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Anne Bigot

inserm and sorbonne universite

32H指数
142论文数
4.1K被引数
收录论文 64
发表时间
A decline in skeletal muscle NOX4 abrogates exercise-induced adaptive homeostasis and exacerbates biological aging骨骼肌NOX4的下降消除了运动诱导的适应性稳态并加剧生物衰老
err2026-06-10
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errOAAI
errChrysovalantou E. Xirouchaki; Esther García-Domínguez; Eamon Coughlan; Meagan J. McGrath; Saveen Giri; Shuwei Liang; Florian Wiede; Anne Bigot; Junichi Sadoshima; Maria C. Gomez-Cabrera; Andrew Philp; Marcus Moberg; William Apró; William Roman; Christina A. Mitchell; Tony Tiganis
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EMILIN1 emerges as a TGFβ/SETDB1-regulated secreted biomarker in Duchenne muscular dystrophyEMILIN1作为一种由TGFβ/SETDB1调控的分泌型生物标志物在杜氏肌营养不良症中显现
err2026-05-09
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errOAAI
errMaeva Zamperoni; Laura Muraine; Minh-Y Tran; Alice Granados; Anne Bigot; Valentin Petit; Mona Bensalah; Jessica Ohana; Véronique Legros; Ekaterina Boyarchuk; Johanna Bruce; Guillaume Chevreux; Véronique Joliot; Elisa Negroni; Maryline Moulin; Capucine Trollet; Slimane Ait-Si-Ali
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Biallelic PAX7 variants cause a novel Satellite Cell-opathy with progressive muscle involvement resembling facioscapulohumeral muscular dystrophy
err2026-01-29
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errMassimo Ganassi; Claudia Strafella; Marco Savarese; Philipp Heher; Elise N. Engquist; Liam McGuire; Mridul Johari; Gian F. De Nicola; Anne Bigot; Vincent Mouly; Sara Bortolani; Eleonora Torchia; Mauro Monforte; Domenica Megalizzi; Andrea Sabino; Enzo Ricci; Emiliano Giardina; Peter S. Zammit; Giorgio Tasca
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HDAC11 deficiency improves muscle phenotype in a Duchenne muscular dystrophy murine model by reducing inflammation and fibrosisHDAC11缺陷通过减少炎症和纤维化,改善杜氏肌营养不良小鼠模型的肌肉表型
err2025-12-15
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PREAI
errRenato Odria; Alexandra Mercado-Amarilla; Carolina Soler-Botija; Daniel M. Borràs; Jessica Ohana; Pau Maestre; Anne Bigot; Xavier Suárez-Calvet; Eduard Gallardo; Gisela Nogales-Gadea; Mònica Suelves
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Oleuropein Aglycone Modulates Oxidative Stress and Autophagy-Related Pathways in Human Skeletal Muscle Cells
err2025-11-01
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errPolacchini, Giulia; Venerando, Andrea; Bigot, Anne; Colitti, Monica
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Generation Using Phage-Display of pH-Dependent Antibodies Against the Tumor-Associated Antigen AXL通过噬菌体展示技术生成针对肿瘤相关抗原AXL的pH依赖性抗体
err2025-10-01
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errTristan Mangeat; Célestine Mairaville; Myriam Chentouf; Madeline Neiveyans; Martine Pugnière; Giang Ngo; Vincent Denis; Corentin Catherine; Alexandre Pichard; Emmanuel Deshayes; Margaux Maurel; Matthieu Gracia; Anne Bigot; Vincent Mouly; Sébastien Estaran; Alain Chavanieu; Pierre Martineau; Bruno Robert
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Ubiquitin-proteasome system dysregulation in FAM111B-related poikiloderma and phenotypic spectrum expansion: new case reports and long-term follow-upFAM111B相关性异色性皮病中泛素-蛋白酶体系统失调及表型谱扩展:新病例报告与长期随访
err2025-08-20
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PREAI
errVirginie Vignard; Mike Maillasson; Anne Bigot; Sébastien Küry; Thomas Besnard; Martin Broly; Aurélie Guého; Emmanuelle Com; Erica Davis; Wallid Deb; Laëtitia Florenceau; Karen Sobriel; Grégoire Ménard; Betty Gardie; Alice Goldenberg; Joseph Porrmann; Randal Richardson; Léa Ruffier; Smail Hadj-Rabia; Stéphane Bézieau; Sébastien Barbarot; Frédéric Ebstein; Sandra Mercier
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Evaluation of synthetic mRNA with selected UTR sequences and alternative poly(A) tail, in vitro and in vivo体外及体内评价具有选择性UTR序列和可变多聚(A)尾的合成mRNA
err2025-07-30
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errAyoub Medjmedj; Hugo Genon; Dounia Hezili; Albert Ngalle Loth; Rudy Clemençon; Cyril Guimpied; Lucile Mollet; Anne Bigot; Frank Wien; Josef Hamacek; Clément Chapat; Federico Perche
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Ageing Signatures and Disturbed Muscle Regeneration in Muscle Proteome of Inclusion Body Myositis肌萎缩侧索硬化症肌肉蛋白质组中的衰老特征及肌肉再生障碍
err2025-06-08
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errGeert M. de Vries; Bob Asselbergh; Alice Monticelli; Peter De Jonghe; Stuart Maudsley; Peter Y. K. Van Den Bergh; Anne Bigot; Jan L. De Bleecker
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DG9 boosts PMO nuclear uptake and exon skipping to restore dystrophic muscle and cardiac functionDG9 通过提高 PMO 核摄取和外显子跳读来恢复肌营养不良骨骼肌和心脏功能
err2025-05-14
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errOAAI
