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Oliver Rackham

kids research institute australia

49H指数
225论文数
9.8K被引数
收录论文 79
发表时间
Specific SLC25 carriers regulate mitochondrial protein synthesis特异性SLC25载体调控线粒体蛋白质合成
err2026-02-25
err0
errOAAI
errDanielle L. Rudler; Laetitia A. Hughes; Martin S. King; Jessica Baker; Richard G. Lee; Andrianto P. Gandadireja; Anisha Sunil; Samuel V. Fagan; Blake Payne; Nicola Gray; Tim McCubbin; Edmund R. S. Kunji; Oliver Rackham; Aleksandra Filipovska
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TANGO2 binds crystallin alpha B and its loss causes desminopathyTANGO2与晶状体蛋白αB结合,其缺失导致desminopathy。
err2025-06-06
err0
errOAAI
errMaike Stentenbach; Laetitia A. Hughes; Samuel V. Fagan; Blake Payne; Danielle L. Rudler; Stefan J. Siira; Tim McCubbin; Anaëlle Chopin; Kara L. Perks; Judith A. Ermer; James Hendry; Teagan S. Er; Shanti Balasubramaniam; Joel A. Eliades; Livia C. Hool; Nicolle H. Packer; Edward S. X. Moh; Benjamin S. Padman; Oliver Rackham; Aleksandra Filipovska
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Hyperactive Nickase Activity Improves Adenine Base Editing
err2024-09-19
err0
PREAI
errGandadireja, Andrianto P.; Vos, Pascal D.; Siira, Stefan J.; Filipovska, Aleksandra; Rackham, Oliver
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Illuminating mitochondrial translation through mouse models
err2024-05-23
err0
errOAAI
errHughes, Laetitia A.; Rackham, Oliver; Filipovska, Aleksandra
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Mutational rescue of the activity of high-fidelity Cas9 enzymes
err2024-04-01
err2
errOAAI
errVos, Pascal D.; Gandadireja, Andrianto P.; Rossetti, Giulia; Siira, Stefan J.; Mantegna, Jessica L.; Filipovska, Aleksandra; Rackham, Oliver
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Quantitative subcellular reconstruction reveals a lipid mediated inter-organelle biogenesis network定量亚细胞重建揭示了脂质介导的细胞器间生物发生网络
err2023-12-21
err8
PREAI
errLee, Richard G.; Rudler, Danielle L.; Raven, Samuel A.; Peng, Liuyu; Chopin, Anaelle; Moh, Edward S. X.; Mccubbin, Tim; Siira, Stefan J.; Fagan, Samuel V.; Debono, Nicholas J.; Stentenbach, Maike; Browne, Jasmin; Rackham, Filip F.; Li, Ji; Simpson, Kaylene J.; Marcellin, Esteban; Packer, Nicolle H.; Reid, Gavin E.; Padman, Benjamin S.; Rackham, Oliver; Filipovska, Aleksandra
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Mitochondrial gene expression is required for platelet function and blood clotting线粒体基因表达是血小板功能和凝血所必需的
err2023-11-01
err5
errOAAI
errRichman, Tara R.; Ermer, Judith A.; Baker, Jessica; Sira, Stefan J.; Kile, Benjamin T.; Linden, Matthew D.; Rackham, Oliver; Filipovska, Aleksandra
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ATFS-1 counteracts mitochondrial DNA damage by promoting repair over transcription
err2023-07-17
err4
PREAI
errDai, Chuan-Yang; Ng, Chai Chee; Hung, Grace Ching Ching; Kirmes, Ina; Hughes, Laetitia A. A.; Du, Yunguang; Brosnan, Christopher A. A.; Ahier, Arnaud; Hahn, Anne; Haynes, Cole M. M.; Rackham, Oliver; Filipovska, Aleksandra; Zuryn, Steven
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Multi-omic profiling reveals an RNA processing rheostat that predisposes to prostate cancer
err2023-04-24
err4
errOAAI
errStentenbach, Maike; Ermer, Judith A.; Rudler, Danielle L.; Perks, Kara L.; Raven, Samuel A.; Lee, Richard G.; McCubbin, Tim; Marcellin, Esteban; Siira, Stefan J.; Rackham, Oliver; Filipovska, Aleksandra
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Copy number variation in tRNA isodecoder genes impairs mammalian development and balanced translation
err2023-04-18
err10
errOAAI
