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David J. Pagliarini

Washington University School of Medicine

47H-index
153Paper Count
9.7KCitation Count
Published Papers 84
Publication Date
The predicted interactome of the human mitochondrial proteome
err2026-08-25
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errAbhinav B. Swaminathan; Mohammad Zulkifli; Rachel M. Guerra; Sofia M. Calabrese; Dimitris T. Kalafatis; David J. Pagliarini; Vishal M. Gohil
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Fmp30p is a mitochondrial phosphatidylinositol hydrolase that modulates CoQ biosynthesis
err2026-05-30
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errZakery N. Baker; Rachel M. Guerra; Sean W. Rogers; David J. Pagliarini
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Targeting TOMM40 and TOMM22 to Rescue Statin-Impaired Mitochondrial Function, Dynamics, and Mitophagy in Skeletal Myotubes
err2025-11-15
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errNeil V. Yang; Sean Rogers; Rachel Guerra; Justin Y. Chao; David J. Pagliarini; Elizabeth Theusch; Ronald M. Krauss
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Uridine-sensitized screening identifies demethoxy-coenzyme Q and NUDT5 as regulators of nucleotide synthesis
err2025-11-13
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errAbigail Strefeler; Zakery N. Baker; Sylvain Chollet; Mads M. Foged; Rachel M. Guerra; Julijana Ivanisevic; Hector Gallart-Ayala; David J. Pagliarini; Alexis A. Jourdain
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Severe Neurological Presentation in Siblings With COQ5-Related Primary Coenzyme Q10 Deficiency: Expanding Clinical and Molecular Spectrum
err2025-11-05
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errWongkittichote, Parith; Guerra, Rachel M.; Wegner, Daniel J.; Toy, Samantha; Hauer, Jacqueline A.; Pagliarini, David J.; Granadillo, Jorge L.
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Mitochondrial dysfunction and lipid dysregulation in yeast lacking phosphatidylserine
err2025-10-01
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errJoshi, Alaumy; Baker, Zakery N.; Stanfield, Rachel A.; Kalafatis, Dimitris T.; Pagliarini, David J.; Gohil, Vishal M.
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DFCP1 is a regulator of starvation-driven ATGL-mediated lipid droplet lipolysis
err2025-01-01
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errIsmail, Victoria A.; Schuetz, Meg; Baker, Zak N.; Castillo-Badillo, Jean A.; Naismith, Teri V.; Pagliarini, David J.; Kast, David J.
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Missense variants in CMS22 patients reveal that PREPL has both enzymatic and nonenzymatic functions
err2024-09-10
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errMonnens, Yenthe; Theodoropoulou, Anastasia; Rosier, Karen; Bhalla, Kritika; Mahy, Alexia; Vanhoutte, Roeland; Meulemans, Sandra; Cavani, Edoardo; Antanasijevic, Aleksandar; Lemmens, Irma; Lee, Jennifer A.; Spellicy, Catherine J.; Schroer, Richard J.; Maselli, Ricardo A.; Laverty, Chamindra G.; Agostinis, Patrizia; Pagliarini, David J.; Verhelst, Steven; Marcaida, Maria J.; Rochtus, Anne; Dal Peraro, Matteo; Creemers, John W. M.
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Fast and deep phosphoproteome analysis with the Orbitrap Astral mass spectrometer
err2024-08-15
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errLancaster, Noah M.; Sinitcyn, Pavel; Forny, Patrick; Peters-Clarke, Trenton M.; Fecher, Caroline; Smith, Andrew J.; Shishkova, Evgenia; Arrey, Tabiwang N.; Pashkova, Anna; Robinson, Margaret Lea; Arp, Nicholas; Fan, Jing; Hansen, Juli; Galmozzi, Andrea; Serrano, Lia R.; Rojas, Julie; Gasch, Audrey P.; Westphall, Michael S.; Stewart, Hamish; Hock, Christian; Damoc, Eugen; Pagliarini, David J.; Zabrouskov, Vlad; Coon, Joshua J.
