未登录 Cardiolipin is required for membrane docking of mitochondrial ribosomes and protein synthesis 线粒体核糖体的膜对接和蛋白质合成需要心磷脂 Lee, Richard G.; Gao, Junjie; Siira, Stefan J.; Shearwood, Anne-Marie; Ermer, Judith A.; Hofferek, Vinzenz; Mathews, James C.; Zheng, Minghao; Reid, Gavin E.; Rackham, Oliver; Filipovska, Aleksandra 分享 收藏
Fidelity of translation initiation is required for coordinated respiratory complex assembly Rudler, Danielle L.; Hughes, Laetitia A.; Perks, Kara L.; Richman, Tara R.; Kuznetsova, Irina; Ermer, Judith A.; Abudulai, Laila N.; Shearwood, Anne-Marie J.; Viola, Helena M.; Hool, Livia C.; Siira, Stefan J.; Rackham, Oliver; Filipovska, Aleksandra 分享 收藏
Stress signaling and cellular proliferation reverse the effects of mitochondrial mistranslation 应激信号和细胞增殖逆转线粒体误认为的影响 Ferreira, Nicola; Perks, Kara L.; Rossetti, Giulia; Rudler, Danielle L.; Hughes, Laetitia A.; Ermer, Judith A.; Scott, Louis H.; Kuznetsova, Irina; Richman, Tara R.; Narayana, Vinod K.; Abudulai, Laila N.; Shearwood, Anne-Marie J.; Cserne Szappanos, Henrietta; Tull, Dedreia; Yeoh, George C.; Hool, Livia C.; Filipovska, Aleksandra; Rackham, Oliver 分享 收藏
Early-onset Parkinson disease caused by a mutation in CHCHD2 and mitochondrial dysfunction Lee, Richard G.; Sedghi, Maryam; Salari, Mehri; Shearwood, Anne-Marie J.; Stentenbach, Maike; Kariminejad, Ariana; Goullee, Hayley; Rackham, Oliver; Laing, Nigel G.; Tajsharghi, Homa; Filipovska, Aleksandra 分享 收藏
Concerted regulation of mitochondrial and nuclear non-coding RNAs by a dual-targeted RNase Z Siira, Stefan J.; Rossetti, Giulia; Richman, Tara R.; Perks, Kara; Ermer, Judith A.; Kuznetsova, Irina; Hughes, Laetitia; Shearwood, Anne-Marie J.; Viola, Helena M.; Hool, Livia C.; Rackham, Oliver; Filipovska, Aleksandra 分享 收藏
Adult-onset obesity is triggered by impaired mitochondrial gene expression Perks, Kara L.; Ferreira, Nicola; Richman, Tara R.; Ermer, Judith A.; Kuznetsova, Irina; Shearwood, Anne-Marie J.; Lee, Richard G.; Viola, Helena M.; Johnstone, Victoria P. A.; Matthews, Vance; Hool, Livia C.; Rackham, Oliver; Filipovska, Aleksandra 分享 收藏
分享 收藏
Transcriptome-wide effects of a POLR3A gene mutation in patients with an unusual phenotype of striatal involvement Azmanov, Dimitar N.; Siira, Stefan J.; Chamova, Teodora; Kaprelyan, Ara; Guergueltcheva, Velina; Shearwood, Anne-Marie J.; Liu, Ganqiang; Morar, Bharti; Rackham, Oliver; Bynevelt, Michael; Grudkova, Margarita; Kamenov, Zdravko; Svechtarov, Vassil; Tournev, Ivailo; Kalaydjieva, Luba; Filipovska, Aleksandra 分享 收藏
Hierarchical RNA Processing Is Required for Mitochondrial Ribosome Assembly Rackham, Oliver; Busch, Jakob D.; Matic, Stanka; Siira, Stefan J.; Kuznetsova, Irina; Atanassov, Ilian; Ermer, Judith A.; Shearwood, Anne-Marie J.; Richman, Tara R.; Stewart, James B.; Mourier, Arnaud; Milenkovic, Dusanka; Larsson, Nils-Goeran; Filipovska, Aleksandra 分享 收藏
A mutation in MT-TW causes a tRNA processing defect and reduced mitochondrial function in a family with Leigh syndrome Duff, Rachael M.; Shearwood, Anne-Marie J.; Ermer, Judith; Rossetti, Giulia; Gooding, Rebecca; Richman, Tara R.; Balasubramaniam, Shanti; Thorburn, David R.; Rackham, Oliver; Lamont, Phillipa J.; Filipovska, Aleksandra 分享 收藏
分享 收藏
分享 收藏
分享 收藏
分享 收藏
分享 收藏
Substrate and inhibitor specificities differ between human cytosolic and mitochondrial thioredoxin reductases: Implications for development of specific inhibitors Rackham, Oliver; Shearwood, Anne-Marie J.; Thyer, Ross; McNamara, Elyshia; Davies, Stefan M. K.; Callus, Bernard A.; Miranda-Vizuete, Antonio; Berners-Price, Susan J.; Cheng, Qing; Arner, Elias S. J.; Filipovska, Aleksandra 分享 收藏
分享 收藏
分享 收藏
分享 收藏