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Neil J. Bulleid

institute biomed science, university sao paulo

54H指数
152论文数
9.3K被引数
收录论文 78
发表时间
The chemical chaperone 4-phenylbutyric acid rescues molecular cell defects of COL3A1 mutations that cause vascular Ehlers Danlos Syndrome (vol 11, 200, 2025)化学伴侣4-苯基丁酸可修复导致血管性埃勒斯-当洛斯综合征(Ehlers-Danlos Syndrome)的COL3A1基因突变所引起的分子细胞缺陷(vol 11, 200, 2025)
err2025-05-23
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errOmar, Ramla; Lee, Michelle A. W.; Gonzalez-Trueba, Laura; Thomson, Cameron R.; Hansen, Uwe; Lianos, Spyridonas; Hazarika, Snoopy; El Abdallah, Omar H. M. E. H.; Ammar, Malak A.; Cassels, Jennifer; Michie, Alison M.; Bulleid, Neil J.; Malfait, Fransiska; Van Agtmael, Tom
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The chemical chaperone 4-phenylbutyric acid rescues molecular cell defects of COL3A1 mutations that cause vascular Ehlers Danlos Syndrome化学伴侣4-苯基丁酸可以拯救导致血管型埃勒斯-当洛斯综合征的COL3A1突变所引起的分子细胞缺陷
err2025-04-25
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errOmar, Ramla; Lee, Michelle A. W.; Gonzalez-Trueba, Laura; Thomson, Cameron R.; Hansen, Uwe; Lianos, Spyridonas; Hazarika, Snoopy; El Abdallah, Omar El; Ammar, Malak A.; Cassels, Jennifer; Michie, Alison M.; Bulleid, Neil J.; Malfait, Fransiska; Van Agtmael, Tom
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Collagen IV deficiency causes hypertrophic remodeling and endothelium-dependent hyperpolarization in small vessel disease with intracerebral hemorrhage
err2024-09-01
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errMcNeilly, Sarah; Thomson, Cameron R.; Gonzalez-Trueba, Laura; Sin, Yuan Yan; Granata, Alessandra; Hamilton, Graham; Lee, Michelle; Boland, Erin; McClure, John D.; Lumbreras-Perales, Cristina; Aman, Alisha; Kumar, Apoorva A.; Cantini, Marco; Gok, Caglar; Graham, Delyth; Tomono, Yasuko; Anderson, Christopher D.; Lu, Yinhui; Smith, Colin; Markus, Hugh S.; Abramowicz, Marc; Vilain, Catheline; Salman, Rustam Al-Shahi; Salmeron-Sanchez, Manuel; Hainsworth, Atticus H.; Fuller, William; Kadler, Karl E.; Bulleid, Neil J.; Van Agtmael, Tom
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Activation of the UPR sensor ATF6α is regulated by its redox-dependent dimerization and ER retention by ERp18
err2022-03-14
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errOka, Ojore Benedict Valentine; Pierre, Arvin Shedrach; Pringle, Marie Anne; Tungkum, Wanida; Cao, Zhenbo; Fleming, Bethany; Bulleid, Neil John
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A cytosolic reductase pathway is required for efficient N-glycosylation of an STT3B-dependent acceptor site
err2021-11-25
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errvan Lith, Marcel; Pringle, Marie Anne; Fleming, Bethany; Gaeta, Giorgia; Im, Jisu; Gilmore, Reid; Bulleid, Neil J.
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Proteome Profile Of Vascular Smooth Muscle Cells During Phenotypic Switching In Human Hypertension
err2021-09-01
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PREAI
errCamargo, Livia L.; Mary, Sheon; Lilla, Sergio; Zanivan, Sara; Bulleid, Neil; Hartley, Richard; Delles, Christian; Leiper, James; Fuller, Will; Montezano, Augusto C.; Touyz, Rhian M.
