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J

James D. Berry

mass general brigham

55H指数
423论文数
1.3W被引数
收录论文 84
发表时间
Functional Activity of TDP-43: A Direct Biomarker for ALSTDP-43的功能活性:肌萎缩侧索硬化症的直接生物标志物
err2026-08-26
err0
errOAAI
errKirti Shila Sonkar; Vito Levi D’Ancona; Jade Cramp; Hannah Shilling; Ellie Giles; Tyler Howell-Bray; Becky Fillingham; Merit E. Cudkowicz; Avindra Nath; Jeffrey D. Rothstein; Robert Bowser; Barbara Borroni; James D. Berry; Ghazaleh Sadri-Vakili; Emanuele Buratti; Ian P. Thrippleton
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What can vowel acoustics reveal about the communicative participation of people living with ALS?
err2025-12-01
err0
PREAI
errHaenssler, Abigail E.; Okada, June; Eshghi, Marziye; Clark, Alison; Iyer, Amrita; Richburg, Brian D.; Cavanaugh, Robert; Onnela, Jukka-Pekka; Burke, Katherine M.; Berry, James D.; Green, Jordan R.; Connaghan, Kathryn P.
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Pridopidine treatment in ALS: subgroup analyses from the HEALEY ALS Platform trial普利多匹定治疗ALS: 来自HEALEY ALS平台试验的亚组分析
err2025-12-01
err0
PREAI
errGeva, Michal; Goldberg, Y. Paul; Leitner, Melanie L.; Cruz-Herranz, Andres; Hand, Randal; Chen, Kelly; Gershoni Emek, Noga; Tan, Andrew M.; Paganoni, Sabrina; Berry, James D.; Macklin, Eric A.; Shefner, Jeremy M.; Cudkowicz, Merit E.; Hayden, Michael R.
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Participation in U.S.-Based ALS Clinical Trials by Sex and Race按性别和种族划分的参与美国本土ALS临床研究的比例
err2025-11-05
err0
errOAAI
errMark P. Levine; Sun Young Chung; Kellen H. Quigg; Judith Carey; Suma Babu; Sabrina Paganoni; James D. Berry
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Autoimmune response to C9orf72 protein in amyotrophic lateral sclerosis肌萎缩侧索硬化对C9orf72蛋白的自身免疫反应
err2025-11-01
err0
PREAI
errJohansson, Emil; Michaelis, Tanner; Lindestam Arlehamn, Cecilia S.; Frazier, April; Tran, Kim N.; Berry, James; Cudkowicz, Merit; Goyal, Namita; Fournier, Christina; Kwan, Justin; Crook, Judy; Sidney, John; Sulzer, Dave L.; Sette, Alessandro
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Design considerations for C9orf72 disease prevention trialsC9orf72疾病预防试验的设计考虑
errBRAIN
IF11.7
err2025-10-01
err0
errOAAI
errBenatar, Michael; Staffaroni, Adam M.; Wuu, Joanne; McDermott, Michael P.; Quintana, Melanie; Swidler, Jean; Andersen, Gail; Huey, Edward D.; Turner, Martin R.; Macklin, Eric A.; Berry, James D.; McMillan, Corey T.; Gendron, Tania; Onyike, Chiadi; Rosen, Howard; Heuer, Hilary W.; Grignon, Anne-Laure; Dave, Kuldip D.; Balas, Calaneet; Gleixner, Amanda; Satlin, Andrew; Dunn, Billy; Dacks, Penny; Boxer, Adam L.
