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Rubén Artero

ISCIII

33H指数
106论文数
5.9K被引数
收录论文 58
发表时间
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Oleic Acid Levels in HSALR Mouse Model of Myotonic Dystrophy Type 11型肌强直性营养不良HSALR小鼠模型中的油酸水平
err2026-05-09
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errDulce Peris-Moreno; Maria Sabater-Arcis; Nerea Moreno; Luis Orduña; Arturo López-Castel; Ariadna Bargiela; Ruben Artero
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Pre- and postsynaptic upregulation of FasII synergistically underlies neuropathological and behavioral phenotypes in a Drosophila model of myotonic dystrophy在肌营养不良果蝇模型中,FasII的突触前和突触后上调协同构成了神经病理和行为的表型基础。
err2025-12-18
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errAlex Chun Koon; Ka Yee Winnie Yeung; Yitao Wu; Lok I Leong; John Tsun Po Cheung; Zhefan Stephen Chen; Shaohong Isaac Peng; Noah S. Armstrong; C. Andrew Frank; Paul Magneron; Mário Gomes-Pereira; Joyce Man See Fung; Ariadna Bargiela; Nerea Moreno; Javier Poyatos-Garcia; Juan Vilchez; Aline Huguet-Lachon; Cassandra Kussius Brewer; Max Zinter; Erin S. Beck; Rubén Artero; Genevieve Gourdon; Vivian Budnik; Travis Thomson; Brian D. McCabe; Ho Yin Edwin Chan
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miR-107 represses DMPK and is sequestered by CUG repeats triggering the MSI2/miR-7 pathogenesis axis in myotonic dystrophymiR-107 抑制 DMPK,并被 CUG 重复序列捕获,从而触发强直性肌营养不良症中的 MSI2/miR-7 致病轴。
err2025-06-04
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errN. Moreno; M. Sabater-Arcis; J. Espinosa-Espinosa; L. Mulet-Rivero; E. García-España; J. González-García; D. Seoane-Miraz; M.J.A. Wood; M.A. Varela; J. Ohana; T. Sevilla; M. Perez Alonso; A. Bargiela; R. Artero
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Use of HSALR female mice as a model for the study of myotonic dystrophy type I
err2025-02-27
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errCarrascosa-Saez, Marc; Colom-Rodrigo, Anna; Gonzalez-Martinez, Irene; Perez-Gomez, Raquel; Garcia-Rey, Andrea; Piqueras-Losilla, Diego; Ballestar, Ana; Llamusi, Beatriz; Cerro-Herreros, Estefania; Artero, Ruben
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Immortalized human myotonic dystrophy type 1 muscle cell lines to address patient heterogeneity (vol 27, 109930, 2024)永生性人类肌强直性营养不良1型肌细胞系用于解决患者异质性 (vol 27, 109930, 2024)
err2024-12-01
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errNunez-Manchon, Judit; Capo, Julia; Martinez-Pineiro, Alicia; Juanola, Eduard; Pesovic, Jovan; Mosqueira-Martin, Laura; Gonzalez-Imaz, Klaudia; Maestre-Mora, Pau; Odria, Renato; Cerro-Herreros, Estefania; Naldaiz-Gastesi, Neia; de Munain, Adolfo Lopez; Artero, Ruben; Savic-Pavicevic, Dusanka; Vallejo-Illarramendi, Ainara; Mamchaoui, Kamel; Bigot, Anne; Mouly, Vincent; Suelves, Monica; Nogales-Gadea, Gisela
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A Novel Class of FKBP12 Ligands Rescues Premature Aging Phenotypes Associated with Myotonic Dystrophy Type 1
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IF5.2
err2024-11-22
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errGarcia-Puga, Mikel; Gerenu, Gorka; Bargiela, Ariadna; Espinosa-Espinosa, Jorge; Mosqueira-Martin, Laura; Sagartzazu-Aizpurua, Maialen; Aizpurua, Jesus M.; Vallejo-Illarramendi, Ainara; Artero, Ruben; de Munain, Adolfo Lopez; Matheu, Ander
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AntimiR treatment corrects myotonic dystrophy primary cell defects across several CTG repeat expansions with a dual mechanism of action
err2024-10-11
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errCerro-Herreros, Estefania; Nunez-Manchon, Judit; Naldaiz-Gastesi, Neia; Carrascosa-Saez, Marc; Garcia-Rey, Andrea; Losilla, Diego Piqueras; Gonzalez-Martinez, Irene; Espinosa-Espinosa, Jorge; Moreno, Kevin; Poyatos-Garcia, Javier; Vilchez, Juan J.; de Munain, Adolfo Lopez; Suelves, Monica; Nogales-Gadea, Gisela; Llamusi, Beatriz; Artero, Ruben
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Msi2 enhances muscle dysfunction in a myotonic dystrophy type 1 mouse model
err2024-08-01
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errSabater-Arcis, Maria; Moreno, Nerea; Sevilla, Teresa; Alonso, Manuel Perez; Bargiela, Ariadna; Artero, Ruben
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Therapeutic potential of oleic acid supplementation in myotonic dystrophy muscle cell models
err2024-05-17
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errMoreno, Nerea; Sabater-Arcis, Maria; Sevilla, Teresa; Alonso, Manuel Perez; Ohana, Jessica; Bargiela, Ariadna; Artero, Ruben
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Taurine activates the AKT-mTOR axis to restore muscle mass and contractile strength in human 3D in vitro models of steroid myopathy
err2024-04-24
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errMughal, Sheeza; Sabater-Arcis, Maria; Artero, Ruben; Ramon-Azcon, Javier; Fernandez-Costa, Juan M.
