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Elena Sieni

university of florence

22H-index
82Paper Count
2.0KCitation Count
Published Papers 27
Publication Date
Central Nervous System Involvement in Children with Hemophagocytic Lymphohistiocytosis: an HLH-2004 Study Report
err2026-08-25
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errElisabet Bergsten; Maurizio Aricó; Itziar Astigarraga; Eiichi Ishii; Gritta Janka; Stephan Ladisch; Kai Lehmberg; Kenneth L. McClain; Milen Minkov; Vasanta Nanduri; Diego A. Rosso; Elena Sieni; AnnaCarin Horne; Jan-Inge Henter
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Disease Extent, Not Lesion Location, Determines Relapse Risk in Single-System Skeletal Langerhans Cell Histiocytosis
err2026-05-12
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errItziar Astigarraga; Helga Arnardottir; Oussama Abla; Maurizio Arico; Jorge Braier; Jean Donadieu; Nicole Grois; Jan-Inge Henter; Stephan Ladisch; Thomas Lehrnbecher; Kenneth McClain; Vasanta Nanduri; Carlos Rodriguez-Galindo; Elena Sieni; Sheila Weitzman; Ulrike Pötschger; Milen Minkov
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Neurodegenerative Langerhans cell histiocytosis: long-term follow-up of 63 patients from the Italian Registry
err2026-05-01
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PREAI
errTrambusti, Irene; Pegoraro, Francesco; Coniglio, Maria Luisa; Gaspari, Stefania; Chiaravalli, Stefano; Corti, Paola; De Fusco, Carmen; Trizzino, Antonino; Verrico, Antonio; Barat, Veronica; Cellini, Monica; Todesco, Alessandra; Tanturli, Michele; Romano, Katiuscia; Chinnici, Aurora; Beneforti, Linda; Mortilla, Marzia; Perrone, Anna; Tondo, Annalisa; Guerrini, Renzo; Barba, Carmen; Sieni, Elena
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Encouraging Outcomes in Pediatric Malignancy-Associated Hemophagocytic Lymphohistiocytosis: Results From the Italian HLH Registry
err2026-03-12
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errFrancesco Pegoraro; Irene Ferri; Aurora Chinnici; Linda Beneforti; Irene Trambusti; Simona Gobbi; Rosa Maria Daniele; Rosamaria Mura; Elena Palmisani; Marco Zecca; Giulia Albrici; Alessandra Todesco; Carmela De Fusco; Samuele Naviglio; Veronica Barat; Fabio Timeus; Marta Pillon; Carmelo Rizzari; Annalisa Tondo; Maria Luisa Coniglio; Elena Sieni
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Long-term MAPK inhibition of childhood refractory-Langerhans cell histiocytosis: an observational study on 288 patients
err2026-02-16
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errJean Donadieu; Dmitry Evseev; Francesco Pegoraro; Elena Sieni; Olga Slater; Caroline Hutter; Itziar Astigarraga; Thomas Lehrnbecher; Cor van den Bos; Mathieu Simonin; Martina Ahlmann; Mohamed Barkaoui; Solenne Le Louet; Aurore Chevallier; François Chalard; Trung Nguyen; Suzanne Holzhauer; Karin Beutel; Henriette Haenicke; Gabriele Escherich
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Real-Life Efficacy and Safety of BRAF Inhibitors in Erdheim-Chester Disease
err2025-11-08
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errFrancesco Pegoraro; Francesco Peyronel; Matthias Papo; Riccardo Sutera; Francesco Catamerò; Francesco Poeta; Jerome Razanamahery; Emmanuel Ledoult; Tanguy Le Scornet; Mathilde de Menthon; Etienne Riviere; Elena Sieni; Stephane Barete; Ahmed Idbaih; Fleur Cohen-Aubart; Zahir Amoura; Jean-François Emile; Augusto Vaglio; Julien Haroche
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Diagnostic impact of exome sequencing in haemophagocytic lymphohistiocytosis: A report from the Italian reference centre
err2025-08-26
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PREAI
errAurora Chinnici; Linda Beneforti; Daniela Balasco; Elia Dirupo; Michele Tanturli; Yasmine El Chazli; Alessandra Todesco; Fabio Timeus; Paola Corti; Carmen de Fusco; Annalisa Tondo; Francesco Pegoraro; Elena Sieni; Maria Luisa Coniglio
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A multidisciplinary non-invasive approach to monitor response to intravenous immunoglobulin treatment in neurodegenerative Langerhans cell histiocytosis: a real-world study
err2024-08-16
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errTrambusti, Irene; Barba, Carmen; Mortilla, Marzia; Rizzi, Susanna; Romano, Katiuscia; Coniglio, Maria Luisa; Lucenteforte, Ersilia; Tondo, Annalisa; Guerrini, Renzo; Sieni, Elena