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Real-World Clinical Experience With Sodium Phenylbutyrate and Taurursodiol at a Single Amyotrophic Lateral Sclerosis Center in the United States美国一家肌萎缩侧索硬化症中心中钠苯丁酸盐和Taurursodiol的实际临床应用经验
err2025-09-18
err0
errOAAI
errNarghes Calcagno; Erica Scirocco; Erin Clampffer; Grace Addy; Sean Morgan; Neel Parikh; Dylan V. Neel; Jennifer Scalia; Rebekah Young; Matteo Locatelli; deMauri S. Mackie; James D. Berry; Sabrina Paganoni
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Skeletal Muscle Biomarkers of Amyotrophic Lateral Sclerosis: A Large-Scale, Multi-Cohort Proteomic Study肌萎缩侧索硬化症的骨骼肌生物标志物:一项大规模、多队列的蛋白质组学研究
err2025-09-01
err0
PREAI
errDergai, Oleksandr; Wuu, Joanne; Koziczak-Holbro, Magdalena; Malaspina, Andrea; Granit, Volkan; Hernandez, Jessica P.; Cooley, Anne; Sachdev, Ruchika; Yu, Lili; Bidinosti, Michael; Flotte, Ludivine; Nash, Mark; Jennings, Lori L.; Berry, James D.; Bruijn, Lucie I.; Brachat, Sophie; Benatar, Michael
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Multicenter Expanded Access Protocol for Research Through Access to Trehalose in People With Amyotrophic Lateral Sclerosis多中心扩展性访问方案:通过向肌萎缩侧索硬化症患者提供海藻糖进行研究
err2025-08-26
err0
errOAAI
errBrooke Krivickas; Erica Scirocco; Elisa Giacomelli; Saloni Sharma; Molly Benson; Mackenzie Keegan; Jennifer Kulesa-Kelley; Lori B. Chibnik; Gabriella Casagrande; Lindsay Heyd; Marianne Chase; Kristin Drake; Silpa Mohapatra; Jennifer Linn Hagar; Meredith Gibbons Hasenoehrl; Derek Dagostino; Alexander V. Sherman; Alex Leite; Hong Yu; Jesse Rosenthal; Timothy Miller; Alexandra McCaffrey; Kelly Gwathmey; Eduardo Locatelli; Elham Bayat; Daragh Heitzman; Eufrosina Young; Namita A. Goyal; Jackie Whitesell; Kevin Felice; Hristelina Ilieva; Andrea Swenson; David Walk; Gustavo Alameda; Laura Foster; Courtney E. McIlduff; Alison Walsh; Lindsay Zilliox; Senda Ajroud-Driss; Cynthia Bodkin; Jonathan Katz; Shafeeq Ladha; Michael Rivner; Laura Rosow; Paul Twydell; Warren Wasiewski; Suma Babu; James D. Berry; Sabrina Paganoni
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Variability across versions of the self-administered ALSFRS-R: a review and call for harmonization自我管理版ALSFRS-R不同版本间的变异性:一项综述与标准化呼吁
err2025-06-28
err0
PREAI
errMatti D. Allen; Ruben P. A. Van eijk; Liam Knox; Jill Carlton; Esther Hobson; Christopher J. Mcdermott; Deirdre Murray; James Berry; Thomas Meyer; Angela Genge
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Listener effort measures clinically meaningful change of dysarthria in amyotrophic lateral sclerosis听者努力测量肌萎缩侧索硬化症中构音障碍的临床意义变化
err2025-06-12
err0
errOAAI
errIndu Navar Bingham; Raquel Norel; Esteban G Roitberg; Julián Peller; Marcos A Trevisan; Carla Agurto; Michele Merler; Diego E Shalom; Felipe Aguirre; Iair Embon; Alan Taitz; Donna Harris; Amy Wright; Katie Seaver; Stacey Sullivan; Jordan R Green; Lyle W Ostrow; Ernest Fraenkel; James D Berry
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Network analysis of the cerebrospinal fluid proteome reveals shared and unique differences between sporadic and familial forms of amyotrophic lateral sclerosis脑脊液蛋白质组网络分析揭示了散发性与家族性肌萎缩侧索硬化症之间的共享及独特差异
err2025-05-15
err0
errOAAI
errTrautwig, Adam N.; Fox, Edward J.; Dammer, Eric B.; Shantaraman, Anantharaman; Ping, Lingyan; Duong, Duc M.; Watson, Caroline M.; Wu, Fang; Asress, Seneshaw; Guo, Qi; Levey, Allan I.; Lah, James J.; Verde, Federico; Doretti, Alberto; Ratti, Antonia; Ticozzi, Nicola; Ly, Cindy V.; Miller, Timothy M.; Garret, Mark A.; Berry, James D.; Thomas, Eleanor V.; Fournier, Christina N.; McEachin, Zachary T.; Seyfried, Nicholas T.; Glass, Jonathan D.
