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D

Duc Nguyen

Department of Anatomy and Cell Biology

23H-index
70Paper Count
2.3KCitation Count
Published Papers 29
Publication Date
Amelioration of Inflammation and Metabolic Blockage in GALC Deficient Mice After Enzyme Replacement Therapy via Extracellular Vesicles
err2025-07-17
err0
errOAAI
errDiego Zelada; Natalia Saldivia; Shayla Samano; Diann George; Kenvi Chaudhari; Duc Nguyen; Daniel Simchuk; Richard B Van Breemen; Maria Irene Givogri
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CRISPR-Cas9 Knock-In of T513M and G41S Mutations in the Murine β-Galactosyl-Ceramidase Gene Re-capitulates Early-Onset and Adult-Onset Forms of Krabbe Disease
err2022-05-10
err7
errOAAI
errRebiai, Rima; Rue, Emily; Zaldua, Steve; Nguyen, Duc; Scesa, Giuseppe; Jastrzebski, Martin; Foster, Robert; Wang, Bin; Jiang, Xuntian; Tai, Leon; Brady, Scott T.; van Breemen, Richard; Givogri, Maria I.; Sands, Mark S.; Bongarzone, Ernesto R.
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The Pathogenic Sphingolipid Psychosine is Secreted in Extracellular Vesicles in the Brain of a Mouse Model of Krabbe Disease
err2022-03-18
err6
errOAAI
errReiter, Cory R.; Rebiai, Rima; Kwak, Angelika; Marshall, Jeff; Wozniak, Dylan; Scesa, Giusepe; Nguyen, Duc; Rue, Emily; Pathmasiri, Chandimal; Pijewski, Robert; van Breemen, Richard; Cologna, Stephanie; Crocker, Stephen J.; Givogri, M. Irene; Bongarzone, Ernesto R.
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Modulating the Electron Affinity of Small Bipyridyl Molecules on Single Gold Nanoparticles for Plasmon-Driven Electron Transfer
err2021-09-30
err13
errOAAI
errSprague-Klein, Emily A.; Ho-Wu, Rosina; Duc Nguyen; Coste, Scott C.; Wu, Yue; McMahon, John J.; Seideman, Tamar; Schatz, George C.; Van Duyne, Richard P.
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Waning efficacy in a long-term AAV-mediated gene therapy study in the murine model of Krabbe disease
err2021-05-01
err19
errOAAI
errHeller, Gregory J.; Marshall, Michael S.; Issa, Yazan; Marshall, Jeffrey N.; Nguyen, Duc; Rue, Emily; Pathmasiri, Koralege C.; Domowicz, Miriam S.; van Breemen, Richard B.; Tai, Leon M.; Cologna, Stephanie M.; Crocker, Stephen J.; Givogri, Maria, I; Sands, Mark S.; Bongarzone, Ernesto R.
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Brainstem development requires galactosylceramidase and is critical for pathogenesis in a model of Krabbe disease
err2020-10-23
err25
errOAAI
errWeinstock, Nadav, I; Kreher, Conlan; Favret, Jacob; Nguyen, Duc; Bongarzone, Ernesto R.; Wrabetz, Lawrence; Feltri, M. Laura; Shin, Daesung
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Krabbe disease successfully treated via monotherapy of intrathecal gene therapy
err2020-08-10
err44
errOAAI
errBradbury, Allison M.; Bagel, Jessica H.; Duc Nguyen; Lykken, Erik A.; Salvador, Jill Pesayco; Jiang, Xuntian; Swain, Gary P.; Assenmacher, Charles A.; Hendricks, Ian J.; Miyadera, Keiko; Hess, Rebecka S.; Ostrager, Arielle; ODonnell, Patricia; Sands, Mark S.; Ory, Daniel S.; Shelton, G. Diane; Bongarzone, Ernesto R.; Gray, Steven J.; Vite, Charles H.
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Macrophages Expressing GALC Improve Peripheral Krabbe Disease by a Mechanism Independent of Cross-Correction
errNEURON
IF15
err2020-07-01
err41
errOAAI
errWeinstock, Nadav I.; Shin, Daesung; Dhimal, Narayan; Hong, Xinying; Irons, Eric E.; Silvestri, Nicholas J.; Reed, Chelsey B.; Duc Nguyen; Sampson, Oliver; Cheng, Yung-Chih; Lau, Joseph T. Y.; Bongarzone, Ernesto R.; Kofler, Julia; Escolar, Maria L.; Gelb, Michael H.; Wrabetz, Lawrence; Feltri, M. Laura
