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Aleksander Edelman

Institut Necker Enfants Malades
H指数:49
被引数:6,113

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荣誉奖项

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A small molecule chaperone rescues keratin-8 mediated trafficking of misfolded podocin to correct genetic Nephrotic Syndrome

小分子伴侣可挽救角蛋白8介导的错误折叠的podocin运输，以纠正遗传性肾病综合征

KIDNEY INTERNATIONAL
IF12.6
2024-04-012
OA
Kuzmuk, Valeryia; Pranke, Iwona; Rollason, Ruth; Butler, Matthew; Ding, Wen Y.; Beesley, Matthew; Waters, Aoife M.; Coward, Richard J.; Sessions, Richard; Tuffin, Jack; Foster, Rebecca R.; Mollet, Geraldine; Antignac, Corinne; Edelman, Aleksander; Welsh, Gavin I.; Saleem, Moin A.
Nonsense mutations accelerate lung disease and decrease survival of cystic fibrosis children
JOURNAL OF CYSTIC FIBROSIS
IF6
2023-11-011
PRE
Orenti, Annalisa; Pranke, Iwona; Faucon, Caroline; Varilh, Jessica; Hatton, Aurelie; Golec, Anita; Dehillotte, Clemence; Durieu, Isabelle; Reix, Philippe; Burgel, Pierre-Regis; Grenet, Dominique; Tasset, Celine; Gachelin, Elsa; Perisson, Caroline; Lepissier, Agathe; Dreano, Elise; Tondelier, Danielle; Chevalier, Benoit; Weiss, Laurence; Kiefer, Sebastien; Laurans, Muriel; Chiron, Raphael; Lemonnier, Lydie; Marguet, Christophe; Jung, Andreas; Edelman, Aleksander; Kerem, Bat-Sheva; Girodon, Emmanuelle; Taulan-Cadars, Magali; Hinzpeter, Alexandre; Kerem, Eitan; Naehrlich, Lutz; Sermet-Gaudelus, Isabelle
Theratyping cystic fibrosis patients to guide elexacaftor/ tezacaftor/ivacaftor out-of-label prescription
EUROPEAN RESPIRATORY JOURNAL
IF21
2023-09-1133
PRE
Dreano, Elise; Burgel, Pierre Regis; Hatton, Aurelie; Bouazza, Naim; Chevalier, Benoit; Macey, Julie; Leroy, Sylvie; Durieu, Isabelle; Weiss, Laurence; Grenet, Dominique; Stremler, Nathalie; Ohlmann, Camille; Reix, Philippe; Porzio, Michele; Claude, Pauline Roux; Remus, Natacha; Douvry, Benoit; Montcouquiol, Sylvie; Cosson, Laure; Mankikian, Julie; Languepin, Jeanne; Houdouin, Veronique; Le Clainche, Laurence; Guillaumot, Anne; Pouradier, Delphine; Tissot, Adrien; Priou, Pascaline; Mely, Laurent; Chedevergne, Frederique; Lebourgeois, Muriel; Lebihan, Jean; Martin, Clemence; Zavala, Flora; Da Silva, Jennifer; Lemonnier, Lydie; Kelly-Aubert, Mairead; Golec, Anita; Foucaud, Pierre; Marguet, Christophe; Edelman, Aleksander; Hinzpeter, Alexandre; de Carli, Paola; Girodon, Emmanuelle; Sermet-Gaudelus, Isabelle; Pranke, Iwona
Keratin 8 is a scaffolding and regulatory protein of ERAD complexes
CELLULAR AND MOLECULAR LIFE SCIENCES
IF6.2
2022-09-013
OA
Pranke, Iwona Maria; Chevalier, Benoit; Premchandar, Aiswarya; Baatallah, Nesrine; Tomaszewski, Kamil F.; Bitam, Sara; Tondelier, Danielle; Golec, Anita; Stolk, Jan; Lukacs, Gergely L.; Hiemstra, Pieter S.; Dadlez, Michal; Lomas, David A.; Irving, James A.; Delaunay-Moisan, Agnes; van Anken, Eelco; Hinzpeter, Alexandre; Sermet-Gaudelus, Isabelle; Edelman, Aleksander
Systemic bis-phosphinic acid derivative restores chloride transport in Cystic Fibrosis mice
SCIENTIFIC REPORTS
IF3.9
2022-04-122
OAAI
da Cunha, Melanie Faria; Pranke, Iwona; Sassi, Ali; Schreiweis, Christiane; Moriceau, Stephanie; Vidovic, Dragana; Hatton, Aurelie; Carlon, Mariane Sylvia; Creste, Geordie; Berhal, Farouk; Prestat, Guillaume; Freund, Romain; Odolczyk, Norbert; Jais, Jean Philippe; Gravier-Pelletier, Christine; Zielenkiewicz, Piotr; Jullien, Vincent; Hinzpeter, Alexandre; Oury, Franck; Edelman, Aleksander; Sermet-Gaudelus, Isabelle
Pharmacological chaperones improve intra-domain stability and inter-domain assembly via distinct binding sites to rescue misfolded CFTR

