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Helen J. Lachmann

university of london

96H指数
752论文数
3.4W被引数
收录论文 206
发表时间
A retrospective study of isatuximab-pomalidomidedexamethasone in relapsed/refractory systemic AL amyloidosis一项关于isatuximab-pomalidomide-dexamethasone在复发/难治性系统性AL淀粉样变性中的回顾性研究
err2025-12-01
err0
errOAAI
errVohra, Sargam Rachit; Ravichandran, Sriram; Foard, Darren; Martinez-Naharro, Ana; Venneri, Lucia; Fontana, Marianna; Whelan, Carol J.; Hawkins, Philip N.; Gillmore, Julian; Lachmann, Helen J.; Mahmood, Shameem; Wechalekar, Ashutosh D.
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Myocardial Amyloid Burden in Transthyretin Amyloidosis转甲状腺素蛋白淀粉样变性中的心肌淀粉样蛋白负荷
errJACC
IF0
err2025-11-08
err0
errOAAI
errAwais Sheikh; Anouk Achten; Alberto Aimo; Yousuf Razvi; Josephine Mansell; Muhammad U. Rauf; Aldostefano Porcari; Rishi Patel; Lucia Venneri; Ana Martinez-Naharro; Carol Whelan; Cristina Quarta; Ruta Virsinskaite; Daniel Feffer Barak; Ashutosh Wechalekar; Helen Lachmann; Daniel Knight; Tushar Kotecha; Peter Kellman; Charlotte Manisty; James Moon; Michele Emdin; Scott D. Solomon; Philip N. Hawkins; Julian Gillmore; Marianna Fontana
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Artificial intelligence-based echocardiographic assessment for monitoring disease progression in transthyretin cardiac amyloidosis基于人工智能的心脏超声评估在监测甲状腺素转运蛋白心脏淀粉样变性疾病进展中的应用
err2025-10-16
err0
errOAAI
errLucia Venneri; Alberto Aimo; Aldostefano Porcari; Irem Sezer; Adam Ioannou; Awais Sheikh; Josephine Mansell; Yousuf Razvi; Surabhi Bhaskar Iyer; Ana Martinez-Naharro; Francesco Bandera; Sze Chi Lim; Matthew Frost; Justin Ezekowitz; Carolyn S.P. Lam; William Moody; Carol Whelan; Helen Lachmann; Ashutosh Wechelakar; Michele Emdin; Philip N. Hawkins; Scott David Solomon; Julian D. Gillmore; Marianna Fontana
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Uncertain Clinical Relevance of Serial Bone Scintigraphy Findings in Treated Transthyretin Amyloid Cardiomyopathy治疗后转甲状腺素蛋白淀粉样变性心肌病中连续骨闪烁显像结果的临床相关性不确定
err2025-07-09
err0
errOAAI
errYousuf Razvi; Aldostefano Porcari; David F. Hutt; Jonathan Lazari; Adam Ioannou; Rishi K. Patel; Muhammad Umaid Rauf; Tamer Rezk; Oliver Hague; Stefano Filisetti; Helen J. Lachmann; Ashutosh D. Wechalekar; Aviva Petrie; Carol J. Whelan; Lucia Venneri; Ana Martinez-Naharro; Janet A. Gilbertson; Dorota Rowczenio; William E. Moody; Richard Steeds; Jennifer H. Pinney; Philip N. Hawkins; Marianna Fontana; Julian D. Gillmore
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Transthyretin amyloid cardiomyopathy: natural history and treatment response assessed by cardiovascular magnetic resonancePatel, R.K.; Ioannou, A.; Sheikh, A.; Razvi, Y.; Mansell, J.; Martinez-Naharro, A.; Knight, D.; Kotecha, T.; Porcari, A.; Chacko, L.; 等. 甲状腺素转运蛋白淀粉样变性心肌病:基于心血管磁共振的自然病程及治疗反应评估。Eur. Heart J. 2025, ehaf412. [Google Scholar] [CrossRef] [PubMed]
err2025-07-01
err4
errOAAI
errPatel, Rishi K.; Ioannou, Adam; Sheikh, Awais; Razvi, Yousuf; Mansell, Josephine; Martinez-Naharro, Ana; Knight, Daniel; Kotecha, Tushar; Porcari, Aldostefano; Chacko, Liza; Brown, James; Manisty, Charlotte; Moon, James C.; Lachmann, Helen J.; Wechalekar, Ashutosh; Whelan, Carol; Venneri, Lucia; Kellman, Peter; Hawkins, Philip N.; Gillmore, Julian D.; Fontana, Marianna
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Treatment outcomes in patients with VEXAS syndrome: a retrospective cohort studyVEXAS综合征患者治疗效果:一项回顾性队列研究
err2025-05-21
