未登录 Imbalanced neurogenesis and gliogenesis in the developing neocortex of mice lacking the proteoglycan Tsukushi 小鼠缺乏蛋白聚糖Tsukushi时,新皮质发育中神经发生和神经胶质生成的失衡 Quaresima, Sabrina; Licursi, Valerio; Ohkubo, Tenta; Istiaq, Arif; Nakashima, Hideyuki; Miranda, Elena; Cacci, Emanuele; Jono, Hirofumi; Nakashima, Kinichi; Ohta, Kunimasa; Lupo, Giuseppe 分享 收藏
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An Inducible Neural Stem Progenitor Cell Model for Testing Therapeutic Interventions Against Neurodegeneration FENIB Giustini, Alessandro; Maiocchi, Alice; Serangeli, Ilaria; Pedrini, Martina; Quintiliani, Anna; Sabato, Valentina; Bonato, Francesca; Seneci, Pierfausto; Lupo, Giuseppe; Passarella, Daniele; Miranda, Elena 分享 收藏
Targeting the Antifungal Activity of Carbon Dots against Candida albicans Biofilm Formation by Tailoring Their Surface Functional Groups Sturabotti, Elisa; Camilli, Alessandro; Georgian Moldoveanu, Vyali; Bonincontro, Graziana; Simonetti, Giovanna; Valletta, Alessio; Serangeli, Ilaria; Miranda, Elena; Amato, Francesco; Giacomo Marrani, Andrea; Migneco, Luisa Maria; Sennato, Simona; Simonis, Beatrice; Vetica, Fabrizio; Leonelli, Francesca 分享 收藏
Glucocorticoids rescue cell surface trafficking of R451C Neuroligin3 and enhance synapse formation 糖皮质激素可挽救R451C神经配体3的细胞表面运输并增强突触形成 Diamanti, Tamara; Trobiani, Laura; Mautone, Lorenza; Serafini, Federica; Gioia, Roberta; Ferrucci, Laura; Lauro, Clotilde; Bianchi, Sara; Perfetto, Camilla; Guglielmo, Stefano; Sollazzo, Raimondo; Giorda, Ezio; Setini, Andrea; Ragozzino, Davide; Miranda, Elena; Comoletti, Davide; Di Angelantonio, Silvia; Cacci, Emanuele; De Jaco, Antonella 分享 收藏
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Polymerogenic neuroserpin causes mitochondrial alterations and activates NFκB but not the UPR in a neuronal model of neurodegeneration FENIB D'Acunto, E.; Gianfrancesco, L.; Serangeli, I; D'Orsi, M.; Sabato, V; Guadagno, N. A.; Bhosale, G.; Caristi, S.; Failla, A., V; De Jaco, A.; Cacci, E.; Duchen, M. R.; Lupo, G.; Galliciotti, G.; Miranda, E. 分享 收藏
Inducible localized delivery of an anti-PD-1 scFv enhances anti-tumor activity of ROR1 CAR-T cells in TNBC Harrasser, Micaela; Gohil, Satyen Harish; Lau, Hiu; Della Peruta, Marco; Muczynski, Vincent; Patel, Dominic; Miranda, Elena; Grigoriadis, Kristiana; Grigoriadis, Anita; Granger, David; Evans, Rachel; Nathwani, Amit Chunilal 分享 收藏
Association between alpha1 antitrypsin (AAT) circulating polymers (CP) and lung and liver disease in patients with AAT deficiency (AATD) Nunez, Alexa; Belmonte, Irene; Miranda, Elena; Loeb, Eduardo; Barrecheguren, Miriam; Farago, Georgina; Rodriguez, Esther; Rodriguez-Frias, Francisco; Miravitlles, Marc; Esquinas, Cristina 分享 收藏
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Neuroserpin Inclusion Bodies in a FENIB Yeast Model Vapore, Valentina; Mazzaglia, Corrado; Sibilia, Diego; Del Vecchio, Mara; Fruhmann, Gernot; Valenti, Marta; Miranda, Elena; Rinaldi, Teresa; Winderickx, Joris; Mazzoni, Cristina 分享 收藏
G392E neuroserpin causing the dementia FENIB is secreted from cells but is not synaptotoxic Ingwersen, Thies; Linnenberg, Christian; D'Acunto, Emanuela; Temori, Shabnam; Paolucci, Irene; Wasilewski, David; Mohammadi, Behnam; Kirchmair, Johannes; Glen, Robert C.; Miranda, Elena; Glatzel, Markus; Galliciotti, Giovanna 分享 收藏
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The structural basis for Z α1-antitrypsin polymerization in the liver Faull, Sarah, V; Elliston, Emma L. K.; Gooptu, Bibek; Jagger, Alistair M.; Aldobiyan, Ibrahim; Redzej, Adam; Badaoui, Magd; Heyer-Chauhan, Nina; Rashid, S. Tamir; Reynolds, Gary M.; Adams, David H.; Miranda, Elena; Orlova, Elena, V; Irving, James A.; Lomas, David A. 分享 收藏
Intrahepatic heteropolymerization of M and Z alpha-1-antitrypsin Laffranchi, Mattia; Elliston, Emma L. K.; Miranda, Elena; Perez, Juan; Ronzoni, Riccardo; Jagger, Alistair M.; Heyer-Chauhan, Nina; Brantly, Mark L.; Fra, Annamaria; Lomas, David A.; Irving, James A. 分享 收藏
Embelin as Lead Compound for New Neuroserpin Polymerization Inhibitors Embelin作为新型神经丝氨酸蛋白酶抑制剂的先导化合物 Visentin, Cristina; Musso, Loana; Broggini, Luca; Bonato, Francesca; Russo, Rosaria; Moriconi, Claudia; Bolognesi, Martino; Miranda, Elena; Dallavalle, Sabrina; Passarella, Daniele; Ricagno, Stefano 分享 收藏
UPR activation specifically modulates glutamate neurotransmission in the cerebellum of a mouse model of autism Trobiani, L.; Favaloro, F. L.; Di Castro, M. A.; Di Mattia, M.; Cariello, M.; Miranda, E.; Canterini, S.; De Stefano, M. E.; Comoletti, D.; Limatola, C.; De Jaco, A. 分享 收藏
α1-Antitrypsin Polymerizes in Alveolar Macrophages of Smokers With and Without α1-Antitrypsin Deficiency Bazzan, Erica; Tine, Mariaenrica; Biondini, Davide; Benetti, Riccardo; Baraldo, Simonetta; Turato, Graziella; Fagiuoli, Stefano; Sonzogni, Aurelio; Rigobello, Chiara; Rea, Federico; Calabrese, Fiorella; Foschino-Barbaro, Maria Pia; Miranda, Elena; Lomas, David A.; Saetta, Marina; Cosio, Manuel G. 分享 收藏
Alpha-1 antitrypsin (AAT) polymerization in alveolar macrophages of AAT deficient individuals and in smokers Bazzan, Erica; Tine, Mariaenrica; Benetti, Riccardo; Miranda, Elena; Biondini, Davide; Turato, Graziella; Sgambato, Manuel A.; Rea, Federico; Calabrese, Fiorella; Baraldo, Simonetta; Lomas, David A.; Cosio, Manuel G.; Saetta, Marina; Rigobello, Chiara 分享 收藏