arrow
Back
W

William B. Guggino

Johns Hopkins University

84H-index
302Paper Count
2.8WCitation Count
Published Papers 97
Publication Date
CFTR and PC2, partners in the primary cilia in autosomal dominant polycystic kidney disease
err2023-09-01
err1
errOAAI
errYanda, Murali K.; Ciobanu, Cristian; Guggino, William B.; Cebotaru, Liudmila
errShare
errSave
The Mitochondrial Ca2+ import complex is altered in ADPKD
err2022-01-01
err6
errOAAI
errYanda, Murali K.; Tomar, Vartika; Cole, Robert; Guggino, William B.; Cebotaru, Liudmila
errShare
errSave
Role of calcium in adult onset polycystic kidney disease
err2019-01-01
err16
errOAAI
errYanda, Murali K.; Liu, Qiangni; Cebotaru, Valeriu; Guggino, William B.; Cebotaru, Liudmila
errShare
errSave
Rescue of CFTR NBD2 mutants N1303K and S1235R is influenced by the functioning of the autophagosome
err2018-09-01
err12
errOAAI
errLiu, Qiangni; Sabirzhanova, Irma; Yanda, Murali K.; Bergbower, Emily A. S.; Boinot, Clement; Guggino, William B.; Cebotaru, Liudmila
errShare
errSave
Wireless control of cellular function by activation of a novel protein responsive to electromagnetic fields
err2018-06-08
err34
errOAAI
errKrishnan, Vijai; Park, Sarah A.; Shin, Samuel S.; Alon, Lina; Tressler, Caitlin M.; Stokes, William; Banerjee, Jineta; Sorrell, Mary E.; Tian, Yuemin; Fridman, Gene Y.; Celnik, Pablo; Pevsner, Jonathan; Guggino, William B.; Gilad, Assaf A.; Pelled, Galit
errShare
errSave
Histone deacetylase 6 inhibition reduces cysts by decreasing cAMP and Ca2+ in knock-out mouse models of polycystic kidney disease
err2017-10-01
err33
errOAAI
errYanda, Murali K.; Liu, Qiangni; Cebotaru, Valeriu; Guggino, William B.; Cebotaru, Liudmila
errShare
errSave
Inhibition of histone deacetylase 6 activity reduces cyst growth in polycystic kidney disease
err2016-07-01
err67
errOAAI
errCebotaru, Liudmila; Liu, Qiangni; Yanda, Murali K.; Boinot, Clement; Outeda, Patricia; Huso, David L.; Watnick, Terry; Guggino, William B.; Cebotaru, Valeriu
errShare
errSave
The R122H Mutation Stabilizes the PRSS1 Protein in Pancreatitis
err2016-04-01
err0
PREAI
errBoinot, Clement; Sabirzhanova, Inna; Guggino, William; Cebotaru, Liudmila
errShare
errSave
C-difficile Toxin B Increases Chloride Secretion in CaCo2 Cells
err2016-04-01
err0
PREAI
errYanda, Murali K.; Boinot, Clement; Sabirzhanova, Inna; Guggino, William; Cebotaru, Liudmila
errShare
errSave
From CFTR biology toward combinatorial pharmacotherapy: expanded classification of cystic fibrosis mutations
err2016-02-01
err473
errOAAI
errVeit, Gudio; Avramescu, Radu G.; Chiang, Annette N.; Houck, Scott A.; Cai, Zhiwei; Peters, Kathryn W.; Hong, Jeong S.; Pollard, Harvey B.; Guggino, William B.; Balch, William E.; Skach, William R.; Cutting, Garry R.; Frizzell, Raymond A.; Sheppard, David N.; Cyr, Douglas M.; Sorscher, Eric J.; Brodsky, Jeffrey L.; Lukacs, Gergely L.
errShare
errSave
Combination of Correctors Rescue ΔF508-CFTR by Reducing Its Association with Hsp40 and Hsp27
err2015-10-01
err40
errOAAI
errLopes-Pacheco, Miqueias; Boinot, Clement; Sabirzhanova, Inna; Morales, Marcelo M.; Guggino, William B.; Cebotaru, Liudmila
errShare
errSave
Rescuing Trafficking Mutants of the ATP-binding Cassette Protein, ABCA4, with Small Molecule Correctors as a Treatment for Stargardt Eye Disease
err2015-08-01
err44
errOAAI
errSabirzhanova, Inna; Pacheco, Miqueias Lopes; Rapino, Daniele; Grover, Rahul; Handa, James T.; Guggino, William B.; Cebotaru, Liudmila
errShare
errSave
Overcoming the Cystic Fibrosis Sputum Barrier to Leading Adeno-associated Virus Gene Therapy Vectors
err2014-08-01
err82
errOAAI
errSchuster, Benjamin S.; Kim, Anthony J.; Kays, Joshua C.; Kanzawa, Mia M.; Guggino, William B.; Boyle, Michael P.; Rowe, Steven M.; Muzyczka, Nicholas; Suk, Jung Soo; Hanes, Justin
errShare
errSave
Mis-regulation of Mammalian Target of Rapamycin (mTOR) Complexes Induced by Albuminuria in Proximal Tubules
err2014-06-01
err36
errOAAI
errPeruchetti, Diogo B.; Cheng, Jie; Caruso-Neves, Celso; Guggino, William B.
errShare
errSave
Polycystin-1 Negatively Regulates Polycystin-2 Expression via the Aggresome/Autophagosome Pathway
err2014-03-01
err29
errOAAI
errCebotaru, Valeriu; Cebotaru, Liudmila; Kim, Hyunho; Chiaravalli, Marco; Boletta, Alessandra; Qian, Feng; Guggino, William B.
errShare
errSave
Gout-causing Q141K mutation in ABCG2 leads to instability of the nucleotide-binding domain and can be corrected with small molecules
err2013-03-14
err98
errOAAI
errWoodward, Owen M.; Tukaye, Deepali N.; Cui, Jinming; Greenwell, Patrick; Constantoulakis, Leeza M.; Parker, Benjamin S.; Rao, Anjana; Koettgen, Michael; Maloney, Peter C.; Guggino, William B.
errShare
errSave
Future Directions in Early Cystic Fibrosis Lung Disease Research An NHLBI Workshop Report
err2012-04-15
err66
errOAAI
errRamsey, Bonnie W.; Banks-Schlegel, Susan; Accurso, Frank J.; Boucher, Richard C.; Cutting, Garry R.; Engelhardt, John F.; Guggino, William B.; Karp, Christopher L.; Knowles, Michael R.; Kolls, Jay K.; LiPuma, John J.; Lynch, Susan; McCray, Paul B., Jr.; Rubenstein, Ronald C.; Singh, Pradeep K.; Sorscher, Eric; Welsh, Michael
errShare
errSave