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IRP1 deficiency alters mitochondrial metabolism and protects against metabolic syndrome pathologies IRP1缺乏改变线粒体代谢并保护免受代谢综合征病理的影响 Gu, Wen; Wilkinson, Nicole; Fillebeen, Carine; Blackburn, Darren M.; Sahinyan, Korin; Bonneil, Eric; Zhao, Tao; Luo, Zhi; Soleimani, Vahab D.; Richard, Vincent; Borchers, Christoph H.; Koulman, Albert; Jenkins, Benjamin; Michalke, Bernhard; Zischka, Hans; Sailer, Judith; Venkataramani, Vivek; Iliopoulos, Othon; Sweeney, Gary; Pantopoulos, Kostas 分享 收藏
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Mutual reinforcement of lymphotoxin-driven myositis and impaired autophagy in murine muscle 淋巴毒素驱动的肌炎与小鼠肌肉中受损的自噬之间的相互强化 Bremer, Juliane; Nagel, Judith; Zschuntzsch, Jana; Zajt, Kamil K.; Palaz, Tayfun; Blank, Thomas; Ikis, Aylin; Fischer, Laura A.; Sensmeyer, Anna S. M.; Wiechers, Lara; Reichelt, Josef J.; Hofmann, Kai P.; Wolf, Monika J.; Leuchtenberger, Corinna; Tripathi, Priyanka; Einer, Claudia; Zischka, Hans; Rothermel, Ulrike; Eck, Anna-L; Reimann, Regina R.; Kana, Veronika; Rushing, Elisabeth; Aguzzi, Adriano; Prinz, Marco; Liebetanz, David; Odoardi, Francesca; Kuo, Chao-Chung; Weis, Joachim; Kraft, Florian; Schmidt, Jens; Heikenwalder, Mathias 分享 收藏
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Copper impairs the intestinal barrier integrity in Wilson disease Fontes, Adriana; Pierson, Hannah; Bierla, Joanna B.; Eberhagen, Carola; Kinschel, Jennifer; Akdogan, Banu; Rieder, Tamara; Sailer, Judith; Reinold, Quirin; Cielecka-Kuszyk, Joanna; Szymanska, Sylwia; Neff, Frauke; Steiger, Katja; Seelbach, Olga; Zibert, Andree; Schmidt, Hartmut H.; Hauck, Stefanie M.; von Toerne, Christine; Michalke, Bernhard; Semrau, Jeremy D.; DiSpirito, Ana M.; Ramalho-Santo, Joao; Kroemer, Guido; Polishchuk, Roman; Azul, Anabela Marisa; Dispirito, Alan; Socha, Piotr; Lutsenko, Svetlana; Zischka, Hans 分享 收藏
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A fluorometric assay to determine labile copper(II) ions in serum (vol 13, 12807, 2023) Maares, Maria; Haupt, Alessia; Schuessler, Christoph; Kulike-Koczula, Marcel; Hackler, Julian; Keil, Claudia; Mohr, Isabelle; Schomburg, Lutz; Suessmuth, Roderich D.; Zischka, Hans; Merle, Uta; Haase, Hajo 分享 收藏
OCaR1 endows exocytic vesicles with autoregulatory competence by preventing uncontrolled Ca2+ release, exocytosis, and pancreatic tissue damage Tsvilovskyy, Volodymyr; Ottenheijm, Roger; Kriebs, Ulrich; Schuetz, Aline; Diakopoulos, Kalliope Nina; Jha, Archana; Bildl, Wolfgang; Wirth, Angela; Boeck, Julia; Jaslan, Dawid; Ferro, Irene; Taberner, Francisco J.; Kalinina, Olga; Hildebrand, Staffan; Wissenbach, Ulrich; Weissgerber, Petra; Vogt, Dominik; Eberhagen, Carola; Mannebach, Stefanie; Berlin, Michael; Kuryshev, Vladimir; Schumacher, Dagmar; Philippaert, Koenraad; Camacho-Londono, Juan E.; Mathar, Ilka; Dieterich, Christoph; Klugbauer, Norbert; Biel, Martin; Wahl-Schott, Christian; Lipp, Peter; Flockerzi, Veit; Zischka, Hans; Alguel, Hana; Lechner, Stefan G.; Lesina, Marina; Grimm, Christian; Fakler, Bernd; Schulte, Uwe; Muallem, Shmuel; Freichel, Marc 分享 收藏