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Long-term outcome and prognosis of mixed histiocytosis (Erdheim-Chester disease and Langerhans Cell Histiocytosis)
err2024-07-01
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errPegoraro, Francesco; Papo, Matthias; Cohen-Aubart, Fleur; Peyronel, Francesco; Lugli, Gianmarco; Trambusti, Irene; Baulier, Gildas; de Menthon, Mathilde; Le Scornet, Tanguy; Oziol, Eric; Ferreira-Maldent, Nicole; Hermine, Olivier; Faucher, Benoit; Koschel, Dirk; Straetmans, Nicole; Abisror, Noemie; Terrier, Benjamin; Lifermann, Francois; Razanamahery, Jerome; Allenbach, Yves; Keraen, Jeremy; Bulifon, Sophie; Hervier, Baptiste; Buccoliero, Annamaria; Charlotte, Frederic; Monzani, Quentin; Boussouar, Samia; Shor, Natalia; Tondo, Annalisa; Barete, Stephane; Idbaih, Ahmed; Tazi, Abdellatif; Sieni, Elena; Amoura, Zahir; Emile, Jean-Francois; Vaglio, Augusto; Haroche, Julien
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HLH as an additional warning sign of inborn errors of immunity beyond familial-HLH in children: a systematic review (vol 15, 1282804, 2024)
err2024-03-26
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errRicci, Silvia; Sarli, Walter Maria; Lodi, Lorenzo; Canessa, Clementina; Lippi, Francesca; Dini, Donata; Ferrari, Marta; Pisano, Laura; Sieni, Elena; Indolfi, Giuseppe; Resti, Massimo; Azzari, Chiara
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Outcome of primary hemophagocytic lymphohistiocytosis: a report on 143 patients from the Italian Registry
err2024-02-22
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errPegoraro, Francesco; Chinnici, Aurora; Beneforti, Linda; Tanturli, Michele; Trambusti, Irene; De Fusco, Carmela; Micalizzi, Concetta; Barat, Veronica; Cesaro, Simone; Gaspari, Stefania; Dell'Acqua, Fabiola; Todesco, Alessandra; Timeus, Fabio; Arico, Maurizio; Favre, Claudio; Tondo, Annalisa; Coniglio, Maria Luisa; Sieni, Elena
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HLH as an additional warning sign of inborn errors of immunity beyond familial-HLH in children: a systematic review
err2024-02-13
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errRicci, Silvia; Sarli, Walter Maria; Lodi, Lorenzo; Canessa, Clementina; Lippi, Francesca; Dini, Donata; Ferrari, Marta; Pisano, Laura; Sieni, Elena; Indolfi, Giuseppe; Resti, Massimo; Azzari, Chiara
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Hemophagocytic inflammatory syndrome in ADA-SCID: report of two cases and literature review
err2023-06-26
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errFratini, Elena Sophia; Migliavacca, Maddalena; Barzaghi, Federica; Fossati, Claudia; Giannelli, Stefania; Monti, Ilaria; Casiraghi, Miriam; Ferrua, Francesca; Recupero, Salvatore; Consiglieri, Giulia; Calbi, Valeria; Tucci, Francesca; Gallo, Vera; Bernardo, Maria Ester; Cenciarelli, Sabina; Palmoni, Monica; Moni, Margherita; Galimberti, Luca; Duse, Marzia; Leonardi, Lucia; Sieni, Elena; Soncini, Elena; Porta, Fulvio; Notarangelo, Lucia Dora; De Santis, Raffaella; Ladogana, Saverio; Aiuti, Alessandro; Cicalese, Maria Pia
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Approaching hemophagocytic lymphohistiocytosis
err2023-06-22
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errChinnici, Aurora; Beneforti, Linda; Pegoraro, Francesco; Trambusti, Irene; Tondo, Annalisa; Favre, Claudio; Coniglio, Maria Luisa; Sieni, Elena
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Clinicogenomic associations in childhood Langerhans cell histiocytosis: an international cohort study
err2023-02-21
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errKemps, Paul G.; Zondag, Timo C. E.; Arnardottir, Helga B.; Solleveld-Westerink, Nienke; Borst, Jelske; Steenwijk, Eline C.; van Egmond, Demi; Swennenhuis, Joost F.; Stelloo, Ellen; Trambusti, Irene; Verdijk, Robert M.; van Noesel, Carel J. M.; Cleven, Arjen H. G.; Scheijde-Vermeulen, Marijn A.; Koudijs, Marco J.; Krskova, Lenka; Hawkins, Cynthia; Egeler, R. Maarten; Brok, Jesper; Greenwood, Tatiana von Bahr; Svojgr, Karel; Beishuizen, Auke; van Laar, Jan A. M.; Poetschger, Ulrike; Hutter, Caroline; Sieni, Elena; Minkov, Milen; Abla, Oussama; van Wezel, Tom; van den Bos, Cor; van Halteren, Astrid G. S.
