arrow
返回
L

Ludo Van Den Bosch

University of Leuven

82H指数
415论文数
3.4W被引数
收录论文 162
发表时间
err分享
err收藏
Using human 3D organoid models to gain mechanistic insight in motor neuron diseases利用人类3D类器官模型探究运动神经元疾病的机制
err2026-07-06
err0
PREAI
errBenedetta Frizzi; Adriana Margarida Barbosa Correia; Irene Faravelli; Ludo Van Den Bosch; Stefania Corti
err分享
err收藏
CREsted: modeling genomic and synthetic cell-type-specific enhancers across tissues and speciesCREsted: 跨组织和物种的基因组和合成细胞类型特异性增强子建模
err2026-04-02
err0
errOAAI
errNiklas Kempynck; Seppe De Winter; Casper H. Blaauw; Vasileios Konstantakos; Eren Can Ekşi; Sam Dieltiens; Darina Abaffyová; Valérie Bercier; Ibrahim I. Taskiran; Gert Hulselmans; Katina Spanier; Valerie Christiaens; Ludo Van Den Bosch; Lukas Mahieu; Stein Aerts
err分享
err收藏
Axonal Eif5a hypusination controls local translation and mitigates defects in FUS-ALS轴突Eif5a催眠控制局部翻译并减轻fus-als的缺陷
err2025-12-22
err0
errOAAI
errDiana Piol; Bilal Khalil; Tessa Robberechts; Theo Killian; Maria Georgopoulou; Gabriele Partel; David Wouters; Nikolai Hecker; Paraskevi Tziortzouda; Yana Verresen; Nikky Corthout; Sam Kint; Katy Vandereyken; Philip Van Damme; Thierry Voet; Kristofer Davie; Suresh Poovathingal; Ludo Van Den Bosch; Stein Aerts; Alejandro Sifrim; Sandrine Da Cruz
err分享
err收藏
C9orf72 hexanucleotide repeat expansions impair microglial response in ALSC9orf72六核苷酸重复扩增会损害ALS中的小胶质细胞反应
err2025-10-14
err0
errOAAI
errPegah Masrori; Baukje Bijnens; Laura Fumagalli; Kristofer Davie; Suresh Kumar Poovathingal; Tim Meese; Annet Storm; Nicole Hersmus; Raheem Fazal; Diede van den Biggelaar; Bob Asselbergh; Roxane Gruel; Johanna Van Den Daele; Heidi Denton; Paula Polanco Miquel; Simona Manzella; Winnok H. De Vos; Siddhartan Chandran; Ludo Van Den Bosch; Dietmar Rudolf Thal; Renzo Mancuso; Philip Van Damme
err分享
err收藏
Pharmacologic Inhibition of Glutamate Dehydrogenase 1 Improves Functional Recovery of Neuromuscular Junctions and Muscle Function in Duchenne Muscular Dystrophy药理学抑制谷氨酸脱氢酶1可改善杜氏肌营养不良症中神经肌肉接头的功能恢复和肌肉功能。
err2025-06-02
err0
errOAAI
errAndreia Pereira-Nunes; Ummi Ammarah; Min Shang; Iris Charatsidou; Himal Sharma; Bruna Pereira Sorroche; Max Nobis; Thibaut Burg; Stijn Verschoren; Frédéric Relaix; Alessio Rotini; Ludo Van Den Bosch; Marcello Delfini; Emanuele Berardi; Massimiliano Mazzone
err分享
err收藏
Lipid metabolism alterations in peripheral neuropathies外周神经病变中的脂质代谢改变
errNeuron
IF15
err2025-04-30
err0
PREAI
errAlessio Silva; Robert Prior; Maurizio D’Antonio; Johannes V. Swinnen; Ludo Van Den Bosch
err分享
err收藏
Dual-targeting CRISPR-CasRx reduces C9orf72 ALS/FTD sense and antisense repeat RNAs in vitro and in vivo双靶向CRISPR-CasRx在体外和体内均可降低C9orf72 ALS/FTD正义和反义重复RNA水平。
err2025-01-08
err1
errOAAI