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Peptide-conjugated antimiRs improve myotonic dystrophy type 1 phenotypes by promoting endogenous MBNL1 expression
err2023-12-01
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errGonzalez-Martinez, Irene; Cerro-Herreros, Estefania; Moreno, Nerea; Garcia-Rey, Andrea; Espinosa-Espinosa, Jorge; Carrascosa-Saez, Marc; Piqueras-Losilla, Diego; Arzumanov, Andrey; Seoane-Miraz, David; Jad, Yahya; Raz, Richard; Wood, Matthew J.; Varela, Miguel A.; Llamusi, Beatriz; Artero, Ruben
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BlockmiR AONs as Site-Specific Therapeutic MBNL Modulation in Myotonic Dystrophy 2D and 3D Muscle Cells and HSALR Mice
err2023-03-31
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errOverby, Sarah J.; Cerro-Herreros, Estefania; Espinosa-Espinosa, Jorge; Gonzalez-Martinez, Irene; Moreno, Nerea; Fernandez-Costa, Juan M.; Balaguer-Trias, Jordina; Ramon-Azcon, Javier; Perez-Alonso, Manuel; Moller, Thorleif; Llamusi, Beatriz; Artero, Ruben
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CRISPR-Cas9 editing of a TNPO3 mutation in a muscle cell model of limb-girdle muscular dystrophy type D2
err2023-03-01
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errPoyatos-Garcia, Javier; Blazquez-Bernal, Agueda; Selva-Gimenez, Marta; Bargiela, Ariadna; Espinosa-Espinosa, Jorge; Vazquez-Manrique, Rafael P.; Bigot, Anne; Artero, Ruben; Vilchez, Juan Jesus
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The myotonic dystrophy type 1 drug development pipeline: 2022 edition
err2023-03-01
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errPascual-Gilabert, Marta; Artero, Ruben; Lopez-Castel, Arturo
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Quantitative magnetic resonance imaging assessment of muscle composition in myotonic dystrophy mice
err2023-01-10
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errBargiela, Ariadna; Ten-Esteve, Amadeo; Marti-Bonmati, Luis; Sevilla, Teresa; Alonso, Manuel Perez; Artero, Ruben
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Moxifloxacin rescues SMA phenotypes in patient-derived cells and animal model
err2022-07-22
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errJanuel, Camille; Menduti, Giovanna; Mamchaoui, Kamel; Martinat, Cecile; Artero, Ruben; Konieczny, Piotr; Boido, Marina
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Proof of concept of peptide-linked blockmiR-induced MBNL functional rescue in myotonic dystrophy type 1 mouse model
err2022-03-01
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errOverby, Sarah J.; Cerro-Herreros, Estefania; Gonzalez-Martinez, Irene; Varela, Miguel A.; Seoane-Miraz, David; Jad, Yahya; Raz, Richard; Moller, Thorleif; Perez-Alonso, Manuel; Wood, Matthew J.; Llamusi, Beatriz; Artero, Ruben
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Preclinical characterization of antagomiR-218 as a potential treatment for myotonic dystrophy
err2021-12-01
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errCerro-Herreros, Estefania; Gonzalez-Martinez, Irene; Moreno, Nerea; Espinosa-Espinosa, Jorge; Fernandez-Costa, Juan M.; Colom-Rodrigo, Anna; Overby, Sarah J.; Seoane-Miraz, David; Poyatos-Garcia, Javier; Vilchez, Juan J.; de Munain, Adolfo Lopez; Varela, Miguel A.; Wood, Matthew J.; Perez-Alonso, Manuel; Llamusi, Beatriz; Artero, Ruben
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Defined d-hexapeptides bind CUG repeats and rescue phenotypes of myotonic dystrophy myotubes in a Drosophila model of the disease
err2021-09-30
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errRapisarda, Anna; Bargiela, Ariadna; Llamusi, Beatriz; Pont, Isabel; Estrada-Tejedor, Roger; Garcia-Espana, Enrique; Artero, Ruben; Perez-Alonso, Manuel
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