Farnesoid X receptor activation by bile acids suppresses lipid peroxidation and ferroptosis 胆汁酸激活法尼酯X受体抑制脂质过氧化和铁死亡 Tschuck, Juliane; Theilacker, Lea; Rothenaigner, Ina; Weiss, Stefanie A. I.; Akdogan, Banu; Van Thanh Lam; Mueller, Constanze; Graf, Roman; Brandner, Stefanie; Puetz, Christian; Rieder, Tamara; Schmitt-Kopplin, Philippe; Vincendeau, Michelle; Zischka, Hans; Schorpp, Kenji; Hadian, Kamyar 分享 收藏
A fluorometric assay to determine labile copper(II) ions in serum 荧光测定法测定血清中不稳定的铜 (II) 离子 Maares, Maria; Haupt, Alessia; Schuessler, Christoph; Kulike-Koczula, Marcel; Hackler, Julian; Keil, Claudia; Mohr, Isabelle; Schomburg, Lutz; Suessmuth, Roderich D.; Zischka, Hans; Merle, Uta; Haase, Hajo 分享 收藏
ARBM101 (Methanobactin SB2) Drains Excess Liver Copper via Biliary Excretion in Wilson's Disease Rats ARBM101 (甲烷菌素SB2) 通过威尔逊氏病大鼠的胆汁排泄排泄过量的肝铜 Einer, Claudia; Munk, Ditte Emilie; Park, Eok; Akdogan, Banu; Nagel, Judith; Lichtmannegger, Josef; Eberhagen, Carola; Rieder, Tamara; Vendelbo, Mikkel H.; Michalke, Bernhard; Wimmer, Ralf; Blutke, Andreas; Feuchtinger, Annette; Dershwitz, Philip; DiSpirito, Ana M.; Islam, Tawhidul; Castro, Rui E.; Min, Byong-Keol; Kim, TaeWon; Choi, Seoyoun; Kim, Dasol; Jung, Chunwon; Lee, Hongjae; Park, Dongsik; Im, Weonbin; Eun, So-Young; Cho, You-Hee; Semrau, Jeremy D.; Rodrigues, Cecilia M. P.; Hohenester, Simon; Sandahl, Thomas Damgaard; DiSpirito, Alan A.; Zischka, Hans 分享 收藏
Excessive copper impairs intrahepatocyte trafficking and secretion of selenoprotein P 过量的铜会损害肝细胞内运输和硒蛋白P的分泌 Schwarz, Maria; Meyer, Caroline E.; Loeser, Alina; Lossow, Kristina; Hackler, Julian; Ott, Christiane; Jaeger, Susanne; Mohr, Isabelle; Eklund, Ella A.; Patel, Angana A. H.; Gul, Nadia; Alvarez, Samantha; Altinonder, Ilayda; Wiel, Clotilde; Maares, Maria; Haase, Hajo; Haertlova, Anetta; Grune, Tilman; Schulze, Matthias B.; Schwerdtle, Tanja; Merle, Uta; Zischka, Hans; Sayin, Volkan I.; Schomburg, Lutz; Kipp, Anna P. 分享 收藏
IMPAIRMENT OF HEPATIC SELENOPROTEIN P SECRETION BY COPPER Schwarz, Maria; Meyer, Caroline E.; Loser, Alina; Lossow, Kristina; Ott, Christiane; Wiel, Clotilde; Grune, Tilman; Schwerdtle, Tanja; Zischka, Hans; Sayin, Volkan I.; Schomburg, Lutz; Kipp, Anna P. 分享 收藏
The decylTPP mitochondria-targeting moiety lowers electron transport chain supercomplex levels in primary human skin fibroblasts 癸基tpp线粒体靶向部分降低了原代人皮肤成纤维细胞中的电子传输链超复合物水平 Bulthuis, Elianne P.; Einer, Claudia; Distelmaier, Felix; Groh, Laszlo; Van Emst-De Vries, Sjenet E.; Van De Westerlo, Els; Van De Wal, Melissa; Wagenaars, Jori; Rodenburg, Richard J.; Smeitink, Jan A. M.; Riksen, Niels P.; Willems, Peter H. G. M.; Adjobo-Hermans, Merel J. W.; Zischka, Hans; Koopman, Werner J. H. 分享 收藏
Loss of UCP1 function augments recruitment of futile lipid cycling for thermogenesis in murine brown fat UCP1功能的丧失增加了小鼠棕色脂肪中无益的脂质循环用于产热的募集 Oeckl, Josef; Janovska, Petra; Adamcova, Katerina; Bardova, Kristina; Brunner, Sarah; Dieckmann, Sebastian; Ecker, Josef; Fromme, Tobias; Funda, Jiri; Gantert, Thomas; Giansanti, Piero; Hidrobo, Maria Soledad; Kuda, Ondrej; Kuster, Bernhard; Li, Yongguo; Pohl, Radek; Schmitt, Sabine; Schweizer, Sabine; Zischka, Hans; Zouhar, Petr; Kopecky, Jan; Klingenspor, Martin 分享 收藏