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CXCL9 as a novel prognostic marker to identify high-risk adults with hemophagocytic lymphohistiocytosis CXCL9作为一种新型预后标志物,用于识别患有噬血细胞性淋巴组织细胞增多症的成人高风险群体。 Rocco, Joseph M.; Oved, Joseph H.; Patel, Rikita J.; Herskovits, A. Zara; Nair, Namitha; Shakoory, Bita; Robertson, Thomas E.; Dileo, Rachel; Jacobs, Max W.; Zerbe, Christa S.; Gordon, Rachael A.; Ombrello, Michael J.; Ombrello, Amanda K.; Shah, Nirali N.; Dimitrova, Dimana; Kanakry, Jennifer; Zelenetz, Andrew D.; Moskowitz, Alison J.; Stuver, Robert; Epstein-Peterson, Zachary D.; Ghione, Paola; Mead, Elena; Shahid, Zainab; Raj, Sandeep; Park, Jae H.; Giralt, Sergio A.; Maillard, Ivan; Geyer, Mark B.; Xiao, Wenbin; Dogan, Ahmet; Lim, Megan; Zwicker, Jeffrey I.; Mones, Jodi; Parameswaran, Rehka; Banaszak, Lauren; Geller, Shamir; Santomasso, Bianca D.; Shouval, Roni; Curran, Kevin J.; Delmonte, Ottavia; Notarangelo, Luigi D.; Cohen, Jeffrey I.; Holland, Steven M.; Salles, Gilles; Horwitz, Steven M.; Vardhana, Santosha A.; Perales, Miguel-Angel; Schwartz, Daniella; Sereti, Irini; Johnson, William T. 分享 收藏
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TGFβ links EBV to multisystem inflammatory syndrome in children TGFβ将EBV与儿童多系统炎症综合征联系起来 Goetzke, Carl Christoph; Massoud, Mona; Frischbutter, Stefan; Guerra, Gabriela Maria; Ferreira-Gomes, Marta; Heinrich, Frederik; von Stuckrad, Anne Sae Lim; Wisniewski, Sebastian; Licha, Jan Robin; Bondareva, Marina; Ehlers, Lisa; Khaldi-Plassart, Samira; Javouhey, Etienne; Pons, Sylvie; Trouillet-Assant, Sophie; Ozsurekci, Yasemin; Zhang, Yu; Poli, Maria Cecilia; Discepolo, Valentina; Lo Vecchio, Andrea; Sahin, Bengue; Verboom, Murielle; Hallensleben, Michael; Heuhsen, Anja Isabelle; Astudillo, Camila; Espinosa, Yazmin; Vial Cox, Maria Cecilia; Dobbs, Kerry; Delmonte, Ottavia M.; Montealegre Sanchez, Gina A.; Magliocco, Mary; Barron, Karyl; Danielson, Jeffrey; Petrov, Lev; Unterwalder, Nadine; Sawitzki, Birgit; Matz, Mareen; Lehmann, Katrin; Gratopp, Alexander; von Bernuth, Horst; Burkhardt, Lisa-Marie; Wiese, Niklas; Peter, Lena; Amini, Leila; Roehmel, Jobst Fridolin; Gewurz, Benjamin E.; Yonker, Lael M.; Witkowski, Mario; Kruglov, Andrey; Mall, Marcus Alexander; Su, Helen C.; Ozen, Seza; Radbruch, Andreas; Belot, Alexandre; Durek, Pawel; Kallinich, Tilmann; Mashreghi, Mir-Farzin 分享 收藏
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A large-scale database of T-cell receptor beta sequences and binding associations from natural and synthetic exposure to SARS-CoV-2 Nolan, Sean; Vignali, Marissa; Klinger, Mark; Dines, Jennifer N.; Kaplan, Ian M.; Svejnoha, Emily; Craft, Tracy; Boland, Katie; Pesesky, Mitchell W.; Gittelman, Rachel M.; Snyder, Thomas M.; Gooley, Christopher J.; Semprini, Simona; Cerchione, Claudio; Nicolini, Fabio; Mazza, Massimiliano; Delmonte, Ottavia M.; Dobbs, Kerry; Carreno-Tarragona, Gonzalo; Barrio, Santiago; Sambri, Vittorio; Martinelli, Giovanni; Goldman, Jason D.; Heath, James R.; Notarangelo, Luigi D.; Martinez-Lopez, Joaquin; Howie, Bryan; Carlson, Jonathan M.; Robins, Harlan S. 分享 收藏