err0
errOAAI
errAdam Al-Hakim; Roochi Trikha; Ei Ei Phyu Htut; Onima Chowdhury; Calman A MacLennan; Ashlyn Chee; Arvind Kaul; James A Poulter; Catherine Cargo; James M S Wason; Sammiya Ahmed; Tanya N Basu; Sukanya Gogoi; James Galloway; Stephen Jolles; Anoop Mistry; Elspeth M Payne; Rachel S Tattersall; Taryn Youngstein; Helen J Lachmann; Austin Kulasekararaj; Sinisa Savic
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Kidney Outcomes in Transthyretin Amyloid Cardiomyopathy
err2025-01-01
err0
errOAAI
errIoannou, Adam; Razvi, Yousuf; Porcari, Aldostefano; Rauf, Muhammad U.; Martinez-Naharro, Ana; Venneri, Lucia; Kazi, Salsabeel; Pasyar, Ali; Luxhoj, Carina M.; Petrie, Aviva; Moody, William; Steeds, Richard P.; Sperry, Brett W.; Witteles, Ronald M.; Whelan, Carol; Wechalekar, Ashutosh; Lachmann, Helen; Hawkins, Philip N.; Solomon, Scott D.; Gillmore, Julian D.; Fontana, Marianna
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Recommendations for Transitioning Young People with Primary Immunodeficiency Disorders and Autoinflammatory Diseases to Adult Care将患有原发性免疫缺陷病和自身炎症性疾病的年轻人转变为成人护理的建议
err2024-12-17
err0
errOAAI
errIsrani, Muskan; Alderson, Eliska; Mahlaoui, Nizar; Obici, Laura; Rossi-Semerano, Linda; Lachmann, Helen; Avramovic, Mojca Zajc; Guffroy, Aurelien; Dalm, Virgil; Rimmer, Rachel; Solis, Leire; Villar, Carlota; Gennery, Andrew R.; Skeffington, Stephanie; Nordin, Julia; Warnatz, Klaus; Korganow, Anne-Sophie; Anton, Jordi; Cattalini, Marco; Berg, Stefan; Soler-Palacin, Pere; Campbell, Mari; Burns, Siobhan O.; ESID Clinical Working Party, Ann; ERN RITA Transition Working Grp Consortium, Anna
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Mevalonate kinase deficiency: an updated clinical overview and revision of the SHARE recommendations
err2024-11-12
err0
errOAAI
errLengvari, Lilla; Takacs, Kata; Lengyel, Anna; Palinkas, Annamaria; Wouters, Carine Helena; Kone-Paut, Isabelle; Kuemmerte-Deschner, Jasmin; Jeyaratnam, Jerold; Anton, Jordi; Lachmann, Helen Jane; Gattorno, Marco; Hofer, Michael; Toplak, NataSa; Weiser, Peter; Kallinich, Tilmann; Ozen, Seza; Hentgen, Veronique; Uziel, Yosef; Horvath, Zsuzsanna; Szabados, Marton; Brogan, Paul; Constantin, Tamas; Frenkel, Joost
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Redefining Cardiac Involvement and Targets of Treatment in Systemic Immunoglobulin AL Amyloidosis
err2024-11-01
err0
errOAAI
errPorcari, Aldostefano; Masi, Ambra; Martinez-Naharro, Ana; Razvi, Yousuf; Patel, Rishi; Ioannou, Adam; Rauf, Muhammad U.; Sinigiani, Giulio; Wisniowski, Brendan; Filisetti, Stefano; Currie-Cathey, Jasmine; O'Beara, Sophie; Kotecha, Tushar; Knight, Dan; Moon, James C.; Sinagra, Gianfranco; Virsinskaite, Ruta; Gilbertson, Janet; Venneri, Lucia; Petrie, Aviva; Lachmann, Helen; Whelan, Carol; Kellman, Peter; Ravichandran, Sriram; Cohen, Oliver; Mahmood, Shameem; Manisty, Charlotte; Hawkins, Philip N.; Gillmore, Julian D.; Wechalekar, Ashutosh D.; Fontana, Marianna
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Microvascular obstruction in cardiac amyloidosis心脏淀粉样变性的微血管阻塞
err2024-10-18
err0
errOAAI
errNetti, Lucrezia; Ioannou, Adam; Martinez-Naharro, Ana; Razvi, Yousuf; Porcari, Aldostefano; Venneri, Lucia; Maestrini, Viviana; Knight, Dan; Virsinskaite, Ruta; Rauf, Muhammad U.; Kotecha, Tushar; Patel, Rishi K.; Wechelakar, Ashutosh; Lachmann, Helen; Kellman, Peter; Manisty, Charlotte; Moon, James; Hawkins, Philip N.; Gillmore, Julian D.; Fontana, Marianna