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Additive Prognostic Impact of Gastrointestinal Involvement in Severe Multisystem Langerhans Cell Histiocytosis
err2021-10-01
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errMinkov, Milen; Poetschger, Ulrike; Thacker, Nirav; Astigarraga, Itziar; Braier, Jorge; Donadieu, Jean; Henter, Jan-Inge; Lehrnbecher, Thomas; Rodriguez-Galindo, Carlos; Sieni, Elena; Nanduri, Vasanta; van den Bos, Cor; Abla, Oussama
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Stem cell transplantation for children with hemophagocytic lymphohistiocytosis: results from the HLH-2004 study
err2020-08-11
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errBergsten, Elisabet; Horne, AnnaCarin; Myrberg, Ida Hed; Arico, Maurizio; Astigarraga, Itziar; Ishii, Eiichi; Janka, Gritta; Ladisch, Stephan; Lehmberg, Kai; McClain, Kenneth L.; Minkov, Milen; Nanduri, Vasanta; Rosso, Diego A.; Sieni, Elena; Winiarski, Jacek; Henter, Jan-Inge
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A Multicenter Study of Patients with Multisystem Langerhans Cell Histiocytosis Who Develop Secondary Hemophagocytic Lymphohistiocytosis
errCANCER
IF5.1
err2018-12-06
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errChellapandian, Deepak; Hines, Melissa R.; Zhang, Rui; Jeng, Michael; van den Bos, Cor; Santa-Maria Lopez, Vicente; Lehmberg, Kai; Sieni, Elena; Wang, Yini; Nakano, Taizo; Williams, James A.; Fustino, Nicholas J.; Astigarraga, Itziar; Dunkel, Ira J.; Abla, Oussama; van Halteren, Astrid G. S.; Pei, Deqing; Cheng, Cheng; Weitzman, Sheila; Sung, Lillian; Nichols, Kim E.
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Recommendations for the Use of Etoposide-Based Therapy and Bone Marrow Transplantation for the Treatment of HLH: Consensus Statements by the HLH Steering Committee of the Histiocyte Society
err2018-09-01
err152
PREAI
errEhl, Stephan; Astigarraga, Itziar; Greenwood, Tatiana von Bahr; Hines, Melissa; Horne, AnnaCarin; Ishii, Eiichi; Janka, Gritta; Jordan, Michael B.; La Rosee, Paul; Lehmberg, Kai; Machowicz, Rafal; Nichols, Kim E.; Sieni, Elena; Wang, Zhao; Henter, Jan-Inge
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Genetic predisposition to hemophagocytic lymphohistiocytosis: Report on 500 patients from the Italian registry
err2016-01-01
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errCetica, Valentina; Sieni, Elena; Pende, Daniela; Danesino, Cesare; De Fusco, Carmen; Locatelli, Franco; Micalizzi, Concetta; Putti, Maria Caterina; Biondi, Andrea; Fagioli, Franca; Moretta, Lorenzo; Griffiths, Gillian M.; Luzzatto, Lucio; Arico, Maurizio
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