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Spatial Profiling of Elements through Matrix-Assisted Laser Desorption Ionization Mass Spectrometry Imaging 基质辅助激光解吸电离质谱成像技术对元素的时空分布表征 Stopka, Sylwia A.; Bodineau, Clement; Baquer, Gerard; Lin, Jia-Ren; Hossain, Md Amin; Martinez, Camilla J.; Regan, Michael S.; Ruiz, Daniela; Fletcher, Stecia-Marie; Pourquie, Olivier; Lutsenko, Svetlana; Payne, Connor N.; Agar, Jeffrey N.; Mazitschek, Ralph; Mcdannold, Nathan J.; Sorger, Peter K.; Santagata, Sandro; Agar, Nathalie Y. R. 分享 收藏
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Elesclomol-copper therapy improves neurodevelopment in two children with Menkes disease Elesclomol-铜疗法改善了两位Menkes病患儿的神经发育。 Godoy-Molina, Elena; Serrano, Natalia L.; Jimenez-Gonzalez, Aquilina; Villaronga, Miquel; Perez-Bryan, Rosa M. Marques; Varela-Fernandez, Ruben; Lotz-Esquivel, Stephanie; Tunon, Alba Hevia; Trivedi, Prachi P.; Horn, Nina; Standing, Joseph F.; Mangas-Sanjuan, Victor; Capdevila, Merce; Mateos, Aurora; Broun, Denis; Lutsenko, Svetlana; Medina-Rivera, Ines; Artuch, Rafael; Jou, Cristina; Roldan, Monica; Arango-Sancho, Pedro; Saez-Villafane, Monica; Ortiz-de-Urbina, Juan J.; Pieras-Lopez, Angela; Duero, Marta; Farre, Rosa; Pijuan, Jordi; Hoenicka, Janet; Sacchettini, James C.; Petris, Michael J.; Gohil, Vishal M.; Palau, Francesc 分享 收藏
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Copper impairs the intestinal barrier integrity in Wilson disease Fontes, Adriana; Pierson, Hannah; Bierla, Joanna B.; Eberhagen, Carola; Kinschel, Jennifer; Akdogan, Banu; Rieder, Tamara; Sailer, Judith; Reinold, Quirin; Cielecka-Kuszyk, Joanna; Szymanska, Sylwia; Neff, Frauke; Steiger, Katja; Seelbach, Olga; Zibert, Andree; Schmidt, Hartmut H.; Hauck, Stefanie M.; von Toerne, Christine; Michalke, Bernhard; Semrau, Jeremy D.; DiSpirito, Ana M.; Ramalho-Santo, Joao; Kroemer, Guido; Polishchuk, Roman; Azul, Anabela Marisa; Dispirito, Alan; Socha, Piotr; Lutsenko, Svetlana; Zischka, Hans 分享 收藏
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The role of intestine in metabolic dysregulation in murine Wilson disease Sarode, Gaurav V.; Mazi, Tagreed A.; Neier, Kari; Shibata, Noreene M.; Jospin, Guillaume; Harder, Nathaniel H. O.; Caceres, Amanda; Heffern, Marie C.; Sharma, Ashok K.; More, Shyam K.; Dave, Maneesh; Schroeder, Shannon M.; Wang, Li; Lasalle, Janine M.; Lutsenko, Svetlana; Medici, Valentina 分享 收藏
α-lipoic acid ameliorates consequences of copper overload by up-regulating selenoproteins and decreasing redox misbalance Α-硫辛酸通过上调硒蛋白和减少氧化还原失衡来改善铜过载的后果 Kabin, Ekaterina; Dong, Yixuan; Roy, Shubhrajit; Smirnova, Julia; Smith, Joshua W.; Ralle, Martina; Summers, Kelly; Yang, Haojun; Dev, Som; Wang, Yu; Devenney, Benjamin; Cole, Robert N.; Palumaa, Peep; Lutsenko, Svetlana 分享 收藏
A Century of Progress on Wilson Disease and the Enduring Challenges of Genetics, Diagnosis, and Treatment 威尔逊病的一个世纪的进展和遗传学，诊断和治疗的持久挑战 Penning, Louis C.; Berenguer, Marina; Czlonkowska, Anna; Double, Kay L.; Dusek, Petr; Espinos, Carmen; Lutsenko, Svetlana; Medici, Valentina; Papenthin, Wiebke; Stremmel, Wolfgang; Willemse, Jose; Weiskirchen, Ralf 分享 收藏
Atp7b-dependent choroid plexus dysfunction Causes transient copper deficit and metabolic changes in the developing mouse brain Washington-Hughes, Clorissa L.; Roy, Shubhrajit; Seneviratne, Herana Kamal; Karuppagounder, Senthilkumar S.; Morel, Yulemni; Jones, Jace W.; Zak, Alex; Xiao, Tong; Boronina, Tatiana N.; Cole, Robert N.; Bumpus, Namandje N.; Chang, Christopher J.; Dawson, Ted M.; Lutsenko, Svetlana 分享 收藏
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Oxysterol misbalance critically contributes to Wilson disease pathogenesis Dev, Som; Muchenditsi, Abigael; Gottlieb, Aline; Deme, Pragney; Murphy, Sean; Gabrielson, Kathleen L.; Dong, Yixuan; Hughes, Robert; Haughey, Norman J.; Hamilton, James P.; Lutsenko, Svetlana 分享 收藏
Connecting copper and cancer: from transition metal signalling to metalloplasia 连接铜和癌症: 从过渡金属信号到金属增生 Ge, Eva J.; Bush, Ashley I.; Casini, Angela; Cobine, Paul A.; Cross, Justin R.; DeNicola, Gina M.; Dou, Q. Ping; Franz, Katherine J.; Gohil, Vishal M.; Gupta, Sanjeev; Kaler, Stephen G.; Lutsenko, Svetlana; Mittal, Vivek; Petris, Michael J.; Polishchuk, Roman; Ralle, Martina; Schilsky, Michael L.; Tonks, Nicholas K.; Vahdat, Linda T.; Van Aelst, Linda; Xi, Dan; Yuan, Peng; Brady, Donita C.; Chang, Christopher J. 分享 收藏
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Systemic deletion of Atp7b modifies the hepatocytes' response to copper overload in the mouse models of Wilson disease Muchenditsi, Abigael; Talbot, C. Conover, Jr.; Gottlieb, Aline; Yang, Haojun; Kang, Byunghak; Boronina, Tatiana; Cole, Robert; Wang, Li; Dev, Som; Hamilton, James P.; Lutsenko, Svetlana 分享 收藏
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