errShah, Md Nur Ahad; Wilton-Clark, Harry; Haque, Farhia; Powell, Brooklynn; Sutanto, Laura Edellein; Maradiya, Radha; Zhabyeyev, Pavel; Roshmi, Rohini Roy; Anwar, Saeed; Aslesh, Tejal; Lim, Kenji Rowel Q.; Maruyama, Rika; Bigot, Anne; Young, Courtney S.; Bittner, Scott; Spencer, Melissa J.; Moulton, Hong M.; Oudit, Gavin Y.; Yokota, Toshifumi
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High-throughput screening identifies bazedoxifene as a potential therapeutic for dysferlin-deficient limb girdle muscular dystrophy高通量筛选鉴定出巴济多昔芬(bazedoxifene)为 dysferlin 缺乏性肢带型肌营养不良的潜在治疗药物。
err2025-03-19
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errBruge, Celine; Bourg, Nathalie; Pellier, Emilie; Tournois, Johana; Polentes, Jerome; Benabides, Manon; Grossi, Noella; Bigot, Anne; Brureau, Anthony; Richard, Isabelle; Nissan, Xavier
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Antisense oligonucleotide-mediated exon 27 skipping restores dysferlin function in dysferlinopathy patient-derived muscle cells
err2025-03-01
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errAnwar, Saeed; Roshmi, Rohini Roy; Woo, Stanley; Haque, Umme Sabrina; Lee, Joshua James Arthur; Duddy, William John; Bigot, Anne; Maruyama, Rika; Yokota, Toshifumi
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Cell-mediated exon skipping normalizes dystrophin expression and muscle function in a new mouse model of Duchenne Muscular Dystrophy (vol 16, 927, 2024)
err2024-09-06
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errGalli, Francesco; Bragg, Laricia; Rossi, Maira; Proietti, Daisy; Perani, Laura; Bacigaluppi, Marco; Tonlorenzi, Rossana; Sibanda, Tendai; Caffarini, Miriam; Talapatra, Avraneel; Santoleri, Sabrina; Meregalli, Mirella; Bano-Otalora, Beatriz; Bigot, Anne; Bozzoni, Irene; Bonini, Chiara; Mouly, Vincent; Torrente, Yvan; Cossu, Giulio
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SETDB1 modulates the TGFβ response in Duchenne muscular dystrophy myotubes
err2024-05-03
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errGranados, Alice; Zamperoni, Maeva; Rapone, Roberta; Moulin, Maryline; Boyarchuk, Ekaterina; Bouyioukos, Costas; Del Maestro, Laurence; Joliot, Veronique; Negroni, Elisa; Mohamed, Myriame; Piquet, Sandra; Bigot, Anne; Le Grand, Fabien; Albini, Sonia; Ait-Si-Ali, Slimane
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miR-379 links glucocorticoid treatment with mitochondrial response in Duchenne muscular dystrophy (vol 10, 9139, 2020)
err2024-03-28
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errOAAI
errSanson, Mathilde; Vu Hong, Ai; Massourides, Emmanuelle; Bourg, Nathalie; Suel, Laurence; Amor, Fatima; Corre, Guillaume; Benit, Paule; Barthelemy, Ines; Blot, Stephane; Bigot, Anne; Pinset, Christian; Rustin, Pierre; Servais, Laurent; Voit, Thomas; Richard, Isabelle; Israeli, David
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Cell-mediated exon skipping normalizes dystrophin expression and muscle function in a new mouse model of Duchenne Muscular Dystrophy
err2024-03-04
err1
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errGalli, Francesco; Bragg, Laricia; Rossi, Maira; Proietti, Daisy; Perani, Laura; Bagicaluppi, Marco; Tonlorenzi, Rossana; Sibanda, Tendai; Caffarini, Miriam; Talapatra, Avraneel; Santoleri, Sabrina; Meregalli, Mirella; Bano-Otalora, Beatriz; Bigot, Anne; Bozzoni, Irene; Bonini, Chiara; Mouly, Vincent; Torrente, Yvan; Cossu, Giulio
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Chronic hypoxia impairs skeletal muscle repair via HIF-2α stabilization
err2024-02-09
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errYin, Amelia; Fu, Wenyan; Elengickal, Anthony; Kim, Joonhee; Liu, Yang; Bigot, Anne; Mamchaoui, Kamal; Call, Jarrod A.; Yin, Hang
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Differential effects of the venoms of Russell's viper and Indian cobra on human myoblasts
err2024-02-07
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errOAAI
errBin Haidar, Husain; Almeida, Jose R.; Williams, Jarred; Guo, Bokai; Bigot, Anne; Senthilkumaran, Subramanian; Vaiyapuri, Sakthivel; Patel, Ketan
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CRISPR-Cas9 KO Cell Line Generation and Development of a Cell-Based Potency Assay for rAAV-FKRP Gene Therapy
errCELLS
IF5.2
err2023-10-12
err3
errOAAI
errGeoffroy, Marine; Pili, Louna; Buffa, Valentina; Caroff, Maelle; Bigot, Anne; Gicquel, Evelyne; Rouby, Gregory; Richard, Isabelle; Fragnoud, Romain
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Identification of a muscle-specific isoform of VMA21 as a potent actor in X-linked myopathy with excessive autophagy pathogenesis
err2023-09-26
err3
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errCocchiararo, Ilaria; Cattaneo, Olivia; Rajendran, Jayasimman; Chabry, Florent; Cornut, Melanie; Soldati, Hadrien; Bigot, Anne; Mamchaoui, Kamel; Gibertini, Sara; Bouche, Axelle; Ham, Daniel J.; Laumonier, Thomas; Prola, Alexandre; Castets, Perrine
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