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Vernon Anderson

The Children's Hospital of Philadelphia

59H指数
347论文数
1.5W被引数
收录论文 42
发表时间
Interpreting the clinical significance of multiple large-scale mitochondrial DNA deletions (MLSMD) in skeletal muscle tissue in the diagnostic evaluation of primary mitochondrial disease在原发性线粒体疾病的诊断评估中,解读在骨骼肌组织中存在的多重大规模线粒体DNA缺失(MLSMD)的临床意义。
err2025-04-09
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errWang, Jing; Peterson, James T.; Santos, Joaquim Diego D.; Chan, Ada J. S.; Diaz-Miranda, Maria Alejandra; Rahaman, Imon; Flickinger, Jean; Goldstein, Amy; Bogush, Emily; Mccormick, Elizabeth M.; Muraresku, Colleen C.; Anderson, Vernon E.; Dulik, Matthew C.; Wallace, Douglas C.; Xiao, Rui; Falk, Marni J.; Viaene, Angela N.; Zolkipli-Cunningham, Zarazuela
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dldhcri3 zebrafish exhibit altered mitochondrial ultrastructure, morphology, and dysfunction partially rescued by probucol or thiamine
err2024-08-20
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errLavorato, Manuela; Iadarola, Donna; Remes, Cristina; Kaur, Prabhjot; Broxton, Chynna; Mathew, Neal D.; Xiao, Rui; Seiler, Christoph; Nakamaru-Ogiso, Eiko; Anderson, Vernon E.; Falk, Marni J.
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N-acetylcysteine and cysteamine bitartrate prevent azide-induced neuromuscular decompensation by restoring glutathione balance in two novel surf1-/- zebrafish deletion models of Leigh syndrome
err2023-02-16
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errHaroon, Suraiya; Yoon, Heeyong; Seiler, Christoph; Osei-Frimpong, Bruce; He, Jie; Nair, Rohini M.; Mathew, Neal D.; Burg, Leonard; Kose, Melis; Venkata, Chavali R. M.; Anderson, Vernon E.; Nakamaru-Ogiso, Eiko; Falk, Marni J.
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Dichloroacetate and thiamine improve survival and mitochondrial stress in a C. elegans model of dihydrolipoamide dehydrogenase deficiency
err2022-10-24
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errBroxton, Chynna N.; Kaur, Prabhjot; Lavorato, Manuela; Ganesh, Smruthi; Xiao, Rui; Mathew, Neal D.; Nakamaru-Ogiso, Eiko; Anderson, Vernon E.; Falk, Marni J.
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Isotope effect analyses provide evidence for an altered transition state for RNA 2′-O-transphosphorylation catalyzed by Zn2+
err2016-01-01
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errZhang, Shuming; Gu, Hong; Chen, Haoyuan; Strong, Emily; Ollie, Edward W.; Kellerman, Daniel; Liang, Danni; Miyagi, Masaru; Anderson, Vernon E.; Piccirilli, Joseph A.; York, Darrin M.; Harris, Michael E.
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Translational research in primary mitochondrial diseases: Challenges and opportunities
err2013-11-01
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PREAI
errMoraes, Carlos T.; Anderson, Vernon; Mohan, Charles
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Catalase Abrogates β-Lapachone-Induced PARP1 Hyperactivation-Directed Programmed Necrosis in NQO1-Positive Breast Cancers
err2013-10-07
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errBey, Erik A.; Reinicke, Kathryn E.; Srougi, Melissa C.; Varnes, Marie; Anderson, Vernon E.; Pink, John J.; Li, Long Shan; Patel, Malina; Cao, Lifen; Moore, Zachary; Rommel, Amy; Boatman, Michael; Lewis, Cheryl; Euhus, David M.; Bornmann, William G.; Buchsbaum, Donald J.; Spitz, Douglas R.; Gao, Jinming; Boothman, David A.
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Experimental and computational analysis of the transition state for ribonuclease A-catalyzed RNA 2′-O-transphosphorylation
err2013-07-22
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errGu, Hong; Zhang, Shuming; Wong, Kin-Yiu; Radak, Brian K.; Dissanayake, Thakshila; Kellerman, Daniel L.; Dai, Qing; Miyagi, Masaru; Anderson, Vernon E.; York, Darrin M.; Piccirilli, Joseph A.; Harris, Michael E.
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Metabolomics and Mass Isotopomer Analysis as a Strategy for Pathway Discovery: Pyrrolyl and Cyclopentenyl Derivatives of the Pro-Drug of Abuse, Levulinate代谢组学和质量同位素分析作为发现途径的策略: 滥用前药乙酰丙酸酯的吡咯基和环戊烯基衍生物
err2012-12-06
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errHarris, Stephanie R.; Zhang, Guo-Fang; Sadhukhan, Sushabhan; Wang, Hua; Shi, Chuan; Puchowicz, Michelle A.; Anderson, Vernon E.; Salomon, Robert G.; Tochtrop, Gregory P.; Brunengraber, Henri
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Metabolism of γ-hydroxybutyrate in perfused rat livers
err2012-05-11
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PREAI
errZhang, Guo-Fang; Sadhukhan, Sushabhan; Ibarra, Rafael A.; Lauden, Stephanie M.; Chuang, Chia-Ying; Sushailo, Sophia; Chatterjee, Priya; Anderson, Vernon E.; Tochtrop, Gregory P.; Brunengraber, Henri
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Peroxisome Proliferator-activated Receptor γ (PPARγ) Mediates a Ski Oncogene-induced Shift from Glycolysis to Oxidative Energy Metabolism
err2011-11-01
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errYe, Fang; Lemieux, Helene; Hoppel, Charles L.; Hanson, Richard W.; Hakimi, Parvin; Croniger, Colleen M.; Puchowicz, Michelle; Anderson, Vernon E.; Fujioka, Hisashi; Stavnezer, Ed
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Metabolism of Levulinate in Perfused Rat Livers and Live Rats CONVERSION TO THE DRUG OF ABUSE 4-HYDROXYPENTANOATE
err2011-02-01
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errHarris, Stephanie R.; Zhang, Guo-Fang; Sadhukhan, Sushabhan; Murphy, Anne M.; Tomcik, Kristyen A.; Vazquez, Edwin J.; Anderson, Vernon E.; Tochtrop, Gregory P.; Brunengraber, Henri
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Cardiolipin: characterization of distinct oxidized molecular species
err2011-01-01
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errKim, Junhwan; Minkler, Paul E.; Salomon, Robert G.; Anderson, Vernon E.; Hoppel, Charles L.
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Photo-oxidation of cardiolipin and cytochrome c with bilayer-embedded Pc 4
err2010-09-01
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errKim, Junhwan; Rodriguez, Myriam E.; Oleinick, Nancy L.; Anderson, Vernon E.
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Kinetic Isotope Effects for RNA Cleavage by 2′-O-Transphosphorylation: Nucleophilic Activation by Specific Base
err2010-07-29
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errHarris, Michael E.; Dai, Qing; Gu, Hong; Kellerman, Daniel L.; Piccirilli, Joseph A.; Anderson, Vernon E.
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