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Refining prognostication in systemic AL amyloidosis: limited value of dFLC
err2024-09-23
err2
PREAI
errKhwaja, Jahanzaib; Ravichandran, Sriram; Bomsztyk, Joshua; Cohen, Oliver; Foard, Darren; Naharro, Ana; Venneri, Lucia; Fontana, Marianna; Whelan, Carol; Hawkins, Philip N.; Gillmore, Julian D.; Lachmann, Helen J.; Mahmood, Shameem; Wechalekar, Ashutosh
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Expansion of the National Amyloidosis Centre staging system to detect early mortality in transthyretin cardiac amyloidosis
err2024-06-23
err0
errOAAI
errNitsche, Christian; Ioannou, Adam; Patel, Rishi K.; Razvi, Yousuf; Porcari, Aldostefano; Rauf, Muhammad U.; Bandera, Francesco; Aimo, Alberto; Emdin, Michele; Martinez-Naharro, Ana; Venneri, Lucia; Petrie, Aviva; Wechalekar, Ashutosh; Lachmann, Helen; Hawkins, Philip N.; Gillmore, Julian D.; Fontana, Marianna
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Cardiopulmonary Exercise Testing in Evaluating Transthyretin Amyloidosis
err2024-04-01
err3
PREAI
errPatel, Rishi K.; Bandera, Francesco; Venneri, Lucia; Porcari, Aldostefano; Razvi, Yousuf; Ioannou, Adam; Chacko, Liza; Martinez-Naharro, Ana; Rauf, Muhammad U.; Knight, Daniel; Brown, James; Petrie, Aviva; Wechalekar, Ashutosh; Whelan, Carol; Lachmann, Helen; Muthurangu, Vivek; Guazzi, Marco; Hawkins, Philip N.; Gillmore, Julian D.; Fontana, Marianna
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Multiorgan Dysfunction and Associated Prognosis in Transthyretin Cardiac Amyloidosis
err2024-02-20
err8
errOAAI
errIoannou, Adam; Nitsche, Christian; Porcari, Aldostefano; Patel, Rishi K.; Razvi, Yousuf; Rauf, Muhammad U.; Martinez-Naharro, Ana; Venneri, Lucia; Accietto, Antonella; Netti, Lucrezia; Bandera, Francesco; Virsinskaite, Ruta; Kotecha, Tushar; Knight, Dan; Petrie, Aviva; Whelan, Carol; Wechalekar, Ashutosh; Lachmann, Helen; Hawkins, Philip N.; Gillmore, Julian D.; Fontana, Marianna
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Deep phenotyping of p.(V142I)-associated variant transthyretin amyloid cardiomyopathy: Distinct from wild-type transthyretin amyloidosis?p.(V142I) 相关变异型甲状腺素运载蛋白淀粉样心肌病的深度表型: 与野生型甲状腺素运载蛋白淀粉样变性不同?
err2024-01-28
err10
errOAAI
errRazvi, Yousuf; Ioannou, Adam; Patel, Rishi K.; Chacko, Liza; Karia, Nina; Riefolo, Mattia; Porcari, Aldostefano; Rauf, Muhammad Umaid; Starr, Neasa; Ganesananthan, Sashiananthan; Blakeney, Iona; Kaza, Nandita; Filisetti, Stefano; Bolhuis, Roos Eline; Rowczenio, Dorota; Gilbertson, Janet; Hutt, David; Mahmood, Shameem; Lachmann, Helen J.; Wechalekar, Ashutosh D.; Kotecha, Tushar; Knight, Daniel S.; Coghlan, John G.; Petrie, Aviva; Whelan, Carol J.; Venneri, Lucia; Martinez-Naharro, Ana; Hawkins, Phillip; Fontana, Marianna; Gillmore, Julian D.
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Myocardial perfusion in cardiac amyloidosis
err2024-01-21
err6
errOAAI
errChacko, Liza; Kotecha, Tushar; Ioannou, Adam; Patel, Niket; Martinez-Naharro, Ana; Razvi, Yousuf; Patel, Rishi; Massa, Paolo; Venneri, Lucia; Brown, James; Porcari, Aldostefano; Knott, Kristopher; Manisty, Charlotte; Knight, Daniel; Lockie, Tim; Rakhit, Roby; Lachmann, Helen; Wechelakar, Ashutosh; Whelan, Carol; Ponticos, Markella; Moon, James; Gonzalez, Arantxa; Gilbertson, Janet; Riefolo, Mattia; Leone, Ornella; Xue, Hui; Hawkins, Philip; Kellman, Peter; Gillmore, Julian; Fontana, Marianna
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