Magnitude and dynamics of the T-cell response to SARS-CoV-2 infection at both individual and population levels 在个人和人群水平上对SARS-CoV-2感染的T细胞反应的大小和动态 Snyder, Thomas M.; Gittelman, Rachel M.; Klinger, Mark; May, Damon H.; Osborne, Edward J.; Taniguchi, Ruth; Jabran Zahid, H.; Kaplan, Ian M.; Dines, Jennifer N.; Noakes, Matthew T.; Pandya, Ravi; Chen, Xiaoyu; Elasady, Summer; Svejnoha, Emily; Ebert, Peter; Pesesky, Mitchell W.; De Almeida, Patricia; O'Donnell, Hope; Degottardi, Quinn; Keitany, Gladys; Lu, Jennifer; Vong, Allen; Elyanow, Rebecca; Fields, Paul; Al-Asadi, Hussein; Greissl, Julia; Baldo, Lance; Semprini, Simona; Cerchione, Claudio; Nicolini, Fabio; Mazza, Massimiliano; Delmonte, Ottavia M.; Dobbs, Kerry; Laguna-Goya, Rocio; Carreno-Tarragona, Gonzalo; Barrio, Santiago; Imberti, Luisa; Sottini, Alessandra; Quiros-Roldan, Eugenia; Rossi, Camillo; Biondi, Andrea; Bettini, Laura Rachele; D'Angio, Mariella; Bonfanti, Paolo; Tompkins, Miranda F.; Alba, Camille; Dalgard, Clifton; Sambri, Vittorio; Martinelli, Giovanni; Goldman, Jason D.; Heath, James R.; Su, Helen C.; Notarangelo, Luigi D.; Paz-Artal, Estela; Martinez-Lopez, Joaquin; Howie, Bryan; Carlson, Jonathan M.; Robins, Harlan S. 分享 收藏
IL-7-dependent and -independent lineages of IL-7R-dependent human T cells Arango-Franco, Carlos A.; Ogishi, Masato; Unger, Susanne; Delmonte, Ottavia M.; Orrego, Julio Cesar; Yatim, Ahmad; Velasquez-Lopera, Margarita M.; Zea-Vera, Andres F.; Bohlen, Jonathan; Chbihi, Marwa; Fayand, Antoine; Sanchez, Juan Pablo; Rojas, Julian; Seeleuthner, Yoann; Le Voyer, Tom; Philippot, Quentin; Payne, Kathryn J.; Gervais, Adrian; Erazo-Borras, Lucia, V; Correa-Londono, Luis A.; Cederholm, Axel; Gallon-Duque, Alejandro; Goncalves, Pedro; Doisne, Jean-Marc; Horev, Liran; Charmeteau-de Muylder, Benedicte; Alvarez, Jesus A.; Arboleda, Diana M.; Perez-Zapata, Lizet; Vasquez-Echeverri, Estefania; Moncada-Velez, Marcela; Lopez, Juan A.; Caicedo, Yolanda; Palterer, Boaz; Patino, Pablo J.; Montoya, Carlos J.; Chaldebas, Matthieu; Zhang, Peng; Nguyen, Tina; Ma, Cindy S.; Jeljeli, Mohamed; Alzate, Juan F.; Cabarcas, Felipe; Khan, Taushif; Rinchai, Darawan; Pretet, Jean-Luc; Boisson, Bertrand; Marr, Nico; Ibrahim, Ruba; Molho-Pessach, Vered; Boisson-Dupuis, Stephanie; Kiritsi, Dimitra; Barata, Joao T.; Landegren, Nils; Neven, Benedicte; Abe, Laurent; Lisco, Andrea; Beziat, Vivien; Jouanguy, Emmanuelle; Bustamante, Jacinta; Di Santo, James P.; Tangye, Stuart G.; Notarangelo, Luigi D.; Cheynier, Remi; Natsuga, Ken; Arias, Andres A.; Franco, Jose Luis; Warnatz, Klaus; Casanova, Jean-Laurent; Puel, Anne 分享 收藏
Case report: Artificial thymic organoids facilitate clinical decisions for a patient with a TP63 variant and severe persistent T cell lymphopenia Gall, Alevtina; Bosticardo, Marita; Ma, Stacey; Chen, Karin; Amini, Kayla; Pala, Francesca; Delmonte, Ottavia M.; Wenger, Tara; Bamshad, Michael; Sleasman, John; Blessing, Matthew; van Oers, Nicolai S. C.; Notarangelo, Luigi D.; de la Morena, M. Teresa 分享 收藏
