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Pierre‐Régis Burgel

assistance publique hopitaux paris (aphp)

61H-index
633Paper Count
1.4WCitation Count
Published Papers 253
Publication Date
A disrupted microbial network and an ecological shift towards anaerobes in NTM-infected cystic fibrosis patients
err2026-04-28
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errHélène Pailhoriès; Lourdes Velo-Suarez; Yann Moalic; Juliana Alcoforado-Diniz; Stéphanie Gouriou; Antoine Bessou; Emmanuelle Cambau; Pierre-Régis Burgel; Jean-Louis Herrmann; Geneviève Héry-Arnaud
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European Respiratory Society clinical practice guideline for the management of adult bronchiectasis
err2025-12-01
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PREAI
errChalmers, James D.; Haworth, Charles S.; Flume, Patrick; Long, Merete B.; Burgel, Pierre-Regis; Dimakou, Katerina; Blasi, Francesco; Herrero-Cortina, Beatriz; Dhar, Raja; Chotirmall, Sanjay H.; Ringshausen, Felix C.; Altenburg, Josje; Morgan, Lucy; Nigro, Mattia; Crichton, Megan L.; Van Meel, Chayenne; Sibila, Oriol; Timothy, Alan; Kompatsiari, Eliza; Hedberg, Tanja; Vandendriessche, Thomas; McShane, Pamela J.; Tonia, Thomy; Winthrop, Kevin; Loebinger, Michael R.; Lorent, Natalie; Goeminne, Pieter; Shteinberg, Michal; Polverino, Eva; Aliberti, Stefano
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Multidimensional prognostic risk stratification of COPD exacerbations: the baseline, acuity, and trigger (BAt) model
err2025-11-25
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PREAI
errHnin W W Aung; Kristina Vermeersch; Hamish J C McAuley; Sanjay Ramakrishnan; Mustafa Abdo; Amber Beersaerts; Steven P Cass; Nicola Smallcombe; Iwein Gyselinck; Hendrik Pott; Tom J C Ward; Adam K A Wright; Christopher E Brightling; Pierre-Régis Burgel; Marco Contoli; Frits M E Franssen; Arturo Huerta; Jennifer K Quint; Bernd Schmeck; Lowie E G W Vanfleteren
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Impact of Increased Use of Single-Inhaler Triple Therapies on COPD Exacerbation Rates; Mortality; and Total Costs: PROMETHEUS France
err2025-11-17
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errGaëtan Deslee; Héloïse Russo; Caroline Fabry-Vendrand; David Koskas; Gabriel Thabut; John P Bell; Melissa Caplen; Prachi Devendra Bhatt; Jennifer Carioto; Bruce Pyenson; Pierre-Régis Burgel
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Beyond Trikafta: new models to assess tissue dependent rescue of N1303K-CFTR
err2025-10-29
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errIwona Pranke†; Valeria Capurro†; Benoit Chevalier†; Emanuela Pesce†; Valeria Tomati; Cristina Pastorino; Mairead Kelly-Aubert; Aurelie Hatton; Elise Dreano; Mariateresa Lena; Renata Bocciardi; Federico Zara; Stefano Pantano; Vito Terlizzi; Cristina Lucanto; Stefano Costa; Laura Claut; Valeria Daccò; Piercarlo Poli; Massimo Maschio; Benedetta Fabrizzi; Nicole Caporelli; Marco Cipolli; Sonia Volpi; Frederique Chedevergne; Laure Cosson; Julie Macey; Sophie Ramel; Laurence Weiss; Dominique Grenet; Laurence Le Clainche-Viala; Benoit Douvry; Bruno Ravoninjatovo; Camille Audousset; Aurélie Tatopoulos; Bénédicte Richaud-Thiriez; Melissa Baravalle; Guillaume Thouvenin; Guillaume Labbé; Marie Mittaine; Philippe Reix; Isabelle Durieu; Julie Mankikian; Stéphanie Bui; Thao Nguyen-Khoa; Karim Khoukh; Clémence Martin; Jennifer Da Silva; Paola De Carli; Carlo Castellani; Federico Cresta; Luis Galietta; Anne Guillemaut; Emmanuelle Girodon; Natacha Remus; Mathis Bulcaen; Marjolein Ensinck; Miroslaw Zajac; Marianne Carlon; Jean LeBihan; Pierre-Régis Burgel; Isabelle Sermet-Gaudelus‡; Alexandre Hinzpeter‡; Nicoletta Pedemonte‡