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Lead Optimization of Benzoxazolone Carboxamides as Orally Bioavailable and CNS Penetrant Acid Ceramidase Inhibitors
err2020-03-16
err14
errOAAI
errDi Martino, Simona; Tardia, Piero; Cilibrasi, Vincenzo; Caputo, Samantha; Mazzonna, Marco; Russo, Debora; Penna, Ilaria; Realini, Natalia; Margaroli, Natasha; Migliore, Marco; Pizzirani, Daniela; Ottonello, Giuliana; Bertozzi, Sine Mandrup; Armirotti, Andrea; Duc Nguyen; Sun, Ying; Bongarzone, Ernesto R.; Lansbury, Peter; Liu, Min; Skerlj, Renato; Scarpelli, Rita
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Investigation of Cobalt Phthalocyanine at the Solid/Liquid Interface by Electrochemical Tip-Enhanced Raman Spectroscopy
err2019-04-01
err43
PREAI
errJiang, Song; Chen, Zhu; Chen, Xu; Duc Nguyen; Mattei, Michael; Goubert, Guillaume; Van Duyne, Richard P.
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Imaging of Carbon Nanotube Electronic States Polarized by the Field of an Excited Quantum Dot
err2019-01-29
err9
PREAI
errDuc Nguyen; Wallum, Alison; Nguyen, Huy A.; Nguyen, Nhan T.; Lyding, Joseph W.; Gruebele, Martin
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Probing Molecular-Scale Catalytic Interactions between Oxygen and Cobalt Phthalocyanine Using Tip-Enhanced Raman Spectroscopy
err2018-04-23
err75
PREAI
errDuc Nguyen; Kang, Gyeongwon; Chiang, Naihao; Chen, Xu; Seideman, Tamar; Hersam, Mark C.; Schatz, George C.; Van Duyne, Richard P.
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Long-Term Improvement of Neurological Signs and Metabolic Dysfunction in a Mouse Model of Krabbe's Disease after Global Gene Therapy
err2018-03-01
err46
errOAAI
errMarshall, Michael S.; Issa, Yazan; Jakubauskas, Benas; Stoskute, Monika; Elackattu, Vince; Marshall, Jeffrey N.; Bogue, Wil; Duc Nguyen; Hauck, Zane; Rue, Emily; Karumuthil-Melethil, Subha; Zaric, Violeta; Bosland, Maarten; van Breemen, Richard B.; Givogri, Maria, I; Gray, Steven J.; Crocker, Stephen J.; Bongarzone, Ernesto R.
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Orientation-dependent imaging of electronically excited quantum dots
err2018-02-07
err19
errOAAI
errDuc Nguyen; Goings, Joshua J.; Nguyen, Huy A.; Lyding, Joseph; Li, Xiaosong; Gruebele, Martin
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Galc ablation in Schwann cells produces a demyelinating peripheral neuropathy characterized by psychosine formation but lacking globoid cells
err2018-02-01
err0
PREAI
errWeinstock, Nadav I.; Shin, Daesung; Bongarzone, Ernesto R.; Nguyen, Duc; Silvestri, Nicholas J.; Wrabetz, Lawrence; Feltri, M. Laura
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Imaging and Manipulating Energy Transfer Among Quantum Dots at Individual Dot Resolution
err2017-05-30
err19
PREAI
errDuc Nguyen; Nguyen, Huy A.; Lyding, Joseph W.; Gruebele, Martin
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Extensional Step Strain Rate Experiments on an Entangled Polymer Solution
err2016-12-29
err7
PREAI
errBhattacharjee, P. K.; Nguyen, D. A.; Masubuchi, Y.; Sridhar, T.
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Imaging Excited Orbitals of Quantum Dots: Experiment and Electronic Structure Theory
err2015-11-13
err24
PREAI
errNienhaus, Lea; Goings, Joshua J.; Duc Nguyen; Wieghold, Sarah; Lyding, Joseph W.; Li, Xiaosong; Gruebele, Martin
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