药理学伴侣通过不同的结合位点改善域内稳定性和域间组装，以挽救错误折叠的CFTR

CELLULAR AND MOLECULAR LIFE SCIENCES
IF6.2
2021-10-2938
OA
Baatallah, Nesrine; Elbahnsi, Ahmad; Mornon, Jean-Paul; Chevalier, Benoit; Pranke, Iwona; Servel, Nathalie; Zelli, Renaud; Decout, Jean-Luc; Edelman, Aleksander; Sermet-Gaudelus, Isabelle; Callebaut, Isabelle; Hinzpeter, Alexandre
New insights into structure and function of bis-phosphinic acid derivatives and implications for CFTR modulation (vol 11, 6842, 2021)
SCIENTIFIC REPORTS
IF3.9
2021-09-150
OAAI
Bitam, Sara; Elbahnsi, Ahmad; Creste, Geordie; Pranke, Iwona; Chevalier, Benoit; Berhal, Farouk; Hoffmann, Brice; Servel, Nathalie; Baatalah, Nesrine; Tondelier, Danielle; Hatton, Aurelie; Moquereau, Christelle; Faria Da Cunha, Melanie; Pastor, Alexandra; Lepissier, Agathe; Hinzpeter, Alexandre; Mornon, Jean-Paul; Prestat, Guillaume; Edelman, Aleksander; Callebaut, Isabelle; Gravier-Pelletier, Christine; Sermet-Gaudelus, Isabelle
New insights into structure and function of bis-phosphinic acid derivatives and implications for CFTR modulation
SCIENTIFIC REPORTS
IF3.9
2021-03-2510
OAAI
Bitam, Sara; Elbahnsi, Ahmad; Creste, Geordie; Pranke, Iwona; Chevalier, Benoit; Berhal, Farouk; Hoffmann, Brice; Servel, Nathalie; Tondelier, Danielle; Hatton, Aurelie; Moquereau, Christelle; Da Cunha, Melanie Faria; Pastor, Alexandra; Lepissier, Agathe; Hinzpeter, Alexandre; Mornon, Jean-Paul; Prestat, Guillaume; Edelman, Aleksander; Callebaut, Isabelle; Gravier-Pelletier, Christine; Sermet-Gaudelus, Isabelle
Author Correction: Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis
SCIENTIFIC REPORTS
IF3.9
2019-11-214
OAAI
Simonin, Juliette; Bille, Emmanuelle; Crambert, Gilles; Noel, Sabrina; Dreano, Elise; Edwards, Aurelie; Hatton, Aurelie; Pranke, Iwona; Villeret, Berengere; Cottart, Charles-Henry; Vrel, Jean-Patrick; Urbach, Valerie; Baatallah, Nesrine; Hinzpeter, Alexandre; Golec, Anita; Touqui, Lhousseine; Nassif, Xavier; Galietta, Luis J. V.; Planelles, Gabrielle; Sallenave, Jean-Michel; Edelman, Aleksander; Sermet-Gaudelus, Isabelle
Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis
SCIENTIFIC REPORTS
IF3.9
2019-04-2467
OAAI
Simonin, Juliette; Bille, Emmanuelle; Crambert, Gilles; Noel, Sabrina; Dreano, Elise; Edwards, Aurelie; Hatton, Aurelie; Pranke, Iwona; Villeret, Berengere; Cattart, Charles-Henry; Vrel, Jean-Patrick; Urbach, Valerie; Baatallah, Nesrine; Hinzpeter, Alexandre; Golec, Anita; Touqui, Lhousseine; Nassif, Xavier; Galietta, Luis J., V; Planelles, Gabrielle; Sallenave, Jean-Michel; Edelman, Aleksander; Sermet-Gaudelus, Isabelle
Cis variants identified in F508del complex alleles modulate CFTR channel rescue by small molecules

在F508del复合等位基因中鉴定的顺式变体通过小分子调节CFTR通道拯救

HUMAN MUTATION
IF3.7
2018-01-1631
OAAI
Baatallah, Nesrine; Bitam, Sara; Martin, Natacha; Servel, Nathalie; Costes, Bruno; Mekki, Chadia; Chevalier, Benoit; Pranke, Iwona; Simonin, Juliette; Girodon, Emmanuelle; Hoffmann, Brice; Mornon, Jean-Paul; Callebaut, Isabelle; Sermet-Gaudelus, Isabelle; Fanen, Pascale; Edelman, Aleksander; Hinzpeter, Alexandre

研究方向

暂未获取到该数据
I
Isabelle Sermet‐Gaudelus
H 指数:65论文数:530被引数:1.8万
A
Alexandre Hinzpeter
H 指数:25论文数:92被引数:1,904
I
Iwona Pranke
H 指数:18论文数:60被引数:1,330
F
Franck Brouillard
H 指数:21论文数:58被引数:1,230
A
Aurélie Hatton
H 指数:20论文数:63被引数:1,696
B
B. Chevalier
H 指数:24论文数:144被引数:2,130
I
Ida Chiara Guerrera
H 指数:31论文数:165被引数:3,017
M
Mario Ollero
H 指数:36论文数:139被引数:4,559
J
Janine Fritsch
H 指数:22论文数:46被引数:1,499
D
Danielle Tondelier
H 指数:12论文数:37被引数:662