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Paul J. Muchowski

university of california san francisco

50H指数
131论文数
1.1W被引数
收录论文 41
发表时间
Deubiquitinase Usp12 functions noncatalytically to induce autophagy and confer neuroprotection in models of Huntington's disease (vol 11, 1065, 2020)
err2020-05-07
err3
errOAAI
errAron, Rebecca; Pellegrini, Pasquale; Green, Edward W.; Maddison, Daniel C.; Opoku-Nsiah, Kwadwo; Oliveira, Anna Osorio; Wong, Jinny S.; Daub, Aaron C.; Giorgini, Flaviano; Muchowski, Paul; Finkbeiner, Steven
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Deubiquitinase Usp12 functions noncatalytically to induce autophagy and confer neuroprotection in models of Huntington's disease (vol 15, pg 128, 2018)
err2020-02-21
err1
errOAAI
errAron, Rebecca; Pellegrini, Pasquale; Green, Edward W.; Maddison, Daniel C.; Opoku-Nsiah, Kwadwo; Osorio Oliviera, Anna; Wong, Jinny S.; Daub, Aaron C.; Giorgini, Flaviano; Muchowski, Paul; Finkbeiner, Steven
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Adaptive and Behavioral Changes in Kynurenine 3-Monooxygenase Knockout Mice: Relevance to Psychotic Disorders
err2017-11-01
err46
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errErhardt, Sophie; Pocivavsek, Ana; Repici, Mariaelena; Liu, Xi-Cong; Imbeault, Sophie; Maddison, Daniel C.; Thomas, Marian A. R.; Smalley, Joshua L.; Larsson, Markus K.; Muchowski, Paul J.; Giorgini, Flaviano; Schwarcz, Robert
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αB-Crystallin overexpression in astrocytes modulates the phenotype of the BACHD mouse model of Huntington's disease
err2016-02-26
err35
errOAAI
errOliveira, Ana Osorio; Osmand, Alexander; Outeiro, Tiago Fleming; Muchowski, Paul Joseph; Finkbeiner, Steven
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Targeted Deletion of Kynurenine 3-Monooxygenase in Mice A NEW TOOL FOR STUDYING KYNURENINE PATHWAY METABOLISM IN PERIPHERY AND BRAIN
err2013-12-01
err105
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errGiorgini, Flaviano; Huang, Shao-Yi; Sathyasaikumar, Korrapati V.; Notarangelo, Francesca M.; Thomas, Marian A. R.; Tararina, Margarita; Wu, Hui-Qiu; Schwarcz, Robert; Muchowski, Paul J.
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Mutant huntingtin impairs immune cell migration in Huntington disease
err2012-11-19
err120
errOAAI
errKwan, Wanda; Traeger, Ulrike; Davalos, Dimitrios; Chou, Austin; Bouchard, Jill; Andre, Ralph; Miller, Aaron; Weiss, Andreas; Giorgini, Flaviano; Cheah, Christine; Moeller, Thomas; Stella, Nephi; Akassoglou, Katerina; Tabrizi, Sarah J.; Muchowski, Paul J.
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IMMUNE DYSFUNCTION IN HD HUMAN MYELOID CELLS IS CAUSED BY NFkB PATHWAY DYSREGULATION AND IS REVERSED BY LOWERING HTT LEVELS
err2012-08-29
err0
PREAI
errTrager, U.; Andre, R.; Lahiri, N.; Magnusson, A.; Pfister, E.; Weiss, A.; Grueninger, S.; Antoniou, M.; Bates, G.; Muchowski, P.; Bjorkqvist, M.; Ostroff, G.; Aronin, N.; Tabrizi, S. J.
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Identification of Novel Potentially Toxic Oligomers Formed in Vitro from Mammalian-derived Expanded huntingtin Exon-1 Protein
err2012-05-01
err108
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errNucifora, Leslie G.; Burke, Kathleen A.; Feng, Xia; Arbez, Nicolas; Zhu, Shanshan; Miller, Jason; Yang, Guocheng; Ratovitski, Tamara; Delannoy, Michael; Muchowski, Paul J.; Finkbeiner, Steven; Legleiter, Justin; Ross, Christopher A.; Poirier, Michelle A.