A pleiotropic recurrent dominant ITPR3 variant causes a complex multisystemic disease Molitor, Anne; Lederle, Alexandre; Radosavljevic, Mirjana; Sapuru, Vinay; Zavorka Thomas, Megan E.; Yang, Jianying; Shirin, Mahsa; Collin-Bund, Virginie; Jerabkova-Roda, Katerina; Miao, Zhichao; Bernard, Alice; Rolli, Veronique; Grenot, Pierre; Castro, Carla Noemi; Rosenzwajg, Michelle; Lewis, Elyssa G.; Person, Richard; Esperon-Moldes, Uxia-Saraiva; Kaare, Milja; Nokelainen, Pekka T.; Batzir, Nurit Assia; Hoffer, Gal Zaks; Paul, Nicodeme; Stemmelen, Tristan; Naegely, Lydie; Hanauer, Antoine; Bibi-Triki, Sabrina; Gruen, Sarah; Jung, Sophie; Busnelli, Ignacio; Tripolszki, Kornelia; Al-Ali, Ruslan; Ordonez, Natalia; Bauer, Peter; Song, Eunkyung; Zajo, Kristin; Partida-Sanchez, Santiago; Robledo-Avila, Frank; Kumanovics, Attila; Louzoun, Yoram; Hirschler, Aurelie; Pichot, Angelique; Toker, Ori; Mejia, Cesar Andres Munoz; Parvaneh, Nima; Knapp, Esther; Hersh, Joseph H.; Kenney, Heather; Delmonte, Ottavia M.; Notarangelo, Luigi D.; Goetz, Jacky G.; Kahwash, Samir B.; Carapito, Christine; Bajwa, Rajinder P. S.; Thomas, Caroline; Ehl, Stephan; Isidor, Bertrand; Carapito, Raphael; Abraham, Roshini S.; Hite, Richard K.; Marcus, Nufar; Bertoli-Avella, Aida; Bahram, Seiamak 分享 收藏
Perturbations of the T-cell receptor repertoire in response to SARS-CoV-2 in immunocompetent and immunocompromised individuals 免疫功能正常和免疫功能低下的个体对SARS-CoV-2的反应对T细胞受体库的扰动 Delmonte, Ottavia M.; Oguz, Cihan; Dobbs, Kerry; Myint-Hpu, Katherine; Palterer, Boaz; Abers, Michael S.; Draper, Deborah; Truong, Meng; Kaplan, Ian M.; Gittelman, Rachel M.; Zhang, Yu; Rosen, Lindsey B.; Snow, Andrew L.; Dalgard, Clifton L.; Burbelo, Peter D.; Imberti, Luisa; Sottini, Alessandra; Quiros-Roldan, Eugenia; Castelli, Francesco; Rossi, Camillo; Brugnoni, Duilio; Biondi, Andrea; Bettini, Laura Rachele; D'Angio, Mariella; Bonfanti, Paolo; Anderson, Megan, V; Saracino, Annalisa; Chironna, Maria; Di Stefano, Mariantonietta; Fiore, Jose Ramon; Santantonio, Teresa; Castagnoli, Riccardo; Marseglia, Gian Luigi; Magliocco, Mary; Bosticardo, Marita; Pala, Francesca; Shaw, Elana; Matthews, Helen; Weber, Sarah E.; Xirasagar, Sandhya; Barnett, Jason; Oler, Andrew J.; Dimitrova, Dimana; Bergerson, Jenna R. E.; Mcdermott, David H.; Rao, V. Koneti; Murphy, Philip M.; Holland, Steven M.; Lisco, Andrea; Su, Helen C.; Lionakis, Michail S.; Cohen, Jeffrey I.; Freeman, Alexandra F.; Snyder, Thomas M.; Lack, Justin; Notarangelo, Luigi D. 分享 收藏
Genetically corrected RAG2-SCID human hematopoietic stem cells restore V(D)J-recombinase and rescue lymphoid deficiency 基因校正的RAG2-SCID人造血干细胞恢复V(D)J-重组酶和拯救淋巴缺陷 Pavel-Dinu, Mara; Gardner, Cameron L.; Nakauchi, Yusuke; Kawai, Tomoki; Delmonte, Ottavia M.; Palterer, Boaz; Bosticardo, Marita; Pala, Francesca; Viel, Sebastien; Malech, Harry L.; Ghanim, Hana Y.; Bode, Nicole M.; Kurgan, Gavin L.; Detweiler, Angela M.; Vakulskas, Christopher A.; Neff, Norma F.; Sheikali, Adam; Menezes, Sherah T.; Chrobok, Jade; Gonzalez, Elaine M. Hernandez; Majeti, Ravindra; Notarangelo, Luigi D.; Porteus, Matthew H. 分享 收藏
