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Brain accumulation of lactosylceramide characterizes GALC deficiency in a zebrafish model of Krabbe disease 半乳糖脑苷脂在斑马鱼Krabbe病模型中积聚是GALC缺乏的特征。 Guerra, Jessica; Belleri, Mirella; Scalvini, Elisa; Capoferri, Davide; Tobia, Chiara; Ravelli, Cosetta; Corli, Marzia; Bresciani, Nicole; Casas, Josefina; Fabrias, Gemma; Dei Cas, Michele; Presta, Marco; Mignani, Luca 分享 收藏
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Serum levels of autotaxin reveal its role as a novel biomarker of migraine Ouro, Alberto; Castro-Mosquera, Monica; Rodriguez-Arrizabalaga, Marina; Debasa-Mouce, Manuel; Romaus-Sanjurjo, Daniel; Aramburu-Nunez, Marta; Iglesias-Rey, Ramon; Casas, Josefina; Lema, Isabel; Castillo, Jose; Leira, Rogelio; Sobrino, Tomas 分享 收藏
Elevated Serum Levels of Acid Sphingomyelinase in Female Patients with Episodic and Chronic Migraine Ouro, Alberto; Castro-Mosquera, Monica; Rodriguez-Arrizabalaga, Marina; Debasa-Mouce, Manuel; Custodia, Antia; Aramburu-Nunez, Marta; Romaus-Sanjurjo, Daniel; Casas, Josefina; Lema, Isabel; Castillo, Jose; Leira, Rogelio; Sobrino, Tomas 分享 收藏
Targeted nanoliposomes to improve enzyme replacement therapy of Fabry disease Tomsen-Melero, Judit; Molto-Abad, Marc; Merlo-Mas, Josep; Diaz-Riascos, Zamira V.; Cristobal-Lecina, Edgar; Soldevila, Andreu; Altendorfer-Kroath, Thomas; Danino, Dganit; Ionita, Inbal; Pedersen, Jan Skov; Snelling, Lyndsey; Clay, Hazel; Carreno, Aida; Corchero, Jose L.; Pulido, Daniel; Casas, Josefina; Veciana, Jaume; Schwartz Jr, Simo; Sala, Santi; Font, Albert; Birngruber, Thomas; Royo, Miriam; Cordoba, Alba; Ventosa, Nora; Abasolo, Ibane; Gonzalez-Mira, Elisabet 分享 收藏
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S1PR1 directs tumorsphere proliferation in ovarian cancer Gendrau-Sanclemente, Nuria; Figueras, Agnes; Gracova, Kristina; Alsina-Sanchis, Elisenda; Marin-Jimenez, Juan Antonio; Casas, Josefina; Vidal, August; Matias-Guiu, Xavier; Fernandez-Gonzalez, Sergi; Barahona, Marc; Marti, Lola; Ponce, Jordi; Vinals, Francesc 分享 收藏
A fluorogenic substrate for the detection of lipid amidases in intact cells Casasampere, Mireia; Ung, Johnson; Inanez, Alejandro; Dufau, Carine; Tsuboi, Kazuhito; Casas, Josefina; Tan, Su -Fern; Feith, David J.; Andrieu-Abadie, Nathalie; Segui, Bruno; Loughran Jr, Thomas P.; Abad, Jose Luis; Fabrias, Gemma 分享 收藏
Obesity promotes fumonisin B1 hepatotoxicity 肥胖促进伏马菌素B1肝毒性 Dopavogui, Leonie; Regnier, Marion; Polizzi, Arnaud; Ponchon, Quentin; Smati, Sarra; Klement, Wendy; Lasserre, Frederic; Lukowicz, Celine; Lippi, Yannick; Fougerat, Anne; Bertrand-Michel, Justine; Naylies, Claire; Canlet, Cecile; Debrauwer, Laurent; Rousseau-Bacquie, Elodie; Gamet-Payrastre, Laurence; Dauriat, Charlene; Casas, Josefina; Croubels, Siska; De Baere, Siegrid; Burger, Hester M.; Chassaing, Benoit; Ellero-Simatos, Sandrine; Guillou, Herve; Oswald, Isabelle P.; Loiseau, Nicolas 分享 收藏
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β-Cyclodextrins as affordable antivirals to treat coronavirus infection Raich-Regue, Dalia; Tenorio, Raquel; Fernandez de Castro, Isabel; Tarres-Freixas, Ferran; Sachse, Martin; Perez-Zsolt, Daniel; Munoz-Basagoiti, Jordana; Fernandez-Sanchez, Sara Y.; Gallemi, Marcal; Ortega-Gonzalez, Paula; Fernandez-Oliva, Alberto; Gabaldon, Jose A.; Nunez-Delicado, Estrella; Casas, Josefina; Roca, Nuria; Cantero, Guillermo; Perez, Monica; Usai, Carla; Lorca-Oro, Cristina; Alert, Julia-Vergara; Segales, Joaquim; Carrillo, Jorge; Blanco, Julia; Sala, Bonaventura Clotet; Ceron-Carrasco, Jose P.; Izquierdo-Useros, Nuria; Risco, Cristina 分享 收藏
RINT1 deficiency disrupts lipid metabolism and underlies a complex hereditary spastic paraplegia Launay, Nathalie; Ruiz, Montserrat; Planas-Serra, Laura; Verdura, Edgard; Rodriguez-Palmero, Agusti; Schluter, Agatha; Goicoechea, Leire; Guilera, Cristina; Casas, Josefina; Campelo, Felix; Jouanguy, Emmanuelle; Casanova, Jean-Laurent; Boespflug-Tanguy, Odile; Cancela, Maria Vazquez; Gutierrez-Solana, Luis Gonzalez; Casasnovas, Carlos; Area-Gomez, Estela; Pujol, Aurora 分享 收藏
Lipid signatures of West Nile virus infection unveil alterations of sphingolipid metabolism providing novel biomarkers 西尼罗病毒感染的脂质特征揭示了鞘脂代谢的变化,提供了新的生物标志物 Mingo-Casas, Patricia; Sanchez-Cespedes, Javier; Blazquez, Ana-Belen; Casas, Josefina; Balsera-Manzanero, Maria; Herrero, Laura; Vazquez, Ana; Pachon, Jeronimo; Aguilar-Guisado, Manuela; Cisneros, Jose Miguel; Saiz, Juan-Carlos; Martin-Acebes, Miguel A. 分享 收藏
Pharmacological Elevation of Cellular Dihydrosphingomyelin Provides a Novel Antiviral Strategy against West Nile Virus Infection Jimenez de Oya, Nereida; San-Felix, Ana; Casasampere, Mireia; Blazquez, Ana-Belen; Mingo-Casas, Patricia; Escribano-Romero, Estela; Calvo-Pinilla, Eva; Poderoso, Teresa; Casas, Josefina; Saiz, Juan-Carlos; Perez-Perez, Maria-Jesus; Martin-Acebes, Miguel A. 分享 收藏
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