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STING-STAT3-mediated endothelial-mesenchymal transition promotes pulmonary fibrosis in SAVI patients STING-STAT3-mediated内皮-间质转化促进SAVI患者肺纤维化 Yang, Dan; Chen, Guibin; Almeida De Jesus, Adriana; Mcninch, Colton; Miranda, Adam; Mehta, Atul; Kedie, Noemi; Hernandez, Maria; Gaurav, Sachin; Yu, Quan; Wei, Jinzhi; Lee, Chyi-Chia; Dalgard, Clifton; Boehm, Manfred; Goldbach-Mansky, Raphaela 分享 收藏
Altered maturation and activation state of circulating monocytes is associated with their enhanced recruitment in pulmonary arterial hypertension 循环单核细胞成熟和活化状态的改变与其在肺动脉高压中的增强招募相关 Harper, Rebecca L.; Zhou, Xin; Marciano, David P.; Cao, Aiqin; Wang, Lingli; Chen, Guibin; Adil, Mir S.; Zhou, Wenyu; Maguire, Peter; Deivanayagam, Shanthi; Yu, Quan; Viswanathan, Vignesh; Yang, Dan; Martin, Marcy; Isobe, Sarasa; Otsuki, Shoichiro; Burgess, Jordan; Inglis, Audrey; Kelley, Devon; del Rosario, Patricia A.; Hsi, Andrew; Haddad, Francois; Zamanian, Roham T.; Boehm, Manfred; Snyder, Michael P. 分享 收藏
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The Ectopyrase CD73 Is a Critical Checkpoint in Thromboinflammation 外切核苷酸酶CD73是血栓性炎症过程中的一个关键检查点。 Panicker, Sumith R.; Wang, Jintao; Becicka, Wyatt; Wigerblad, Gustaf; Berreby, Gil; Garrad, Evan; Moitra, Jaideep; Fujii, Takeo; Agasti, Suchhanda; Moreno, Eries Jay; Murray, Elizabeth; Toney, Bernard; Osgood, Sharon; Cowling, Bretagne; Huffstutler, Rebecca; Carney, Katherine; Ferrante, Elisa; Elmer, Francesca; Mackman, Nigel; Brofferio, Alessandra; Knight, Jason; Boehm, Manfred; Tourdot, Benjamin; Kanthi, Yogendra 分享 收藏
Long-term engraftment and maturation of autologous iPSC-derived cardiomyocytes in two rhesus macaques Lin, Yongshun; Sato, Noriko; Hong, Sogun; Nakamura, Kenta; Ferrante, Elisa A.; Yu, Zu Xi; Chen, Marcus Y.; Nakamura, Daisy S.; Yang, Xiulan; Clevenger, Randall R.; Hunt, Timothy J.; Taylor, Joni L.; Jeffries, Kenneth R.; Keeran, Karen J.; Neidig, Lauren E.; Mehta, Atul; Schwartzbeck, Robin; Yu, Shiqin Judy; Kelly, Conor; Navarengom, Keron; Takeda, Kazuyo; Adler, Stephen S.; Choyke, Peter L.; Zou, Jizhong; Murry, Charles E.; Boehm, Manfred; Dunbar, Cynthia E. 分享 收藏
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Biallelic human SHARPIN loss of function induces autoinflammation and immunodeficiency 双等位基因人SHARPIN功能丧失诱导自身炎症和免疫缺陷 Oda, Hirotsugu; Manthiram, Kalpana; Chavan, Pallavi Pimpale; Rieser, Eva; Veli, Oenay; Kaya, Oeykue; Rauch, Charles; Nakabo, Shuichiro; Kuehn, Hye Sun; Swart, Mariel; Wang, Yanli; Celik, Nisa Ilgim; Molitor, Anne; Ziaee, Vahid; Movahedi, Nasim; Shahrooei, Mohammad; Parvaneh, Nima; Alipour-Olyei, Nasrin; Carapito, Raphael; Xu, Qin; Preite, Silvia; Beck, David B.; Chae, Jae Jin; Nehrebecky, Michele; Ombrello, Amanda K.; Hoffmann, Patrycja; Romeo, Tina; Deuitch, Natalie T.; Matthiasardottir, Brynja; Mullikin, James; Komarow, Hirsh; Stoddard, Jennifer; Niemela, Julie; Dobbs, Kerry; Sweeney, Colin L.; Anderton, Holly; Lawlor, Kate E.; Yoshitomi, Hiroyuki; Yang, Dan; Boehm, Manfred; Davis, Jeremy; Mudd, Pamela; Randazzo, Davide; Tsai, Wanxia Li; Gadina, Massimo; Kaplan, Mariana J.; Toguchida, Junya; Mayer, Christian T.; Rosenzweig, Sergio D.; Notarangelo, Luigi D.; Iwai, Kazuhiro; Silke, John; Schwartzberg, Pamela L.; Boisson, Bertrand; Casanova, Jean-Laurent; Bahram, Seiamak; Rao, Anand Prahalad; Peltzer, Nieves; Walczak, Henning; Lalaoui, Najoua; Aksentijevich, Ivona; Kastner, Daniel L. 分享 收藏