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Suppression of -synuclein toxicity and vesicle trafficking defects by phosphorylation at S129 in yeast depends on genetic context
err2012-02-21
err64
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errSancenon, Vicente; Lee, Sue-Ann; Patrick, Christina; Griffith, Janice; Paulino, Amy; Outeiro, Tiago F.; Reggiori, Fulvio; Masliah, Eliezer; Muchowski, Paul J.
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Identifying polyglutamine protein species in situ that best predict neurodegeneration (vol 7, pg 925, 2011)
err2012-02-15
err3
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errMiller, Jason; Arrasate, Montserrat; Brooks, Elizabeth; Libeu, Clare Peters; Legleiter, Justin; Hatters, Danny; Curtis, Jessica; Cheung, Kenneth; Krishnan, Preethi; Mitra, Siddhartha; Widjaja, Kartika; Shaby, Benjamin A.; Lotz, Gregor P.; Newhouse, Yvonne; Mitchell, Emily J.; Osmand, Alex; Gray, Michelle; Thulasiramin, Vanitha; Saudou, Frederic; Segal, Mark; Yang, X. William; Masliah, Eliezer; Thompson, Leslie M.; Muchowski, Paul J.; Weisgraber, Karl H.; Finkbeiner, Steven
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Identifying polyglutamine protein species in situ that best predict neurodegeneration
err2011-10-30
err195
errOAAI
errMiller, Jason; Arrasate, Montserrat; Brooks, Elizabeth; Libeu, Clare Peters; Legleiter, Justin; Hatters, Danny; Curtis, Jessica; Cheung, Kenneth; Krishnan, Preethi; Mitra, Siddhartha; Widjaja, Kartika; Shaby, Benjamin A.; Lotz, Gregor P.; Newhouse, Yvonne; Mitchell, Emily J.; Osmand, Alex; Gray, Michelle; Thulasiramin, Vanitha; Saudou, Frederic; Segal, Mark; Yang, X. William; Masliah, Eliezer; Thompson, Leslie M.; Muchowski, Paul J.; Weisgraber, Karl H.; Finkbeiner, Steven
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The Kynurenine Pathway Modulates Neurodegeneration in a Drosophila Model of Huntington's Disease
err2011-06-01
err221
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errCampesan, Susanna; Green, Edward W.; Breda, Carlo; Sathyasaikumar, Korrapati V.; Muchowski, Paul J.; Schwarcz, Robert; Kyriacou, Charalambos P.; Giorgini, Flaviano
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Functional Gene Expression Profiling in Yeast Implicates Translational Dysfunction in Mutant Huntingtin Toxicity
err2011-01-01
err48
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errTauber, Eran; Miller-Fleming, Leonor; Mason, Robert P.; Kwan, Wanda; Clapp, Jannine; Butler, Nicola J.; Outeiro, Tiago F.; Muchowski, Paul J.; Giorgini, Flaviano
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Hsp70 and Hsp40 Functionally Interact with Soluble Mutant Huntingtin Oligomers in a Classic ATP-dependent Reaction Cycle
err2010-12-01
err83
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errLotz, Gregor P.; Legleiter, Justin; Aron, Rebecca; Mitchell, Emily J.; Huang, Shao-Yi; Ng, Cheping; Glabe, Charles; Thompson, Leslie M.; Muchowski, Paul J.
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VALIDATION OF KMO AS A CANDIDATE THERAPEUTIC TARGET FOR HUNTINGTON'S DISEASE IN DROSOPHILA MELANOGASTER
err2010-11-16
err0
PREAI
errCampesan, S.; Green, E. W.; Sathyasaikumar, K. V.; Breda, C.; Muchowski, P. J.; Schwarcz, R.; Kyriacou, C. P.; Giorgini, F.
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Mutant Huntingtin Fragments Form Oligomers in a Polyglutamine Length-dependent Manner in Vitro and in Vivo
err2010-05-01
err212
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errLegleiter, Justin; Mitchell, Emily; Lotz, Gregor P.; Sapp, Ellen; Ng, Cheping; DiFiglia, Marian; Thompson, Leslie M.; Muchowski, Paul J.
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Of mice, rats and men: Revisiting the quinolinic acid hypothesis of Huntington's disease
err2010-02-01
err143
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errSchwarcz, Robert; Guidetti, Paolo; Sathyasaikumar, Korrapati V.; Muchowski, Paul J.
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