errKempthorne, Liam; Vaizoglu, Deniz; Cammack, Alexander J.; Carcole, Mireia; Roberts, Martha J.; Mikheenko, Alla; Fisher, Alessia; Suklai, Pacharaporn; Muralidharan, Bhavana; Kroll, Francois; Moens, Thomas G.; Yshii, Lidia; Verschoren, Stijn; Holbling, Benedikt V.; Moreira, Francisco C.; Katona, Eszter; Coneys, Rachel; de Oliveira, Paula; Zhang, Yong-Jie; Jansen, Karen; Daughrity, Lillian M.; Mcgown, Alexander; Ramesh, Tennore M.; van den Bosch, Ludo; Lignani, Gabriele; Rahim, Ahad A.; Coyne, Alyssa N.; Petrucelli, Leonard; Rihel, Jason
err分享
err收藏
C21ORF2 mutations point towards primary cilia dysfunction in amyotrophic lateral sclerosis
errBRAIN
IF11.7
err2024-12-20
err0
PREAI
errDe Decker, Mathias; Zelina, Pavol; Moens, Thomas G.; Beckers, Jimmy; Contardo, Matilde; Dittlau, Katarina Stoklund; Van Schoor, Evelien; Ronisz, Alicja; Eggermont, Kristel; Moisse, Matthieu; Chandran, Siddharthan; Veldink, Jan H.; Thal, Dietmar Rudolf; van den Bosch, Ludo; Pasterkamp, R. Jeroen; Van Damme, Philip
err分享
err收藏
A pathogenic mutation in the ALS/FTD gene VCP induces mitochondrial hypermetabolism by modulating the permeability transition poreALS/FTD基因VCP的致病性突变通过调节通透性转换孔诱导线粒体高代谢
err2024-10-10
err0
errOAAI
errVanderhaeghe, Silke; Prerad, Jovan; Tharkeshwar, Arun Kumar; Goethals, Elien; Vints, Katlijn; Beckers, Jimmy; Scheveneels, Wendy; Debroux, Eveline; Princen, Katrien; Van Damme, Philip; Fivaz, Marc; Griffioen, Gerard; van den Bosch, Ludo
err分享
err收藏
Novel Far-Red Fluorescent 1,4-Dihydropyridines for L-Type Calcium Channel Imaging用于L型钙通道成像的新型远红荧光1,4-二氢吡啶
err2024-10-10
err0
PREAI
errBorgarelli, Carlotta; Klingl, Yvonne E.; Escamilla-Ayala, Abril; Scarponi, Carlotta; La Rovere, Rita M. L.; Dittlau, Katarina Stoklund; Bultynck, Geert; Sampaolesi, Maurilio; Schoenberger, Matthias; Munck, Sebastian; Van Den Bosch, Ludo; De Borggraeve, Wim M.; Ismalaj, Ermal
err分享
err收藏
Targeting EGLN2/PHD1 protects motor neurons and normalizes the astrocytic interferon response靶向EGLN2/PHD1保护运动神经元并使星形胶质细胞干扰素反应正常化
err2024-09-01
err1
errOAAI
errGermeys, Christine; Vandoorne, Tijs; Davie, Kristofer; Poovathingal, Suresh; Heeren, Kara; Vermeire, Wendy; Nami, Fatemeharefeh; Moisse, Matthieu; Quaegebeur, Annelies; Sierksma, Annerieke; Rue, Laura; Sicart, Adria; Eykens, Caroline; De Cock, Lenja; De Strooper, Bart; Carmeliet, Peter; Van Damme, Philip; De Bock, Katrien; van den Bosch, Ludo
err分享
err收藏
A deep phenotyping study in mouse and iPSC models to understand the role of oligodendroglia in optic neuropathy in Wolfram syndrome
err2024-08-28
err0
errOAAI
errAhuja, K.; Vandenabeele, M.; Nami, F.; Lefevere, E.; Van Hoecke, J.; Bergmans, S.; Claes, M.; Vervliet, T.; Neyrinck, K.; Burg, T.; De Herdt, D.; Bhaskar, P.; Zhu, Y.; Looser, Z. J.; Loncke, J.; Gsell, W.; Plaas, M.; Agostinis, P.; Swinnen, J. V.; van den Bosch, L.; Bultynck, G.; Saab, A. S.; Wolfs, E.; Chai, Y. C.; Himmelreich, U.; Verfaillie, C.; Moons, L.; De Groef, L.