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Global prevalence of CFTR variants with respect to their responsiveness to elexacaftor-tezacaftor-ivacaftor
err2025-10-17
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errP-R Burgel; A. Orenti; E. Cromwell; M. Macek; H.H. Gutierrez; B. Karadag; A. Faro; J.G. van Rens; L. Naehrlich; E. Bakkeheim; S.B. Carr; A. Lindblad; A. Zolin; E. Lammertyn; R. Ruseckaite; M. Zampoli; C.A. Byrnes; LVRF da Silva-Filho; A. Elbert; S.Y. Cheng; A.L. Stephenson
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Pregnancy after lung transplantation: TRIGGER study on anti-human leucocyte antigen alloimmunization and antibody-mediated rejection risk
err2025-10-08
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PREAI
errA. Leclerc; I. Danner-Boucher; A. Walencik; B. Guyomarch; C. Bry; V. Dochez; J. Le Pavec; O. Brugière; M. Reynaud-Gaubert; B. Coiffard; R. Kessler; X. Demant; J. Macey; C. Merveilleux du Vignaux; C. Saint -Raymond; P-R. Burgel; N. Carlier; J. Silleran-Chassany; B. Bayeh; F-X. Blanc; A. Tissot
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Identification of structural predictors of lung function improvement in adults with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor using deep-learning
err2025-09-30
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PREAI
errGuillaume Chassagnon; Rafael Marini; Valentin Ong; Jennifer Da Silva; Denis Habip Gatenyo; Isabelle Honore; Reem Kanaan; Nicolas Carlier; Johanna Fesenbeckh; Espérie Burnet; Marie-Pierre Revel; Clémence Martin; Pierre-Régis Burgel
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Outpatient Parenteral Antimicrobial Therapy in a Tertiary Hospital in France: A Description of Service Models and Costs
err2025-09-28
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errEspérie Burnet; Alicia Le Bras; Guillaume Roucoux; Christian Dupont; Etienne Canouï; Clément Leclaire; Jérémie Zerbit; Pierre Régis Burgel; Clémence Martin; Isabelle Durand-Zaleski; Martin Duracinsky
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Sweat chloride and lung function responses to elexacaftor–tezacaftor–ivacaftor in people with cystic fibrosis with two versus one responsive CFTR variants: an analysis of two real-world observational studies
err2025-09-03
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PREAI
errPierre-Régis Burgel; Jennifer Da Silva; Emmanuelle Girodon; Isabelle Durieu; Martine Reynaud-Gaubert; Marlene Murris-Espin; Raphael Chiron; Dominique Grenet; Sophie Ramel; Laurent Mely; Rebecca Hamidfar; Benoit Douvry; Véronique Houdouin; Camille Audousset; Julie Macey; Marie Mittaine; Laurence Weiss; Laure Cosson; Isabelle Danner-Boucher; Philippe Reix; Mélisande Baravalle; Espérie Burnet; Isabelle Sermet-Gaudelus; Clémence Martin; Jean-Louis Paillasseur
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Bronchiectasis in France: data on disease characteristics in 630 patients from the European Bronchiectasis registry (EMBARC)
err2025-09-01
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errBurgel, Pierre-Regis; Bergeron, Anne; Maitre, Bernard; Andrejak, Claire; Audoly, Cristina; Boitiaux, Jean-Francois; Camara, Boubou; Coolen-Allou, Nathalie; Douvry, Benoit; Chatte, Gerard; Fanton, Annlyse; Leroy, Sylvie; Martin, Clemence; Michaux, Karine; Payet, Annabelle; Pegliasco, Herve; Schlemmer, Frederic; Vignal, Guillaume; Duchange, Agnes; Burnet, Esperie; Chalmers, James D.; Murris-Espin, Marlene
