未登录 dldhcri3 zebrafish exhibit altered mitochondrial ultrastructure, morphology, and dysfunction partially rescued by probucol or thiamine Lavorato, Manuela; Iadarola, Donna; Remes, Cristina; Kaur, Prabhjot; Broxton, Chynna; Mathew, Neal D.; Xiao, Rui; Seiler, Christoph; Nakamaru-Ogiso, Eiko; Anderson, Vernon E.; Falk, Marni J. 分享 收藏
Dre2, a conserved eukaryotic Fe/S cluster protein, functions in cytosolic Fe/S protein biogenesis Zhang, Yan; Lyver, Elise R.; Nakamaru-Ogiso, Eiko; Yoon, Heeyong; Amutha, Boominathan; Lee, Dong-Woo; Bi, Erfei; Ohnishi, Tomoko; Daldal, Fevzi; Pain, Debkumar; Dancis, Andrew 分享 收藏
N-acetylcysteine and cysteamine bitartrate prevent azide-induced neuromuscular decompensation by restoring glutathione balance in two novel surf1-/- zebrafish deletion models of Leigh syndrome Haroon, Suraiya; Yoon, Heeyong; Seiler, Christoph; Osei-Frimpong, Bruce; He, Jie; Nair, Rohini M.; Mathew, Neal D.; Burg, Leonard; Kose, Melis; Venkata, Chavali R. M.; Anderson, Vernon E.; Nakamaru-Ogiso, Eiko; Falk, Marni J. 分享 收藏
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Dichloroacetate improves mitochondrial function, physiology, and morphology in FBXL4 disease models Lavorato, Manuela; Nakamaru-Ogiso, Eiko; Mathew, Neal D.; Herman, Elizabeth; Shah, Nina; Haroon, Suraiya; Xiao, Rui; Seiler, Christoph; Falk, Marni J. 分享 收藏
Reduced ER-mitochondria connectivity promotes neuroblastoma multidrug resistance Coku, Jorida; Booth, David M.; Skoda, Jan; Pedrotty, Madison C.; Vogel, Jennifer; Liu, Kangning; Vu, Annette; Carpenter, Erica L.; Ye, Jamie C.; Chen, Michelle A.; Dunbar, Peter; Scadden, Elizabeth; Yun, Taekyung D.; Nakamaru-Ogiso, Eiko; Area-Gomez, Estela; Li, Yimei; Goldsmith, Kelly C.; Reynolds, C. Patrick; Hajnoczky, Gyorgy; Hogarty, Michael D. 分享 收藏
The FusX TALE Base Editor (FusXTBE) for Rapid Mitochondrial DNA Programming of Human Cells In Vitro and Zebrafish Disease Models In Vivo Sabharwal, Ankit; Kar, Bibekananda; Restrepo-Castillo, Santiago; Holmberg, Shannon R.; Mathew, Neal D.; Kendall, Benjamin Luke; Cotter, Ryan P.; WareJoncas, Zachary; Seiler, Christoph; Nakamaru-Ogiso, Eiko; Clark, Karl J.; Ekker, Stephen C. 分享 收藏
Combinatorial glucose, nicotinic acid and N-acetylcysteine therapy has synergistic effect in preclinical C. elegans and zebrafish models of mitochondrial complex I disease Guha, Sujay; Mathew, Neal D.; Konkwo, Chigoziri; Ostrovsky, Julian; Kwon, Young Joon; Polyak, Erzsebet; Seiler, Christoph; Bennett, Michael; Xiao, Rui; Zhang, Zhe; Nakamaru-Ogiso, Eiko; Falk, Marni J. 分享 收藏
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Regulation of nuclear epigenome by mitochondrial DNA heteroplasmy Kopinski, Piotr K.; Janssen, Kevin A.; Schaefer, Patrick M.; Trefely, Sophie; Perry, Caroline E.; Potluri, Prasanth; Tintos-Hernandez, Jesus A.; Singh, Larry N.; Karch, Kelly R.; Campbell, Sydney L.; Doan, Mary T.; Jiang, Helen; Nissim, Itzhak; Nakamaru-Ogiso, Eiko; Wellen, Kathryn E.; Snyder, Nathaniel W.; Garcia, Benjamin A.; Wallace, Douglas C. 分享 收藏
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Telomere Dysfunction Induces Sirtuin Repression that Drives Telomere-Dependent Disease Amano, Hisayuki; Chaudhury, Arindam; Rodriguez-Aguayo, Cristian; Lu, Lan; Akhanov, Viktor; Catic, Andre; Popov, Yury, V; Verdin, Eric; Johnson, Hannah; Stossi, Fabio; Sinclair, David A.; Nakamaru-Ogiso, Eiko; Lopez-Berestein, Gabriel; Chang, Jeffrey T.; Neilson, Joel R.; Meeker, Alan; Finegold, Milton; Baur, Joseph A.; Sahin, Ergun 分享 收藏
Pre-clinical evaluation of cysteamine bitartrate as a therapeutic agent for mitochondrial respiratory chain disease Guha, Sujay; Konkwo, Chigoziri; Lavorato, Manuela; Mathew, Neal D.; Peng, Min; Ostrovsky, Julian; Kwon, Young-Joon; Polyak, Erzsebet; Lightfoot, Richard; Seiler, Christoph; Xiao, Rui; Bennett, Michael; Zhang, Zhe; Nakamaru-Ogiso, Eiko; Falk, Marni J. 分享 收藏
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Nicotinamide adenine dinucleotide is transported into mammalian mitochondria Davila, Antonio; Liu, Ling; Chellappa, Karthikeyani; Redpath, Philip; Nakamaru-Ogiso, Eiko; Paolella, Lauren M.; Zhang, Zhigang; Migaud, Marie E.; Rabinowitz, Joshua D.; Baur, Joseph A. 分享 收藏
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Transition-metal-free chemo- and regioselective vinylation of azaallyls Li, Minyan; Gutierrez, Osvaldo; Berritt, Simon; Pascual-Escudero, Ana; Yesilcimen, Ahmet; Yang, Xiaodong; Adrio, Javier; Huang, Georgia; Nakamaru-Ogiso, Eiko; Kozlowski, Marisa C.; Walsh, Patrick J. 分享 收藏
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The circadian gene Rev-erbα improves cellular bioenergetics and provides preconditioning for protection against oxidative stress Sengupta, Shaon; Yang, Guang; O'Donnell, John C.; Hinson, Maurice D.; McCormack, Shana E.; Falk, Marni J.; La, Ping; Robinson, Michael B.; Williams, Monica L.; Yohannes, Mekdes T.; Polyak, Erzsebet; Nakamaru-Ogiso, Eiko; Dennery, Phyllis A. 分享 收藏
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