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Structure and Electron-Transfer Pathway of the Human Methionine Sulfoxide Reductase MsrB3
err2020-10-01
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errJavitt, Gabriel; Cao, Zhenbo; Resnick, Efrat; Gabizon, Ronen; Bulleid, Neil J.; Fass, Deborah
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The mammalian cytosolic thioredoxin reductase pathway acts via a membrane protein to reduce ER-localised proteins哺乳动物胞质硫氧还蛋白还原酶途径通过膜蛋白减少ER定位蛋白
err2020-04-30
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errCao, Xiaofei; Lilla, Sergio; Cao, Zhenbo; Pringle, Marie Anne; Oka, Ojore B., V; Robinson, Philip J.; Szmaja, Tomasz; van Lith, Marcel; Zanivan, Sara; Bulleid, Neil J.
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Protein secondary structure determines the temporal relationship between folding and disulfide formation
err2020-02-01
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errRobinson, Philip J.; Kanemura, Shingo; Cao, Xiaofei; Bulleid, Neil J.
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INTERPLAY BETWEEN NOX-REGULATED OXIDATIVE STRESS AND ER STRESS RESPONSE IN EXPERIMENTAL HYPERTENSION
err2018-10-01
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PREAI
errCamargo, Livia L.; Harvey, Adam P.; Rios, Francisco J.; Tsiropoulou, Sofi A.; Silva, Renee de Nazare de Oliveira; Cao, Zhenbo; McMaster, Claire; Burchmore, Richard J.; Hartley, Richard C.; Bulleid, Neil; Montezano, Augusto; Touyz, Rhian M.
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Vascular Nox (NADPH Oxidase) Compartmentalization, Protein Hyperoxidation, and Endoplasmic Reticulum Stress Response in Hypertension
err2018-07-01
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errCamargo, Livia L.; Harvey, Adam P.; Rios, Francisco J.; Tsiropoulou, Sofia; Oliveira Da Silva, Renee de Nazare; Cao, Zhenbo; Graham, Delyth; McMaster, Claire; Burchmore, Richard J.; Hartley, Richard C.; Bulleid, Neil; Montezano, Augusto C.; Touyz, Rhian M.
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Methionine sulfoxide reductase B3 requires resolving cysteine residues for full activity and can act as a stereospecific methionine oxidase
err2018-02-28
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errCao, Zhenbo; Mitchell, Lorna; Hsia, Oliver; Scarpa, Miriam; Caldwell, Stuart T.; Alfred, Arina D.; Gennaris, Alexandra; Collet, Jean-Francois; Hartley, Richard C.; Bulleid, Neil J.
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How Are Proteins Reduced in the Endoplasmic Reticulum?
err2018-01-01
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errEllgaard, Lars; Sevier, Carolyn S.; Bulleid, Neil J.
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IgG light chain-independent secretion of heavy chain dimers: consequence for therapeutic antibody production and design
err2017-09-08
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errStoyle, Chloe L.; Stephens, Paul E.; Humphreys, David P.; Heywood, Sam; Cain, Katharine; Bulleid, Neil J.
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NOX COMPARTMENTALIZATION AND PROTEIN OXIDATION IN VASCULAR SMOOTH MUSCLE CELLS - IMPLICATIONS IN VASCULAR DYSFUNCTION IN HYPERTENSION
errHEART
IF4.4
err2017-06-05
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errCamargo, Livia de Lucca; Montezano, Augusto Cesar; Tsiropoulou, Sofia; Harvey, Adam; Hood, Katie; Cao, Zhenbo; Burchmore, Richard; Bulleid, Neil; Touyz, Rhian
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Folding of a single domain protein entering the endoplasmic reticulum precedes disulfide formation
err2017-04-01
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errRobinson, Philip J.; Pringle, Marie Anne; Woolhead, Cheryl A.; Bulleid, Neil J.
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Cytosolic thioredoxin reductase 1 is required for correct disulfide formation in the ER
err2017-01-16
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errPoet, Greg J.; Oka, Ojore B. V.; van Lith, Marcel; Cao, Zhenbo; Robinson, Philip J.; Pringle, Marie Anne; Arner, Elias S. J.; Bulleid, Neil J.
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