err分享
err收藏
Disruption of MAM integrity in mutant FUS oligodendroglial progenitors from hiPSCs (vol 147, 6, 2024)来自hipsc的突变FUS少突胶质祖细胞中MAM完整性的破坏 (147卷,6,2024)
err2024-06-13
err0
errOAAI
errZhu, Yingli; Burg, Thibaut; Neyrinck, Katrien; Vervliet, Tim; Nami, Fatemeharefeh; Vervoort, Ellen; Ahuja, Karan; Sassano, Maria Livia; Chai, Yoke Chin; Tharkeshwar, Arun Kumar; De Smedt, Jonathan; Hu, Haibo; Bultynck, Geert; Agostinis, Patrizia; Swinnen, Johannes V.; van den Bosch, Ludo; da Costa, Rodrigo Furtado Madeiro; Verfaillie, Catherine
err分享
err收藏
Advances and challenges in modeling inherited peripheral neuropathies using iPSCs使用iPSCs对遗传性周围神经病进行建模的进展和挑战
err2024-06-03
err1
errOAAI
errVan Lent, Jonas; Prior, Robert; Siles, Gonzalo Perez; Cutrupi, Anthony N.; Kennerson, Marina L.; Vangansewinkel, Tim; Wolfs, Esther; Mukherjee-Clavin, Bipasha; Nevin, Zachary; Judge, Luke; Conklin, Bruce; Tyynismaa, Henna; Clark, Alex J.; Bennett, David L.; Van Den Bosch, Ludo; Saporta, Mario; Timmerman, Vincent
err分享
err收藏
PMP22 duplication dysregulates lipid homeostasis and plasma membrane organization in developing human Schwann cellsPMP22复制在发育中的人类雪旺氏细胞中异常调节脂质稳态和质膜组织
errBRAIN
IF11.7
err2024-05-14
err3
errOAAI
errPrior, Robert; Silva, Alessio; Vangansewinkel, Tim; Idkowiak, Jakub; Tharkeshwar, Arun Kumar; Hellings, Tom P.; Michailidou, Iliana; Vreijling, Jeroen; Loos, Maarten; Koopmans, Bastijn; Vlek, Nina; Agaser, Cedrick; Kuipers, Thomas B.; Michiels, Christine; Rossaert, Elisabeth; Verschoren, Stijn; Vermeire, Wendy; de Laat, Vincent; Dehairs, Jonas; Eggermont, Kristel; van den Biggelaar, Diede; Bademosi, Adekunle T.; Meunier, Frederic A.; Vandeven, Martin; Van Damme, Philip; Mei, Hailiang; Swinnen, Johannes, V; Lambrichts, Ivo; Baas, Frank; Fluiter, Kees; Wolfs, Esther; van den Bosch, Ludo
err分享
err收藏
FUS unveiled in mitochondrial DNA repair and targeted ligase-1 expression rescues repair-defects in FUS-linked motor neuron disease
err2024-03-09
err6
errOAAI
errKodavati, Manohar; Wang, Haibo; Guo, Wenting; Mitra, Joy; Hegde, Pavana M.; Provasek, Vincent; Rao, Vikas H. Maloji; Vedula, Indira; Zhang, Aijun; Mitra, Sankar; Tomkinson, Alan E.; Hamilton, Dale J.; van den Bosch, Ludo; Hegde, Muralidhar L.
err分享
err收藏
The sense of antisense therapies in ALSALS的反义治疗意义
err2024-03-01
err12
errOAAI
errVan Daele, Sien H.; Masrori, Pegah; Van Damme, Philip; Van Den Bosch, Ludo
err分享
err收藏
TUBA4A downregulation as observed in ALS post-mortem motor cortex causes ALS-related abnormalities in zebrafish在ALS死后运动皮层中观察到的TUBA4A下调导致斑马鱼中ALS相关的异常
err2024-02-21
err1
errOAAI
errVan Schoor, Evelien; Strubbe, Dufie; Braems, Elke; Weishaupt, Jochen; Ludolph, Albert C.; Van Damme, Philip; Thal, Dietmar Rudolf; Bercier, Valerie; Van den Bosch, Ludo
err分享
err收藏