errHughes, Laetitia A.; Rudler, Danielle L.; Siira, Stefan J.; McCubbin, Tim; Raven, Samuel A.; Browne, Jasmin M.; Ermer, Judith A.; Rientjes, Jeanette; Rodger, Jennifer; Marcellin, Esteban; Rackham, Oliver; Filipovska, Aleksandra
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Frankenstein Cas9: engineering improved gene editing systems
err2022-10-28
err2
PREAI
errVos, Pascal D.; Filipovska, Aleksandra; Rackham, Oliver
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ANGEL2 phosphatase activity is required for non-canonical mitochondrial RNA processing
err2022-09-30
err7
errOAAI
errClemente, Paula; Calvo-Garrido, Javier; Pearce, Sarah F.; Schober, Florian A.; Shigematsu, Megumi; Siira, Stefan J.; Laine, Isabelle; Spahr, Henrik; Steinmetzger, Christian; Petzold, Katja; Kirino, Yohei; Wibom, Rolf; Rackham, Oliver; Filipovska, Aleksandra; Rorbach, Joanna; Freyer, Christoph; Wredenberg, Anna
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Shackled ribosomes unleashed
err2022-07-14
err0
PREAI
errFilipovska, Aleksandra; Rackham, Oliver
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Computationally designed hyperactive Cas9 enzymes
err2022-05-31
err10
errOAAI
errVos, Pascal D.; Rossetti, Giulia; Mantegna, Jessica L.; Siira, Stefan J.; Gandadireja, Andrianto P.; Bruce, Mitchell; Raven, Samuel A.; Khersonsky, Olga; Fleishman, Sarel J.; Filipovska, Aleksandra; Rackham, Oliver
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Organization and expression of the mammalian mitochondrial genome
err2022-04-22
err61
PREAI
errRackham, Oliver; Filipovska, Aleksandra
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In silico evolution of nucleic acid-binding proteins from a nonfunctional scaffold
err2022-02-24
err7
PREAI
errRaven, Samuel A.; Payne, Blake; Bruce, Mitchell; Filipovska, Aleksandra; Rackham, Oliver
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Deleterious variants in CRLS1 lead to cardiolipin deficiency and cause an autosomal recessive multi-system mitochondrial disease
err2022-02-11
err24
errOAAI
errLee, Richard G.; Balasubramaniam, Shanti; Stentenbach, Maike; Kralj, Tom; McCubbin, Timothy; Padman, Benjamin; Smith, Janine; Riley, Lisa G.; Priyadarshi, Archana; Peng, Liuyu; Nuske, Madison R.; Webster, Richard; Peacock, Ken; Roberts, Philip; Stark, Zornitza; Lemire, Gabrielle; Ito, Yoko A.; Boycott, Kym M.; Geraghty, Michael T.; Klinken, Jan Bert; Ferdinandusse, Sacha; Zhou, Ying; Walsh, Rebecca; Marcellin, Esteban; Thorburn, David R.; Rosciolli, Tony; Fletcher, Janice; Rackham, Oliver; Vaz, Frederic M.; Reid, Gavin E.; Filipovska, Aleksandra
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Healthcare professionals' views to inform revision of the BAPM newborn early warning trigger and track system
err2021-11-25
err0
PREAI
errOjha, Shalini; MacAllister, Kathryn; Abdula, Sara; Madar, John; Rackham, Oliver; Tyler, Wendy
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The FASTK family proteins fine-tune mitochondrial RNA processing
err2021-11-08
err23
errOAAI
errOhkubo, Akira; Van Haute, Lindsey S.; Rudler, Danielle; Stentenbach, Maike S.; Steiner, Florian; Rackham, Oliver S.; Minczuk, Michal; Filipovska, Aleksandra S.; Martinou, Jean-Claude
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A common genetic variant of a mitochondrial RNA processing enzyme predisposes to insulin resistance
err2021-09-24
err9
errOAAI
errRossetti, Giulia; Ermer, Judith A.; Stentenbach, Maike; Siira, Stefan J.; Richman, Tara R.; Milenkovic, Dusanka; Perks, Kara L.; Hughes, Laetitia A.; Jamieson, Emma; Xiafukaiti, Gulibaikelamu; Ward, Natalie C.; Takahashi, Satoru; Gray, Nicola; Viola, Helena M.; Hool, Livia C.; Rackham, Oliver; Filipovska, Aleksandra
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