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Elexacaftor-tezacaftor-ivacaftor in people with cystic fibrosis harbouring two CFTR Class I variants: real-world data from the French compassionate programme
err2025-08-30
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PREAI
errPierre-Régis Burgel; Emmanuelle Girodon; Neeraj Sharma; Caroline Raynal; Jennifer Da Silva; Souphatta Sasorith; Clémence Martin; Isabelle Sermet-Gaudelus; Karen Raraigh
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Symptoms, risk of future exacerbations, and response to long-term macrolide treatment in bronchiectasis: an observational study
err2025-08-27
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errOriol Sibila; Jamie Stobo; Lidia Perea; Yong-Hua Gao; Jin-Fu Xu; Holly Lind; Kateryna Viligorska; Arietta Spinou; Eva Polverino; Felix C Ringshausen; Montserrat Vendrell; Pierre-Régis Burgel; Charles S Haworth; Michael R Loebinger; Natalie Lorent; Raja Dhar; Hayoung Choi; Sanjay H Chotirmall; Anthony De Soyza; John R Hurst; Jeremy S Brown; Menno van der Eerden; Paula Kauppi; Emma D Johnson; Raul Mendez; Katerina Dimakou; Apostolos Bossios; Antoni Torres; Francesco Blasi; Michal Shteinberg; Stuart J Elborn; Pieter C Goeminne; Stefano Aliberti; Lata Jayaram; Noel Karalus; Steven L Taylor; Megan L Martin; Lucy D Burr; Conroy Wong; Lotte Terpstra; Josje Altenburg; Wim Boersma; James D Chalmers
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News article
err2025-07-22
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PREAI
errChris Smith; Pierre-Regis Burgel; Mattijs Bulcaen
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Decreased insulin dose-adjusted hemoglobin A1c in adults with cystic fibrosis-related diabetes treated with elexacaftor-tezacaftor-ivacaftor
err2025-07-02
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errEspérie Burnet; Deborah Grunewald; Etienne Larger; Florence Camus-Bablon; Catherine Eisenhauer; François Mifsud; Clémence Martin; Isabelle Honoré; Reem Kanaan; Nicolas Carlier; Johanna Fesenbeckh; Helen Mosnier-Pudar; Pierre-Régis Burgel
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Cystic Fibrosis Liver Disease Progression in the Era of Elexacaftor-Tezacaftor-Ivacaftor
err2025-07-01
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errCharlotte Mouliade; Lucia Parlati; Stylianos Tzedakis; Mathis Collier; Samir Bouam; Anais Vallet-Pichard; Valérie D’Halluin-Venier; Reem Kanaan; Stanislas Pol; Philippe Sogni; Pierre-Régis Burgel; Vincent Mallet
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Pregnancy and neonatal outcome following in utero exposure to CFTR modulators: A multicentre prospective case series
err2025-06-21
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errSophie Gautier; Bénédicte Coulm; Marie-Andrée Thompson-Bos; Laurent Chouchana; Camille Audousset; Elisabeth Elefant; Julie Mankikian; Pierre-Regis Burgel; Charles Garabedian; Benoît Marin; Annie-Pierre Jonville - Bera
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Population Pharmacokinetics of Elexacaftor, Tezacaftor and Ivacaftor in a Real-World Cohort of Adults with Cystic Fibrosis
err2025-05-22
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PREAI
errMagnas, Paulette; Bouazza, Naim; Foissac, Frantz; Bournaud, Leo Froelicher; Lui, Gabrielle; Carlier, Nicolas; Da Silva, Jennifer; Fesenbeckh, Johanna; Kanaan, Reem; Honore, Isabelle; Martin, Clemence; Treluyer, Jean-Marc; Burgel, Pierre-Regis; Benaboud, Sihem
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