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Ian A. Blair

University of Pennsylvania

80H-index
660Paper Count
2.9WCitation Count
Published Papers 209
Publication Date
Therapeutic activity of a hematopoietic stem cell-delivered cell-penetrating frataxin in Friedreich’s ataxia models
err2026-05-13
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errOAAI
errJeffrey Pido-Lopez; Shefta E Moula; Enas Shaban; Konstantinos Stamatiou; Bethan J. Critchley; Thomas E. Whittaker; Stina Svensson; Sara Anjomani-Virmouni; Ester Kalef-Ezra; Lucinda Carr; Jane Hassel; Adrian J. Thrasher; Manju A. Kurian; Ian A. Blair; Teerapat Rojsajjakul; Giorgia Santilli; Arturo Sala
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Safety and efficacy of individualised exercise and NAD+ precursor supplementation in patients with Friedreich's ataxia in the USA: a single-centre, 2 × 2 factorial, randomised controlled trial
err2026-04-17
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PREAI
errKimberly Y Lin; Anna Bucha; Kara McSweeney; Kristin L Wade; Antoneta Karaj; Jaclyn Tamaroff; Shannon O’Malley; Nicole M Chung; Nicolette A Cilenti; Julianne Wanner; Gabriel K Adzika; Clementina Mesaros; Ian A Blair; Teerapat Rojsajjakul; Suraj Serai; Jennifer Farmer; Kyle Bryant; Yingying Lu; Michael O Harhay; David R Weber
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Expression and processing of mature human frataxin after gene therapy in mice
err2024-04-10
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errOAAI
errRojsajjakul, Teerapat; Selvan, Nithya; De, Bishnu; Rosenberg, Jonathan B.; Kaminsky, Stephen M.; Sondhi, Dolan; Janki, Peter; Crystal, Ronald G.; Mesaros, Clementina; Khanna, Richie; Blair, Ian A.
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Bile Acid Metabolism Mediates Cholesterol Homeostasis and Promotes Tumorigenesis in Clear Cell Renal Cell Carcinoma
err2024-02-28
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PREAI
errRiscal, Romain; Gardner, Sarah M.; Coffey, Nathan J.; Carens, Madeleine; Mesaros, Clementina; Xu, Jimmy P.; Xue, Yizheng; Davis, Leah; Demczyszyn, Sara; Vogt, Austin; Olia, Adam; Finan, Jennifer M.; Godfrey, Jason; Schultz, David C.; Blair, Ian A.; Keith, Brian; Marmorstein, Ronen; Skuli, Nicolas; Simon, M. Celeste
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Quantification of human mature frataxin protein expression in nonhuman primate hearts after gene therapy
err2023-10-27
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errOAAI
errRojsajjakul, Teerapat; Hordeaux, Juliette J.; Choudhury, Gourav R.; Hinderer, Christian J.; Mesaros, Clementina; Wilson, James M.; Blair, Ian A.
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Chimeric kinase ALK induces expression of NAMPT and selectively depends on this metabolic enzyme to sustain its own oncogenic function
errLEUKEMIA
IF13.4
err2023-09-29
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errOAAI
errZhang, Qian; Basappa, Johnvesly; Wang, Hong Y.; Nunez-Cruz, Selene; Lobello, Cosimo; Wang, Shengchun; Liu, Xiaobin; Chekol, Seble; Guo, Lili; Ziober, Amy; Nejati, Reza; Shestov, Alex; Feldman, Michael; Glickson, Jerry D.; Turner, Suzanne D.; Blair, Ian A.; Van Dang, Chi; Wasik, Mariusz A.
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Activation of the bile acid pathway promotes tumorigenesis in clear cell renal cell carcinoma
err2023-08-15
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PREAI
errRiscal, Romain; Gardner, Sarah; Carens, Madeleine; Mesaros, Clementina; Xu, Jimmy; Coffey, Nate; Davis, Leah; Vogt, Austin; Olia, Adam; Finan, Jennifer; Godfrey, Jason; Blair, Ian; Keith, Brian; Marmorstein, Ronen; Skuli, Nicolas; Simon, Celeste
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Liquid Chromatography-Mass Spectrometry Analysis of Frataxin Proteoforms in Whole Blood as Biomarkers of the Genetic Disease Friedreich's Ataxia
err2023-02-17
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errOAAI
errRojsajjakul, Teerapat; Wu, Linfeng; Grady, Connor B.; Hwang, Wei-Ting; Mesaros, Clementina; Lynch, David R.; Blair, Ian A.
