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SaveBeneficial effect of ursodeoxycholic acid in patients with acyl-CoA oxidase 2 (ACOX2) deficiency-associated hypertransaminasemia
Alonso-Pena, Marta; Espinosa-Escudero, Ricardo; Herraez, Elisa; Briz, Oscar; Cagigal, Maria Luisa; Gonzalez-Santiago, Jesus M.; Ortega-Alonso, Aida; Fernandez-Rodriguez, Conrado; Bujanda, Luis; Calvo Sanchez, Marta; D'Avola, Delia; Londono, Maria-Carlota; Diago, Moises; Fernandez-Checa, Jose C.; Garcia-Ruiz, Carmen; Andrade, Raul J.; Lammert, Frank; Prieto, Jesus; Crespo, Javier; Juamperez, Javier; Diaz-Gonzalez, Alvaro; Monte, Maria J.; Marin, Jose J. G.
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SaveRecombinant porphobilinogen deaminase targeted to the liver corrects enzymopenia in a mouse model of acute intermittent porphyria
Cordoba, Karol M.; Serrano-Mendioroz, Irantzu; Jerico, Daniel; Merino, Maria; Jiang, Lei; Sampedro, Ana; Alegre, Manuel; Corrales, Fernando; Garrido, Maria J.; Martini, Paolo G., V; Luis Lanciego, Jose; Prieto, Jesus; Berraondo, Pedro; Fontanellas, Antonio
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SaveGlycoproteogenomics characterizes the CD44 splicing code associated with bladder cancer invasion
Gaiteiro, Cristiana; Soares, Janine; Relvas-Santos, Marta; Peixoto, Andreia; Ferreira, Dylan; Paulo, Paula; Brandao, Andreia; Fernandes, Elisabete; Azevedo, Rita; Palmeira, Carlos; Freitas, Rui; Miranda, Andreia; Osorio, Hugo; Prieto, Jesus; Lima, Luis; Silva, Andre M. N.; Santos, Lucio Lara; Ferreira, Jose Alexandre
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SaveBrain ventricular enlargement in human and murine acute intermittent porphyria
Jerico, Daniel; Luis, Elkin O.; Cusso, Lorena; Fernandez-Seara, Maria A.; Morales, Xabier; Cordoba, Karol M.; Benito, Marina; Sampedro, Ana; Larriva, Maria; Ramirez, Maria J.; Enriquez de Salamanca, Rafael; Ortiz-de-Solorzano, Carlos; Alegre, Manuel; Prieto, Jesus; Luis Lanciego, Jose; D'Avola, Delia; Gonzalez-Aseguinolaza, Gloria; Pastor, Maria A.; Desco, Manuel; Fontanellas, Antonio
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SaveDisruption of SIRT7 Increases the Efficacy of Checkpoint Inhibitor via MEF2D Regulation of Programmed Cell Death 1 Ligand 1 in Hepatocellular Carcinoma Cells
Xiang, Junyu; Zhang, Ni; Sun, Hui; Su, Li; Zhang, Chengcheng; Xu, Huailong; Feng, Juan; Wang, Meiling; Chen, Jun; Liu, Limei; Shan, Juanjuan; Shen, Junjie; Yang, Zhi; Wang, Guiqin; Zhou, Haijun; Prieto, Jesus; Avila, Matias A.; Liu, Chungang; Qian, Cheng
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SaveShort-Term Local Expression of a PD-L1 Blocking Antibody from a Self-Replicating RNA Vector Induces Potent Antitumor Responses
Cristina Ballesteros-Briones, Maria; Martisova, Eva; Casales, Erkuden; Silva-Pilipich, Noelia; Bunuales, Maria; Galindo, Javier; Mancheno, Uxua; Gorraiz, Marta; Lasarte, Juan J.; Kochan, Grazyna; Escors, David; Sanchez-Paulete, Alfonso R.; Melero, Ignacio; Prieto, Jesus; Hernandez-Alcoceba, Ruben; Hervas-Stubbs, Sandra; Smerdou, Cristian
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SaveGenetic and pathophysiological factors leading to deficient acyl-CoA oxidase 2 (ACOX2) activity in hepatocytes, an alteration which causes oxidative and endoplasmic reticulum stress in liver cells
Alonso-Pena, Marta; Hermanns, Heike; Herraez, Elisa; Briz, Oscar; Monte, Maria; Sanchez-Martin, Manuel; Berrocal, Pablo; Garcia-Tunon, Ignacio; Espinosa-Escudero, Ricardo A.; Prieto, Jesus; Geier, Andreas; Marin, Jose
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SaveLiver Expression of a MiniATP7B Gene Results in Long-Term Restoration of Copper Homeostasis in a Wilson Disease Model in Mice
Murillo, Oihana; Moreno, Daniel; Gazquez, Cristina; Barberia, Miren; Cenzano, Itziar; Navarro, Inigo; Uriarte, Iker; Sebastian, Victor; Arruebo, Manuel; Ferrer, Veronica; Benichou, Bernard; Combal, Jean Philippe; Prieto, Jesus; Hernandez-Alcoceba, Ruben; Gonzalez Aseguinolaza, Gloria
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SaveCardiotrophin-1 is an anti-inflammatory cytokine and promotes IL-4-induced M2 macrophage polarization
Carneros, David; Santamaria, Eva M.; Larequi, Eduardo; Miguel Velez-Ortiz, Jose; Reboredo, Mercedes; Mancheno, Uxua; Jesus Perugorria, Maria; Navas, Placido; Romero-Gomez, Manuel; Prieto, Jesus; Hervas-Stubbs, Sandra; Bustos, Matilde
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SaveA new HDV mouse model identifies mitochondrial antiviral signaling protein (MAVS) as a key player in IFN-β induction (vol 67, pg 669, 2017)
Suarez-Amaran, Lester; Usai, Carla; Di Scala, Marianna; Godoy, Cristina; Ni, Yi; Hommel, Mirja; Palomo, Laura; Segura, Victor; Olague, Cristina; Vales, Africa; Ruiz-Ripa, Alicia; Buti, Maria; Salido, Eduardo; Prieto, Jesus; Urban, Stephan; Rodriguez-Frias, Francisco; Aldabe, Rafael; Gonzalez-Aseguinolaza, Gloria
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SaveMicroRNA-506 promotes primary biliary cholangitis-like features in cholangiocytes and immune activation
Erice, Oihane; Munoz-Garrido, Patricia; Vaquero, Javier; Perugorria, Maria J.; Fernandez-Barrena, Maite G.; Saez, Elena; Santos-Laso, Alvaro; Arbelaiz, Ander; Jimenez-Agueero, Raul; Fernandez-Irigoyen, Joaquin; Santamaria, Enrique; Torrano, Veronica; Carracedo, Arkaitz; Ananthanarayanan, Meenakshisundaram; Marzioni, Marco; Prieto, Jesus; Beuers, Ulrich; Elferink, Ronald P. Oude; LaRusso, Nicholas F.; Bujanda, Luis; Marin, Jose J. G.; Banales, Jesus M.
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SaveTargeting the anion exchanger 2 with specific peptides as a new therapeutic approach in B lymphoid neoplasms
Celay, Jon; Lozano, Teresa; Concepcion, Axel R.; Beltran, Elena; Rudilla, Francesc; Jose Garcia-Barchino, Maria; Robles, Eloy F.; Rabal, Obdulia; de Miguel, Irene; Panizo, Carlos; Casares, Noelia; Oyarzabal, Julen; Prieto, Jesus; Medina, Juan F.; Jose Lasarte, Juan; Angel Martinez-Climent, Jose
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