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A Preliminary Investigation of Acoustic Features for Remote Monitoring of Respiration in ALSALS患者远程呼吸监测的声学特征初步研究
err2025-05-14
err0
PREAI
errKathryn P. Connaghan; Marziye Eshghi; Abigail E. Haenssler; Jordan R. Green; Joycelyn Wang; Zoe Scheier; Mackenzie Keegan; Alison Clark; Jukka-Pekka Onnela; Katherine M. Burke; James D. Berry
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Clinical assessment and interpretation of dysarthria in ALS using attention based deep learning AI models基于注意力机制的深度学习AI模型在ALS中对于构音障碍的临床评估与解读
err2025-05-08
err0
errOAAI
errMerler, Michele; Agurto, Carla; Peller, Julian; Roitberg, Esteban; Taitz, Alan; Trevisan, Marcos A.; Navar, Indu; Berry, James D.; Ostrow, Lyle W.; Cecchi, Guillermo A.; Norel, Raquel
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Clinician Perspectives Highlight the Need for Early Dyadic Coping Skills for People Living With Amyotrophic Lateral Sclerosis
err2025-03-01
err0
PREAI
errRush, Christina L.; Lyons, Chris; Gittle, Jenna; Seward, Morgan; Scalia, Jennifer; Ho, Doreen; Babu, Suma; Garret, Mark A.; Brizzi, Kate; Berry, James D.; Fava, Maurizio; Lindenberger, Elizabeth; Vranceanu, Ana-Maria; Healey, Sean M.
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Efficacy and Safety of Zilucoplan in Amyotrophic Lateral Sclerosis, A Randomized Clinical TrialZilucoplan治疗肌萎缩侧索硬化症的疗效与安全性:一项随机临床试验
err2025-02-17
err3
errOAAI
errPaganoni, Sabrina; Fournier, Christina N.; Macklin, Eric A.; Chibnik, Lori B.; Quintana, Melanie; Saville, Benjamin R.; Detry, Michelle A.; Vestrucci, Matteo; Marion, Joe; Mcglothlin, Anna; Ajroud-Driss, Senda; Chase, Marianne; Pothier, Lindsay; Harkey, Brittney A.; Yu, Hong; Sherman, Alexander V.; Shefner, Jeremy M.; Hall, Meghan; Kittle, Gale; Berry, James D.; Babu, Suma; Andrews, Jinsy; Dagostino, Derek; Tustison, Eric; Giacomelli, Elisa; Scirocco, Erica; Alameda, Gustavo; Locatelli, Eduardo; Ho, Doreen; Quick, Adam; Katz, Jonathan; Heitzman, Daragh; Appel, Stanley H.; Shroff, Sheetal; Felice, Kevin; Maragakis, Nicholas J.; Simmons, Zachary; Miller, Timothy M.; Olney, Nicholas; Weiss, Michael D.; Goutman, Stephen A.; Fernandes, Joseph Americo; Jawdat, Omar; Owegi, Margaret Ayo; Foster, Laura A.; Vu, Tuan; Ilieva, Hristelina; Newman, Daniel S.; Arcila-Londono, Ximena; Jackson, Carlayne E.; Ladha, Shafeeq; Heiman-Patterson, Terry; Caress, James B.; Swenson, Andrea; Peltier, Amanda; Lewis, Richard; Fee, Dominic; Elliott, Matthew; Kasarskis, Edward J.; Elman, Lauren; Rosenfeld, Jeffrey; Walk, David; Mcilduff, Courtney; Twydell, Paul; Young, Eufrosina; Johnson, Kristin; Rezania, Kourosh; Goyal, Namita A.; Cohen, Jeffrey A.; Benatar, Michael; Jones, Vovanti; Glass, Jonathan; Shah, Jaimin; Beydoun, Said R.; Wymer, James P.; Zilliox, Lindsay; Nayar, Shakti; Pattee, Gary L.; Martinez-Thompson, Jennifer; Harvey, Brittany; Patel, Shital; Mahoney, Paul; Duda, Petra W.; Cudkowicz, Merit E.
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Free-living monitoring of ALS progression in upper limbs using wearable accelerometers
err2024-12-21
err0
errOAAI
errStraczkiewicz, Marcin; Burke, Katherine M.; Calcagno, Narghes; Premasiri, Alan; Vieira, Fernando G.; Onnela, Jukka-Pekka; Berry, James D.
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