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Ruxolitinib and exemestane for estrogen receptor positive, aromatase inhibitor resistant advanced breast cancer
err2022-11-11
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errOAAI
errMakhlin, Igor; McAndrew, Nicholas P.; Wileyto, E. Paul; Clark, Amy S.; Holmes, Robin; Bottalico, Lisa N.; Mesaros, Clementina; Blair, Ian A.; Jeschke, Grace R.; Fox, Kevin R.; Domchek, Susan M.; Matro, Jennifer M.; Bradbury, Angela R.; Feldman, Michael D.; Hexner, Elizabeth O.; Bromberg, Jacqueline F.; DeMichele, Angela
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Frataxin controls ketone body metabolism through regulation of OXCT1
err2022-07-26
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errOAAI
errDong, Yi N. A.; Mesaros, Clementina; Xu, Peining; Mercado-Ayon, Elizabeth; Halawani, Sarah; Ngaba, Lucie Vanessa; Warren, Nathan; Sleiman, Patrick; Rodden, Layne N.; Schadt, Kimberly A.; Blair, Ian A.; Lynch, David R.
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Simultaneous Quantification of Mitochondrial Mature Frataxin and Extra-Mitochondrial Frataxin Isoform E in Friedreich's Ataxia Blood
err2022-04-28
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errOAAI
errWang, Qingqing; Laboureur, Laurent; Weng, Liwei; Eskenazi, Nicolas M.; Hauser, Lauren A.; Mesaros, Clementina; Lynch, David R.; Blair, Ian A.
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DNA methylation in Friedreich ataxia silences expression of frataxin isoform E
err2022-03-23
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errOAAI
errRodden, Layne N.; Gilliam, Kaitlyn M.; Lam, Christina; Rojsajjakul, Teerapat; Mesaros, Clementina; Dionisi, Chiara; Pook, Mark; Pandolfo, Massimo; Lynch, David R.; Blair, Ian A.; Bidichandani, Sanjay, I
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Bcl-xL Enforces a Slow-Cycling State Necessary for Survival in the Nutrient-Deprived Microenvironment of Pancreatic Cancer
err2022-03-22
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errOAAI
errSela, Yogev; Li, Jinyang; Maheswaran, Shivahamy; Norgard, Robert; Yuan, Salina; Hubbi, Maimon; Doepner, Miriam; Xu, Jimmy P.; Ho, Elaine S.; Mesaros, Clementina; Sheehan, Colin; Croley, Grace; Muir, Alexander; Blair, Ian A.; Shalem, Ophir; Dang, Chi V.; Stanger, Ben Z.
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Cholesterol Auxotrophy as a Targetable Vulnerability in Clear Cell Renal Cell Carcinoma
err2021-07-08
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errOAAI
errRiscal, Romain; Bull, Caroline J.; Mesaros, Clementina; Finan, Jennifer M.; Carens, Madeleine; Ho, Elaine S.; Xu, Jimmy P.; Godfrey, Jason; Brennan, Paul; Johansson, Mattias; Purdue, Mark P.; Chanock, Stephen J.; Mariosa, Daniela; Timpson, Nicholas J.; Vincent, Emma E.; Keith, Brian; Blair, Ian A.; Skuli, Nicolas; Simon, M. Celeste
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Efficient Labeling of Native Human IgG by Proximity-Based Sortase-Mediated Isopeptide Ligation
err2021-05-24
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errOAAI
errYu, Wendy; Gillespie, Kevin P.; Chhay, Bonirath; Svensson, Anne-Sophie; Nygren, Per-Ake; Blair, Ian A.; Yu, Feifan; Tsourkas, Andrew
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Effects of systemic inflammation on relapse in early breast cancer
err2021-01-22
err27
errOAAI
errMcAndrew, Nicholas P.; Bottalico, Lisa; Mesaros, Clementina; Blair, Ian A.; Tsao, Patricia Y.; Rosado, Jennifer M.; Ganguly, Tapan; Song, Sarah J.; Gimotty, Phyllis A.; Mao, Jun J.; DeMichele, Angela
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Upregulation of Antioxidant Capacity and Nucleotide Precursor Availability Suffices for Oncogenic Transformation
err2021-01-01
err59
errOAAI
errZhang, Yang; Xu, Yi; Lu, Wenyun; Ghergurovich, Jonathan M.; Guo, Lili; Blair, Ian A.; Rabinowitz, Joshua D.; Yang, Xiaolu
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