cells in the humanized BRGSF mouse model
err2025-10-01
err0
PREAI
errPokhreal, Deepak; Curioni, Anna, V; Creusat, Florent; Martin, Gaelle H.; Sonego, Fabiane; Thiam, Kader; Mordant, Pierre; Mal, Herve; Bellamri, Nessrine; Flament, Heloise; Crestani, Bruno; Helou, Doumet Georges
err分享
err收藏
Lysosomal Storage Disorders
err2025-10-01
err0
PREAI
errCefalo, Jacopo; Crestani, Bruno; Guyard, Alice; Pettazzoni, Magali; Mauhin, Wladimir; Debray, Marie-Pierre; Borie, Raphael
err分享
err收藏
Stratifying GAP Stages by MUC5B rs35705950 T-Allele Carriage Refines Survival Prediction in IPF根据MUC5B rs35705950 T等位基因携带情况对GAP分期进行分层,可优化IPF患者的生存预测。
errLung
IF3.9
err2025-07-30
err0
PREAI
errJoanne J. van der Vis; Antje Prasse; Elisabetta A. Renzoni; Carmel J. W. Stock; Toby M. Maher; Francesco Bonella; Raphael Borie; Bruno Crestani; Wim A. Wuyts; Philip L. Molyneaux; Johannes C. Kelder; Jan C. Grutters; Coline H. M. van Moorsel
err分享
err收藏
Identification of FGFR4 as a regulator of myofibroblast differentiation in pulmonary fibrosis
err2024-12-01
err0
PREAI
errGhanem, Mada; Justet, Aurelien; Jaillet, Madeleine; Vasarmidi, Eirini; Boghanim, Tiara; Hachem, Mouna; Vadel, Aurelie; Joannes, Audrey; Mordant, Pierre; Balayev, Agshin; Adams, Taylor; Mal, Herve; Cazes, Aurelie; Pote, Nicolas; Mailleux, Arnaud; Crestani, Bruno
err分享
err收藏
Rare genetic interstitial lung diseases: a pictorial essay
err2024-11-13
err1
errOAAI
errBorie, Raphael; Berteloot, Laureline; Kannengiesser, Caroline; Griese, Matthias; Cazes, Aurelie; Crestani, Bruno; Hadchouel, Alice; Debray, Marie Pierre
err分享
err收藏
Lucile Sese1⇈Isabella Annesi-Maesano2Pierre Antoine Juge3Sophie Mayer4Johanna Sigaux5Bruno Crestani6Lucas Semerano5Boris Dessimond2Raphaël Borie6Marie-Pierre Debray7Bernard Combe8Pierre-Yves Brillet9Yurdagul Uzunhan10Philippe Dieudé3Hilario Nunes10
err2024-10-30
err0
PREAI
errSese, Lucile; Annesi-Maesano, Isabella; Juge, Pierre Antoine; Mayer, Sophie; Sigaux, Johanna; Crestani, Bruno; Semerano, Lucas; Dessimond, Boris; Borie, Raphael; Debray, Marie-Pierre; Combe, Bernard; Brillet, Pierre-Yves; Uzunhan, Yurdagul; Dieude, Philippe; Nunes, Hilario
err分享
err收藏
Analysis of transcriptional profile of lung fibroblasts derived from patients with progressive pulmonary fibrosis (PPF)
err2024-10-30
err0
PREAI
errVoisin, Tom; Morzadec, Claudie; Lettelier, Alice; Le Naoures, Cecile; De Latour, Bertrand Richard; Crestan, Bruno; Jouneau, Stephane; Vernhet, Laurent; Joannes, Audrey
err分享
err收藏