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Loss of prohibitin 2 in Schwann cells dysregulates key transcription factors controlling developmental myelination Wilson, Emma R.; Nunes, Gustavo Della-Flora; Shen, Shichen; Moore, Seth; Gawron, Joseph; Maxwell, Jessica; Syed, Umair; Hurley, Edward; Lanka, Meghana; Qu, Jun; Desaubry, Laurent; Wrabetz, Lawrence; Poitelon, Yannick; Feltri, M. Laura Share Save
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p38γ MAPK delays myelination and remyelination and is abundant in multiple sclerosis lesions Marziali, Leandro N.; Hwang, Yoonchan; Palmisano, Marilena; Cuenda, Ana; Sim, Fraser J.; Gonzalez, Alberto; Volsko, Christina; Dutta, Ranjan; Trapp, Bruce D.; Wrabetz, Lawrence; Feltri, Maria L. Share Save
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Prohibitin 1 is essential to preserve mitochondria and myelin integrity in Schwann cells Nunes, Gustavo Della-Flora; Wilson, Emma R.; Marziali, Leandro N.; Hurley, Edward; Silvestri, Nicholas; He, Bin; O'Malley, Bert W.; Beirowski, Bogdan; Poitelon, Yannick; Wrabetz, Lawrence; Feltri, M. Laura Share Save
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αVintegrins in Schwann cells promote attachment to axons, but are dispensable in vivo Catignas, Kathleen K.; Frick, Luciana R.; Pellegatta, Marta; Hurley, Edward; Kolb, Zachary; Addabbo, Kathryn; McCarty, Joseph H.; Hynes, Richard O.; van der Flier, Arjan; Poitelon, Yannick; Wrabetz, Lawrence; Laura Feltri, Maria Share Save
Macrophages Expressing GALC Improve Peripheral Krabbe Disease by a Mechanism Independent of Cross-Correction Weinstock, Nadav I.; Shin, Daesung; Dhimal, Narayan; Hong, Xinying; Irons, Eric E.; Silvestri, Nicholas J.; Reed, Chelsey B.; Duc Nguyen; Sampson, Oliver; Cheng, Yung-Chih; Lau, Joseph T. Y.; Bongarzone, Ernesto R.; Kofler, Julia; Escolar, Maria L.; Gelb, Michael H.; Wrabetz, Lawrence; Feltri, M. Laura Share Save
Neuregulin 1 type III improves peripheral nerve myelination in a mouse model of congenital hypomyelinating neuropathy (vol 28, pg 1260, 2019) Belin, Sophie; Ornaghi, Francesca; Shackleford, Ghjuvan'Ghjacumu; Wang, Jie; Scapin, Cristina; Lopez-Anido, Camila; Silvestri, Nicholas; Robertson, Neil; Williamson, Courtney; Ishii, Akihiro; Taveggia, Carla; Svaren, John; Bansal, Rashmi; Schwab, Markus H.; Nave, Klaus; Fratta, Pietro; D'Antonio, Maurizio; Poitelon, Yannick; Feltri, M. Laura; Wrabetz, Lawrence Share Save
Schwann cells ER-associated degradation contributes to myelin maintenance in adult nerves and limits demyelination in CMT1B mice Volpi, Vera G.; Ferri, Cinzia; Fregno, Ilaria; Del Carro, Ubaldo; Bianchi, Francesca; Scapin, Cristina; Pettinato, Emanuela; Solda, Tatiana; Feltri, M. Laura; Molinari, Maurizio; Wrabetz, Lawrence; D'Antonio, Maurizio Share Save
Neuregulin 1 type III improves peripheral nerve myelination in a mouse model of congenital hypomyelinating neuropathy (vol 28, pg 1260, 2019) Belin, Sophie; Ornaghi, Francesca; Shackleford, Ghjuvan'Ghjacumu; Wang, Jie; Scapin, Cristina; Lopez-Anido, Camila; Silvestri, Nicholas; Robertson, Neil; Williamson, Courtney; Ishii, Akihiro; Taveggia, Carla; Svaren, John; Bansal, Rashmi; Schwab, Markus H.; Nave, Klaus; Fratta, Pietro; D'Antonio, Maurizio; Poitelon, Yannick; Feltri, M. Laura; Wrabetz, Lawrence Share Save
Neuregulin 1 type III improves peripheral nerve myelination in a mouse model of congenital hypomyelinating neuropathy Belin, Sophie; Ornaghi, Francesca; Shackleford, Ghjuvan Ghjacumu; Wang, Jie; Scapin, Cristina; Lopez-Anido, Camila; Silvestri, Nicholas; Robertson, Neil; Williamson, Courtney; Ishii, Akihiro; Taveggia, Carla; Svaren, John; Bansal, Rashmi; Schwab, Markus H.; Nave, Klaus; Fratta, Pietro; D'Antonio, Maurizio; Poitelon, Yannick; Feltri, M. Laura; Wrabetz, Lawrence Share Save
Enhanced axonal neuregulin-1 type-III signaling ameliorates neurophysiology and hypomyelination in a Charcot-Marie-Tooth type 1B mouse model Scapin, Cristina; Ferri, Cinzia; Pettinato, Emanuela; Zambroni, Desiree; Bianchi, Francesca; Del Carro, Ubaldo; Belin, Sophie; Caruso, Donatella; Mitro, Nico; Pellegatta, Marta; Taveggia, Carla; Schwab, Markus H.; Nave, Klaus-Armin; Feltri, M. Laura; Wrabetz, Lawrence; D'Antonio, Maurizio Share Save
A nonsense mutation in myelin protein zero causes congenital hypomyelination neuropathy through altered P0 membrane targeting and gain of abnormal function Fratta, Pietro; Ornaghi, Francesca; Dati, Gabriele; Zambroni, Desiree; Saveri, Paola; Belin, Sophie; D'Adamo, Patrizia; Shy, Michael; Quattrini, Angelo; Feltri, M. Laura; Wrabetz, Lawrence Share Save
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Consensus guidelines for newborn screening, diagnosis and treatment of infantile Krabbe disease Kwon, Jennifer M.; Matern, Dietrich; Kurtzberg, Joanne; Wrabetz, Lawrence; Gelb, Michael H.; Wenger, David A.; Ficicioglu, Can; Waldman, Amy T.; Burton, Barbara K.; Hopkins, Patrick V.; Orsini, Joseph J. Share Save