Pilot study to evaluate the safety and effectiveness of etidronate treatment for arterial calcification due to deficiency of CD73 (ACDC) Ferrante, Elisa A.; Cudrici, Cornelia D.; Rashidi, Mahmood; Fu, Yi-Ping; Huffstutler, Rebecca; Carney, Katherine; Chen, Marcus Y.; St Hilaire, Cynthia; Smith, Kevin; Bagheri, Hadi; Katz, James D.; Ferreira, Carlos R.; Gahl, William A.; Bohm, Manfred; Brofferio, Alessandra 分享 收藏
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Age-related loss of Notch3 underlies brain vascular contractility deficiencies, glymphatic dysfunction, and neurodegeneration in mice Romay, Milagros C.; Knutsen, Russell H.; Ma, Feiyang; Mompeon, Ana; Hernandez, Gloria E.; Salvador, Jocelynda; Mirkov, Snezana; Batra, Ayush; Sullivan, David P.; Procissi, Daniele; Buchanan, Samuel; Kronquist, Elise; Ferrante, Elisa A.; Muller, William A.; Walshon, Jordain; Steffens, Alicia; McCortney, Kathleen; Horbinski, Craig; Tournier-Lasserve, Elisabeth; Sonabend, Adam M.; Sorond, Farzaneh A.; Wang, Michael M.; Boehm, Manfred; Kozel, Beth A.; Iruela-Arispe, M. Luisa 分享 收藏
Images in Vascular Medicine: High-resolution CT imaging of arterial calcification in the hands and legs of patients with CD73 deficiency Baral, Aneesha; Hussaini, Farah F.; Lee, Simone C.; Matthew, Brianna P.; Ferrante, Elisa A.; Brofferio, Alessandra; Cudrici, Cornelia D.; Rollison, Shirley F.; Chen, Marcus Y.; Boehm, Manfred; Wen, Han 分享 收藏
Mast cell activation and degranulation in acute artery injury: A target for post-operative therapy Harper, Rebecca L.; Fang, Fang; San, Hong; Negro, Alejandra; St. Hilaire, Cynthia; Yang, Dan; Chen, Guibin; Yu, Zhen; Dmitrieva, Natalia I.; Lanzer, Jan; Davaine, Jean-Michel; Schwartzbeck, Robin; Walts, Avram D.; Kovacic, Jason C.; Boehm, Manfred 分享 收藏
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Constitutively active Lyn kinase causes a cutaneous small vessel vasculitis and liver fibrosis syndrome 组成型活性Lyn激酶引起皮肤小血管血管炎和肝纤维化综合征 de Jesus, Adriana A.; Chen, Guibin; Yang, Dan; Brdicka, Tomas; Ruth, Natasha M.; Bennin, David; Cebecauerova, Dita; Malcova, Hana; Freeman, Helen; Martin, Neil; Svojgr, Karel; Passo, Murray H.; Bhuyan, Farzana; Alehashemi, Sara; Rastegar, Andre T.; Uss, Katsiaryna; Kardava, Lela; Marrero, Bernadette; Duric, Iris; Omoyinmi, Ebun; Peldova, Petra; Lee, Chyi-Chia Richard; Kleiner, David E.; Hadigan, Colleen M.; Hewitt, Stephen M.; Pittaluga, Stefania; Carmona-Rivera, Carmelo; Calvo, Katherine R.; Shah, Nirali; Balascakova, Miroslava; Fink, Danielle L.; Kotalova, Radana; Parackova, Zuzana; Peterkova, Lucie; Kuzilkova, Daniela; Campr, Vit; Sramkova, Lucie; Biancotto, Angelique; Brooks, Stephen R.; Manes, Cameron; Meffre, Eric; Harper, Rebecca L.; Kuehn, Hyesun; Kaplan, Mariana J.; Brogan, Paul; Rosenzweig, Sergio D.; Merchant, Melinda; Deng, Zuoming; Huttenlocher, Anna; Moir, Susan L.; Kuhns, Douglas B.; Boehm, Manfred; Kramarzova, Karolina Skvarova; Goldbach-Mansky, Raphaela 分享 收藏
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Bioprinted 3D outer retina barrier uncovers RPE-dependent choroidal phenotype in advanced macular degeneration 生物打印的3D外视网膜屏障揭示了晚期黄斑变性中RPE依赖性脉络膜表型 Song, Min Jae; Quinn, Russ; Nguyen, Eric; Hampton, Christopher; Sharma, Ruchi; Park, Tea Soon; Koster, Celine; Voss, Ty; Tristan, Carlos; Weber, Claire; Singh, Anju; Dejene, Roba; Bose, Devika; Chen, Yu-Chi; Derr, Paige; Derr, Kristy; Michael, Sam; Barone, Francesca; Chen, Guibin; Boehm, Manfred; Maminishkis, Arvydas; Singec, Ilyas; Ferrer, Marc; Bharti, Kapil 分享 收藏
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