COVID-19 Vaccination in Patients with Inborn Errors of Immunity Reduces Hospitalization and Critical Care Needs Related to COVID-19: a USIDNET Report McDonnell, John; Cousins, Kimberley; Younger, M. Elizabeth M.; Lane, Adam; Abolhassani, Hassan; Abraham, Roshini S.; Al-Tamemi, Salem; Aldave-Becerra, Juan Carlos; Al-Faris, Eman Hesham; Alfaro-Murillo, Alberto; Alkhater, Suzan A.; Alsaati, Nouf; Doss, Alexa Michelle Altman; Anderson, Melissa; Angarola, Ernestina; Ariue, Barbara; Arnold, Danielle E.; Assa'ad, Amal H.; Aytekin, Caner; Bank, Meaghan; Bergerson, Jenna R. E.; Bleesing, Jack; Boesing, John; Bouso, Carolina; Brodszki, Nicholas; Cabanillas, Diana; Cady, Carol; Callahan, Meghan A.; Caorsi, Roberta; Carbone, Javier; Carrabba, Maria; Castagnoli, Riccardo; Catanzaro, Jason R.; Chan, Samantha; Chandra, Sharat; Chapdelaine, Hugo; Chavoshzadeh, Zahra; Chong, Hey Jin; Connors, Lori; Consonni, Filippo; Correa-Jimenez, Oscar; Cunningham-Rundles, Charlotte; D'Astous-Gauthier, Katherine; Delmonte, Ottavia Maria; Demirdag, Yesim Yilmaz; Deshpande, Deepti R.; Diaz-Cabrera, Natalie M.; Dimitriades, Victoria R.; El-Owaidy, Rasha; Elghazali, Gehad; Al-Hammadi, Suleiman; Fabio, Giovanna; Faure, Astrid Schellnast; Feng, Jin; Fernandez, James M.; Fill, Lauren; Franco, Guacira R.; Frenck, Robert W.; Fuleihan, Ramsay L.; Giardino, Giuliana; Galant-Swafford, Jessica; Gambineri, Eleonora; Garabedian, Elizabeth K.; Geerlinks, Ashley V.; Goudouris, Ekaterini; Grecco, Octavio; Pan-Hammarstrom, Qiang; Khani, Hedieh Haji Khodaverdi; Hammarstrom, Lennart; Hartog, Nicholas L.; Heimall, Jennifer; Hernandez-Molina, Gabriela; Horner, Caroline C.; Hostoffer, Robert W.; Hristova, Nataliya; Hsiao, Kuang-Chih; Ivankovich-Escoto, Gabriela; Jaber, Faris; Jalil, Maaz; Jamee, Mahnaz; Jean, Tiffany; Jeong, Stephanie; Jhaveri, Devi; Jordan, Michael B.; Joshi, Avni Y.; Kalkat, Amanpreet; Kanarek, Henry J.; Kellner, Erinn S.; Khojah, Amer; Khoury, Ruby; Kokron, Cristina M.; Kumar, Ashish; Lecerf, Kelsey; Lehman, Heather K.; Leiding, Jennifer W.; Lesmana, Harry; Lim, Xin Rong; Lopes, Joao Pedro; Lopez, Ana Laura; Tarquini, Lucia; Lundgren, Ingrid S.; Magnusson, Julieann; Marinho, Ana Karolina B. B.; Marseglia, Gian Luigi; Martone, Giulia M.; Mechtler, Annamaria G.; Mendonca, Leonardo; Milner, Joshua D.; Mustillo, Peter J.; Naderi, Asal Gharib; Naviglio, Samuele; Nell, Jeremy; Niebur, Hana B.; Notarangelo, Luigi; Oleastro, Matias; Ortega-Lopez, Maria Claudia; Patel, Neil R.; Petrovic, Gordana; Pignata, Claudio; Porras, Oscar; Prince, Benjamin T.; Puck, Jennifer M.; Qamar, Nashmia; Rabusin, Marco; Raje, Nikita; Regairaz, Lorena; Risma, Kimberly A.; Ristagno, Elizabeth H.; Routes, John; Roxo-Junior, Persio; Salemi, Negin; Scalchunes, Christopher; Schuval, Susan J.; Seneviratne, Suranjith L.; Shankar, Ashwin; Sherkat, Roya; Shin, Junghee Jenny; Siddiqi, Abeer; Signa, Sara; Sobh, Ali; Lima, Fabiana Mascarenhas Souza; Stenehjem, Kristen K.; Tam, Jonathan S.; Tang, Monica; Barros, Myrthes Toledo; Verbsky, James; Vergadi, Eleni; Voelker, Dayne H.; Volpi, Stefano; Wall, Luke A.; Wang, Christine; Williams, Kelli W.; Wu, Eveline Y.; Wu, Shan Shan; Zhou, Jessie J.; Cook, Alexandria; Sullivan, Kathleen E.; Marsh, Rebecca 分享 收藏
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Mulibrey nanism and immunological complications: a comprehensive case report and literature review Gazzin, Andrea; Pala, Francesca; Bosticardo, Marita; Niemela, Julie; Stoddard, Jennifer; Biasin, Eleonora; Quarello, Paola; Carli, Diana; Ferroni, Francesca; Delmonte, Ottavia M.; Montin, Davide; Rosenzweig, Sergio D.; Licciardi, Francesco; Notarangelo, Luigi D. 分享 收藏