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Coenzyme Q4 is a functional substitute for coenzyme Q10 and can be targeted to the mitochondria
err2024-05-01
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errSteenberge, Laura H.; Rogers, Sean; Sung, Andrew Y.; Fan, Jing; Pagliarini, David J.
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COQ4 is required for the oxidative decarboxylation of the C1 carbon of coenzyme Q in eukaryotic cells
err2024-03-01
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errPelosi, Ludovic; Morbiato, Laura; Burgardt, Arthur; Tonello, Fiorella; Bartlett, Abigail K.; Guerra, Rachel M.; Ferizhendi, Katayoun Kazemzadeh; Desbats, Maria Andrea; Rascalou, Berengere; Marchi, Marco; Vazquez-Fonseca, Luis; Agosto, Caterina; Zanotti, Giuseppe; Roger-Margueritat, Morgane; Alcazar-Fabra, Maria; Garcia-Corzo, Laura; Sanchez-Cuesta, Ana; Navas, Placido; Brea-Calvo, Gloria; Trevisson, Eva; Wendisch, Volker F.; Pagliarini, David J.; Salviati, Leonardo; Pierrel, Fabien
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Reducing mitochondrial mysteries
err2023-10-26
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errGuerra, Rachel M.; Pagliarini, David J.
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PPTC7 maintains mitochondrial protein content by suppressing receptor-mediated mitophagy
err2023-10-13
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errNiemi, Natalie M.; Serrano, Lia R.; Muehlbauer, Laura K.; Balnis, Catherine E.; Wei, Lianjie; Smith, Andrew J.; Kozul, Keri-Lyn; Forny, Merima; Connor, Olivia M.; Rashan, Edrees H.; Shishkova, Evgenia; Schueler, Kathryn L.; Keller, Mark P.; Attie, Alan D.; Friedman, Jonathan R.; Pagan, Julia K.; Coon, Joshua J.; Pagliarini, David J.
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Hem25p is required for mitochondrial IPP transport in fungi
err2023-10-09
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errTai, Jonathan; Guerra, Rachel M.; Rogers, Sean W.; Fang, Zixiang; Muehlbauer, Laura K.; Shishkova, Evgenia; Overmyer, Katherine A.; Coon, Joshua J.; Pagliarini, David J.
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Mitochondrial proteome research: the road ahead
err2023-09-29
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errBaker, Zakery N.; Forny, Patrick; Pagliarini, David J.
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Coenzyme Q biochemistry and biosynthesis
err2023-05-01
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errGuerra, Rachel M.; Pagliarini, David J.
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Aim18p and Aim46p are chalcone isomerase domain-containing mitochondrial hemoproteins in cerevisiae
err2023-03-01
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errSchmitz, Jonathan M.; Wolters, John F.; Murray, Nathan H.; Guerra, Rachel M.; Bingman, Craig A.; Hittinger, Chris Todd; Pagliarini, David J.
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Structure and functionality of a multimeric human COQ7:COQ9 complex
err2022-11-01
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errManicki, Mateusz; Aydin, Halil; Abriata, Luciano A.; Overmyer, Katherine A.; Guerra, Rachel M.; Coon, Joshua J.; Dal Peraro, Matteo; Frost, Adam; Pagliarini, David J.
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Small-molecule inhibition of the archetypal UbiB protein COQ8
err2022-10-27
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errMurray, Nathan H.; Asquith, Christopher R. M.; Fang, Zixiang; East, Michael P.; Ptak, Naomi; Smith, Robert W.; Vasta, James D.; Zimprich, Chad A.; Corona, Cesear R.; Robers, Matthew B.; Johnson, Gary L.; Bingman, Craig A.; Pagliarini, David J.
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Nitric oxide-driven modifications of lipoic arm inhibit α-ketoacid dehydrogenases
err2022-10-20
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errSeim, Gretchen L.; John, Steven, V; Arp, Nicholas L.; Fang, Zixiang; Pagliarini, David J.; Fan, Jing
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